Wakamboona here, kana kusangana nekuzvimba kamwe kamwe kwerumwe rutivi rwechiso chako, muromo wakazvimba, kunzwa kunhuhwirira kune rumwe rutivi rwechiso chako, kana kutsemuka kusinganzwisisike mururimi rwako? Izvi zvingasava chiitiko chemazuva ese. Zvingave zviratidzo zvechirwere chisingawanzoitiki chatiri kuda kutaura nezvacho.
Chii chinonzi Melkersson-Rosenthal Syndrome?
Zvakanaka, ngatitarisei kuti Melkersson-Rosenthal Syndrome chii, kana kuti MRS muchidimbu. Zvichitaurwa zviri nyore, chirwere chetsinga chisingawanzoitiki. Kureva kuti, chinonyanya kukanganisa sisitimu yetsinga muchiso chedu. Zviratidzo zvikuru zvechirwere ichi kuzvimba kwechiso, kuputika kusinganzwisisike mururimi (senge migero yakadzika), uye kuoma mitezo kwechiso, kunova kurasikirwa nebasa kune rimwe kana divi rese rechiso. Fungidzira, kamwe kamwe, kona yemuromo inodonhedzwa pasi uye haugone kuvhara maziso ako zvakanaka.
Dambudziko iri rekuti 'MRS' dzimwe nguva rinogona kuva chiratidzo chechirwere cheramangwana, chakadai sechirwere cheCrohn (chirwere chisingaperi chekuzvimba kwemudumbu) kana sarcoidosis (chirwere chinokonzera mapundu madiki, akazvimba muzvikamu zvakasiyana zvemuviri). Vanachiremba dzimwe nguva vanodana chirwere ichi kuti `Orofacial Granulomatosis` . Idambudziko rinokonzera mapundu madiki, ane mapundu anonzi granulomas, ayo anoperekedzwa nekuzvimba kumeso nemuromo.
Ndiani anogona kuva nechirwere ichi che'MRS'? Chinowanzoitika sei?
Zvino ungave uchifunga kuti, "Ndiani anogona kubatwa nechirwere ichi?" Kutaura zvazviri, chirwere ichi chinonzi `MRS` chinogona kukura chero pazera ripi zvaro. Zvisinei, chinowanzoitika kune vechidiki, kazhinji vari mumakore avo ekutanga ekuma20, apo zviratidzo zvinotanga kuoneka.
Asi kana zvasvika pakuti chirwere ichi chakajairika sei, MRS chirwere chisingawanzoitiki . Zvinonzi chinokanganisa vanhu vashoma, vanenge 0.08%. Asi masayendisiti anotenda kuti nekuda kwekuti zviratidzo zvacho zvakafanana nezvimwe zvirwere, panogona kunge paine vanhu vakawanda vasati vaonekwa kuti vane chirwere ichi. Izvi zvinoreva kuti panogona kunge paine vanhu vakawanda vanotambura nechirwere ichi kupfuura nhamba iyi. Saka kana uine zviratidzo zvakaita seizvi, usarega kufunga kuti, "Izvi zvinoitika kuvanhu vashoma, hapana nzira yandingazviwana nayo." Chinhu chakakosha kutsvaga mazano ekurapa.
Ndezvipi zvinokonzera `MRS`?
Zvakanaka, ngationei kuti chii chinokonzera chirwere ichi che 'MRS'. Kutaura chokwadi, masayendisiti haasati akwanisa kuwana chikonzero chaicho . Asi pane zvinhu zvishoma zvinofungidzirwa kuti zvinokonzera chirwere ichi:
- Chirwere cheCrohn: Sezvandambotaura, ichi chirwere chisingaperi chekuzvimba kwemudumbu. Zvakaonekwa kuti vanhu vane chirwere ichi vari panjodzi huru yekubatwa nechirwere cheMRS.
- Kugara nhaka kwemajini: Izvi zvinoreva kuti inogona kupfuudzwa kubva kuchizvarwa kuenda kune chimwe chizvarwa. Kana mumwe munhu mumhuri akambova nechirwere ichi, ichocho chingavewo chikonzero. Asi izvi hazvisati zvaratidzwa.
- Kunzwa kwakanyanya kwemuviri: Apa ndipo apo masoja emuviri wedu anopindura zvakanyanya kune chimwe chinhu (chatinodaidza kuti 'antigen' kana kuti 'allergen' - zvichireva kuti chinogona kunge chiri chinhu chinokonzera allergy). Zvakafanana neallergy, asi zvakaoma zvishoma.
- Sarcoidosis: Ichi chirwere chinokonzerawo mapundu madiki (granulomas) muzvikamu zvakasiyana zvemuviri. Chirwere ichi chinofungidzirwawo kuti chine chekuita neMRS.
- Utachiona hwemavhairasi kana hwebhakitiriya: Pane vamwe vanofunga kuti chirwere ichi chinogona kuitika dzimwe nguva mushure mehutachiona hunokonzerwa nehutachiona kana bhakitiriya.
Ko `MRS` chirwere cheAutoimmune (chirwere chemuviri)` here?
Zvino vamwe vanhu vangave vachishamisika kuti, "Ichi chirwere cheAutoimmune here?" Kureva kuti, chirwere chemuviri wedu chinorwisa masero edu ane hutano here? Kutaura zvazviri, 'MRS' haionekwi sechirwere cheAutoimmune.
Izvi zvinorongwa sechirwere chetsinga . Izvi zvinoreva kuti idambudziko reuropi kana tsinga. Zvinonziwo chirwere chegranulomatous . Izvi zvinoreva kuti ichirwere chisingaperi, chakazvimba, chine mapundu (granuloma) chinoumbwa munyama dzemuviri. Wanzwisisa here? Saka hachiwire zvakananga muchikamu che "autoimmune."
Ndezvipi zviratidzo zve `MRS`?
Zvakanaka, ngatitarisei zviratidzo zvechirwere ichi che'MRS', kana kuti chirwere che'(Orofacial Granulomatosis)' chandambotaura. Pane zviratidzo zvikuru zvitatu zvinoonekwa mune izvi. Izvi zvinonzi 'classic triad of symptoms' .
1. Kuoma kwechiso: Ichi chirwere apo pane kushaya simba kana kuti kusanzwa kune rumwe rutivi rwechiso, dzimwe nguva kumativi ese. Izvi zvingasavepo pakutanga, asi zvinogona kuonekwa mumatanho ekupedzisira. Sezvo chirwere ichi chichienderera mberi, nguva yekuoma uku inogona kuwedzera. Fungidzira, kamwe kamwe usingakwanise kufambisa rumwe rutivi rwemuromo wako, uchinetseka kuvhara maziso ako, kana kuti kona yemuromo wako ichibuda mvura paunenge uchinwa mvura.
2. Kuzvimba kwechiso: Vanhu vane MRS vanowanzozvimba pachiso (Orofacial edema). Kuzvimba kwemiromo (Cheilitis granulomatosis) kunowanzoitika. Muromo wepamusoro unowanzozvimba pamberi pemuromo wepazasi. Miromo inogona kunge yakaoma, yakatsemuka, ichirwadza, uye inogona kutotsvuka-tsvuku. Mune vamwe vanhu, miromo inogona kuoma sedombo. Kwete miromo chete, asiwo matama, maziso emaziso, uye dzimwe nguva kunyange ganda remusoro rinogona kuzvimba. Kuzvimba uku kunogona kuwedzera uye kugara kwenguva yakareba sezvo chirwere ichi chichidzoka.
3. Rurimi rwakakamurwa:Izvi zvinokonzera matombo akadzika, akaita semigero pamusoro perurimi. Vanachiremba vanodanawo kuti "Scrotal tongue" kana kuti "Lingua plicata". Izvi hazviwanzo rwadza, asi vamwe vanhu vanogona kuzvimba, kuvaviwa, uye kunzwa kupisa parurimi. Zvinogonawo kukonzera kurasikirwa nekuravira uye kutungamira kuzvirwere zvemuromo.
Chinhu chakakosha ndechekuti havasi vese vane hunhu uhu hutatu. Vamwe vanhu vanogona kunge vaine hunhu humwe chete kana huviri hwehunhu uhu. Vamwe vanogona kunge vaine hunhu uhu hutatu.
Zviratidzo izvi hazvigari nguva dzose. Zvinouya zvoenda. Kekutanga, zvinogona kungotora maawa mashoma chete . Asi kana zvikazodzoka gare gare, zvinogona kunge zvakanyanya uye zvichitora nguva yakareba.
Zvimwe zviratidzo
Kuwedzera kune zviratidzo zvikuru izvi, panogona kunge paine zvimwe zviratidzo zvakawanda:
- Dzungu
- Musoro wemusoro unonzi migraine
- Kurira munzeve (tinnitus) kana kurasikirwa nekunzwa
- Kana chirwere chacho chanyanya uye chapora, dzimwe nguva mavanga anogona kuoneka pachiso .
- Kuoma kumedza
- Matambudziko ekuona: Maziso akaoma, kuona zvisipo, uye kuzvimba kwemaziso (uveitis).
MRS inoonekwa sei?
Zvino ungave uchishamisika kuti, "Ndingaziva sei kuti iyi i 'MRS'?" Kutaura zvazviri, 'MRS' yakaoma kuziva. Nekuti zviratidzo zvayo zvinogona kuvhiringidzwa nezvimwe zvirwere. Semuenzaniso, zviratidzo zvayo zvinogona kunge zvakafanana ne 'Allergic reactions' kana 'Bell's palsy', chimwe chirwere chinokonzera kuoma mitezo pachiso.
Chiremba anowanzo ongorora MRS nekutarisa nhoroondo yako kana uine zviratidzo zviviri kubva pazviratidzo zvitatu zvandambotaura. Dzimwe nguva, kuti usimbise chirwere uye kubvisa zvimwe zvirwere, chidimbu chidiki chenyama kubva pamuromo wako chinogona kutorwa kuti chiongororwe (biopsy). Izvi zvinotarisa kuvapo kwegranulomas.
Zvakare, chiremba anogona kukutumira kune dzimwe nyanzvi dzakawanda, sezvo izvi zvichigona kukanganisa masisitimu akasiyana-siyana. Izvi zvinosanganisira:
- Chiremba wezvirwere zveallergy
- Chiremba weganda
- Chiremba weGastroenterologist - Tarisa zvinhu zvakaita sechirwere cheCrohn.
- Chiremba wezvirwere zvemuviri
- Chiremba wemaziso
Pane mushonga we 'MRS' here? Ndeapi marapirwo aripo?
Zvakanaka, mubvunzo mukuru une vanhu vazhinji pari zvino ndewekuti, "Pane mushonga wakakwana wechirwere ichi che 'MRS' here?" Zvinosuwisa kuti hapana mushonga chaiwo we 'MRS' parizvino.
Dzimwe nguva zviratidzo zvinopera pasina kurapwa, asi zvinogona kudzoka zvakare.
Saka, unorapwa sei? Kana zviratidzo zvikadzoka uye zvichinetsa, kune nzira dzakawanda dzekurapa dzinogona kubatsira kuderedza marwadzo, kudzivirira hutachiona, uye kugadzirisa chitarisiko. Dzinosanganisira:
- Mishonga inorwisa mabhakitiriya: Kana paine hutachiona hwebhakitiriya.
- Mishonga inorwisa mabhakitiriya: Inoderedza zviratidzo zvakaita seallergy uye kuzvimba.
- Corticosteroids: Iyi mishonga ine simba inoderedza kuzvimba nekuzvimba. Inogona kupihwa sejekiseni zvakananga munzvimbo yakazvimba, kana semapiritsi.
- Mishonga inodzvinyirira muviri: Iyi inobatsira kuderedza kuzvimba nekudzora zvishoma mashandiro emuviri wemuviri.
- Methotrexate: Uyu mushonga unodzorawo dziviriro yemuviri uye unoderedza kuzvimba.
- Mishonga isingashandisi masteroidal anti-inflammatory (NSAIDs): Inoderedza marwadzo nekuzvimba (semuenzaniso, Ibuprofen, Diclofenac).
- Kuvhiyiwa: Dzimwe nguva kuvhiyiwa kunogona kuitwa kuderedza kuzvimba kwemiromo yakazvimba zvakanyanya kana kuderedza kumanikidzwa kwetsinga dzechiso. Zvisinei, izvi hazviwanzoitwa.
- Mishonga inodzivirira TNF-alpha: Iyi mishonga inobatsirawo kumisa kuzvimba. Inowanzo pihwa kana mimwe mishonga isingashande.
Mishonga iyi yakagadzirirwa kudzora zviratidzo uye kuderedza kusagadzikana. Chiremba wako ndiye achasarudza mushonga wakakunakira.
Ko chirwere che 'MRS' chinogona kudzivirirwa here?
Dambudziko iri rekuti 'MRS' rinogona kudzivirirwa here? Kutaura zvazviri, sezvo masayendisiti asati anyatsonzwisisa zvinokonzera izvi, hapana nzira yakasimbiswa yekudzivirira. Saka, tinofanira kutarisa pakuziva zviratidzo nekukurumidza uye kutsvaga kurapwa kwakakodzera.
'MAI' vachapora sei? Vachapora here?
Remangwana remunhu ane MRS rakamira sei? Izvi zvinosiyana kubva pamunhu nemunhu. Vamwe vanhu vane zviratidzo zvishoma, senge kamwe chete mumakore mashoma, uye zvinopera zvega. Kune vamwe, zviratidzo zvinogona kuoneka kakawanda, senge mazuva mashoma ega ega, uye zvinogona kuwedzera nguva imwe neimwe.
Dambudziko iri rinogona kuva rehupenyu hwese, uye kuzvimba kunogona kugara kwenguva refu. Asi masayendisiti haafungi kuti chirwere ichi chinokanganisa hupenyu hwese. Izvi zvinoreva kuti unogona kurarama hupenyu hwakajairika nacho, asi unofanira kurarama nezviratidzo zvacho. Saka, kuramba wakasimba mupfungwa kwakakoshawo.
Mibvunzo yekubvunza chiremba wako
Kana uine Melkersson-Rosenthal Syndrome, kana kuti uchifungidzira kuti unayo, zvakanaka kubvunza chiremba wako mibvunzo iyi:
- Ungati sei nechokwadi kuti iyi ndiyo Melkersson-Rosenthal Syndrome? Hazvingave chimwe chinhu here?
- Ndedzipi dzimwe nyanzvi dzandinofanira kuona? (semuenzaniso, chiremba weganda, chiremba wetsinga, nezvimwewo)
- Kana zviratidzo zvikadzoka, ndinofanira kutsvaga rubatsiro rwechiremba riini? Ndezvipi zviratidzo zvandinofanira kunyanya kunetseka nazvo?
- Ndinofanira kuongororwa chirwere cheCrohn kana sarcoidosis here?
- Ndingaitei kuti ndidzivirire hutachiona, kuzvimba kusingaperi, uye mavanga?
- Munokurudzira kuongororwa kwemajini here? Zvingakuudzai chii?
- Pane mapoka ekutsigirana anobatsira vanhu vane zvirwere izvi here? Pane zvakanakira here kuti ndipinde maari?
Saka, ndezvipi zvinhu zvakakosha zvatinofanira kuyeuka kubva munyaya iyi?
Melkersson-Rosenthal Syndrome (MRS) chirwere chisingawanzoitiki chinokanganisa tsinga dzechiso. Kana ukasangana nekuzvimba kwechiso kamwe kamwe, kuoma mitezo yechiso, kana kutsemuka kusinganzwisisike mururimi rwako, unofanira kuona chiremba.
Kunyangwe pasina mushonga chaiwo weizvi, kune mishonga inoshanda yekudzora zviratidzo, kuderedza kusagadzikana, uye kudzivirira matambudziko. Saka usazvidya mwoyo. Nekuonekwa nekukurumidza uye kurapwa kwakakodzera, unogona kurarama zvakanaka nechirwere ichi. Hausi wega, uye vanachiremba vako nevadikanwi vanogona kukubatsira.
Chirwere cheMelkersson -Rosenthal, MRS, kuzvimba kwechiso, kuoma mitezo yechiso, rurimi rwakatsemuka, neuropathy, granulomatosis yemuromo











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