So w’adwene reyera mpofirim? Ebetumi ayɛ Long QT Syndrome (LQTS). Momma yɛnka eyi ho asɛm!

So woahu obi wɔ w’abusua mu anaa obi a wunim no sɛ ɔtotɔ piti mpofirim na ɔhwe ase bere a ɔreyɛ apɔw-mu-teɛteɛ anaa bere a ehu aka no kɛse no pɛn? Ɛtɔ da bi a, komayare bi da nneɛma a ɛtete saa akyi a yɛntee ho asɛm pii, nanso ebetumi ayɛ aniberesɛm kɛse. Tebea a ɛte saa no biako ne Long QT Syndrome (LQTS). Ɛwom sɛ ebia edin no bɛyɛ te sɛ nea ɛyɛ den kakra de, nanso momma yɛnte ase kɛkɛ.

Dɛn ne Long QT Syndrome (LQTS)?

Sɛ yɛbɛka no tiawa a, Long QT Syndrome (LQTS) yɛ ɔhaw a ɛwɔ wo koma no anyinam ahoɔden nhyehyɛe mu.

Fa wo koma sɛ biribi a ɛrehyerɛn wɔ mfoninitwa afiri so. Sɛ ɛbɔ pɛnkoro wie a, ɛsɛ sɛ wɔbɔ no ka kakra ansa na atumi abɔ bio. Saa na ɛsɛ sɛ koma no anyinam ahoɔden nhyehyɛe no san nya ahoɔden wɔ ne bɔ ntam. Bere a egye ansa na eyi aba no ne nea yesusuw wɔ ECG (Electrocardiogram) so sɛ QT ntamgyinafo .

Saa recharge bere yi ware ma obi a ɔwɔ LQTS sen obi a ɔte ase. Eyi kyerɛ sɛ koma no anyinam ahoɔden nhyehyɛe no gye bere tenten ansa na asiesie ne ho ama ɔbɔ a edi hɔ no.

Ɔkwan bɛn so na eyi ba?

Nneɛma nketenkete a anyinam ahoɔden wom a wɔfrɛ no ions (sɛ nhwɛso no, sodium, potassium, calcium) na ɛhwɛ anyinam ahoɔden dwumadi a ɛwɔ yɛn koma mu no so. Saa ions yi fa apon nketenkete a wɔfrɛ no ion akwan so kɔ koma ntini nkwammoaa mu na efi mu ba .

Wɔ Long QT Syndrome mu no, saa ion akwan yi ntumi nyɛ adwuma yiye anaasɛ ɛyera sɛnea ɛsɛ. Eyi ma koma no san nya ahoɔden akyiri dodo.

Dɛn ne LQTS ahorow atitiriw?

Wobetumi akyekyɛ LQTS mu ayɛ no ahorow atitiriw abien: nea wonya fi awo mu ne nea wonya.

1. LQTS a wonya fi awo mu/a wofi awo mu

Eyi fi awosu mu sintɔ bi. Ɛno kyerɛ sɛ wonya fi awofo hɔ ma mmofra. Ɛha nso, ahorow atitiriw pii wɔ hɔ.

2. LQTS a wɔanya

Ɛnyɛ awosu mu nneɛma na ɛde eyi ba. Ebia wɔbɛwo nnipa binom a wɔn ion akwan no ayɛ mmerɛw kakra. Nanso ɛno nyɛ ɔhaw. Nanso, tebea yi betumi asɔre esiane biribi a efi akyi nti.

Nneɛma atitiriw a enti ɛte saa ne:

• Nnuru bi: Nnuru bi a ekum ɔyare mmoawa, nnuru a ekum adwenemhaw, nnuru a ekum apɔw-mu-teɛteɛ, ne nnuru a ɛma obi ho yɛ hyew.
• Nipadua mu nkyene dodow a ɛso tew: Potassium, magnesium, anaa calcium dodow a ɛso tew wɔ mogya no mu.
• Nneɛma afoforo a ɛde ba: Adidi mu haw te sɛ anorexia nervosa, ntini a ɛsɛe, ne awuduru bi.

Dɛn na ebetumi ayɛ saa sɛnkyerɛnne ahorow yi?

Ade a ɛyɛ hu sen biara wɔ LQTS ho ne sɛ nnipa bɛyɛ 50% nhu sɛnkyerɛnne biara . Nanso, sɛ yare no ho sɛnkyerɛnne ahorow ba ampa a, ɛtaa yɛ aniberesɛm. Saa sɛnkyerɛnne ahorow yi ba bere a koma a ɛyɛ hu a yɛadi kan aka ho asɛm a wɔfrɛ no Torsades de Pointes no ba no.

Tebea horow a ɛda adi kɛse sɛ yare no ho sɛnkyerɛnne bɛda adi:

• Bere a woreyɛ apɔw-mu-teɛteɛ anaasɛ bere a woawie no.
• Wɔ adwene mu nkanyan a emu yɛ den mpofirim mu (e.g., bere a ehu aka no kɛse, ne ho dwiriw no).
• Bere a wɔada anaa bere a woresɔre mpofirim afi nna mu no.

Hena na ɔwɔ asiane kɛse mu sɛ obenya saa tebea yi?

Nnipa a wodi so yi wɔ asiane kɛse mu sɛ wobenya LQTS:

• Obi a ɔwɔ LQTS mogya abusuafo a wɔbɛn wɔn (awofo, anuanom, mmofra).
• Nnipa a wɔwɔ abusua abakɔsɛm a ɛkyerɛ sɛ wɔte nkae a wontumi nkyerɛkyerɛ mu, wɔn akisikuru, anaasɛ wowuwu mpofirim wɔ wɔn mmofraase.
• Mmofra a wɔwo wɔn asotifo (esiane asiane a ɛwɔ hɔ sɛ wobenya Jervell ne Lange-Nielsen Syndrome nti).
• Nnipa a wɔwɔ komayare afoforo te sɛ cardiomyopathy.
• Nnipa a wɔde nnuru a ɛma QT ntam kwan kyɛ di dwuma.

Wobɛyɛ dɛn ahu sɛ wowɔ LQTS?

Ɔkwan titiriw a wɔfa so hu eyi ne ECG (Electrocardiogram).Sɔhwɛ. Oduruyɛfo no susuw QT ntamgyinafo wɔ ECG no so. Mpɛn pii no, sɛ saa bere yi boro milisekɔn 450 a, wobetumi asusuw sɛ LQTS wɔ hɔ.

Nea ɛka ho no, oduruyɛfo no betumi akamfo nhwehwɛmu afoforo pii akyerɛ:

• Mogya mu nhwehwɛmu: Hwɛ sɛnea nkyene te sɛ potassium ne magnesium wɔ nipadua no mu.
• Apɔw-mu-teɛteɛ mu Adwennwen Sɔhwɛ: Hwɛ sɛnea wo koma dwumadi sesa bere a woteɛteɛ w’apɔw mu no.
• Ambulatory Monitor (Holter Monitor): Wɔde afiri ketewaa bi si wo moma so de kɔ so kyerɛw wo koma no nnyigyei nnɔnhwerew 24 anaa nea ɛboro saa.
• Awosu mu nhwehwɛmu: Hwɛ sɛ awosu mu nsakrae a ɛbata LQTS ho anaa.

Dɛn ne ayaresa ahorow a wɔde sa eyi?

Ɛwom sɛ wontumi nsa LQTS koraa de, nanso ayaresa ahorow bi wɔ hɔ a ebetumi aboa ma wɔadi yare no ho sɛnkyerɛnne ahorow so, asiw owu mpofirim ho asiane ano, na wɔatra ase sɛnea ɛsɛ.

Nneɛma a ɛsɛ sɛ wususuw ho bere a wo ne LQTS te no

Ɛyɛ yie sɛ wobɛtra ase a ɛfata, a ɛyɛ pɛ wɔ LQTS mu. Nanso, nneɛma kakraa bi wɔ hɔ a ɛsɛ sɛ wohwɛ yiye wɔ wo da biara da asetra mu.

1. Dede ne adwennwen a ɛba mpofirim

Wɔ nnipa a wɔwɔ LQTS ahorow bi fam no, dede a ano yɛ den mpofirim (e.g., alarm, telefon a ɛrebɔ) anaasɛ mpofirim ahodwiriw anaa ehu betumi ayɛ asiane.

• Ka kyerɛ w’abusuafo ne wo nnamfo sɛ ɛnyɛ nea asiane biara nni ho sɛ wobɛserew wo.
• Sɛ́ anka wode alarm dɔn a ano yɛ den bedi dwuma no, fa nea ɛbɔ nnwom brɛoo di dwuma.

2. Apɔw-mu-teɛteɛ ne agumadi

Wɔ nnipa a wɔwɔ LQTS ahorow bi fam no, akansi agumadi ne apɔw-mu-teɛteɛ a emu yɛ den betumi ayɛ nea asiane wom titiriw.

• Hwɛ hu sɛ wubebisa wo duruyɛfo apɔw-mu-teɛteɛ a ɛfata ne nea ɛmfata mma wo.
• Asuguare yɛ asiane titiriw ma nnipa binom. Asiane wɔ hɔ sɛ wobɛmene sɛ wo ho dwiriw wo wɔ nsu no mu a. Mma wo nkutoo nkɔ asuguare.

3. Hwɛ yiye titiriw wɔ nnuru ho!

Eyi ne ade a ɛho hia sen biara. Nnuru pii a wɔtaa de di dwuma mpo betumi ama LQTS asɛe kɛse.

• Ka kyerɛ oduruyɛfo biara a ɔsa wo yare sɛ wowɔ LQTS.
• Ansa na wobɛkyerɛw nnuru ama wo ma tebea foforo biara no, wo ne wo koma ho ɔyaresafo nkasa.
• Mma ntɔ nnuru biara a wɔtɔn mfi nnurutɔnbea anaa baabi foforo biara a wonkɔ oduruyɛfo nkyɛn (gye nneɛma te sɛ paracetamol a ɛnyɛ den ne aspirin).

Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?

Sɛ wohu sɛ wowɔ LQTS wie a, anyɛ yiye koraa no, ɛsɛ sɛ wokɔ wo duruyɛfo nkyɛn pɛnkoro afe biara kɔhwɛ wo. Ɛyɛ papa sɛ wobɛkɔ akɔhwɛ electrophysiologist, oduruyɛfo a ne ho akokwaw wɔ koma a ɛyɛ den mu.

Sɛ wo ba no wɔ saa tebea yi a, ɛho behia sɛ wokɔ oduruyɛfo nkyɛn mpɛn pii efisɛ ɛsɛ sɛ wɔyɛ nsakrae wɔ nnuru dodow a wɔde ma no mu sɛnea wɔn mu duru te.

Bere bɛn na ɛsɛ sɛ mekɔ ETU (Emergency Treatment Unit)?

Sɛ obi nnim hwee na ɔhwe ase a, frɛ ambulance ntɛm ara. Saa bere yi de, sɛ obi wɔ hɔ a wɔatete no sɛ ɔnyɛ CPR (cardiopulmonary resuscitation) a, ma no. Wɔ tebea a ɛte sɛɛ mu no, sekan biara ho hia.