So wunim saa nneɛma yi fa wo koma benkum so ahurututu no ho? (Left Ventricular Non-Compaction - LVNC) Momma yɛnkasa!

Ɛnnɛ yɛrebɛka koma no tebea bi a ɛyɛ den kakra, nanso ebetumi ayɛ nea ɛho hia yiye ho asɛm. Ebia wontee eyi ho asɛm da. Wɔfrɛ no Left Ventricular Non-Compaction (LVNC) sɛnea nnuruyɛfo frɛ no no. Ebia edin no bɛyɛ te sɛ asɛm kɛse, nanso mma ɛnhaw wo, momma yɛmma ɛnyɛ mmerɛw.

Enti dɛn ne benkum so ventricular noncongestive heart failure (LVNC)?

Sɛ yɛbɛka no tiawa a, eyi yɛ tebea a ɛba bere a yɛn koma no benkum so dan a ɛwɔ fam, Benkum Ventricle no nnyin yiye no. Susuw ho hwɛ, mpɛn pii no, yɛn koma benkum so ahurututu yi yɛ nam a ɛyɛ den yiye na ɛyɛ torotoro. Ɛyɛ ɔfã titiriw a ɛma mogya kɔ yɛn nipadua nyinaa mu. Nanso wɔ obi a ɔwɔ saa (LVNC) yi mu no, benkum so ahurututu no te sɛ ɔpon, ɛyɛ den kakra, na wɔahyehyɛ no te sɛ asau. Ɛwɔ nkoko so su, te sɛ abodoo mu.

Wɔtaa bu eyi sɛ komayare a wɔde awo obi. Wei kyerɛ sɛ ebia saa tebea yi wɔ wo komam fi bere a wɔwoo wo no . Sɛ wɔansa no yiye a, saa (LVNC) yi betumi de komayare a emu yɛ den aba, kyerɛ sɛ, komayare.

Ɔkwan bɛn so na LVNC tebea yi ka koma no dwumadi?

Afei hwɛ, yɛn koma benkum so ahurututu no wɔ adwuma bi a ɛho hia yiye. Ɛyɛ eyi na ɛma mogya a oxygen pii wom no fi ahurututu mu kɔ nipadua no nyinaa mu. Te sɛ nsu motor ara pɛ. Nanso, sɛ saa (LVNC) tebea yi ba a, benkum so ahurututu a ɛte sɛ ɔpon no ntumi ntwitwa anaasɛ ennye n’ahome yiye. Ɛne sɛ, ɛyɛ den ma no sɛ ɛbɛkyekyere mogya no na apia akɔ n’anim, anaasɛ ɛbɛma ahomegye na ɔde mogya ahyɛ mu ma bio. Enti, nea efi mu ba ne sɛ adwuma a ɛne sɛ wɔde mogya bɛkɔ nipadua no nyinaa mu no nkɔ yiye . Eyi nti na ɔhaw ahorow fi ase sɔre no.

Ɛho yɛ na dɛn na wɔfrɛ tebea yi LVNC?

Eyi yɛ tebea a ɛntaa nsi ankasa. Sɛnea aduruyɛ ho abenfo kyerɛ no, nnipa bɛyɛ dumien pɛ wɔ ɔpepem biako mu na wohu sɛ wɔwɔ saa yare yi afe biara. Nanso, ebia dodow ankasa no bɛboro saa koraa . Nea enti a ɛte saa ne sɛ nnipa binom nkyerɛ yare no ho sɛnkyerɛnne biara. Afei wɔnkɔ oduruyɛfo nkyɛn, na ɛno nti wonnya nhu sɛ wɔwɔ yare no.

Dɛn ne LVNC ho sɛnkyerɛnne ahorow?

Eyi ne ade a ɛho hia sen biara. Ebia nnipa binom renkyerɛ yare no ho sɛnkyerɛnne biara . Nanso, afoforo betumi anya komayare a emu yɛ den paa. Sɛ nhwɛso no, koma betumi awu mpofirim. Nnipa a wɔwɔ LVNC no mu bɛyɛ nkyem abiɛsa mu abien wɔ asiane mu sɛ wobenya komayare .

Okay, enti momma yɛnhwɛ sɛnkyerɛnne ahorow a obi a ɔwɔ (LVNC) betumi ada no adi:

Nsɛnkyerɛnne a wɔtaa hu:

• Mogya a ɛyɛ mmerɛw betumi ayɛ. Eyinom yɛ nea asiane wom kɛse, efisɛ sɛ mogya a ɛtɔ kɔ amemene no mu anaa ahurututu mu a, ebetumi ayɛ ɔhaw kɛse.
• Ebia ɛbɛyɛ den ama wo sɛ wobɛhome bere a woada mpa so no.
• Nnipa a wɔtotɔ piti .
• Koma a ɛbɔ - Eyi betumi ayɛ te sɛ sanku a ɛrebɔ wɔ koko no mu, anaasɛ ɛte sɛ nea koma no retu mmirika.
• Apɔw-mu-teɛteɛ a wontumi nyɛ, ahome a ɛyɛ tiaa bere a wɔabɔ mmɔden kakra mpo (Dyspnea) .
• Koma a ɛbɔ ntɛmntɛm (Arrhythmia) .
• (Lymphedema) - .
• Ahome tiaa / Dyspnea - Wote nka sɛ wo home ayɛ basaa wɔ mmɔdenbɔ ketewaa bi mpo mu.

Dɛn nti na LVNC tebea yi ba? Dɛn na ɛde ba?

Mpɛn pii no, saa (LVNC) tebea yi fi awosu mu nsakrae (Gene mutation) a ɛba ansa na wɔrewo wo. Eyi yɛ ade a ɛyɛ den yiye. Saa awosu mu nsakrae yi betumi aba kwa, a ɛkyerɛ sɛ ntease biara nnim, anaasɛ wobetumi anya afi w’awofo hɔ. Ɛno kyerɛ sɛ ebetumi ayɛ biribi a ɛkɔ so wɔ mmusua mu. Susuw ho hwɛ, mmusua bi wɔ komayare a ɛte sɛɛ a ɛdɔɔso.

Afei nso, mmea ɔha biara mu kakraa bi pɛ betumi anya LVNC nea edi kan wɔ nyinsɛn mu a ntease biara nnim. Nnuruyɛfo susuw sɛ ebia eyi fi nhyɛso kɛse a ɛba koma ntini no so bere a wɔyem no. Wɔ mmea binom fam no, saa sɛnkyerɛnne ahorow yi fi hɔ bere a wɔawo awie no. Nanso wɔ afoforo fam no, LVNC betumi anya nkɛntɛnso a ɛtra hɔ kyɛ.

Ɔkwan bɛn so na nnuruyɛfo hu LVNC tebea yi?

Oduruyɛfo bi bɛyɛ nhwehwɛmu ahorow pii de ahu sɛ ebia wowɔ saa (LVNC) tebea yi anaasɛ wunni bi pɛpɛɛpɛ. Momma yɛnhwɛ nea wɔyɛ:

• Echocardiogram: Eyi hwɛ sɛnea wo koma rebɔ mogya yiye, sɛnea ntini ahorow no reyɛ adwuma yiye, ne sɛ ebia ɔhaw bi wɔ ntini ahorow no mu anaa. Ɛte sɛ nea wɔde ultrasound scan yɛ koma no. Ɛha na wudi kan hu sɛnea benkum so ahurututu no te sɛ spongy no.
• Electrocardiogram (ECG): Eyi kyerɛ sɛnea wo koma no anyinam ahoɔden yɛ adwuma. Ebetumi ahu ɔhaw biara a ɛwɔ wo koma a ɛbɔ no mu.
• Mfoniniyɛ mu nhwehwɛmu titiriw: Eyinom bi ne koma mu CT mfonini ne magnetic resonance imaging (MRI). Eyinom betumi akyerɛ sɛnea wɔahyehyɛ koma no, te sɛ sɛnea wɔyɛɛ koma no ne sɛnea n’afasu no mu yɛ duru. Wɔ LVNC mu no, wotumi hu sɛnea ɛte sɛ sponge no pefee wɔ saa scan ahorow yi so.
• Coronary angiogram: Eyi hwehwɛ sɛnea mogya fa coronary ntini a ɛde mogya kɔ koma no mu no mu, ne sɛ ebia biribi asiw koma no mu anaa. Ɛtɔ mmere bi a, ebia sɔhwɛ yi nso ho behia na ama wɔatumi ayi komayare afoforo afi hɔ.

Dɛn ne ayaresa ahorow a wɔde sa LVNC tebea yi?

Ɛsono sɛnea wɔsa LVNC a egyina wo sɛnkyerɛnne ahorow so. Ɛnyɛ obiara na wɔne no di wɔ ɔkwan koro so. Sɛ nhwɛso no, sɛ wowɔ komayare a, wo duruyɛfo betumi akyerɛw wo nnuru te sɛ:

• Nnuru a esiw enzyme a ɛdannan angiotensin ano (nneɛma a esiw ACE ano): Sɛ nhwɛso no, benazepril (Lotensin®) anaa lisinopril (Prinivil®, Zestril®) anaa sacubitril-valsartan (Entresto®) (nnuru a esiw angiotensin-neprilysin ano). Eyinom yɛ adwuma denam wo mogya ntini (ntini ne ntini) a ɛma wo ho dwo na wobue mu ma ɛyɛ mmerɛw sɛ mogya bɛfa mu no so. Eyi ma adwuma a ɛda koma no so no so tew.
• Beta-blockers: Sɛ nhwɛso no, metoprolol (Lopressor®, Toprol XL®) anaa atenolol (Tenormin®). Eyinom siw hormone ahorow bi ano (e.g. adrenaline), na ɛma mogya mmoroso so tew na ɛhwɛ koma bɔ so.
• Digoxin (Digoxin®, Lanoxin®): Eyi hwɛ wo koma bɔ so, ɛma ahoɔden a wo koma bɔ no yɛ kɛse kakra, na ɛma mogya no tu mpɔn.
• Diuretics anaa "nsuo aduru": Eyinom yɛ adwuma denam nipadua no a ɛma nkyene ne nsu a ɛboro so fa nsu mu fi mu no so. Eyi ma ɔfe so tew na ɛtew adwuma a ɛwɔ koma no so no so.

Ɛtɔ mmere bi a, sɛ asiane wɔ hɔ sɛ koma no bɛtɔ mpofirim a, oduruyɛfo no betumi akamfo akyerɛ sɛ wɔmfa afiri bi a wɔfrɛ no Implantable Cardioverter Defibrillator (ICD) nhyɛ koma no honam ani. Eyi yɛ afiri ketewaa bi a wɔde batere na ɛyɛ adwuma. Ɛhu nnyigyei a ɛyɛ ntɛmntɛm a ɛde nkwa to asiane mu wɔ koma no mu na ɛde anyinam ahoɔden kɔ koma no mu ma ɛsan yɛ nnyigyei a ɛfata. Wɔ tebea horow a emu yɛ den yiye mu no, sɛ ayaresa afoforo antumi anyɛ yiye a, ebia ɛho behia sɛ wɔde koma foforo ma .

So wobetumi asa LVNC tebea yi koraa? So wobetumi adan no?

Oh dabi. Mprempren wonni aduru biara a wɔde sa LVNC . Ɛne sɛ, wontumi nsan n’akyi. Nanso mma ɛnhaw wo. Ayaresa betumi ama w'asetra atu mpɔn na atew nsɛnnennen a ebetumi aba esiane komayare nti no so . Na, sɛnea madi kan aka no, wɔ nsɛm a emu yɛ den sen biara mu no, ebia ɛho behia sɛ wɔde koma foforo ma.

Yɛbɛyɛ dɛn akwati saa LVNC tebea yi?

Ɔkwan biara nni hɔ a wɔbɛfa so asiw LVNC ano. Nea enti a ɛte saa ne sɛ mpɛn pii no, awosu mu nneɛma na ɛde ba. However, if you have the gene mutation that causes the condition, or if you think you may have it (for example, if someone in your family has the condition), genetic testing can be very helpful.Awosu ho ɔfotufo bi bɛkyerɛkyerɛ nea efii wo nhwehwɛmu mu bae mu akyerɛ wo ne w’abusua. Wɔbɛboa wo ama woate nea ɛkyerɛ sɛ wowɔ LVNC ne asiane a ɛwɔ wo mu sɛ wode bɛma wo mma no ase.

So aduruyɛ mu tebea afoforo bi wɔ hɔ a ɛbata LVNC tebea yi ho?

Aane. Ɛtɔ da bi a, wobetumi ahu saa tebea a wɔfrɛ no (LVNC) yi nso sɛ awosu mu tebea afoforo (syndromes) fã. Eyinom yɛ nea ɛyɛ den kakra, nanso nnuruyɛfo nso susuw saa tebea horow yi ho bere a wɔrehu (LVNC) no. Nhwɛso kakraa bi ni:

• Barth yare a ɛma obi nya ɔyare no
• Noonan yare a ɛma obi nya ɔyare no
• Roifman yare a ɛma obi nya ɔyare no
• Toriello Carey yare a ɛma obi nya ɔyare no

Dɛn ne obi a ɔwɔ LVNC daakye? Nkwa nna yɛ dɛn?

Adwene a obi a ɔwɔ LVNC bɛhwɛ no betumi ayɛ soronko. Ɛsono nnipa biara. Sɛ wɔde ayaresa pa di dwuma a, wobetumi adi sɛnkyerɛnne ahorow no so , na nnipa binom tra ase sɛnea wɔtaa tra ase.

LVNC yɛ tebea a ebetumi akum obi, nanso ɛnyɛ bere nyinaa na ɛte saa . Nnipa dodow no ara a wɔwɔ LVNC no nkum yare no. The most important thing is to see a cardiologist regularly and get tested . Obetumi aboa wo ma woahwɛ wo koma akwahosan so na wɔatew asiane a ɛwɔ hɔ sɛ wubehyia nsɛnnennen no so.

Sɛ me anaa me ba wɔ LVNC a, nsɛm bɛn na ɛsɛ sɛ mibisa oduruyɛfo no?

Sɛ wo anaa wo ba anya (LVNC), anaa sɛ wowɔ biribi a ɛhaw wo a, ɛyɛ papa sɛ wubebisa wo duruyɛfo nsɛm te sɛ eyinom:

• Dɛn na ɛbɛyɛ sɛ ɛde me/me ba LVNC tebea no ba? (i.e. so ɛyɛ awosu anaa biribi foforo) .
• So wokamfo kyerɛ sɛ wɔnyɛ awosu mu nhwehwɛmu de hwehwɛ LVNC? Sɛ saa a, so ɛbɛyɛ nea ɛho hia ma abusua no mufo afoforo?
• Nhwehwɛmu bɛn na ɛsɛ sɛ me/me ba no yɛ na ama wahu LVNC? Dɛn na metumi ahwɛ kwan afi wɔn hɔ?
• Dɛn ne ayaresa a wobetumi apaw ama LVNC? Ayaresa bɛn na eye ma me/me ba? So nsunsuanso bɔne bi wɔ saa ayaresa ahorow yi mu?
• Sɛ me anaa me ba koma yare mpofirim a, dɛn ne sɛnkyerɛnne ahorow no? Dɛn na ɛsɛ sɛ meyɛ ntɛm ara?

Saa nsɛmmisa yi bɛboa wo ma wo ne wo duruyɛfo asusuw ho na woanya wo tebea no ho ntease pa.

Enti, nneɛma bɛn na ɛho hia paa a ɛsɛ sɛ yɛkae fi saa asɛm yi mu?

Left ventricular non-functioning heart (LVNC) yɛ komayare a ɛntaa nsi, na ɛtaa fi awo mu. Eyi ne bere a koma no benkum so ahurututu no nnyin yiye. Sɛ́ anka ɛbɛyɛ ntini a ɛyɛ mmerɛw na ɛyɛ den no, ɛbɛyɛ den na ayɛ sɛ sponge. Eyi ma koma no ntumi mfa mogya nkɔ yiye.

Sɛ wowɔ (LVNC) a, .Nea ɛho hia sen biara ne sɛ wobɛkɔ koma ho oduruyɛfo nkyɛn daa na woadi wɔn afotu akyi. Ɛwom sɛ wonni eyi ano aduru de, nanso ayaresa a wo duruyɛfo de ma wo no betumi atew asiane a ɛwɔ hɔ sɛ wubehyia ɔhaw ahorow no so na ama w’asetra atu mpɔn. Ɛho hia sɛ woremmɔ hu na wonya ayaresa a ɛfata . Kae sɛ ɛnyɛ wo nkutoo na wowɔ hɔ, na nnuruyɛfo wɔ hɔ sɛ wɔbɛboa wo.