Kua rongo pea koe i te aorta, te uaua toto matua e pupuhi ana i te toto puta noa i tō tātou tinana. Whakaarohia, me pēhea mēnā ka ngoikore tēnei uaua matua, kei te wāhi tonu e hono ana ki te ngākau, i te "pūtake", ka pupuhi ake, ka pūwero atu pērā i te poihau? Koinei te mea e kiia nei e tātou he aneurysm i roto i te rongoā. He tino morearea tēnei, nā te mea i ngā wā katoa ka taea e tēnei pakitara ngoikore te wehe, te pakaru rānei. Ki te tupu tēnā, ka nui te toto i roto i te tinana, ā, ka puta he hua morearea ki te ora. Nō reira, he tino nui te pokanga Whakakapinga Pūtake Aorta e mahia ana hei whakamutu i ēnei āhuatanga morearea ki te ora. I tēnei rā, ka kōrerohia e tātou tēnei mea mā te ngāwari, i roto i te huarahi e mārama ai koe.
He aha tēnei pokanga whakakapinga pakiaka aorta?
He whakarāpopototanga noa iho tēnei, he mahi tākuta hei whakatika i te aneurysm i roto i te pūtake aortic, te uaua matua e hono ana i tō ngākau. I ētahi wā, ka whakakapia te pūtake o tō aorta me te takirere i roto. I ētahi wā anō, ko te pūtake o tō aorta anake ka whakakapia, ka waiho tō takirere noa kia ora tonu. Mā tō tākuta e whakatau ko tēhea momo tākuta e tika ana māu i runga i ngā āhuatanga maha, tae atu ki te āhua o tō takirere.
He aha ngā momo matua o tēnei pokanga?
E rua ngā tikanga matua o tēnei pokanga. Ko tētahi he whakakapi i te pūtake o te aorta me te takirere. Ko tētahi he whakakapi i te pūtake anake, me te waiho i te takirere kia mau tonu. He painga, he ngoikoretanga hoki ō ia mea.
1. Te Whakakapinga Pūtake Aorta (ARR)
Ka kiia hoki tēnei tikanga ko te tikanga Bentall . Ka mahia mō te hunga he aneurysm aortic me te raruraru ki te takirere. Hei tauira, mēnā kāore te takirere e kati tika, ā, ka turuturu te toto ki muri (regurgitation aortic valve) mēnā rānei kua whakapakeketia te takirere (kua mārō).
- Painga matua: Ko te painga nui o tēnei, kāore koe e hiahia ki tētahi pokanga motuhake hei whakatika anō i te takirere i muri i te pokanga. Ka whakatauhia te raruraru o te aneurysm me te takirere i te wā kotahi.
- Ngā Mōrearea: Mena ka whakauruhia he takirere ā-ringa ki roto i tēnei pokanga, me tango e koe ngā rongoā whakangawari toto/whakaiti toto mō te toenga o tō oranga. He iti noa te mōrearea o te toto totoka, te toto rānei nā ēnei rongoā.
2. Te Whakakapinga Pūtake Tiaki-Taurere (VSRR)
Koinei te kōwhiringa pai rawa atu mēnā kei te mahi tika tō takirere aorta, kāore he raruraru. Hei tauira, mēnā kāore he turuturu toto, he matotoru rānei mai i te takirere, ka taea te whiriwhiri i tēnei tikanga. Koinei te otinga pai rawa atu mō te hunga e pāngia ana e te aneurysms i te wā taitamariki nā ngā āhuatanga ira.
Ko tēnei tikanga he whakakapi i te pūtake o tō aorta me te hono anō i tō ake takirere tūturu ki reira. E rua ngā tikanga matua, i tapaina i muri i ngā tākuta nāna i kimi.
- Te tikanga Yacoub: Ko te mahi tēnei ko te whakahou i te takirere aorta. He pai tēnei mō te hunga kaumātua he aneurysms ā rātou nā ngā take ehara i te ira.
- Te tikanga a Rawiri: Kei roto i tēnei ko te whakaurunga anō o te takirere aorta. He tikanga noa ake tēnei engari he uaua ake i te tikanga a Hakopa. He pai ake mō te hunga rangatahi he mate ira, he takirere aorta bicuspid rānei.
Ko te painga nui o te pokanga VSRR ko te kore e hiahiatia he rongoā whakangawari toto mō te toenga o tō oranga. Ka whakaitihia hoki te mōrearea o te whiu, ngā mate pāwera rānei pērā i te endocarditis.
Me ako tātou i ētahi kōrero mō te pūtake aorta?
Ko te pūtake o te aorta te wāhanga tuatahi o te oko toto nui rawa atu o te tinana, te aorta, te wāhi e hono atu ai ki te ngākau. He rite ki te pūtake o te rākau. Ko te aorta, e puta mai ana i te ngākau, ka piko ki runga, pērā i te piko. Ka tīmata taua piko i te wāhi e tīmata ai te pūtake o te aorta. He tino uaua tēnei wāhanga.
- Takirere Aorta: Koinei te wāhi e tukuna ai e te takirere e mahi ana hei kēti te toto kia rere mai i te ngākau ki te aorta, engari ka ārai i te rere hoki mai.
- Ngā uaua coronary: Ko ngā oko toto tino nui e rua e tuku toto ana ki te ngākau ka tīmata i te turanga o tēnei aorta.
- Ngā Sinuse o Valsalva: Koinei te ingoa i hoatu ki ngā pupuhi iti e puta mai ana i te wāhi e tīmata ai ngā uaua coronary.
I a tātou e tamariki ana, he tino ngāwari ēnei wāhanga katoa. Engari i a tātou e pakeke haere ana, ka heke te ngāwari o tēnei wāhanga. Koinei te take e puta ai ētahi raruraru. Nā te mea he tino uaua tēnei wāhanga, he uaua hoki ngā pokanga e mahia ana ki runga. Heoi, mā te āwhina a ngā taote pokanga mātau me ngā tohunga, ka taea te mahi angitu i tēnei pokanga, ā, ka ora anō tō ngākau.
Ko wai rā te tangata e hiahia ana ki tēnei pokanga?
E hiahiatia ana tēnei pokanga mō te hunga he aneurysm kei roto i te aorta e mōrearea ana ki te pahū, ki te pakaru rānei. I ētahi wā ka puta ēnei nā ngā huringa o te aorta i te pakeketanga. Waihoki, ko ngā āhuatanga ira pēnei i te Marfan syndrome me te Loeys-Dietz syndrome ka taea te whakaputa i ngā aneurysm whakamate i te wā taitamariki.
Whakaarohia, ki te kore te tangata e pangia ana e te Marfan syndrome e whiwhi maimoatanga, he nui te tūponotanga ka pakaru te aneurysm ka mate. Ko te tau toharite o te mate mō te hunga o taua rōpū he 32 tau te pakeke. Engari, ki te whiwhi koe i tēnei pokanga, ka taea e koe te whakaroa i tō roanga o te ora ki te oranga o te tangata noa.Nō reira, ki te mea he mate ira tō tetahi o tō whānau, he mea nui kia kōrero koe ki tō tākuta mō tō mōrearea, kia whakatauhia ai hoki te wā pai mō te pokanga.
| Āhuatanga hauora/tūponotanga mōrearea | Te whānui o te aneurysm e hiahia ana ki te pokanga |
|---|---|
| Ki te kore he āhuatanga ira motuhake, he āhuatanga mōrearea rānei | 5.5 henimita |
| Mena kei a koe te mate Marfan | 5.0 henimita |
| Mena kei a koe ētahi atu mōrearea pēnei i te Marfan syndrome me te hītori whānau, te tere o te tipu, te whakamahere rānei kia hapu | 4.5 henimita |
| Mena he mōrearea anō ōu, pērā i te takirere aorta bicuspid me te toto toto tiketike | 5.0 henimita |
Ko te mea nui, kāore ēnei tau e ōrite mō te katoa. Ka rerekē pea tēnei whakatau i runga i tō tau, i tō hauora whānui, me ngā āhuatanga pēnei i te toto toto tiketike kāore i te whakahaeretia me te kai hikareti. Nō reira, kōrero ki tō tākuta mō ō mōrearea me te wā pai mō te pokanga.
He aha ngā mea ka tū i mua, i te wā, me muri i te pokanga?
I te mea he pokanga nui tēnei, me whakarite pai.
I mua i te pokanga
Ka tirohia koe e tō tākuta i roto i te whakamātautau katoa. Ka tukuna atu hoki koe e ia ki tētahi tākuta niho mō tētahi tirotiro niho. Hei tāpiritanga, ka whakahaerehia e rātou ētahi whakamātautau, pēnei i:
- Ngā whakamātautau toto: Tirohia te mahi a te whatukuhu.
- Matawai CT, MRI rānei o te ngākau: Ka taea e tēnei te tirotiro i ngā wāhanga katoa o te aorta. I ētahi wā ka taea te whakatika i ētahi atu raruraru i roto i te pokanga kotahi.
- Angiography Coronary: Tirohia te āhua o ngā uaua coronary e tuku toto ana ki te ngākau.
- Uira-orooro Duplex: Ka tirohia te āhua o ngā uaua carotid i te kaki. Mēnā he raruraru ki ēnei, ka nui ake te tūponotanga o te pararutiki i te wā e pokanga ana.
I tua atu, ka pātai atu tō tākuta ki a koe mō ēnei mea:
- Ngā rongoā e tangohia ana e koe: Me kōrero koe ki tō tākuta mō ngā rongoā, ngā huaora rānei e tangohia ana e koe. Tērā pea ka hiahiatia kia mutu te tango i ētahi rongoā i mua i te pokanga.
- Ētahi atu āhuatanga hauora: Mena he āhuatanga hauora tōu pēnei i te toto toto tiketike, me whakahaere pai i mua i te pokanga.
- Tō āhua o nāianei: Me whakamōhio mai ki a mātou mēnā he mate tōu, pērā i te makariri, te kirika rānei.
- Te kai paipa: Me mutu rawa te kai paipa i te iti rawa i te kotahi marama i mua i te pokanga.
I te wā o te pokanga
Ka hoatu he rongoā whakamoe ki a koe kia moe rawa koe. Kātahi ka honoa koe ki tētahi mīhini ngākau-pūkahukahu (cardiopulmonary bypass) . Mā tēnei mīhini e mahi te mahi a tō ngākau me ō pūkahukahu i te wā o te pokanga. Kātahi ka whai te taote pokanga i ēnei mahi:
1. Median Sternotomy: Ka tapahia te waenganui o te uma hei wehe i te wheua uma (sternum) me te uru atu ki te ngākau.
2. Te tango i te aneurysm: Ka tapahia, ka tangohia te wāhanga ngoikore me te pupuhi o te aorta.
3. Tāurunga o te hononga toto: Ka tāuruhia he oko toto horihori (whakapiri) hei whakakapi i te wāhanga kua tangohia.
4. Te whakakapi, te tiaki rānei i te takirere: Ka whakakapia e koe te takirere, ka tāuta anō rānei i tō ake takirere e ai ki te tikanga ARR, VSRR rānei i kōrerotia i mua ake nei.
5. Te tārai toto i te uaua o te ngākau: Ka honoa ngā uaua o te ngākau e tuku toto ana ki te ngākau ki te tārai hou.
6. Te tuitui i te tapahi: Hei whakamutunga, ka tuituia anō te tapahi o te uma.
E whā ki te ono hāora te roa o tēnei pokanga.
I muri i te pokanga
I muri i te pokanga, me noho koe ki te wāhanga tiaki nui (ICU) mō ētahi rā. Kātahi ka whakawhitia koe ki tētahi wāhanga noa. E tata ana ki te wiki te roa o te noho hōhipera katoa. I roto i tēnei wā:
- Ka hoatu e ahau he rongoā whakamamae ki a koe.
- Tērā pea ka honoa koe ki tētahi mīhini hei āwhina i a koe ki te manawa.
- Hei ārai i te toto totoka, ka mauhia he tōkena motuhake.
- Ka hoatu he rongoā whakaiti toto ki ētahi tāngata.
Kia hoki koe ki te kāinga i te hōhipera, me whai i ngā tohutohu a te tākuta. Kaua e tere. Kia ora wawe koe. Kāore e taea e koe te taraiwa kia ora rā anō koe.
He aha ngā painga, ngā mōrearea, me ngā reiti angitu o te pokanga?
| Wāhanga | Whakaahuatanga |
|---|---|
| Painga matua | Hei ārai i tētahi āhuatanga ohorere ka mate pea, ina pahū, ina pakaru rānei te aneurysm. He mahi whakaora ora tēnei. |
| Ngā tūponotanga me ngā raruraru | Pērā i ngā pokanga nui katoa, he tūponotanga anō kei reira. Tērā pea ka puta te toto, te toto totoka, te mate pāwera, te mate manawa, te whiu rānei, me te ngoikore o te whatukuhu. Engari he tino onge ēnei. |
| Te wā whakaora | E ono ki te tekau mā rua wiki , e rua ki te toru marama rānei te roa hei whakaora katoa. He mea tino nui te whai wāhi atu ki tētahi kaupapa whakaora ngākau i tēnei wā. |
| Angitu me te oranga tonutanga | He tino angitu ēnei pokanga. I waenganui i te 98% me te 99% o te tangata ka ora i te pokanga. Ahakoa i muri i te 10 tau, tata ki te 86% - 90% kāore e hiahia ki tētahi atu pokanga. He otinga mō te wā roa tēnei. |
Āhea koe me toro atu ki te tākuta?
Kia tino aro ki tō tinana i a koe e ora ana. Ki te kite koe i tētahi o ēnei e whai ake nei , waea atu ki tō tākuta tonu:
- Ngā pātai e pā ana ki te tapahi:
- Te whero, te mamae, te pupuhi, te mahana rānei huri noa i te wāhi i tapahia.
- Ka tino mākū te takai, ka turuturu mai te toto, te wai mārama rānei.
- He rerenga waikura kakariki, kōwhai rānei.
- Kei te neke haere ngā taha o te tapahi.
- Ētahi atu pātai:
- Te mamae o te uma, te uaua rānei ki te manawa ahakoa te okiokinga.
- Te pupuhi o ngā waewae, te kore rānei e taea te neke i ngā waewae.
- Te whanoke, te hiamoe, te ngenge nui rānei.
- Te maremare toto, te hūpē kakariki/kōwhai rānei.
- E mātao ana, e pāngia ana hoki e te kirika.
- Toto i roto i te tūtae.
Āhea koe me haere ki te Wāhanga Maimoatanga Ohotata (ETU)?
Mena he aneurysm tōu kāore anō kia rongoatia, haere tonu ki te tari ohorere o te hōhipera tata (ETU) mena ka pāngia koe e ēnei tohu. Tērā pea he tohu ēnei o te pakaru o te aneurysm:
- He mamae ohorere, kāore e taea te whakamātau i te uma, i te tuara rānei o runga. Tērā pea ka rite ki te mea e haehaetia ana i roto i te tinana.
- Te werawera me te mākūkū.
- Te uaua ki te manawa.
- Pōuriuri, māuiui rānei te upoko.
- Ka piki ake te tere o te manawa.
- Whakapairuaki me te ruaki.
He mea noa te mataku ina rongo koe mō te pokanga ngākau. Engari kia maumahara, he mea tēnei pokanga hei whakaora i tō ora, hei hoatu hoki i te whai wāhi ki a koe ki te ora hauora mō te wā roa. He mātau tō tākuta me tō rōpū hauora ki te mahi i ēnei momo pokanga. Nō reira, kōrero ki a rātou mō ō pātai, ō mataku rānei.
Karere Tangohia ki te Kāinga
- Ko te Whakakapinga Pūtake Aorta he pokanga whakaora ora e mahia ana hei ārai i te pakaru o te aneurysm i te pūtake o te aorta o te ngākau.
- I runga i te āhua o tō takirere aorta, ka taea te mahi i tēnei pokanga me te takirere (ARR) me te takirere kua tiakina rānei (VSRR).
- He tino angitu tēnei pokanga. Neke atu i te 98% te ōrau ora. He otinga hoki mō te wā roa.
- He mea nui kia mutu te momi hikareti me te whakahaere i ngā mate pēnei i te toto toto tiketike i mua i te pokanga.
- Ki te puta he tohu rerekē ki a koe (te pangia o te motu, te mamae nui o te uma) i a koe e ora ana, me whakamōhio tonu atu ki tō tākuta.
- Mena he āwangawanga, he ruarua rānei āu mō tēnei pokanga, kōrero noa atu ki tō tākuta. Mā rātou koe e āwhina.

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