So ɛtɔ mmere bi a wote nka sɛ wo moma so ayɛ wo den kakra, ɛyɛ den sɛ wobɛhome, anaasɛ worebɔ mmɔden kakra mpo? Eyinom betumi ayɛ ɔhaw bi a ɛwɔ w’ahurututu mu ntini a ɛyɛ adwuma te sɛ ɔpon ketewaa bi wɔ wo koma mu no ho sɛnkyerɛnne. Mma ɛnhaw wo, yɛbɛka eyi ho asɛm kɔ akyiri na yɛayɛ no tiawa koraa nnɛ. Sɛ wote eyi ase a, ɛbɛma woanya ahotɔ kɛse.
Dɛn ne Ahurututu Mu Yare?
Sɛ yɛbɛka no tiawa a, Pulmonary Valve Disease yɛ tebea biara a Pulmonary Valve, valve a ɛho hia yiye wɔ yɛn koma mu no nyɛ adwuma yiye. Fa no sɛ ɔpon ano hwɛfo. Ɛyɛ nea ɛma mogya fi dan a ɛwɔ fam a ɛwɔ wo koma no nifa so, Right Ventricle , mu kɔ ntini titiriw a ɛde mogya kɔ ahurututu mu, Pulmonary Artery , no mu . Sɛ mogya no du ahurututu no mu a, ɛgye mframa pa foforo. Afei, saa mogya a oxygen ahyɛ mu ma no kyekyɛ kɔ nipadua no nyinaa mu, na ɛma yɛn nkwammoaa no nya nkwa.
Enti, sɛ ɔhaw bi wɔ saa ahurututu mu ntini yi ho a, ɛbɛyɛ den sɛ wo mogya bɛkɔ w’ahurututu mu. Dɛn na ɛba saa bere no? Nipadua no mu ntini, nkwammoaa, ne akwaa ahorow no nya oxygen akyiri. Eyi te sɛ nsu paipu a esiw na nsu a ɛsen no brɛoo. Eyi nti na yɛwɔ ɔhaw ahorow.
Dɛn ne Pulmonary Valve Disease ahorow?
Ahurututu mu ntini mu yare atitiriw abiɛsa na ɛwɔ hɔ. Momma yɛnhwɛ nea wɔyɛ, tiawa koraa:
1. Pulmonary Valve Regurgitation: Eyi ne bere a valve no ntumi nto mu yiye, na mogya bi tu kɔ akyi. Fa no sɛ nsu faucet a wɔanto mu yiye na nsu a ɛtɔ gu fam nkakrankakra. Afei ɛsɛ sɛ koma no yɛ adwumaden de pia saa mogya no san kɔ n’anim.
2. Pulmonary Valve Stenosis: Eyi ne bere a valve no yɛ teateaa, anaasɛ sɛ yɛbɛka no yiye a, esiw ano. Eyi ma ɔkwan a mogya fa so sen no yɛ teateaa. Fa no sɛ ɛte sɛ nea worepiapia nsu paipu, a ɛma ɔkwan a nsu fa so no yɛ teateaa. Eyi ma ɛsɛ sɛ koma no yɛ adwumaden de pia mogya no kɔ n’anim.
3. Pulmonary Atresia: Eyi yɛ tebea a emu yɛ den. Eyi ne bere a wɔwo akokoaa a ɔwɔ valve a ennyaa anaasɛ ennyinii yiye . Eyi yɛ komayare a wɔde awo obi.
Pulmonary Valve Disease abu so dɛn?
Ma yɛnhwɛ sɛnea nyarewa yi abu so.
Pulmonary valve regurgitation (mogya a ɛsen fa valve no mu kɔ akyi) abu so kɛse ankasa.. Wɔwo nnipa binom a ɛsono wɔn valve nhyehyɛe kakra. Nnipa a wɔwɔ nipadua mu nsonsonoe yi taa nya ahurututu mu ntini a ɛsan kɔ nipadua no mu. Nanso, mpɛn pii no, ɛyɛ mmerɛw yiye. Ɛno nkyerɛ sɛ ɛyɛ biribi a ɛsɛ sɛ yesuro anaa ɛsɛ sɛ yɛsa. Wɔ nnipa dodow no ara fam no, ɛmfa ɔhaw akɛse biara mma.
Pulmonary valve stenosis (valve no a ɛyɛ teateaa) ba nnipa bɛyɛ 7% a wɔwɔ komayare a wɔde awo wɔn no mu.
Wɔ United States no, wɔwo nkokoaa bɛyɛ 7,000 biara mu biako a ɔwɔ ahurututu mu atresia (a ahurututu no nni hɔ bere a wɔawo no). Ɛwom sɛ akontaabu a ɛwɔ yɛn man yi mu no nyɛ pɛpɛɛpɛ de, nanso eyi yɛ tebea a ɛsɛ sɛ wosusuw ho.
Dɛn na ebetumi ayɛ yare yi ho sɛnkyerɛnne?
Pulmonary Valve Disease ho sɛnkyerɛnne betumi ayɛ soronko wɔ onipa biara ho. Ebia nnipa binom benya saa sɛnkyerɛnne ahorow yi:
- Koko mu yaw: Ɛte sɛ nea wɔrepiapia wo koko, ɛtɔ mmere bi mpo a bere a worehome no.
- Ɔbrɛ: Ɔbrɛ a wobɛte nka ara kwa, atenka a ɛte sɛ nea woayɛ mmerɛw araa ma wuntumi nyɛ hwee.
- Ti a ɛyɛ hare: Ɛte nka sɛ wo ho yɛ wo yaw, ɛtɔ mmere bi mpo a wototɔ piti.
- Ahome a ɛyɛ tiaa: Ɛyɛ den sɛ wobɛhome, ɛyɛ wo yaw, bere a wonam kakra anaa woreforo antweri mpo no.
- Apɔw-mu-teɛteɛ a mintumi: M’ani nnye ho sɛ mɛtu mmirika, ahuruhuruw, anaa mɛteɛteɛ m’apɔw mu sɛnea na meyɛ kan no, na sɛ meyɛ saa mpo a, mebrɛ ntɛm.
Nanso kae sɛ ebia nnipa a wɔwɔ stenosis a ɛnyɛ den anaasɛ wɔn regurgitation a ɛnyɛ den no rennya yare no ho sɛnkyerɛnne biara. Ɛno nti na aduruyɛ mu nhwehwɛmu ho hia no.
Sɛ akokoaa bi wɔ Pulmonary Atresia a, ebetumi ayɛ den sɛ ɔbɛhome, ɛbɛyɛ den ama no sɛ ɔbɛma aduan, wɔtaa da, na ɛtɔ mmere bi a ne honam ani yɛ bruu (Cyanosis). Eyi yɛ biribi a ɛsɛ sɛ wohwɛ so yiye. Sɛ́ awofo no, sɛ muhu saa sɛnkyerɛnne ahorow yi bi a, ɛsɛ sɛ mokɔ oduruyɛfo nkyɛn ntɛm ara.
Dɛn na ɛde Pulmonary Valve Disease ba?
Ɛsono nea ɛde yare yi ba, na egyina yare ko a obi wɔ so. Ma yɛnhwɛ sɛnea ɛyɛ adwuma.
- Nea Ɛde Ahurututu Mu Yare Ba: Mpɛn pii no, ɛyɛ den sɛ wubehu nea ɛde eyi ba pɔtee. Nanso, saa tebea yi betumi aba esiane awosu mu ɔhaw ahorow bi nti anaasɛ sɛ ɛna no nya yare bi te sɛ rubella bere a ɔyem a. Rubella yɛ yareɛ a ɛtumi ka akokoaa no, enti ɛho hia sɛ yɛhwɛ yie wɔ nyinsɛn mu.
- Nneɛma a ɛde ahurututu mu ntini a ɛsan kɔ nipadua no mu ba:Eyi betumi de nneɛma pii aba. Sɛ nhwɛso no, mogya mmoroso (titiriw ahurututu mu mogya mmoroso), endocarditis, rheumatic fever, ne nea ɛkeka ho Ebetumi nso afi koma mu nsɛm bi a wonya fi awo mu anaa wɔn ayaresa mu. Saa tebea yi abu so titiriw wɔ nnipa a wɔanya komayare bi a wɔfrɛ no Tetralogy of Fallot mu.
- Causes of Pulmonary Atresia: In many cases, the exact cause of this condition is unknown. Nanso, wosusuw sɛ nsakrae a ɛba akokoaa awosu mu, awuduru a ɛwɔ nneɛma a atwa yɛn ho ahyia mu bere a ɔyem, anaa biribi a ɛna no nom na ɛde ba.
Dɛn ne nsɛnnennen a ebetumi afi yare yi mu aba?
Pulmonary Valve Disease ma ɛsɛ sɛ wo koma no ventricle nifa no yɛ adwumaden kɛse na ama mogya akɔ w’ahurututu mu. Eyi betumi asɛe wo koma na ama ayɛ kɛse. Ɛwom sɛ ɛntaa nsi de, nanso sɛ tebea yi mu yɛ den a, ebetumi ama obi anya komayare . Eyi kyerɛ sɛ wo koma ntumi mfa mogya a ɛdɔɔso nkɔ wo nipadua mu.
Mmofra a wɔwɔ Pulmonary Atresia betumi anya mmerɛbo mu yare ne koma a ɛnyɛ ne kwan so, enti ɛho hia sɛ wɔsa wɔn yare ntɛm.
Ɔkwan bɛn so na wohu yare yi?
Sɛ wokɔ oduruyɛfo nkyɛn a, sɛ ɔte nnyigyei bi a ɛnteɛ bere a ɔretie wo koma (a ɔde afiri a wɔde tie asɛm ) , ebetumi ayɛ Pulmonary Regurgitation anaa Pulmonary Stenosis ho sɛnkyerɛnne. Saa nwiinwii yi yɛ nnyigyei a ɛnteɛ a mogya a ɛsen fa ntini ahorow no mu de ba.
Nhwehwɛmu bɛn na wɔyɛ de hu tebea yi?
Oduruyɛfo no betumi ayɛ nhwehwɛmu ahorow a edidi so yi de ahu ahurututu mu ntini mu yare:
- Fetal Echocardiogram: Eyi boa ma wohu tebea horow te sɛ Pulmonary Atresia ansa na wɔawo akokoaa no.
- Echocardiogram (Echo): Eyi tumi hwɛ nneɛma pii, te sɛ sɛnea koma no yɛ adwuma ne sɛnea ntini ahorow no te. Wɔde di dwuma de hu `Atresia`, `Stenosis` anaa `Regurgitation`. Ɛte sɛ nea wode nnyigyei retwa koma no mfonini.
- Pulse Oximetry: Wɔde eyi hwɛ oxygen dodow a ɛwɔ mogya no mu wɔ `atresia` ho. Ɛyɛ sɔhwɛ a ɛnyɛ den a wɔyɛ denam biribi a wɔde kyekyere nsateaa no so.
- Koma mu Catheterization: Wɔyɛ eyi wɔ nsɛm a ɛfa `Atresia` anaa `Stenosis` ho. Ɔkwan a wɔfa so de afiri ketewaa bi fa mogya ntini bi mu kɔ koma no mu de susuw nhyɛso no, na sɛ ɛho hia a, wɔde sa.
- Electrocardiogram (EKG/ECG): Wɔyɛ eyi de hwɛ sɛnea koma no anyinam ahoɔden yɛ adwuma wɔ nsɛm a ɛfa `Atresia` anaa `Regurgitation` ho.
- Koma MRI (Magnetic Resonance Imaging): Eyi boa ma wotwa koma no ho mfonini a ɛkɔ akyiri wɔ nsɛm a ɛfa `Stenosis` anaa `Regurgitation` ho.
- Chest X-ray: Eyi boa ma wohu koma no kɛse ne ahurututu no tebea wɔ `regurgitation` ho.
Ɔkwan bɛn so na wɔsa Pulmonary Valve Disease?
Ɛsono sɛnea wɔde eyi sa yare a egyina tebea a wowɔ no so. Ɛtɔ da bi a wotumi de nnuru siw ano, ɛtɔ da bi mpo a ebetumi afa oprehyɛn ho.
Nnuru ne ayaresa pɔtee bi
Ayaresa ahorow pii wɔ hɔ a wɔde sa ahurututu mu ntini mu yare:
- Balloon Valvuloplasty: Wɔyɛ eyi de trɛw ahurututu mu ntini a ɛyɛ teateaa mu. Wɔyɛ eyi denam afiri ketewaa bi a ɛte sɛ balloon a wɔde hyɛ valve no mu na wɔde mframa gu mu no so.
- Nnuru anaa stent a wɔde si hɔ (ma ``Atresia``): Wɔyɛ eyi na ama ``Ductus Arteriosus``, mogya ntini a ɛto mu ntɛmntɛm bere a wɔawo akokoaa akyi no, abue. Sɛ wɔma saa afiri yi bue a, ɛboa ma mogya kɔ ahurututu no mu.
- Nnuru a ɛma nsu fi nipadua no mu: Wɔde nnuru yi ma sɛnea ɛbɛyɛ a nsu ankɔ nipadua no mu esiane komayare a mogya a efi ntini ahorow no mu ba nti. Wɔma nipadua no fa nsu mu yi nsu a ɛboro so fi mu.
- Nnuru a wɔde sa Pulmonary Hypertension (mogya a ɛkɔ soro wɔ ahurututu mu) anaa Endocarditis (koma mu yare) (ma Regurgitation): Wɔde nnuru ma de siw tebea horow yi ano.
- Transcatheter adeyɛ anaa koma a wɔabue mu oprehyɛn: Wɔde saa akwan yi siesie valve a ɛretu anaasɛ wɔde valve foforo hyɛ mu.
Nsɛnnennen/nsunsuanso bɔne a efi ayaresa mu ba
Ebia ɛbɛyɛ den ama nkokoaa binom sɛ wobedidi bere a wɔayɛ wɔn oprehyɛn akyi, na ebia ebehia sɛ wɔfa afiri ketewa bi mu fa wɔn hwene mu ma wɔn aduan (tube feeding).
Sɛ wɔsesa valve no wie a, ɛho behia sɛ wo ba no nom nnuru a ekum ɔyare mmoawa bere a wɔayɛ wɔn sẽ ho adwuma no. Saa nnuru yi brɛ asiane a ɛwɔ hɔ sɛ obi benya komayare bi a wɔfrɛ no endocarditis no ase.
Sɛ wosiesie ahurututu mu ntini bi wie a, ebetumi atu bio, na ebia ɛsɛ sɛ oduruyɛfo no trɛw mu anaasɛ ɔsesa.
Sɛnea ɛte wɔ oprehyɛn biara mu no, hokwan ketewaa bi wɔ hɔ sɛ ɔyare mmoawa anaa mogya tu, nanso nnuruyɛfo hwɛ yiye wɔ saa asɛm no ho paa.
Bere tenten ahe na egye ansa na obi ho atɔ no wɔ ayaresa mu?
Sɛ wɔyɛ oprehyɛn ma `Pulmonary Atresia` wie a, wo ba no bɛtena ayaresabea bɛyɛ dapɛn biako anaa abien. Bere a wɔayɛ oprehyɛn ama `Pulmonary Valve Regurgitation` akyi no, ahoɔden a obi bɛsan anya no betumi agye adapɛn pii, asram pii mpo. `Valvuloplasty` akyi ma `Pulmonary Stenosis`, ɛho behia sɛ wokwati dwumadi ahorow a emu yɛ den bɛyɛ dapɛn biako.
Sɛ wowɔ Pulmonary Valve Disease a, dɛn na wubetumi ahwɛ kwan?
Ebia osuahu a wunya wɔ saa yare yi ho no bɛyɛ soronko wɔ obi foforo de ho. Nnipa binom nnya yare no ho sɛnkyerɛnne kakraa bi pɛ na ebia ɛho renhia sɛ wɔyɛ wɔn oprehyɛn. Ebia afoforo behia sɛ wɔyɛ wɔn ahurututu mu ntini oprehyɛn bɛboro pɛnkoro wɔ wɔn nkwa nna mu.
Nsusuwii a ɛfa ahurututu mu ntini mu yare ho
Adwene a mmofra a wɔayɛ wɔn valvuloplasty ma ahurututu mu ntini a ɛyɛ mmerɛw no ye yiye . Mpɛn pii no, wonhia biribiara sen sɛ wɔbɛkɔ mmofra komayare ho ɔyaresafo nkyɛn daa. Ebia ɛho behia sɛ nnipa binom san bue wɔn valve no wɔ bɛyɛ mfe 15 akyi.
Sɛ wɔansa ahurututu mu atresia betumi adi awu, nanso mmofra pii tra ase kosi mpanyin afe so wɔ oprehyɛn akyi.
Anidaso a ɛwɔ hɔ ma nnipa a wɔn ahurututu mu ntini a ɛyɛ mmerɛw anaasɛ ɛkɔ fam no yɛ papa. Wɔ nnipa a wɔwɔ yare a emu yɛ den fam no, nea wɔhwɛ no gyina sɛnea wonya ayaresa ntɛmntɛm no so.
Mɛyɛ dɛn atumi atew asiane no so?
Worentumi ntew asiane a ɛwɔ hɔ sɛ wo ba benya Pulmonary Valve Disease, tebea a ɛba a wonnim nea ɛde ba no so. Nanso sɛ woreyɛ nhyehyɛe sɛ wobɛnyinsɛn a, hwɛ hu sɛ woanya Rubella Vaccine no.
Wubetumi atew asiane a ɛwɔ hɔ sɛ wubenya Pulmonary Valve Regurgitation so denam tebea horow a ɛde ba te sɛ Pulmonary Hypertension, Endocarditis, ne Rheumatic Fever a wobɛkwati so.
Mɛyɛ dɛn ahwɛ me ho?
Di nneɛma a wubetumi adi so no ho dwuma na ma wo koma anya apɔwmuden.
- Di wo mogya mmoroso ne srade dodow so.
- Kwati tawa ho nneɛma koraa.
- Yɛ apɔw-mu-teɛteɛ daa. Sɛ obi nantew simma 30 kɛkɛ da biara mpo ye.
- Di nnuaba, nhabannuru, ne nnuan a srade nnim anaasɛ enni mu. Yɛn mpɔtam hɔ aduan fata yiye ma eyi.
Bere bɛn na ɛsɛ sɛ mekɔ me duruyɛfo nkyɛn?
Mma wo bere a wo ne wo koma ho ɔyaresafo bɛkɔ akɔhwɛ wo akyi no nmpa wo ti so. Obetumi ahwɛ sɛ wo valve no da so ara reyɛ adwuma yiye anaa. Ebia ɔbɛpɛ nso sɛ ɔsan yɛ nhwehwɛmu a wɔde huu wo yare no bi wɔ nea edi kan no mu. Nhwɛsoɔ:
- Echocardiogram (Echo) .
- CT scan (Kɔmputa so Tomography - CT mfonini) .
- Koma mu MRI
- EKG (Electrocardiogram - EKG) .
Bere bɛn na ɛsɛ sɛ mekɔ Emergency Department (ETU) ?
Sɛ wowɔ saa sɛnkyerɛnne yi bi a, kɔ baabi a wɔhwɛ wɔn a wɔwɔ ayaresa a egye ntɛmpɛ mu ntɛm ara:
- Nnipa a wɔtaa totɔ piti.
- Ɔhome a ɛyɛ den kɛse.
- Sɛ wote nka sɛ wo koma rebɔ ntɛmntɛm (Heart Palpitations).
- Nsɛnkyerɛnne a ɛkyerɛ sɛ ɔyare anaa mogya retu, te sɛ atiridiinini ne mogya a ɛwɔ nsu mu, wɔ oprehyɛn akyi.
Nsɛm bɛn na ɛsɛ sɛ mibisa me duruyɛfo?
Wubetumi abisa oduruyɛfo no nsɛm te sɛ eyinom:
- Dɛn ne ayaresa a eye sen biara ma me (anaa me ba)?
- So wunim nea ɛde me (anaa me ba) Ahurututu Mu Yare no ba?
- Mpɛn ahe na ɛsɛ sɛ me (anaa me ba) ba bɛhwɛ wo?
- So akuw bi wɔ hɔ a wɔboa mmofra a wɔwɔ komayare awofo?
Awiei koraa no, nkrasɛm a wɔde kɔ fie
Ɛyɛ ade a ɛfata sɛ wobɛte nka sɛ wo ho nyɛ wo dɛ kakra bere a wuhu sɛ wo ba (anaa w’ankasa wo koma) wɔ Pulmonary Valve Disease no. Nanso mma ɛnhaw wo. Koma ho animdefo di saa valve haw ahorow yi ho dwuma bere nyinaa. Wobetumi de wɔn suahu adi dwuma de ahu ayaresa a eye sen biara ama wo anaa wo ba.
Nsuro sɛ wubebisa nsɛm wɔ biribiara a wonte ase ho. Kɔ nhwehwɛmu a wo duruyɛfo hyɛ nyinaa, na nom nnuru a wɔde ma wo no nyinaa wɔ bere ano. Ɛnyɛ wo nkutoo na wowɔ hɔ, na nnuruyɛfo, ayarehwɛfo, ne w’abusua wɔ hɔ a wɔbɛboa wo wɔ akwantu yi mu. Adwempa a wobɛkɔ so atra hɔ nso ho hia yiye na ama wo ho atɔ wo ntɛmntɛm.
` Ahurututu mu Valve Yare, Koma mu Valve, Koma Yare, Ɔhome a Ɛyɛ Den, Koko mu Ɛyaw, Koma Yare a Wɔde Wo Awo, Koma Valve Ho Nsɛnnennen, Ahurututu mu Stenosis, Pulmonary Regurgitation, Pulmonary Atresia











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