So woate mogya mu nhwehwɛmu bi a wɔfrɛ no ‘Ceruloplasmin’ ho asɛm pɛn? Ebia wo duruyɛfo aka wo sɛ yɛ nhwehwɛmu yi, anaasɛ ebia obi a ɔwɔ w’abusua mu ama wɔayɛ. Ɛyɛ ade a ɛfata sɛ wobɛte nka sɛ w’adwene atu afra kakra bere a wote saa din yi no. Ebia wowɔ nsɛmmisa pii wɔ w’adwene mu, te sɛ nea ɛhwehwɛ, so asiane ahorow bi wɔ eyi a wobɛyɛ mu, ne nea amanneɛbɔ no bɛka. Enti mma ɛnhaw wo. Ɛnnɛ, yɛbɛka Ceruloplasmin sɔhwɛ yi ho asɛm wɔ ɔkwan a ɛyɛ mmerɛw yiye so, wɔ ɔkwan a wubetumi ate ase so.
Nea edi kan no, ma yɛnhwɛ, dɛn ne Ceruloplasmin?
Sɛ yɛbɛka no tiawa a, ceruloplasmin yɛ protein bi a ɛwɔ yɛn nipadua mu. mmerɛbo, akwaa a ɛho hia paa wɔ yɛn nipadua mu no na ɛyɛ. Adwuma titiriw a protein yi yɛ ne sɛ ɛde kɔbere, ade a ɛho hia ma yɛn nipadua no, fa mogya no mu kɔ mmeae a ɛho hia wɔ nipadua no mu nyinaa. Eyi te sɛ bɔs a ɛde akwantufo kɔ kurow no mu nyinaa.
Saa kɔbere yi ho hia yɛn nipadua paa.
- Yɛ ahoɔden ma nipadua no.
- Kura yɛn nnompe akwahosan mu.
- Yɛ aduru a wɔfrɛ no melanin a ɛma yɛn honam ani, yɛn ani, ne yɛn ti nhwi kɔla.
- Afei nso, saa protein yi boa ma yɛyɛ dade a yenya fi nnuan a yedi mu no ho adwuma ma ɛyɛ nea yebetumi de adi dwuma.
Enti wubetumi ahu sɛnea ɛho hia sɛ protein a wɔfrɛ no ceruloplasmin yi yɛ adwuma yiye wɔ yɛn nipadua mu. Sɛ ne dodow sua anaasɛ ɛkɔ soro a, ɛkyerɛ sɛ ebia ɔhaw bi wɔ nipadua no mu.
Dɛn nti na oduruyɛfo bi bɛkamfo nhwehwɛmu yi akyerɛ?
Nneɛma pii nti na oduruyɛfo betumi ahyɛ sɛ wɔbɛyɛ nhwehwɛmu yi. Ade titiriw a ɛtaa ba ne sɛ wobesi awosu mu tebea bi a wosusuw sɛ wɔfrɛ no Wilson yare no so dua .
Dɛn ne Wilson yare no?
Eyi yɛ awosu mu tebea a ɛntaa nsi nanso ɛyɛ aniberesɛm. Obi a ɔwɔ saa yare yi ntumi nni kɔbere a ɛwɔ ne nipadua mu no ho dwuma yiye. Mpɛn pii no, yɛn mmerɛbo no nam bile so yi kɔbere a ɛboro so fi nipadua no mu. Nanso wɔ obi a ɔwɔ Wilson yare no mu no, saa adeyɛ yi ntumi nyɛ adwuma yiye. Ne saa nti, kɔbere fi ase boaboa ano wɔ mmerɛbo, amemene, aniwa, ne akwaa afoforo mu. Eyi betumi de nkwa ato asiane mu.
Ade a ɛyɛ nwonwa a ɛkɔ so wɔ yare yi mu ne sɛ kɔbere dodow a ɛwɔ ɔyarefo no mogya mu no sua , bere a kɔbere dodow a ɛwɔ nsu mu no dɔɔso yiye . Afei nso, mpɛn pii no, ceruloplasmin dodow no sua.
Nea ɛka ho no, kɔbere a enni nipadua no muWɔyɛ sɔhwɛ yi nso wɔ nsɛm a wosusuw sɛ kɔbere nni mu no mu. Nneɛma pii wɔ hɔ a ebetumi ama kɔbere a enni nipadua no mu aba.
- Malabsorption: Nnipa binom ntumi nnye aduannuru a ɛwɔ aduan a wodi mu no yiye esiane dwensɔtwaa mu nyarewa nti.
- Aduan pa a wonnya nni: Nipadua no nnya kɔbere a ehia esiane aduan a ɛkari pɛ a enni nti.
- Menkes yare: Eyi nso yɛ awosu mu yare a ɛntaa nsi koraa. Wɔ saa yare yi mu no, nipadua no ntumi nnye kɔbere.
- Total parenteral nutrition (TPN): Wɔnam ntini bi so ma nnipa a wontumi nnidi wɔ ano esiane ayaresa tebea bi nti. Ɛtɔ mmere bi a, ebia kɔbere dodow a ɛwɔ mu no sua.
- Zinc a wɔnom boro so: Sɛ obi di nnuan anaa nneɛma a wɔde ka ho a zinc wom pii a, ebetumi asiw kɔbere a ɛbɛtwe afi dwensɔtwaa no mu no ano.
Nsɛnkyerɛnne bɛn na ebetumi ama woahia nhwehwɛmu yi?
Oduruyɛfo nkyerɛw sɔhwɛ bi kɛkɛ. Wɔbɛgyina wo sɛnkyerɛnne ne w’abusua abakɔsɛm so ahyɛ nhwehwɛmu yi. Sɛ wowɔ sɛnkyerɛnne ahorow a wɔabobɔ din wɔ ase ha no bi a, wo duruyɛfo betumi ahyɛ sɛ wɔnyɛ ceruloplasmin nhwehwɛmu.
| Ayaresa tebea a wosusuw sɛ ɛwɔ hɔ | Nsɛnkyerɛnne a ɛtaa ba |
|---|---|
| Wilson yare no |
|
| Kɔbere a Ɛho Hia |
Sɔhwɛ no yɛ mmerɛw yiye, nsuro!
Eyi te sɛ mogya mu nhwehwɛmu foforo biara a wɔyɛ no daa. Wobetumi awie wɔ simma kakraa bi mu.
1. Nea edi kan no, phlebotomist no de elastic band (tourniquet) bɛtwa wo nsateaa anaa wo nsa akyi ho ahyia na ama woahu ntini pa.
2. Afei, wɔde aduru a ekum ɔyare mmoawa hohoro baabi a wɔde ade no ahyɛ mu no yiye.
3. Afei, wɔde ade ketewaa bi hyɛ ntini no mu na wɔboaboa mogya dodow a ɛho hia ano gu toa ketewa bi mu.
4. Awiei koraa no, woyi ade no, wɔde kotoku bi gu baabi a ɛwɔ hɔ, na wɔde plaster ketewaa bi gu so.
Nnipa binom wɔ suro kakra wɔ nnade ho, ɛnte saa? Ɛtaa ba paa. Sɛ wowɔ ehu a ɛte saa a, di kan ka kyerɛ onipa a ɔtwe wo mogya no. Afei wɔbɛboa wo. Wubetumi atew ehu yi so denam nneɛma te sɛ nea worenhwɛ ade no na wohome brɛoo no so.
Wɔsɔ mogya a wɔfa saa kwan yi so no fã a ɛyɛ nsu a wɔfrɛ no plasma no hwɛ. Eyi nti, wɔde afiri (centrifuge) di dwuma wɔ aduruyɛdan mu de yiyi mogya no mu nneɛma mu.
So ahosiesie titiriw bi wɔ hɔ a ehia ansa na wɔayɛ sɔhwɛ no?
Dabi, ahosiesie titiriw biara nni hɔ a ɛho hia ma sɔhwɛ yi. Wubetumi adidi na woanom sɛnea ɛsɛ. Nanso afotu bi ni: Nom nsu pii ansa na woayɛ mogya mu nhwehwɛmu biara. Eyi bɛboa ma wo nipadua no anya nsu, na ama ayɛ mmerɛw sɛ wubenya ntini bi na ama ayɛ mmerɛw sɛ wobɛma mogya.
Dɛn na sɔhwɛ no mu aba ka?
Eyi ne asɛmmisa kɛse a ɛwɔ obiara adwene mu. Mma wo ho nnpopo bere a woanya w’amanneɛbɔ no na woahwɛ nɔma ahorow no. Onipa a obetumi ate ase yiye ne wo duruyɛfo. Efisɛ "Normal Range" a ɛwɔ amanneɛbɔ no so mpo betumi ayɛ soronko kakra a egyina nneɛma te sɛ wo mfe, wo bɔbeasu, sɛ ebia woanyinsɛn, anaasɛ sɛ wode awo ano aduru redi dwuma so.
Mpɛn pii no, ebia wo ceruloplasmin dodow bɛyɛ nea ɛba fam, ɛyɛ nea ɛfata, anaasɛ ɛkɔ soro.
| Nsunsuansoɔ | Nea ebetumi akyerɛ |
|---|---|
| Sɛ ceruloplasmin dodow no sua sen sɛnea ɛte daa (ɛba fam)... | |
Eyi betumi akyerɛ sɛ wo nipadua no mfa kɔbere nni dwuma yiye. Eyi betumi afi:
Nanso, ɛtɔ mmere bi a eyi betumi akyerɛ kɔbere a enni nipadua no mu ara kwa, sen sɛ ɛbɛyɛ yare titiriw bi a ɛde ba. | |
| Sɛ ceruloplasmin dodow no boro sɛnea ɛte daa (ɛkɔ soro)... | |
Eyi betumi akyerɛ sɛ kɔbere pii wɔ nipadua no mu wɔ ɔkwan a ɛnteɛ so. Saa dodow yi nso kɔ soro bere a ɔfe, ɔyare mmoawa, anaa opira wɔ nipadua no mu no. Eyi betumi afi:
Ade a ɛho hia sen biara: Sɛ wo dodow kɔ soro a, ɛnkyerɛ bere nyinaa sɛ wowɔ yare a emu yɛ den. Enti mma wo ho nnpopo bere a woahu amanneɛbɔ no awie no, na akyinnye biara nni ho sɛ wo ne wo duruyɛfo nkasa ho asɛm. | |
Dɛn na ɛba akyi? So wopɛ sɛ wokɔ oduruyɛfo nkyɛn?
Yiw, koraa. Sɛ wo mogya mu nhwehwɛmu no ba wie a, ɛsɛ sɛ wode saa amanneɛbɔ no kɔma oduruyɛfo a ɔresa wo yare no. Ɔbɛsusuw wo yare no ho sɛnkyerɛnne, nea efi nhwehwɛmu afoforo mu ba, ne nea efi ceruloplasmin mu ba yi ho na waba awiei pɛpɛɛpɛ wɔ wo tebea no ho.
Ebia, ebia oduruyɛfo no gyina amanneɛbɔ yi so bɛka akyerɛ wo sɛ yɛ nhwehwɛmu foforo bi.
- Nsu mu nhwehwɛmu
- Mmɛn dwumadi ho nhwehwɛmu
- Mogya mu nhwehwɛmu afoforo
Sɛ adwenem naayɛ a emu yɛ den wɔ hɔ sɛ Wilson yare no wɔ hɔ a, wobetumi akamfo akyerɛ sɛ wɔnyɛ mmerɛbo mu nhwehwɛmu , na ɛntaa nsi koraa. Eyi betumi ama yɛahu sɛnea mmerɛbo no asɛe ne kɔbere dodow a ɛwɔ hɔ no ho mfonini pefee.
Sɛ wowɔ nsɛmmisa anaa nsɛm bi a ɛhaw wo wɔ nea ebefi mu aba no ho a, bisa oduruyɛfo no biribiara ho asɛm.
Nkrasɛm a Wɔde Kɔ Fie
- Ceruloplasmin yɛ protein a ɛho hia a mmerɛbo no yɛ a ɛde kɔbere kɔ nipadua no mu.
- Wɔde mogya mu nhwehwɛmu yi di dwuma titiriw de hu tebea horow te sɛ Wilson yare ne kɔbere a enni nipadua no mu.
- Eyi yɛ mogya mu nhwehwɛmu a ɛnyɛ den koraa, asiane nnim, a wɔyɛ no daa, enti ɛho nhia sɛ wosuro.
- Ɛnyɛ bere nyinaa na wo ceruloplasmin dodow, sɛ́ ɛyɛ nea ɛba fam anaasɛ ɛkɔ soro no, nkyerɛ sɛ wowɔ aduruyɛ mu tebea a emu yɛ den. Ebetumi nso asesa esiane nneɛma a ɛtaa de ba te sɛ nyinsɛn ne ɔyare mmoawa nti.
- Ade a ɛho hia sen biara ne sɛ, sɛ wo nsa ka wo sɔhwɛ ho amanneɛbɔ wie a, akyinnye biara nni ho sɛ ɛsɛ sɛ wo ne wo duruyɛfo hyia na wosusuw ho, sen sɛ wobɛbɔ mmɔden sɛ w’ankasa wobɛte ase.











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