A châng chuan doctor-te chuan kan hriat ngai loh damdawi bik tak tak an pe ṭhin. Triheptanoin hi chutiang damdawi tui bik pakhat a ni. Mi zawng zawng hnena pek a ni tlangpui lo. A bik takin LC-FAOD, a nih loh leh Long-chain fatty acid oxidation disorders an tih, genetic condition hmuh tur awm lo tak nei tan hman a ni. Chuvângin, i doctor-in he damdawi hi nangmah emaw, i fate emaw tân a pe a nih chuan, he thuziak hian a chungchânga zawhnate, ngaihtuahna, leh hlauhnate chu awlsam taka hriatthiam nân nasa takin a ṭanpui ang che.
He damdawi hi eng nge thleng tak tak?
A awlsam zawngin han sawi ila. Kan taksa cell te hian hna thawk turin chakna an mamawh a. He chakna siam chhuah nan hian kan taksa hian kan ei leh in atanga carbohydrates leh thau te a hmang ber a ni. Mahse, LC-FAOD tih hming pu genetic condition neiah chuan taksain long-chain fatty acids chu a ti chhe thei lo va, chakna a siam thei lo. An genes chak lohna a ni.
Hei hi Triheptanoin a lo lut a, damdawi aiin thau supplement a ni zawk. Thau chi khat bik a awm a, chu chu taksain awlsam takin a hip lut thei a, chakna ah a chantir thei a ni. Phên dangin sawi ila, he damdawi hian LC-FAOD avanga taksain a hmuh theih loh chakna leh calorie chu kawng dang hmangin a pe a ni.
He damdawi hi i ei hmaa i doctor hnena i hrilh tur thilte
He damdawi hi i pek hmain i doctor tan i hriselna chanchin kimchang a hriat a pawimawh hle. A hnuaia thil awmte hi hrilh ngei ang che:
| Nangmah nghawngtu dinhmun | Engvangin nge doctor hnenah i hrilh ang? |
|---|---|
| Feeding tube hmanga siam a ni | He damdawi hi feeding tube hmanga pek a ngai mai thei a, chuvangin doctor chuan hei hi a hriat chian a ngai a ni. |
| Pancreatic natna a ni | Pancreatic natna vei te hian he damdawi hi an ei dan a inang lo thei a, chuvangin hriattir hmasak a pawimawh hle. |
| Allergy chi hrang hrang (Allergies) . | He damdawi chauh ni lo, damdawi dang, ei tur, emaw, preservative dang emaw allergy i neih chuan i doctor hriattir a pawimawh hle. |
| Naupai emaw, naupai tum emaw | Naupai laia damdawi eng pawh hi damdawi lam thurawn chauh ei tur a ni. Chuvangin i dinhmun chu doctor hnenah hrilh rawh. |
| Naute hnute pek | Damdawi i ei chu i naute hnenah hnute hnute hmangin a kal thei a ni. Chuvangin nu hnute petu i nih chuan i doctor hnenah hrilh ngei ang che. |
He damdawi hi engtin nge ka hman ang?
He damdawi hman dan dik tak hriat a pawimawh hle.
- Doctor thupek zawm rawh: Damdawi hi a pek ang chiah chiah, a pek zat leh a hun takah ei tur a ni. I duh angin dosage hi thlak ngai suh.
- Chaw ei ruala ei: He damdawi hi chaw ei rual emaw, chaw ei zawhah emaw ei fo tur a ni.
- Instructions chhiar rawh: Damdawi nena rawn kal INSTRUCTIONS FOR USE chu uluk takin chhiar rawh. Thil chiang lo a awm a nih chuan i doctor hnenah chiang zawka hrilh turin zak suh.
- Naupang hnena pek a nih chuan: He damdawi hi nausen piang thar tan pawh special case thenkhatah pek theih a ni. Mahse, hemi chungchangah hian i fa doctor chauhin thutlukna a siam thei a ni. Chuvangin i doctor-in a hrilh ang che.
Pawimawh: He damdawi hi i tan chauh pek a ni. Nangmah ang bawka natna lanchhuahna nei pawh ni se, eng chhan vangin midang hnenah share suh.
Damdawi ka ei tam lutuk chuan engtin nge ni ang?
Dose pek aia tam i ei nia i hriat chuan, tihsual emaw, accident emaw pawh nise, Colombo National Hospital-a National Poisons Information Center-ah phone nghal rawh. Chutiang a nih loh chuan hun khawhral lo la, damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal mai rawh.
Damdawi dose i ei loh chuan engtin nge i tih ang?
Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Dose khatah darkar 3 atanga darkar 4 chhung dah tur a ni. Mahse, ni khat chhunga full dose ei hun a awm loh chuan (entir nan, a tuk hun a nih dawn chuan) missed dose chu skip la, a hun pangngaiah dose dang ei leh rawh. Dose hloh tawh chu vawi khatah vawi hnih ei ngai suh.
Damdawi ei avanga side effect awm thei
Damdawi dang ang bawkin triheptanoin hian mi thenkhatah side effect a nei thei a ni. Chûng zînga ṭhenkhat chu a pawi hle a, ṭhenkhat erawh chu a nêm hle thung.
| Side effect awm dan (nature) a ni | Natna |
|---|---|
| Side effects te chu doctor hnenah report nghal tur a ni | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui, lei emaw kawr emaw a hring, thawk harsa. |
| Side effects te chu a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hriattir tur a ni | |
| Pum natna | Pum natna emaw, natna emaw. |
| Kawthalo | Flatulence a awm. |
| Luak chhuak leh Luak chhuak | Luak chhuak emaw, luak chhuak emaw ang maia hriatna. |
He list-ah hian side effect zawng zawng a tel lo. Thil danglam tak i tawn chuan i doctor nen sawiho rawh.
Damdawi dahkhawm leh paih dan
Khawiah nge ka dah ang?
- Naupang leh ran vulhte hmuh theih lohna hmunah him takin dah rawh .
- Room temperature (20 leh 25 degree Celsius inkar) ah dah tur a ni. Freeze ngai suh.
- Damdawi chu a rawn lut original bottle-ah dah la.
- Damdawi la awm zawng zawng chu bottle hawn atanga thla 9 hnuah emaw, expiry date (a hmasa ber emaw) hnuah paih vek tur a ni.
Engtin nge damdawi \ul lo i tihbo theih ang?
Damdawi expired emaw hman loh emaw chu bawlhhlawh bawmah paih mai mai suh.
- A tha ber chu damdawi take-back program-a hlan hi a ni. Chutiang hmun chungchang chu i awmna hmuna damdawi dawr emaw, damdawi in emaw i zawt thei ang.
- Chutiang program i hmuh loh chuan damdawi chu bottle atang chuan la chhuakin, tea hnah hman tawh, coffee ground emaw, lei emaw ang chi thil nen uluk takin pawlh la, plastic bag nghet taka khar chhungah dah la, bawlhhlawh bawmah paih rawh.
- I paih chhuah dan tur i hriat chian loh chuan doctor zawt rawh.
Take-Home Thuchah a ni
- Triheptanoin hi special nutritional supplement a ni a, natna hlauhawm tak LC-FAOD tih hming pu tan a ni.
- He damdawi hi doctor-in a tih angin ei fo la, chaw ei rualin ei thin ang che.
- Damdawi dang i ei leh damdawi dang i neih apiang chu i doctor hnenah hrilh rawh.
- Allergy symptoms i neih chuan vun rawng leh vun hring te i neih chuan doctor lam pan nghal rawh.
- He damdawi hi i tan chauh a ni. Midang hnenah share ngai suh.
- He damdawi chungchangah hian harsatna, zawhna, rinhlelhna i neih chuan, a chungchang sawipui tur tha ber leh inhmeh ber chu i doctor hi a ni.











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