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ꯑꯩꯈꯣꯌꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯑꯀꯛꯅꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ? (ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ)

ꯑꯩꯈꯣꯌꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯑꯀꯛꯅꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ? (ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ)

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ? ꯑꯩꯈꯣꯌꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯦꯖꯃꯥꯒꯨꯝꯕꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ ꯍꯥꯌꯅꯥ ꯈꯜꯂꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯂꯩ꯫ ꯃꯁꯤꯕꯨ ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯃꯃꯤꯡ ꯑꯁꯤ ꯈꯔꯥ ꯁꯥꯡꯏ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯃꯁꯤꯕꯨ ꯊꯣꯏꯗꯣꯛꯅꯥ "ꯂꯝ" ꯍꯥꯌꯅꯥ ꯀꯧꯒꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯤꯡ ꯑꯁꯤ ꯐꯣꯡꯗꯣꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯃꯁꯤ ꯑꯁꯤꯒꯨꯝꯅꯥ ꯈꯟꯊꯕꯤꯌꯨ: "ꯂꯤꯝꯐ-ꯑꯦꯡ-ꯒꯦ-ꯑꯣ-ꯂꯤ-ꯑꯣ-ꯃꯌꯣ-ꯃꯥ-ꯇꯣ-ꯁꯤꯁ"꯫ ꯃꯁꯤ ꯈꯔꯥ ꯍꯦꯟꯅꯥ ꯂꯨꯝꯂꯕꯁꯨ, ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯑꯆꯝꯕꯥ ꯋꯥꯍꯟꯊꯣꯛ ꯑꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯂꯝ ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?

LAM ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡ ꯍꯦꯅꯒꯠꯂꯛꯇꯨꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯁꯦꯃꯒꯠꯂꯀꯄꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯔꯤꯕꯥ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯅꯁꯤꯡꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯂꯪꯁ ꯈꯛꯇꯥ ꯅꯠꯇꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯁꯨ ꯒ꯭ꯔꯣꯊꯁꯤꯡ ꯑꯁꯤ ꯁꯦꯃꯒꯠꯄꯥ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯆꯍꯤ 20 ꯑꯃꯁꯨꯡ 40ꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯊꯣꯀꯏ, ꯍꯥꯌꯕꯗꯤ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯃꯥꯡꯗꯥ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯨꯄꯤꯒꯤ ꯍꯣꯔꯃꯣꯟ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯅꯕꯗꯥ ꯊꯧꯗꯥꯡ ꯂꯧꯔꯤ ꯍꯥꯌꯅꯥ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯊꯥꯖꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤ ꯂꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤꯗꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯌꯥꯏ, ꯑꯅꯤꯁꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯔꯥ ꯈꯦꯠꯅꯕꯥ ꯂꯩ꯫

ꯂꯝ ꯃꯈꯜ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯄꯥꯎꯈꯨꯝ ꯑꯃꯥ꯫
ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.-ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯖꯤꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯀꯥ ꯃꯔꯤ ꯂꯩꯅꯩ꯫ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤ ꯈꯔꯗꯁꯨ LAM ꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯍꯦꯔꯤꯇꯦꯖ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫
ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯔꯦꯟꯗꯝ ꯖꯦꯅꯦꯇꯤꯛ ꯆꯦꯟꯖ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤ ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯅꯠꯇꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯗꯣꯃꯗꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯃꯈꯂꯒꯤ ꯂꯝ ꯂꯩꯔꯕꯗꯤ ꯃꯗꯨ ꯑꯗꯣꯃꯒꯤ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯌꯧꯍꯅꯕꯥ ꯉꯝꯂꯣꯏ꯫

ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯏ꯫ ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯀꯦꯂꯒꯤ ꯃꯇꯨꯡ ꯏꯟꯅꯥ ꯃꯁꯤꯅꯥ ꯅꯨꯄꯤ ꯱꯴꯰,꯰꯰꯰ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯈꯛꯇꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯇꯤꯎꯕꯔ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ 30% ꯑꯃꯁꯨꯡ 80%ꯒꯤ ꯃꯔꯛꯇꯥꯗꯤ LAMꯁꯨ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ, ꯍꯥꯌꯕꯗꯤ ꯑꯦꯖꯃꯥ ꯑꯃꯁꯨꯡ ꯕ꯭ꯔꯣꯉ꯭ꯀꯏꯇꯤꯁꯀꯥ ꯌꯥꯝꯅꯥ ꯃꯥꯟꯅꯩ꯫ ꯃꯁꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯏꯑꯣꯡ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯃꯇꯝ ꯈꯔꯥ ꯆꯪꯂꯝꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯆꯦꯀꯁꯤꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨ ꯑꯣꯏ꯫

  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (dyspnea): ꯃꯁꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯅꯤ꯫ ꯑꯍꯧꯕꯗꯥ ꯃꯁꯤ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯇꯧꯕꯈꯛꯇꯗꯥ ꯐꯥꯎꯔꯕꯁꯨ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯆꯤꯜꯂꯀꯄꯥ ꯌꯥꯏ꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (wheezing): ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯨꯔꯥꯅꯕꯥ ꯈꯣꯟꯖꯦꯜ ꯑꯃꯥ , ꯃꯁꯤ ꯑꯅꯥꯕꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯥ ꯃꯥꯟꯅꯩ꯫
  • ꯈꯣꯡꯗꯥ ꯑꯅꯥꯕꯥ (chest pain): ꯑꯅꯥꯕꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯃꯇꯃꯗꯥ ꯐꯥꯎꯕꯥ ꯌꯥꯏ꯫
  • ꯀꯣꯛ ꯆꯤꯀꯄꯥ: ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ (persistent dry cough) ꯂꯩꯕꯥ ꯌꯥꯏ꯫
  • ꯏ ꯁꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ‘ꯆꯥꯏꯜ’ (chail) : ꯆꯥꯏꯜ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯗꯥꯏꯖꯦꯁ꯭ꯇꯤꯚ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯃ꯭ꯌꯨꯀꯁ ꯐ꯭ꯂꯨꯏꯗ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯃꯆꯨ ꯁꯉ꯭ꯒꯣꯝ ꯑꯣꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯊꯧꯗꯣꯛ ꯑꯃꯥ ꯊꯣꯛꯂꯕꯗꯤ ꯊꯦꯡꯊꯕꯥ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯐꯩ .

ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯂꯝ ꯑꯁꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯀꯔꯤꯅꯣ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯱ ꯑꯃꯁꯨꯡ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯲ ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯅꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯑꯍꯣꯡꯕꯁꯤꯡ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯁꯤꯅꯤ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯉꯥꯀꯁꯦꯜ ꯂꯥꯟꯃꯤꯁꯤꯡꯒꯨꯝꯕꯅꯤ꯫ ꯃꯈꯣꯌꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯊꯕꯛ ꯑꯁꯤ ꯁꯦꯜ ꯈꯔꯗꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯁꯤꯡ ꯌꯥꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯊꯤꯡꯕꯅꯤ꯫ ꯑꯩꯈꯣꯌꯅꯥ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤꯕꯨ ꯇꯤꯎꯃꯔ ꯁꯞꯞꯔꯦꯁꯔ ꯖꯤꯅꯁꯤꯡ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯉꯥꯀꯊꯣꯛꯅꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯗꯥ ꯑꯁꯣꯏꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯝꯂꯕꯗꯤ ꯈꯅꯕꯤꯌꯨ꯫ ꯊꯣꯛꯂꯤꯕꯥ ꯑꯁꯤꯗꯤ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯅꯥ "ꯑꯣꯀꯦ, ꯃꯇꯤꯛ ꯆꯥꯔꯦ, ꯌꯦꯟꯊꯣꯀꯄꯥ ꯂꯦꯄꯀꯅꯨ" ꯍꯥꯌꯕꯒꯤ ꯁꯤꯒꯅꯦꯜ ꯑꯗꯨ ꯐꯪꯗꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯍꯧꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯍꯩꯗꯤ:

  • ꯂꯪꯁꯇꯥ ꯁꯤꯁ꯭ꯇꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫
  • ꯀꯤꯗꯅꯤꯁꯤꯡꯗꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ (angiomyolipomas) ꯁꯦꯝꯃꯤ꯫
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫

ꯅꯍꯥꯛꯅꯥ ꯑꯁꯣꯏ-ꯑꯉꯥꯝ ꯌꯥꯑꯣꯗꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯃꯃꯥ-ꯃꯄꯥꯗꯒꯤ ꯂꯧꯕꯥ ꯌꯥꯏ (ꯃꯁꯤꯅꯥ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ ꯊꯣꯀꯍꯜꯂꯤ), ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯃꯔꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯅꯥ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ (ꯃꯁꯤꯅꯥ ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ LAM ꯊꯣꯀꯍꯜꯂꯤ)꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯔꯤꯁ꯭ꯀꯁꯤꯡ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯁꯤ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯑꯣꯏꯅꯥ ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ ꯍꯥꯌꯅꯥ ꯈꯉꯅꯕꯥ ꯂꯪꯁ ꯁꯣꯀꯄꯥ ꯑꯁꯤꯅꯤ ꯫ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯦꯡꯅꯒꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯇꯁꯦꯡꯕꯗꯤ, ꯅꯨꯄꯤ ꯀꯌꯥꯅꯥ ꯂꯪꯁ ꯑꯦꯕꯁꯦꯁ ꯑꯃꯥ ꯂꯩꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯍꯣꯁ꯭ꯄꯤꯇꯥꯂꯗꯥ ꯊꯃꯖꯤꯜꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯍꯥꯅꯕꯥ ꯑꯣꯏꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯑꯇꯩ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯁꯨ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯂꯩꯕꯥ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯇꯥꯀꯄꯥ꯫
ꯂꯪꯁ ꯀꯣꯂꯥꯞꯁ (ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ) . ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ (cysts) ꯅꯥꯕꯥ ꯌꯥꯏ, ꯃꯗꯨꯅꯥ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯆꯦꯁ꯭ꯠ ꯋꯥꯜ (chest wall)ꯒꯤ ꯃꯔꯛꯇꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯅꯥ ꯈꯪꯍꯧꯗꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯈꯣꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯆꯥꯏꯂꯣꯁ ꯐ꯭ꯂꯨꯏꯗ ꯌꯥꯎꯕꯥ (Chylothorax) ꯂꯤꯝꯐ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯁꯉ꯭ꯒꯣꯃꯒꯤ ꯐ꯭ꯂꯨꯏꯗ (chyle) ꯑꯃꯅꯥ ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯈꯣꯃꯖꯤꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯁꯨ ꯑꯋꯥꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫
ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗ ꯑꯦꯛꯌꯨꯃꯨꯂꯦꯁꯟ (Pleural Effusion) ꯂꯪꯁꯄꯨ ꯀꯨꯄꯁꯤꯜꯂꯤꯕꯥ ꯃꯦꯝꯕ꯭ꯔꯦꯅꯁꯤꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯄ꯭ꯂꯨꯔꯦꯜ ꯐ꯭ꯂꯨꯏꯗ ꯅꯠꯇꯕꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗꯁꯤꯡ ꯊꯨꯒꯥꯌꯕꯥ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯉꯗꯣꯀꯄꯒꯦ?

ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯇꯥꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯍꯥꯛꯅꯥ ꯃꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯇꯧꯅꯕꯥ ꯑꯣꯔꯗꯔ ꯇꯧꯒꯅꯤ꯫

ꯗꯣꯛꯇꯔꯅꯥ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ꯫

  • ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯇꯦꯁ꯭ꯇꯁꯤꯡ: ꯃꯁꯤꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯦꯁꯤꯟ ꯑꯃꯒꯥ ꯁꯝꯅꯕꯥ ꯇꯤꯎꯕ ꯑꯃꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯀꯄꯥ ꯌꯥꯎꯏ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯁꯤꯡ ꯑꯗꯨ ꯀꯌꯥꯝ ꯐꯖꯅꯥ ꯊꯕꯛ ꯇꯧꯔꯤꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯀꯌꯥꯝ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯉꯝꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯂꯦꯄꯊꯣꯀꯄꯥ ꯉꯃꯒꯅꯤ꯫
  • ꯄꯂꯁ ꯑꯣꯛꯁꯤꯃꯦꯠꯔꯤ: ꯀ꯭ꯂꯤꯞ ꯑꯃꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯈꯨꯠꯂꯥꯏ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯗꯥ ꯌꯥꯎꯔꯤꯕꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯂꯦꯄꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯏꯆꯝ ꯆꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯋꯥꯕꯥ ꯂꯩꯇꯕꯥ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯤ꯫
  • ꯏꯃꯦꯖꯤꯡ ꯁ꯭ꯀꯦꯅꯁꯤꯡ: ꯱.
  • ꯁꯤ.ꯇꯤ.ꯁ꯭ꯀꯦꯟ (ꯀꯝꯞꯌꯨꯇꯦꯠ ꯇꯣꯃꯣꯒ꯭ꯔꯥꯐꯤ):ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯑꯀꯨꯞꯄꯥ 3D ꯏꯃꯦꯖꯁꯤꯡ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯅꯥ LAMꯒꯤꯗꯃꯛꯇꯥ ꯑꯀꯛꯅꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯈꯪꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • HRCT ꯁ꯭ꯀꯦꯟ (ꯍꯥꯏ-ꯔꯤꯖꯣꯂꯨꯁꯟ ꯀꯝꯞꯌꯨꯇꯦꯠ ꯇꯣꯃꯣꯒ꯭ꯔꯥꯐꯤ): ꯃꯁꯤ ꯁꯤ.ꯇꯤ. ꯃꯁꯤꯅꯥ ꯂꯪꯁꯀꯤ ꯌꯥꯝꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯔꯨꯛ ꯑꯃꯒꯤ ꯌꯥꯝꯅꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯕꯥ ꯏꯃꯦꯖꯁꯤꯡ ꯂꯧꯕꯥ ꯉꯝꯃꯤ꯫ ꯃꯁꯤ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡ ꯈꯉꯗꯣꯛꯅꯕꯒꯤꯗꯃꯛ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
  • VEGF-D ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: VEGF-D ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯏꯗꯥ ꯌꯥꯎꯕꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯅꯤ꯫ LAMꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯏꯗꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯂꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ ꯑꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯉꯗꯣꯀꯄꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • ꯂꯪꯁ ꯕꯥꯏꯑꯣꯞꯁꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯇꯩ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯑꯗꯨ 100% ꯁꯣꯌꯗꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯇꯦꯁ꯭ꯠ ꯇꯧꯅꯕꯒꯤꯗꯃꯛ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯒꯤ ꯌꯥꯝꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯇꯤꯁꯨ ꯑꯃꯥ ꯂꯧꯅꯕꯥ ꯋꯥꯔꯦꯞ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯁ꯭ꯀꯣꯄꯤ (ꯑꯦꯌꯔꯋꯦꯁꯤꯡꯗꯥ ꯀꯦꯃꯦꯔꯥ ꯑꯃꯥ ꯊꯥꯕꯥ ꯌꯥꯕꯥ ꯊꯤꯟ ꯇꯨꯕ ꯑꯃꯥ) ꯅꯠꯠꯔꯒꯥ ꯚꯤ.ꯑꯦ.ꯇꯤ.ꯑꯦꯁ.(ꯚꯤꯗꯤꯑꯣ-ꯑꯦꯁꯤꯁ꯭ꯇꯦꯗ ꯊꯣꯔꯥꯁꯤꯛ ꯁꯔꯖꯔꯤ) ꯀꯧꯕꯥ ꯊꯧꯑꯣꯡ ꯑꯃꯥ ꯁꯤꯖꯤꯟꯅꯗꯨꯅꯥ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯀꯔꯤꯅꯣ?

ꯑꯍꯥꯅꯕꯗꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯍꯤꯗꯥꯛ ꯂꯥꯡꯊꯛ ꯑꯃꯠꯇꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯐꯪꯗ꯭ꯔꯤ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯍꯧꯖꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯕꯥ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯊꯦꯡꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯌꯥꯝꯅꯥ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯂꯩꯔꯦ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ . ꯃꯁꯤꯕꯨ ꯔꯦꯄꯥꯃꯥꯏꯁꯤꯟ ꯍꯥꯌꯅꯥꯁꯨ ꯀꯧꯏ꯫ ꯃꯁꯤꯒꯤ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯕꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯆꯥꯎꯈꯠꯄꯥ ꯊꯤꯡꯗꯨꯅꯥ ꯊꯕꯛ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯆꯥꯎꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯃꯒꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯂꯩꯕꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯗꯁꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯏ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ: ꯁꯤꯔꯣꯂꯤꯃꯁꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯈꯔꯗꯤ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯀꯤꯗꯅꯤꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏꯅꯐꯦꯛꯁꯅꯁꯤꯡꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯍꯧꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯀꯥꯟꯅꯕꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯣꯡꯊꯤꯕꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯟꯅ-ꯅꯩꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯅꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡꯁꯨ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯕꯥ ꯌꯥꯏ꯫

  • ꯑꯣꯛꯁꯤꯖꯦꯟ ꯊꯦꯔꯥꯄꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯝꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯌꯨꯃꯗꯥ ꯁꯤꯖꯤꯟꯅꯅꯕꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯇꯦꯉ꯭ꯀꯁꯤꯡ ꯄꯤꯔꯤ꯫
  • ꯏꯅꯍꯦꯜ ꯇꯧꯔꯕꯥ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯗꯤꯂꯦꯇꯔꯁꯤꯡ: ꯏꯅꯍꯦꯂꯔ ꯑꯃꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯄꯤꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯄꯂꯃꯣꯅꯥꯔꯤ ꯔꯤꯍꯦꯕꯤꯂꯤꯇꯦꯁꯟ: ꯃꯁꯤ ꯂꯪꯁꯀꯤ ꯑꯈꯟꯅꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯄ꯭ꯔꯣꯒ꯭ꯔꯥꯝ ꯑꯃꯒꯨꯝꯅꯥ ꯑꯣꯏ꯫ ꯃꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯅꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯍꯦꯅꯒꯠꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯥ: ꯱.ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯆꯥꯎꯈꯠꯂꯛꯂꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯣꯞꯄꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯃꯠꯇꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ ꯃꯇꯃꯗꯥ, ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯑꯁꯤ ꯑꯔꯣꯏꯕꯥ ꯑꯣꯄꯁꯟ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯍꯦꯅꯒꯠꯂꯛꯂꯤꯕꯅꯣ?

ꯃꯁꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯒꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯈꯦꯠꯅꯩ꯫ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯇꯧꯕꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯐꯦꯛꯇꯔ ꯀꯌꯥꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫

  • ꯅꯍꯥꯛꯅꯥ ꯂꯩꯔꯤꯕꯥ LAMꯒꯤ ꯃꯈꯜ: ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ TSC-LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯈꯔꯥ ꯍꯟꯊꯕꯥ ꯌꯥꯏ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯆꯍꯤ: ꯅꯨꯄꯤ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯇꯨꯡꯗꯥ, ꯍꯀꯆꯥꯡꯗꯥ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯑꯗꯨ ꯊꯤꯡꯖꯤꯜꯂꯤ ꯅꯠꯠꯔꯒꯥ ꯍꯟꯊꯔꯀꯏ꯫
  • ꯂꯥꯏꯌꯦꯡꯕꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯔꯦꯁꯄꯣꯟꯁ: ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫

ꯐꯤꯚꯝ ꯑꯁꯤ ꯃꯃꯥꯡꯉꯩꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯟꯅꯥ ꯐꯔꯦ ꯫ ꯃꯣꯗꯔꯟ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ 90% ꯍꯦꯅꯕꯗꯤ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 10ꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯤꯡꯂꯤ꯫ ꯃꯤꯑꯣꯏ ꯀꯌꯥ (ꯆꯥꯎꯔꯥꯛꯅꯥ 64%)ꯗꯤ ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯆꯍꯤ 20 ꯅꯠꯠꯔꯒꯥ ꯃꯁꯤꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯍꯤꯡꯕꯥ ꯉꯝꯃꯤ꯫

ꯀꯗꯥꯏꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯒꯗꯒꯦ ꯑꯃꯁꯨꯡ ꯏ.ꯇꯤ.ꯌꯨ

LAMꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯉꯩꯗꯥ, ꯀꯗꯥꯏꯗꯥ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯒꯗꯒꯦ ꯑꯃꯁꯨꯡ ꯀꯗꯥꯏꯗꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯗꯤꯄꯥꯔꯇꯃꯦꯟꯇ (ETU)ꯗꯥ ꯆꯠꯀꯗꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯈꯪꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯈꯨꯗꯣꯡꯆꯥꯕ ꯀꯔꯤ ꯇꯧꯒꯗꯒꯦ꯫
ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯕꯤꯌꯨ...
ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯀꯣꯛ ꯆꯤꯀꯄꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯂꯤꯕꯥ ꯎꯔꯕꯗꯤ꯫
ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯍꯪꯁꯤꯡ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯧꯔꯤꯕꯥ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯑꯗꯨꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯍꯪ ꯑꯃꯍꯦꯛꯇꯥ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯀꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯈꯜ ꯇꯥꯔꯕꯗꯤ꯫
ꯈꯨꯗꯛꯇꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇ ꯌꯨꯅꯤꯠ (ꯏ.ꯇꯤ.ꯌꯨ.)ꯗꯥ ꯆꯠꯂꯨ...
ꯂꯪꯁ ꯑꯦꯛꯁꯞꯂꯣꯁꯅꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫

  • ꯈꯪꯍꯧꯗꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯅꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯁꯥꯊꯤꯕꯥ, ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ꯫
  • ꯏ ꯊꯣꯀꯄꯥ꯫
  • ꯂꯤꯞ, ꯈꯣꯡ ꯅꯠꯠꯔꯒꯥ ꯅꯥꯀꯣꯡꯗꯥ ꯕ꯭ꯂꯨ ꯗꯤꯁꯀꯂꯔ ꯑꯣꯏꯕꯥ (cyanosis)꯫

ꯃꯤꯑꯣꯏ ꯈꯔꯅꯥ ꯂꯝ ꯑꯁꯤ ꯀꯦꯟꯁꯔꯅꯤ ꯍꯥꯌꯅꯥ ꯍꯪꯏ꯫ LAM ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯀꯦꯟꯁꯔ ꯍꯥꯌꯅꯥ ꯂꯧꯅꯗꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯑꯣꯡ ꯈꯔꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯃꯐꯝ ꯑꯃꯗꯒꯤ ꯂꯪꯁꯇꯥ ꯂꯥꯀꯄꯒꯤ ꯃꯑꯣꯡ ꯑꯁꯤꯅꯆꯤꯡꯕꯗꯥ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯀꯦꯟꯁꯔꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯃꯒꯨꯟ ꯂꯩ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯕꯗꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯒꯥ ꯃꯥꯟꯅꯗꯦ꯫

ꯅꯍꯥꯛꯅꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯄꯨꯟꯁꯤꯗꯥ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯕꯥ ꯈꯪꯂꯕꯥ ꯃꯇꯃꯗꯥ ꯁꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯅꯣꯔꯃꯦꯂꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯅꯍꯥꯛ ꯈꯛꯇꯅꯥ ꯅꯠꯇꯦ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯁꯤꯡ, ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯃꯔꯨꯄꯁꯤꯡꯒꯤ ꯃꯇꯦꯡꯅꯥ ꯅꯍꯥꯛꯅꯥ ꯁꯤꯡꯅꯕꯥ ꯑꯁꯤ ꯃꯥꯌꯣꯛꯅꯕꯒꯤ ꯄꯥꯉ꯭ꯒꯜ ꯐꯪꯒꯅꯤ꯫

ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫

  • LAM (Lymphangioleiomyomatosis) ꯍꯥꯌꯕꯁꯤ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯈꯣꯡꯗꯥ ꯑꯅꯥꯕꯥ, ꯑꯃꯁꯨꯡ ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ꯫
  • ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ ꯑꯁꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯃꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯍꯧꯗꯅꯥ, ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯊꯦꯡꯅꯔꯕꯗꯤ, ꯈꯨꯗꯛꯇꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯔꯨꯃꯗꯥ ꯆꯠꯂꯨ꯫
  • ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯐꯍꯅꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯁꯨ, ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯀꯄꯨ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯕꯥ ꯄꯨꯟꯁꯤ ꯑꯃꯥ ꯍꯤꯡꯕꯥ ꯉꯃꯍꯜꯂꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ, ꯂꯥꯏꯌꯦꯡ ꯅꯠꯠꯔꯒꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯑꯃꯨꯛꯇꯪ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯗꯥ ꯀꯩꯗꯧꯉꯩꯗꯥ ꯂꯥꯡꯇꯛꯅꯒꯅꯨ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ., ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ, ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ, ꯁꯤꯔꯣꯂꯤꯃꯁ, ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ, ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯂꯥꯌꯅꯥ꯫
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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ꯑꯩꯈꯣꯌꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯑꯀꯛꯅꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ? (ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ)
ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ꯫জুলাই ৭, ২০২৬

ꯑꯩꯈꯣꯌꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯑꯀꯛꯅꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ? (ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ)

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ? ꯑꯩꯈꯣꯌꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯦꯖꯃꯥꯒꯨꯝꯕꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ ꯍꯥꯌꯅꯥ ꯈꯜꯂꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯥ ꯂꯩ꯫ ꯃꯁꯤꯕꯨ ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯃꯃꯤꯡ ꯑꯁꯤ ꯈꯔꯥ ꯁꯥꯡꯏ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯃꯁꯤꯕꯨ ꯊꯣꯏꯗꯣꯛꯅꯥ "ꯂꯝ" ꯍꯥꯌꯅꯥ ꯀꯧꯒꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯤꯡ ꯑꯁꯤ ꯐꯣꯡꯗꯣꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯃꯁꯤ ꯑꯁꯤꯒꯨꯝꯅꯥ ꯈꯟꯊꯕꯤꯌꯨ: "ꯂꯤꯝꯐ-ꯑꯦꯡ-ꯒꯦ-ꯑꯣ-ꯂꯤ-ꯑꯣ-ꯃꯌꯣ-ꯃꯥ-ꯇꯣ-ꯁꯤꯁ"꯫ ꯃꯁꯤ ꯈꯔꯥ ꯍꯦꯟꯅꯥ ꯂꯨꯝꯂꯕꯁꯨ, ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯑꯆꯝꯕꯥ ꯋꯥꯍꯟꯊꯣꯛ ꯑꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯂꯝ ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?

LAM ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡ ꯍꯦꯅꯒꯠꯂꯛꯇꯨꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯁꯦꯃꯒꯠꯂꯀꯄꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯔꯤꯕꯥ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯅꯁꯤꯡꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯂꯪꯁ ꯈꯛꯇꯥ ꯅꯠꯇꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯁꯨ ꯒ꯭ꯔꯣꯊꯁꯤꯡ ꯑꯁꯤ ꯁꯦꯃꯒꯠꯄꯥ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯆꯍꯤ 20 ꯑꯃꯁꯨꯡ 40ꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯊꯣꯀꯏ, ꯍꯥꯌꯕꯗꯤ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯃꯥꯡꯗꯥ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯨꯄꯤꯒꯤ ꯍꯣꯔꯃꯣꯟ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯅꯕꯗꯥ ꯊꯧꯗꯥꯡ ꯂꯧꯔꯤ ꯍꯥꯌꯅꯥ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯊꯥꯖꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤ ꯂꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤꯗꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯌꯥꯏ, ꯑꯅꯤꯁꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯔꯥ ꯈꯦꯠꯅꯕꯥ ꯂꯩ꯫

ꯂꯝ ꯃꯈꯜ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯄꯥꯎꯈꯨꯝ ꯑꯃꯥ꯫
ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.-ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯖꯤꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯀꯥ ꯃꯔꯤ ꯂꯩꯅꯩ꯫ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤ ꯈꯔꯗꯁꯨ LAM ꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯍꯦꯔꯤꯇꯦꯖ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫
ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯔꯦꯟꯗꯝ ꯖꯦꯅꯦꯇꯤꯛ ꯆꯦꯟꯖ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤ ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯅꯠꯇꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯗꯣꯃꯗꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯃꯈꯂꯒꯤ ꯂꯝ ꯂꯩꯔꯕꯗꯤ ꯃꯗꯨ ꯑꯗꯣꯃꯒꯤ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯌꯧꯍꯅꯕꯥ ꯉꯝꯂꯣꯏ꯫

ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯏ꯫ ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯀꯦꯂꯒꯤ ꯃꯇꯨꯡ ꯏꯟꯅꯥ ꯃꯁꯤꯅꯥ ꯅꯨꯄꯤ ꯱꯴꯰,꯰꯰꯰ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯈꯛꯇꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯇꯤꯎꯕꯔ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ 30% ꯑꯃꯁꯨꯡ 80%ꯒꯤ ꯃꯔꯛꯇꯥꯗꯤ LAMꯁꯨ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ, ꯍꯥꯌꯕꯗꯤ ꯑꯦꯖꯃꯥ ꯑꯃꯁꯨꯡ ꯕ꯭ꯔꯣꯉ꯭ꯀꯏꯇꯤꯁꯀꯥ ꯌꯥꯝꯅꯥ ꯃꯥꯟꯅꯩ꯫ ꯃꯁꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯏꯑꯣꯡ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯃꯇꯝ ꯈꯔꯥ ꯆꯪꯂꯝꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯆꯦꯀꯁꯤꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨ ꯑꯣꯏ꯫

  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (dyspnea): ꯃꯁꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯅꯤ꯫ ꯑꯍꯧꯕꯗꯥ ꯃꯁꯤ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯇꯧꯕꯈꯛꯇꯗꯥ ꯐꯥꯎꯔꯕꯁꯨ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯆꯤꯜꯂꯀꯄꯥ ꯌꯥꯏ꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (wheezing): ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯨꯔꯥꯅꯕꯥ ꯈꯣꯟꯖꯦꯜ ꯑꯃꯥ , ꯃꯁꯤ ꯑꯅꯥꯕꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯥ ꯃꯥꯟꯅꯩ꯫
  • ꯈꯣꯡꯗꯥ ꯑꯅꯥꯕꯥ (chest pain): ꯑꯅꯥꯕꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯃꯇꯃꯗꯥ ꯐꯥꯎꯕꯥ ꯌꯥꯏ꯫
  • ꯀꯣꯛ ꯆꯤꯀꯄꯥ: ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ (persistent dry cough) ꯂꯩꯕꯥ ꯌꯥꯏ꯫
  • ꯏ ꯁꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ‘ꯆꯥꯏꯜ’ (chail) : ꯆꯥꯏꯜ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯗꯥꯏꯖꯦꯁ꯭ꯇꯤꯚ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯃ꯭ꯌꯨꯀꯁ ꯐ꯭ꯂꯨꯏꯗ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯃꯆꯨ ꯁꯉ꯭ꯒꯣꯝ ꯑꯣꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯊꯧꯗꯣꯛ ꯑꯃꯥ ꯊꯣꯛꯂꯕꯗꯤ ꯊꯦꯡꯊꯕꯥ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯐꯩ .

ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯂꯝ ꯑꯁꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯀꯔꯤꯅꯣ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯱ ꯑꯃꯁꯨꯡ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯲ ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯅꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯑꯍꯣꯡꯕꯁꯤꯡ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯁꯤꯅꯤ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯉꯥꯀꯁꯦꯜ ꯂꯥꯟꯃꯤꯁꯤꯡꯒꯨꯝꯕꯅꯤ꯫ ꯃꯈꯣꯌꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯊꯕꯛ ꯑꯁꯤ ꯁꯦꯜ ꯈꯔꯗꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯁꯤꯡ ꯌꯥꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯊꯤꯡꯕꯅꯤ꯫ ꯑꯩꯈꯣꯌꯅꯥ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤꯕꯨ ꯇꯤꯎꯃꯔ ꯁꯞꯞꯔꯦꯁꯔ ꯖꯤꯅꯁꯤꯡ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯉꯥꯀꯊꯣꯛꯅꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯗꯥ ꯑꯁꯣꯏꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯝꯂꯕꯗꯤ ꯈꯅꯕꯤꯌꯨ꯫ ꯊꯣꯛꯂꯤꯕꯥ ꯑꯁꯤꯗꯤ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯅꯥ "ꯑꯣꯀꯦ, ꯃꯇꯤꯛ ꯆꯥꯔꯦ, ꯌꯦꯟꯊꯣꯀꯄꯥ ꯂꯦꯄꯀꯅꯨ" ꯍꯥꯌꯕꯒꯤ ꯁꯤꯒꯅꯦꯜ ꯑꯗꯨ ꯐꯪꯗꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯍꯧꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯍꯩꯗꯤ:

  • ꯂꯪꯁꯇꯥ ꯁꯤꯁ꯭ꯇꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫
  • ꯀꯤꯗꯅꯤꯁꯤꯡꯗꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ (angiomyolipomas) ꯁꯦꯝꯃꯤ꯫
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫

ꯅꯍꯥꯛꯅꯥ ꯑꯁꯣꯏ-ꯑꯉꯥꯝ ꯌꯥꯑꯣꯗꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯃꯃꯥ-ꯃꯄꯥꯗꯒꯤ ꯂꯧꯕꯥ ꯌꯥꯏ (ꯃꯁꯤꯅꯥ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ ꯊꯣꯀꯍꯜꯂꯤ), ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯃꯔꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯅꯥ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ (ꯃꯁꯤꯅꯥ ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ LAM ꯊꯣꯀꯍꯜꯂꯤ)꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯔꯤꯁ꯭ꯀꯁꯤꯡ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯁꯤ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯑꯣꯏꯅꯥ ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ ꯍꯥꯌꯅꯥ ꯈꯉꯅꯕꯥ ꯂꯪꯁ ꯁꯣꯀꯄꯥ ꯑꯁꯤꯅꯤ ꯫ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯦꯡꯅꯒꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯇꯁꯦꯡꯕꯗꯤ, ꯅꯨꯄꯤ ꯀꯌꯥꯅꯥ ꯂꯪꯁ ꯑꯦꯕꯁꯦꯁ ꯑꯃꯥ ꯂꯩꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯍꯣꯁ꯭ꯄꯤꯇꯥꯂꯗꯥ ꯊꯃꯖꯤꯜꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯍꯥꯅꯕꯥ ꯑꯣꯏꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯑꯇꯩ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯁꯨ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯂꯩꯕꯥ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯇꯥꯀꯄꯥ꯫
ꯂꯪꯁ ꯀꯣꯂꯥꯞꯁ (ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ) . ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ (cysts) ꯅꯥꯕꯥ ꯌꯥꯏ, ꯃꯗꯨꯅꯥ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯆꯦꯁ꯭ꯠ ꯋꯥꯜ (chest wall)ꯒꯤ ꯃꯔꯛꯇꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯅꯥ ꯈꯪꯍꯧꯗꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯈꯣꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯆꯥꯏꯂꯣꯁ ꯐ꯭ꯂꯨꯏꯗ ꯌꯥꯎꯕꯥ (Chylothorax) ꯂꯤꯝꯐ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯁꯉ꯭ꯒꯣꯃꯒꯤ ꯐ꯭ꯂꯨꯏꯗ (chyle) ꯑꯃꯅꯥ ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯈꯣꯃꯖꯤꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯁꯨ ꯑꯋꯥꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫
ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗ ꯑꯦꯛꯌꯨꯃꯨꯂꯦꯁꯟ (Pleural Effusion) ꯂꯪꯁꯄꯨ ꯀꯨꯄꯁꯤꯜꯂꯤꯕꯥ ꯃꯦꯝꯕ꯭ꯔꯦꯅꯁꯤꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯄ꯭ꯂꯨꯔꯦꯜ ꯐ꯭ꯂꯨꯏꯗ ꯅꯠꯇꯕꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗꯁꯤꯡ ꯊꯨꯒꯥꯌꯕꯥ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯉꯗꯣꯀꯄꯒꯦ?

ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯇꯥꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯍꯥꯛꯅꯥ ꯃꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯇꯧꯅꯕꯥ ꯑꯣꯔꯗꯔ ꯇꯧꯒꯅꯤ꯫

ꯗꯣꯛꯇꯔꯅꯥ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ꯫

  • ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯇꯦꯁ꯭ꯇꯁꯤꯡ: ꯃꯁꯤꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯦꯁꯤꯟ ꯑꯃꯒꯥ ꯁꯝꯅꯕꯥ ꯇꯤꯎꯕ ꯑꯃꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯀꯄꯥ ꯌꯥꯎꯏ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯁꯤꯡ ꯑꯗꯨ ꯀꯌꯥꯝ ꯐꯖꯅꯥ ꯊꯕꯛ ꯇꯧꯔꯤꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯀꯌꯥꯝ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯉꯝꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯂꯦꯄꯊꯣꯀꯄꯥ ꯉꯃꯒꯅꯤ꯫
  • ꯄꯂꯁ ꯑꯣꯛꯁꯤꯃꯦꯠꯔꯤ: ꯀ꯭ꯂꯤꯞ ꯑꯃꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯈꯨꯠꯂꯥꯏ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯗꯥ ꯌꯥꯎꯔꯤꯕꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯂꯦꯄꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯏꯆꯝ ꯆꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯋꯥꯕꯥ ꯂꯩꯇꯕꯥ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯤ꯫
  • ꯏꯃꯦꯖꯤꯡ ꯁ꯭ꯀꯦꯅꯁꯤꯡ: ꯱.
  • ꯁꯤ.ꯇꯤ.ꯁ꯭ꯀꯦꯟ (ꯀꯝꯞꯌꯨꯇꯦꯠ ꯇꯣꯃꯣꯒ꯭ꯔꯥꯐꯤ):ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯑꯀꯨꯞꯄꯥ 3D ꯏꯃꯦꯖꯁꯤꯡ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯅꯥ LAMꯒꯤꯗꯃꯛꯇꯥ ꯑꯀꯛꯅꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯈꯪꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • HRCT ꯁ꯭ꯀꯦꯟ (ꯍꯥꯏ-ꯔꯤꯖꯣꯂꯨꯁꯟ ꯀꯝꯞꯌꯨꯇꯦꯠ ꯇꯣꯃꯣꯒ꯭ꯔꯥꯐꯤ): ꯃꯁꯤ ꯁꯤ.ꯇꯤ. ꯃꯁꯤꯅꯥ ꯂꯪꯁꯀꯤ ꯌꯥꯝꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯔꯨꯛ ꯑꯃꯒꯤ ꯌꯥꯝꯅꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯕꯥ ꯏꯃꯦꯖꯁꯤꯡ ꯂꯧꯕꯥ ꯉꯝꯃꯤ꯫ ꯃꯁꯤ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡ ꯈꯉꯗꯣꯛꯅꯕꯒꯤꯗꯃꯛ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
  • VEGF-D ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: VEGF-D ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯏꯗꯥ ꯌꯥꯎꯕꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯅꯤ꯫ LAMꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯏꯗꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯂꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ ꯑꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯉꯗꯣꯀꯄꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • ꯂꯪꯁ ꯕꯥꯏꯑꯣꯞꯁꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯇꯩ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯑꯗꯨ 100% ꯁꯣꯌꯗꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯇꯦꯁ꯭ꯠ ꯇꯧꯅꯕꯒꯤꯗꯃꯛ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯒꯤ ꯌꯥꯝꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯇꯤꯁꯨ ꯑꯃꯥ ꯂꯧꯅꯕꯥ ꯋꯥꯔꯦꯞ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯁ꯭ꯀꯣꯄꯤ (ꯑꯦꯌꯔꯋꯦꯁꯤꯡꯗꯥ ꯀꯦꯃꯦꯔꯥ ꯑꯃꯥ ꯊꯥꯕꯥ ꯌꯥꯕꯥ ꯊꯤꯟ ꯇꯨꯕ ꯑꯃꯥ) ꯅꯠꯠꯔꯒꯥ ꯚꯤ.ꯑꯦ.ꯇꯤ.ꯑꯦꯁ.(ꯚꯤꯗꯤꯑꯣ-ꯑꯦꯁꯤꯁ꯭ꯇꯦꯗ ꯊꯣꯔꯥꯁꯤꯛ ꯁꯔꯖꯔꯤ) ꯀꯧꯕꯥ ꯊꯧꯑꯣꯡ ꯑꯃꯥ ꯁꯤꯖꯤꯟꯅꯗꯨꯅꯥ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯀꯔꯤꯅꯣ?

ꯑꯍꯥꯅꯕꯗꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯍꯤꯗꯥꯛ ꯂꯥꯡꯊꯛ ꯑꯃꯠꯇꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯐꯪꯗ꯭ꯔꯤ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯍꯧꯖꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯕꯥ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯊꯦꯡꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯌꯥꯝꯅꯥ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯂꯩꯔꯦ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ . ꯃꯁꯤꯕꯨ ꯔꯦꯄꯥꯃꯥꯏꯁꯤꯟ ꯍꯥꯌꯅꯥꯁꯨ ꯀꯧꯏ꯫ ꯃꯁꯤꯒꯤ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯕꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯆꯥꯎꯈꯠꯄꯥ ꯊꯤꯡꯗꯨꯅꯥ ꯊꯕꯛ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯆꯥꯎꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯃꯒꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯂꯩꯕꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯗꯁꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯏ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ: ꯁꯤꯔꯣꯂꯤꯃꯁꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯈꯔꯗꯤ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯀꯤꯗꯅꯤꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏꯅꯐꯦꯛꯁꯅꯁꯤꯡꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯍꯧꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯀꯥꯟꯅꯕꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯣꯡꯊꯤꯕꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯟꯅ-ꯅꯩꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯅꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡꯁꯨ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯕꯥ ꯌꯥꯏ꯫

  • ꯑꯣꯛꯁꯤꯖꯦꯟ ꯊꯦꯔꯥꯄꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯝꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯌꯨꯃꯗꯥ ꯁꯤꯖꯤꯟꯅꯅꯕꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯇꯦꯉ꯭ꯀꯁꯤꯡ ꯄꯤꯔꯤ꯫
  • ꯏꯅꯍꯦꯜ ꯇꯧꯔꯕꯥ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯗꯤꯂꯦꯇꯔꯁꯤꯡ: ꯏꯅꯍꯦꯂꯔ ꯑꯃꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯄꯤꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯄꯂꯃꯣꯅꯥꯔꯤ ꯔꯤꯍꯦꯕꯤꯂꯤꯇꯦꯁꯟ: ꯃꯁꯤ ꯂꯪꯁꯀꯤ ꯑꯈꯟꯅꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯄ꯭ꯔꯣꯒ꯭ꯔꯥꯝ ꯑꯃꯒꯨꯝꯅꯥ ꯑꯣꯏ꯫ ꯃꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯅꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯍꯦꯅꯒꯠꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
  • ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯥ: ꯱.ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯆꯥꯎꯈꯠꯂꯛꯂꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯣꯞꯄꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯃꯠꯇꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ ꯃꯇꯃꯗꯥ, ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯑꯁꯤ ꯑꯔꯣꯏꯕꯥ ꯑꯣꯄꯁꯟ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯍꯦꯅꯒꯠꯂꯛꯂꯤꯕꯅꯣ?

ꯃꯁꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯒꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯈꯦꯠꯅꯩ꯫ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯇꯧꯕꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯐꯦꯛꯇꯔ ꯀꯌꯥꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫

  • ꯅꯍꯥꯛꯅꯥ ꯂꯩꯔꯤꯕꯥ LAMꯒꯤ ꯃꯈꯜ: ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ TSC-LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯈꯔꯥ ꯍꯟꯊꯕꯥ ꯌꯥꯏ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯆꯍꯤ: ꯅꯨꯄꯤ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯇꯨꯡꯗꯥ, ꯍꯀꯆꯥꯡꯗꯥ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯑꯗꯨ ꯊꯤꯡꯖꯤꯜꯂꯤ ꯅꯠꯠꯔꯒꯥ ꯍꯟꯊꯔꯀꯏ꯫
  • ꯂꯥꯏꯌꯦꯡꯕꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯔꯦꯁꯄꯣꯟꯁ: ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫

ꯐꯤꯚꯝ ꯑꯁꯤ ꯃꯃꯥꯡꯉꯩꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯟꯅꯥ ꯐꯔꯦ ꯫ ꯃꯣꯗꯔꯟ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ 90% ꯍꯦꯅꯕꯗꯤ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 10ꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯤꯡꯂꯤ꯫ ꯃꯤꯑꯣꯏ ꯀꯌꯥ (ꯆꯥꯎꯔꯥꯛꯅꯥ 64%)ꯗꯤ ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯆꯍꯤ 20 ꯅꯠꯠꯔꯒꯥ ꯃꯁꯤꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯍꯤꯡꯕꯥ ꯉꯝꯃꯤ꯫

ꯀꯗꯥꯏꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯒꯗꯒꯦ ꯑꯃꯁꯨꯡ ꯏ.ꯇꯤ.ꯌꯨ

LAMꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯉꯩꯗꯥ, ꯀꯗꯥꯏꯗꯥ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯒꯗꯒꯦ ꯑꯃꯁꯨꯡ ꯀꯗꯥꯏꯗꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯗꯤꯄꯥꯔꯇꯃꯦꯟꯇ (ETU)ꯗꯥ ꯆꯠꯀꯗꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯈꯪꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯈꯨꯗꯣꯡꯆꯥꯕ ꯀꯔꯤ ꯇꯧꯒꯗꯒꯦ꯫
ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯕꯤꯌꯨ...
ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯀꯣꯛ ꯆꯤꯀꯄꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯂꯤꯕꯥ ꯎꯔꯕꯗꯤ꯫
ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯍꯪꯁꯤꯡ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯧꯔꯤꯕꯥ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯑꯗꯨꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯍꯪ ꯑꯃꯍꯦꯛꯇꯥ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯀꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯈꯜ ꯇꯥꯔꯕꯗꯤ꯫
ꯈꯨꯗꯛꯇꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇ ꯌꯨꯅꯤꯠ (ꯏ.ꯇꯤ.ꯌꯨ.)ꯗꯥ ꯆꯠꯂꯨ...
ꯂꯪꯁ ꯑꯦꯛꯁꯞꯂꯣꯁꯅꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫

  • ꯈꯪꯍꯧꯗꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯅꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯁꯥꯊꯤꯕꯥ, ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ꯫
  • ꯏ ꯊꯣꯀꯄꯥ꯫
  • ꯂꯤꯞ, ꯈꯣꯡ ꯅꯠꯠꯔꯒꯥ ꯅꯥꯀꯣꯡꯗꯥ ꯕ꯭ꯂꯨ ꯗꯤꯁꯀꯂꯔ ꯑꯣꯏꯕꯥ (cyanosis)꯫

ꯃꯤꯑꯣꯏ ꯈꯔꯅꯥ ꯂꯝ ꯑꯁꯤ ꯀꯦꯟꯁꯔꯅꯤ ꯍꯥꯌꯅꯥ ꯍꯪꯏ꯫ LAM ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯀꯦꯟꯁꯔ ꯍꯥꯌꯅꯥ ꯂꯧꯅꯗꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯑꯣꯡ ꯈꯔꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯃꯐꯝ ꯑꯃꯗꯒꯤ ꯂꯪꯁꯇꯥ ꯂꯥꯀꯄꯒꯤ ꯃꯑꯣꯡ ꯑꯁꯤꯅꯆꯤꯡꯕꯗꯥ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯀꯦꯟꯁꯔꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯃꯒꯨꯟ ꯂꯩ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯕꯗꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯒꯥ ꯃꯥꯟꯅꯗꯦ꯫

ꯅꯍꯥꯛꯅꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯄꯨꯟꯁꯤꯗꯥ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯕꯥ ꯈꯪꯂꯕꯥ ꯃꯇꯃꯗꯥ ꯁꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯅꯣꯔꯃꯦꯂꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯅꯍꯥꯛ ꯈꯛꯇꯅꯥ ꯅꯠꯇꯦ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯁꯤꯡ, ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯃꯔꯨꯄꯁꯤꯡꯒꯤ ꯃꯇꯦꯡꯅꯥ ꯅꯍꯥꯛꯅꯥ ꯁꯤꯡꯅꯕꯥ ꯑꯁꯤ ꯃꯥꯌꯣꯛꯅꯕꯒꯤ ꯄꯥꯉ꯭ꯒꯜ ꯐꯪꯒꯅꯤ꯫

ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫

  • LAM (Lymphangioleiomyomatosis) ꯍꯥꯌꯕꯁꯤ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯈꯣꯡꯗꯥ ꯑꯅꯥꯕꯥ, ꯑꯃꯁꯨꯡ ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ꯫
  • ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ ꯑꯁꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯃꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯍꯧꯗꯅꯥ, ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯊꯦꯡꯅꯔꯕꯗꯤ, ꯈꯨꯗꯛꯇꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯔꯨꯃꯗꯥ ꯆꯠꯂꯨ꯫
  • ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯐꯍꯅꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯁꯨ, ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯀꯄꯨ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯕꯥ ꯄꯨꯟꯁꯤ ꯑꯃꯥ ꯍꯤꯡꯕꯥ ꯉꯃꯍꯜꯂꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ, ꯂꯥꯏꯌꯦꯡ ꯅꯠꯠꯔꯒꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯑꯃꯨꯛꯇꯪ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯗꯥ ꯀꯩꯗꯧꯉꯩꯗꯥ ꯂꯥꯡꯇꯛꯅꯒꯅꯨ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ., ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ, ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ, ꯁꯤꯔꯣꯂꯤꯃꯁ, ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ, ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯂꯥꯌꯅꯥ꯫
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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