I mit leh vun var te chu a sen deuh deuh niin i hria ngai em? Chu chu hmuh chu a hlauhawm deuh a ni lawm ni? Liver natna chi khat niin i ngai mai thei. Hei hi a chhan awm thei pakhat chu Gilbert’s syndrome an tih hi a ni. Mahse a hming i hriat chuan hlau suh, i ngaihtuah angin a hlauhawm lo. Dik tak chuan natna aiin genetic condition a ni zawk.
A awlsam zawngin Gilbert-a syndrome hi eng nge ni?
Gilbert’s syndrome hi kan chhungkuaah a awm fo thin a, chu chu thlahtute atanga lo chhuak a ni tihna a ni. Hetiang vei hian an thisenah bawlhhlawh bilirubin an tih chu a tam lutuk a.
Tunah chuan bilirubin hi eng nge a nih i ngaihtuah tawh mai thei. A awlsam khawp mai. Kan taksaa thisen sen (red blood cells) te hian dam chhung hun an nei bawk. Chu dam chhung chu a tawp chuan an chhe vek thin. Bilirubin hi yellow pigment, a nih loh leh bawlhhlawh a ni a, thisen sen (red blood cells) a chhiat chuan a lo awm thin. A tlangpuiin kan thin hian he bilirubin hi a la a, a process a, bile hmangin taksa atangin a paih chhuak thin.
Mahse Gilbert’s syndrome vei teah chuan liver hian he hna thawk thei enzyme bik a siam chhuak tlem hle. Chuvangin bilirubin hi a tifai vek thei lo va, a then chu thisenah a awm reng bawk. Thisen a bilirubin level a san chuan a chang chuan mit leh vun a sen thin. Hei hi jaundice kan ti bawk .
A pawimawh ber chu Gilbert’s syndrome hi natna hlauhawm tak a ni lo tih hi a ni. Enkawl a ngai lo. Hun rei tak chhung chu i nun a tichhe lovang.
Hetiang dinhmun a lo awm chhan hi eng nge ni?
Hei hi kan genes a danglamna tlemte vang a ni. Kan nu leh pate hnen atanga vun rawng leh sam hring ang chi thil kan rochun ang bawkin hei pawh hi a dik a ni.
Kan taksaah hian gene pakhat UGT1A1 a awm a . He gene hian a hmaa ka sawi tawh ang khan bilirubin tifai thei liver enzyme siam turin min hrilh a ni. Gilbert’s syndrome hi he gene-a mutation tenau vang a ni.
Hetiang dinhmun hi i neih theih nan chuan mutated gene copy pahnih i neih a ngai a ni. Hei hian i nu leh i pa te hnen atangin gene hi i rochun a ngai tihna a ni . Mahse, gene pahnih nei mah la, mi zawng zawngin Gilbert’s syndrome symptoms an lantir vek dawn lo. Tin, hmeichhia aiin mipaah he natna hi a tam zawk bawk.
Gilbert’s syndrome natna lan chhuah dan chu engte nge ni?
Dik tak chuan, Gilbert’s syndrome vei tam zawk chuan symptoms an nei lo . An taksaa bilirubin level control turin liver enzyme an nei tling a ni.
A lan chhuahna ber leh a châng chuan a lan chhuahna awmchhun chu mit leh vun var, jaundice tia hriat a ni. Mit sen i neih chuan doctor pan a pawimawh a, checkup neih a pawimawh , a chhan dang a awm thei bawk.
Mi thenkhat chuan mit sen rual hian a hnuaia symptoms te hi an nei thei a ni:
- Luak chhuak leh pum na
- Pum natna
- Chau lutuk tih hriatna (chau) .
- Zun dum
Engvangin nge ka mit hi a chang chuan a sen mai mai a, a sen vek loh?
Hei hi zawhna tha tak a ni. Kan bilirubin level tisang thei thil engemaw tak a awm. Hei hi mit sen (yellowing) kan hmuh tlangpui hun a ni.
| Bilirubin level sang leh jaundice a awm theihna case | |
|---|---|
| Rimtawng | Exam, hnathawhna hmuna harsatna, etc. vangin. |
| Tui tlakchhamna (dehydration). | Taksa tana tui in tlem. |
| Chaw ei skip | Chawhmeh leh chawhmeh ei loh. |
| Exercise tam lutuk | Exercise hahthlak tak tak tih tur, squatting ang chi te. |
| Hri kai theihna dinhmun | Khawsik emaw, khawsik emaw ang chi natna i neih hian. |
| Zu in a in thin | Zu hian liver-ah phurrit a siam belh zel a ni. |
| Damdawi thenkhat | Liver tichhe thei damdawi thenkhat ei. |
| Hmeichhia tan thlasik hun | Thla tin thlasik hun ni chhungin. |
Engtin nge he dinhmun hi kan hriat theih ang?
Gilbert’s syndrome hi pianpui natna ni mah se, kum 20 emaw kum 30 emaw velah hian hmuhchhuah a ni fo. Chu pawh chu thil thleng mai mai a ni.
Chhan dang vangin thisen test i nei niin han ngaihtuah teh. Tichuan i doctor chuan i thisena bilirubin level chu a pangngai aia a sang deuh tih a hmu a. Tichuan Gilbert-a syndrome i nei tih a ringhlel mai thei.
Tichuan, thin natna hlauhawm dang a awm loh nan doctor chuan test eng emaw zat a ti thei a, chungte chu:
- Liver Function Tests (LFT): Hei hi thisen test hman tlanglawn tak a ni.
- Liver Ultrasound: Liver lama harsatna dang awm leh awm loh enfiah nan.
- Gene Tests: UGT1A1 gene mutation i neih leh neih loh finfiah rawh.
- Liver Biopsy: Hei hi tih a tlem hle.
Enkawlna leh keimahni ngeiin kan tih theihte
Thu lawmawm tak chu Gilbert’s syndrome vei tam zawk chuan enkawlna engmah an mamawh lo , i mit a sen chuan hun rei tak chhung harsatna a thlen lo vang.
Chuvangin kan tih tur chu a hmaa ka sawi tawh, bilirubin level tisangtu thilte atanga a hla thei ang bera awm hi a ni.
- Chaw ei hi skip suh, a bik takin chaw nghei lai hian.
- Tui leh tui tam tak in thin ang che. I taksa chu tui tlakchham tir suh.
- Stress hi enkawl rawh. Ngaihtuahna, music ngaihthlak, emaw, i hobby nuam tak tih ang chi thil hahdam tak ti rawh.
- Mut tha rawh. Ni khatah darkar 7-8 tal mut thin ang che.
- Zu in khap emaw, bansan emaw .
- Exercise hahthlak lutuk hi pumpelh rawh. Exercise tlem lutuk hi a tha a, mahse i theihna chin piah lamah in nawr luih suh.
Damdawi ei huna i hriat tur chu!
Hei hi a pawimawh hle. Gilbert’s syndrome i neih chuan damdawi thar i ei hmain hei hi i hriat hmasak a ngai a ni.
Kan thin a bilirubin tifai tu enzyme tho hian taksa atanga damdawi thenkhat a tichhia a, a paih chhuak bawk. Chuvangin, Gilbert’s syndrome i neih avangin chu enzyme hnathawh chu a tlahniam deuh a ni. Chuvangin, chutiang damdawi i ei chuan taksaah a tam lutukin a pungkhawm thin.Side effect a awm theihna a sang hle.
Entirnan, heng damdawi te hi han en teh:
- Acetaminophen - (Panadol, Paracetamol te a awm) a ni.
- Irinotecan - cancer enkawlna atana hman thin damdawi a ni
- HIV leh hepatitis C damdawi thenkhat (Protease inhibitors) .
Chuvangin, eng damdawi thar pawh i ei pawhin, Gilbert’s syndrome i vei tih i doctor hnenah hrilh ngei ang che. I tana tha tur damdawi him tak a pe thei che a ni. Doctor-in a pek loh damdawi engmah ei ngai suh, a rawt aia tam ei ngai suh.
Take-Home Thuchah a ni
- Gilbert’s syndrome hi natna tlanglawn tak, hlauhawm lo, thlahtute atanga lo chhuak a ni. Hlauh tur natna a ni lo.
- Thisenah bilirubin level a san avangin mit leh vun chu a sen (jaundice) a ni. Hei hi stress emaw, natna emaw avanga lo awm a ni tlangpui.
- Hemi atan hian enkawlna bik a ngai lo. A tha ber chu bilirubin level tisang thei thil tih loh hi a ni.
- A pawimawh ber: Gilbert’s syndrome i neih chuan damdawi thar i ei hmain i doctor hnenah hrilh hmasa phawt ang che.











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