So wo koma a ɛyɛ den no haw wo? Momma yensua Short QT Syndrome (SQTS) ho ade .

So ɛtɔ mmere bi a wo tirim yɛ wo yaw, wo koko rebɔ, anaasɛ wote nka sɛ wo ho reyera a ntease biara nnim? Ɛwom sɛ yesusuw sɛ eyinom yɛ nneɛma a ɛfata de, nanso ɛtɔ mmere bi a ebia ntease a anibere wom kɛse bi wɔ saa sɛnkyerɛnne ahorow yi akyi a yennim. Ɛnnɛ yɛreka komayare bi a ɛntaa nsi, nanso ebetumi ayɛ nea ɛho hia yiye ho asɛm. Ɛno ne Short QT Syndrome, anaa SQTS tiawa.

Sɛ yɛbɛka no tiawa a, dɛn ne Short QT Syndrome (SQTS)?

Short QT Syndrome (SQTS) yɛ komayare a ɛntaa nsi koraa, a efi awosu mu. Eyi ne bere a yɛn koma mu nnyigyei yɛ nea ɛnkɔ so pɛpɛɛpɛ. Sɛ yɛbɛka no tiawa a, sɛ yɛn koma bɔ pɛnkoro wie a, egye yɛn ahome bere tiaa bi na yɛasiesie yɛn ho ama ɛbɔ a edi hɔ no. Ɛte sɛ nea wɔretwe rɔba bi na afei wɔayi afi hɔ, na afei ɛsan tu kɔ baabi a ɛwɔ. Wɔ obi a ɔwɔ SQTS mu no, saa ahomegye yi, anaasɛ ne ho tɔ no ntɛmntɛm anaasɛ ɛyɛ tiaa sen obi a ɔte ase.

Eyi ne nea yɛfrɛ no wɔ aduruyɛ mu sɛ "QT ntam a ɛyɛ tiaa" a ɛwɔ koma no mu. Saa ahoɔhare yi betumi de ɔhaw ahorow bi aba koma no anyinam ahoɔden nsɛnkyerɛnne nhyehyɛe no mu, na ama koma no nnyigyei ayɛ nea ɛnkɔ so pɛpɛɛpɛ. Yɛfrɛ eyi ``arrhythmia''. Eyi betumi ama wo ho ayɛ wo yaw, woatotɔ piti, na wo koko ayɛ wo yaw. Wɔ tebea horow bi a emu yɛ den mu no, koma no tumi gyae bɔ mpofirim mpo (koma no gyaee). Enti, ɛho hia paa sɛ yehu eyi.

Momma yɛnte nea QT ntamgyinafo no yɛ ase ankasa?

So woayɛ ECG nhwehwɛmu pɛn? Wubehu line graph wɔ amanneɛbɔ no so a ɛkɔ soro ne fam. Saa na nnuruyɛfo susuw anyinam ahoɔden a ɛwɔ yɛn koma mu no. Susuw ECG (Electrocardiogram) ho sɛ afiri a ɛkyerɛw anyinam ahoɔden nsɛnkyerɛnne a ɛwɔ yɛn koma mu.

Yɛn koma bɔ denam anyinam ahoɔden nsɛnkyerɛnne so. Koma no atifi adan (atria) ne ase (mitra) no twetwe na ɛbɔ mogya esiane anyinam ahoɔden nsɛnkyerɛnne yi nti. Wɔde P, Q, R, S, ne T asorɔkye a ɛwɔ ECG so no gyina hɔ ma saa adeyɛ yi.

• P asorɔkye: Eyi ba bere a koma no atifi (atria) no twetwe no.
• QRS complex: Eyi ba bere a koma no mu adan (nkwaboaa) a ɛwɔ fam no twetwe no.
• T asorɔkye: Eyi ba bere a ventricles no resan aba sɛnea na ɛte kan na wɔresiesie wɔn ho ama twetwe a edi hɔ no.

"QT ntamgyinafoɔ" yɛ berɛ a ɛfiri QRS complex no mfitiaseɛ kɔsi T asorɔkye no awieeɛ. Eyi kyerɛ bere tenten a egye ansa na koma no mu adan a ɛwɔ fam no atwetwe na afei asan agye n’ahome bio na asan ayɛ sɛnea na ɛte kan no.

Mpɛn pii no, QT ntamgyinafo a obi a ɔwɔ apɔwmuden wɔ no yɛ sikɔne 0.35 kosi 0.45. Nanso, wɔ obi a ɔwɔ SQTS mu no, saa bere yi nnu sikani 0.34. Eyi kyerɛ sɛ koma no siesie ne ho ma ɛbɔ a edi hɔ no ntɛmntɛm sen sɛnea na wɔhwɛ kwan no.

Nsonsonoe bɛn na ɛda Long QT ne Short QT ntam?

Eyi nso ho hia wo. Tebea bi wɔ hɔ a wɔfrɛ no Short QT ne Long QT Syndrome nso.

• Short QT Syndrome (SQTS): QT ntam kwan no yɛ tiaa wɔ ɔkwan a ɛnteɛ so (ennu sikɔne 0.34). Koma no ho tɔ no ntɛmntɛm dodo .
• Long QT Syndrome (LQTS): QT ntam kwan no ware wɔ ɔkwan a ɛnteɛ so (ɛboro sikɔne 0.45). Koma no gye bere tenten ansa na ne ho atɔ no.

Saa tebea abien yi nyinaa betumi de koma a ɛbɔ no ho haw aba.

Hena na onya saa tebea yi? Dɛn na ɛde ba?

SQTS yɛ tebea a ɛntaa nsi koraa . Akontaabu pɔtee biara nni hɔ a ɛkyerɛ nnipa dodow a wɔwɔ wiase no. Ɛyɛ awosu mu yare. Eyi kyerɛ sɛ wobetumi anya afi awofo hɔ ama mmofra. Anaasɛ ebetumi aba wɔ obi a onni abusua abakɔsɛm biara mu, sɛ awosu mu nkwaadɔm mu nsakrae foforo.

Nhwehwɛmu ahorow bi ada no adi sɛ saa sɛnkyerɛnne ahorow yi taa da adi wɔ abofra nkwa afe a edi kan no mu. Afei, sɛnkyerɛnne ahorow no betumi asan ada adi wɔ mpanyin afe so, wɔ mfe 20 kosi 40 ntam.

Dɛn ne eyi ho sɛnkyerɛnne atitiriw?

Ɛnyɛ obiara a ɔwɔ SQTS na obenya yare no ho sɛnkyerɛnne. Nnipa binom tra ase sɛnea ɛsɛ a wonni sɛnkyerɛnne biara. Nanso sɛ sɛnkyerɛnne ahorow ba ampa a, ebia ɛbɛyɛ te sɛ eyi.

Awerɛhosɛm ne sɛ, nnipa binom (bɛyɛ baanum biara mu baanu) na wodi kan hu sɛ wɔwɔ SQTS bere a wɔanya komayare mpofirim akyi.

Ɔkwan bɛn so na wobetumi ahu yare no?

Sɛ wowɔ saa nsɛnkyerɛnne yi a, wo duruyɛfo no bedi kan abisa wo wo yare no ho sɛnkyerɛnne na wahwɛ wo. Afei, sɛ wosusuw sɛ wowɔ SQTS a, wɔbɛkra sɔhwɛ ahorow a edidi so yi:

• ECG (Electrocardiogram): Eyi ne sɔhwɛ a ɛho hia sen biara. Ɛsusuw wo QT ntamgyinafo. Sɛ ennu sikani 0.34, na sɛ wowɔ sɛnkyerɛnne afoforo a, wobetumi asusuw sɛ SQTS wɔ hɔ.
• Awosu mu Nhwehwɛmu: Eyi betumi asi so dua sɛ ebia awosu mu nsakrae bi wɔ hɔ a ɛde SQTS ba anaa.

Ɔkwan bɛn so na wɔsa?

Koma ho ɔyaresafo na ɔsa SQTS yare. Ayaresa ahorow pii wɔ hɔ a wobetumi apaw. Wo duruyɛfo na ɔbɛkyerɛ ayaresa a ɛfata sen biara ma wo tebea no.

1. Implantable Cardioverter Defibrillator (ICD): Eyi yɛ afiri ketewaa bi. Wɔyɛ oprehyɛn de hyɛ koko no were a ɛbɛn koma no ase. Ɛte sɛ ade ketewaa bi a ɛbɔ koma no ho ban. Saa afiri yi hwɛ sɛnea koma no bɔ no so bere nyinaa. Sɛ nnyigyei bi a ɛyɛ hu a ɛnkɔ so daa ba a, ehu na ɛde anyinam ahoɔden ketewaa bi kɔ koma no mu, na ɛma nnyigyei no san ba. Eyi ne ayaresa a wotumi de ho to so sen biara ma mpanyimfo.

2. Nnuru: Nnuru bi wɔ hɔ a ɛko tia koma a ɛbɔ denneennen a wɔde ma de siw koma no nnyigyei so. Sɛ nhwɛso no, aduru bi a wɔfrɛ no quinidine boa ma QT ntam kwan no yɛ nea ɛfata. Ebia wo duruyɛfo nso bɛkyerɛw nnuru afoforo te sɛ beta-blockers.

Saa tebea yi ka w’asetra dɛn?

Eyi yɛ asɛm a ɛyɛ nkate. Nnipa binom a wɔwɔ SQTS wɔ asiane mu sɛ koma betumi awu mpofirim. Wɔkyerɛ sɛ asiane yi yɛ kɛse titiriw wɔ mfe 0-1 kosi 20-40 ntam. Sɛ saa tebea yi ka akokoaa a wɔawo no foforo a, ɛtɔ mmere bi a wɔfrɛ no Sudden Infant Death Syndrome (SIDS).

Nanso, eyi nkyerɛ sɛ obiara a ɔwɔ SQTS wɔ asiane yi.

Nnipa dodow no ara tra ase sɛnea ɛsɛ, apɔwmuden a wɔde ayaresa a ɛfata (titiriw ICD a wɔde hyɛ nipadua mu) na wodi wɔn duruyɛfo akwankyerɛ akyi. Ebia nnipa binom nnya yare no ho sɛnkyerɛnne biara da. Esiane sɛ eyi yɛ tebea a ɛntaa nsi nti, nhwehwɛmu da so ara kɔ so. Enti ade a eye sen biara a wubetumi ayɛ ne sɛ wo ne wo koma ho ɔyaresafo bɛkasa na woadi w’asetra ho dwuma wɔ ɔkwan a ɛfata wo tebea no so.

So yebetumi akwati asiane yi?

Esiane sɛ SQTS yɛ awosu mu tebea nti, ɔkwan biara nni hɔ a yɛbɛfa so asiw ano. Ɛyɛ biribi a yentumi nyɛ ho hwee.

Nanso sɛ wohu sɛ wowɔ SQTS a, ade a eye sen biara a wubetumi ayɛ ne sɛ wobɛkɔ wo koma ho oduruyɛfo nkyɛn daa na woakɔhwɛ wo daa. Ɔbɛhwɛ wo koma akwahosan daa na wama wo afotu ne ayaresa a ɛho hia na ama asiane a ɛwɔ hɔ sɛ wubenya nsɛnnennen a emu yɛ den te sɛ koma a ɛbɛtɔ mpofirim no so atew.