Ebia woate Sickle Cell Yare ho asɛm . Sɛ yɛbɛka no tiawa a, ɛyɛ tebea a ɛka sɛnea wo nipadua no yɛ mogya mu nkwammoaa kɔkɔɔ . Sɛnea wunim no, mogya mu nkwammoaa kɔkɔɔ yi na ɛde mframa pa kɔ wo nipadua nyinaa mu. Bere a nkwammoaa a ɛte apɔw yɛ torotoro, kurukuruwa, na ɛyɛ mmerɛw no, Sickle Cell Disease ma ɛyɛ den na ɛyɛ te sɛ sickle. Saa nsusuwii a ɛnteɛ yi betumi de ‘ nsɛnnennen ’ ahorow aba . Nanso, mma wo ho nnyɛ wo hu; wo duruyɛfo betumi aboa wo ma woasa nsɛm yi pii na mpo asiw bi ano. Momma yɛnbom nsusuw eyinom ho.
Ɛyaw – Ɔhaw a Ɛtaa Ba
Ɛyaw ne Sickle Cell Disease ho sɛnkyerɛnne a abu so sen biara na ɛtaa yɛ nea ɛhaw adwene sen biara . Ɛba efisɛ nkwammoaa a ɛte sɛ nkankyee no kɔhyɛ mogya ntini nketenkete mu . Fa no sɛ kar kɛse bi a akɔhyɛ abɔnten teateaa bi so; sɛ saa nkwammoaa yi siw mogya ntini mu a, ɛma ɛyɛ yaw.
Saa ɛyaw yi taa ba akyi, nan, nsa, yafunu, anaa moma so. Ebetumi aba sɛ ‘ɛyaw ahokyere’ (anaasɛ adeyɛ) a emu yɛ den mpofirim. Wɔ mmabun ne mpanyimfo fam no, ɛtɔ mmere bi a eyi betumi ada adi sɛ ɛyaw a ɛtra hɔ kyɛ a enni sabea.
Mpɛn pii no, wubetumi anya ahotɔ afi saa nsɛm yi mu denam nnuru a wɔde kum ɛyaw a wɔtɔn te sɛ Paracetamol anaa Ibuprofen so. Nanso, yɛsrɛ sɛ kae: mma obiara a onnii mfe 19 Aspirin da.Sɛ ɛyaw no mu yɛ den a, ebia wo duruyɛfo bɛkyerɛw nnuru a ano yɛ den a egyina opioid so ama wo. Wɔ tebea horow bi mu no, ebia ɛho behia sɛ wɔde obi kɔ ayaresabea na ama wɔatumi adi ɛyaw no ho dwuma yiye.
Ebia wo duruyɛfo bɛkamfo nea edidi so yi akyerɛ sɛ ɛbɛboa ma wɔasiw ɛyaw a ɛtaa ba no ano anaasɛ ɛbɛtew so:
- Kɔ so nya nsu pa denam nsu pii a wobɛnom so.
- Kwati ɔhyew a ano yɛ den ne awɔw a ano yɛ den.
- Kwati sɛ wobɛtra mmeae a ɛkorɔn bere tenten.
- Wɔtaa de nnuru te sɛ Hydroxyurea di dwuma ma mmofra ne mpanyimfo nyinaa de tew ɔhaw ahorow yi a ɛtaa ba no so.
Mogya a ɛtɔ mogya mu
Eyi yɛ ɔhaw foforo a ɛtaa ba. Wɔ sickle cell yare mu no, mogya mu nkwammoaa kɔkɔɔ a ɛnyɛ ne kwan so no wuwu ntɛmntɛm sen nkwammoaa a ɛte apɔw. Esiane sɛ wo nipadua ntumi nyɛ nkwammoaa foforo ntɛmntɛm mfa nsi ananmu nti, oxygen a ɛkɔ wo ntini ahorow mu no so tew, na ebetumi ama woate nka sɛ woabrɛ kɛse, woayɛ mmerɛw, na woayɛ basaa . Ebia wo koma bɛbɔ ntɛmntɛm anaasɛ wobɛhome a ɛyɛ tiaa nso. Wɔ mmofra fam no, mogya a ɛtɔ kɔ nipadua mu no betumi aka wɔn nyin mpo.
Sɛ mogya a ɛtɔ kɔ nipadua mu no mu yɛ den a, ebia ɛho behia sɛ wɔde mogya ma . Nanso, mogya a wɔtaa ma no betumi ama iron ayɛ wo dodo, na ebetumi apira wo koma, wo mmerɛbo, ne wo dwensɔtwaa. Enti, wo duruyɛfo bɛhwɛ wo dade dodow so daa na ama watumi adi eyi ho dwuma. Wɔ mpanyimfo fam no, Hydroxyurea nso betumi aboa ma wɔadi mogya a ɛtɔ kɔ nipadua mu no ho dwuma.
| Nsɛnnennen a ɛba | Nsɛnkyerɛnne Titiriw | Adeyɛ a Ɛho Hia |
|---|---|---|
| Splenic Sequestration a Wɔde Siesie Nnipa | Yafunu mu yaw wɔ benkum so, ɛyɛ fitaa, ɛyɛ mmerɛw kɛse, koma a ɛbɔ ntɛmntɛm. | Eyi yɛ aduruyɛ mu tebea a egye ntɛmpɛ a ɛde nkwa to asiane mu. Hwehwɛ ɔhwɛ ntɛm ara wɔ dwumadibea a ɛhwɛ ntɛmpɛ a ɛbɛn hɔ no. |
| Chest Syndrome a Ɛyɛ Hu a Ɛyɛ Den | Atiridiinini, ɔhome a ɛyɛ den, koko mu yaw, ɔfe. | Eyi yɛ tebea a emu yɛ den. Hwehwɛ ɔhwɛ ntɛm ara wɔ dwumadibea a ɛhwɛ ntɛmpɛ a ɛbɛn hɔ no. |
Nyarewa ne Nneɛma Afoforo a Egye Ntɛmntɛm
Nyarewa a Ɛyɛ Mmerewa a Ɛkɔ Anim
Nnipa a wɔwɔ Sickle Cell Disease, titiriw mmofra nkumaa, wɔ asiane kɛse mu sɛ wobenya ɔyare mmoawa. Nea enti a ɛte saa ne sɛ yare no betumi asɛe akyi berɛmo no . Akisikuru no yɛ adwuma sɛ ade a wɔde yi mmoawa ne mmoawa fi wo mogya mu. Sɛ ɛnyɛ adwuma yiye a, ɛyɛ mmerɛw sɛ ɔyare mmoawa no bɛkɔ so.
Ɛsɛ sɛ wɔsa ɔyare mmoawa ketewaa bi mpo ansa na ayɛ nea emu yɛ den. Sɛ wo anaa wo ba nya atiridiinini a ɛyɛ 101°F (38.3°C) anaa nea ɛboro saa a, kɔ wo duruyɛfo nkyɛn anaa kɔ adwumayɛbea a ɛbɛn wo a wɔhwɛ ntɛmpɛ so ntɛm ara.
Splenic Sequestration a Wɔde Siesie Nnipa
Eyi yɛ tebea a egye ntɛmpɛ a ɛde nkwa to asiane mu a ɛka mmofra nkumaa kɛse. Ɛba bere a sickle cells siw mogya a ɛkɔ akyi berɛmo no mu, na ɛma ɛyɛ kɛse na ɛyɛ yaw no. Bere a ebia mmofra binom renkyerɛ yare no ho sɛnkyerɛnne a ɛda adi pefee no, hwɛ sɛnea wɔyɛ mmerɛw, honam ani hwɛbea ne anofafa a ɛyɛ mmerɛw, ɔbrɛ kɛse, yafunu benkum so ɛyaw, ne koma a ɛbɔ ntɛmntɛm. Sɛ wuhu saa nsɛnkyerɛnne yi a, kɔ baabi a wɔhwɛ wɔn a wɔwɔ ayaresa a egye ntɛmpɛ mu ntɛm ara.
Chest Syndrome a Ɛyɛ Hu a Ɛyɛ Den
Eyi yɛ tebea a emu yɛ den yiye a sickle cells siw mogya ntini a ɛwɔ ahurututu mu no kwan. Sɛ wo ho yɛ wo hyew, ɛyɛ den sɛ wobɛhome, wo koko yɛ wo yaw, anaa wofefe , hwehwɛ ayaresa ntɛm ara. Nnuruyɛfo betumi de mframa pa, nnuru a ekum ɔyare mmoawa, ne ɛtɔ mmere bi a, mogya a wɔde ma.
Nsɛnnennen Afoforo a Ɛtena Bere Tenten
Bere kɔ so no, Sickle Cell Disease betumi de nsɛnnennen foforo aba:
- Avascular Necrosis: Sɛ mogya a ɛkɔ nkwaa atitiriw mu (te sɛ asen) no siw a, nnompe mu ntini no betumi afi ase awu. Eyi abu so wɔ mmerante ne mmabaa a wɔadu mpanyin afe so mu. Bere a ɛyaw ano aduru betumi aboa no, nnipa binom hia oprehyɛn.
- Akwaa a Ɛsɛe: Asiane kɛse wɔ hɔ sɛ ɔhaw ahorow a ɛbɛba aniwa, koma, asaabo, ne mmerɛbo mu, ne mogya a ɛbɛtɔ ne akisikuru. Esiane eyi nti, wo duruyɛfo bɛhwɛ sɛnea w’akwaa no yɛ adwuma daa.
Nnompe mu Ntini a Wɔde Si Hɔ Ne Nnɛyi Ayaresa
Wɔ wɔn a wɔtaa nya nsɛnnennen a emu yɛ den fam no, wobetumi asusuw Nnompe mu Ntini a Wɔde Sisi Ho. Saa adeyɛ yi de nkwammoaa a ɛwɔ apɔwmuden si sickle cells a ɛma ntini no ananmu. Wɔ tebea horow bi mu no, eyi betumi ama wɔanya ayaresa a ɛtra hɔ daa.
Nanso, eyi nyɛ ade a obiara betumi apaw. Ɛhwehwɛ sɛ wɔhwehwɛ obi a ɔde ma a ne ntini hyia. Bio nso, sɛ wowɔ akwaa ho nsɛm a ɛwɔ hɔ dedaw (te sɛ koma anaa asaabo mu haw ahorow) a, oprehyɛn no de asiane kɛse ba. Ɛsan nso hwehwɛ sɛ obi bɛtra ayaresabea akyɛ, na wontumi nkyerɛ sɛ wobedi nkonim. Yɛsrɛ sɛ wo ne w’aduruyɛfo kuw no nsusuw ho sɛ ebia eyi yɛ ɔkwan a ɛfata ma wo anaa w’abusua.
Bio nso, mprempren nnuru te sɛ Crizanlizumab wɔ hɔ a ɛbɛboa ma ɛyaw ho haw ahorow so atew. Hwɛ hu sɛ wubebisa wo duruyɛfo no akwan horow yi ho asɛm.
Nkrasɛm a Wɔde Kɔ Fie
- Sickle Cell Disease yɛ awosu mu tebea a ɛsakra mogya mu nkwammoaa kɔkɔɔ no nsusuwii, na ɛde nsɛnnennen a emu yɛ den te sɛ ɛyaw, mogya a ɛtɔ kɔ nipadua mu, ne akwaa a ɛsɛe ba.
- Sɛ wote ɛyaw ho haw, atiridiinini, ɛyɛ den sɛ wobɛhome, anaasɛ wo ho ayɛ wo hyew dodo a, kɔ ayaresabea ntɛm ara anaa kɔ adwumayɛbea a ɛbɛn wo a wɔhwɛ ntɛmpɛ so.
- Nsu pa a wobɛkɔ so anya, asetra pa a wobɛkɔ so akura mu, na woadi nnuru a wɔakyerɛw ama wo (te sɛ Hydroxyurea) akyi pɛpɛɛpɛ no betumi aboa ma woadi nsɛnnennen dodow no ara ho dwuma.
- Wɔ mmofra fam no, ɛho hia sɛ wohu nnuru a wɔde bɔ wɔn ho ban nyinaa ho nsɛm na wɔnom nnuru a ekum ɔyare mmoawa da biara da na wɔasiw ɔyare mmoawa ano.
- Sɛ wowɔ nsɛmmisa anaa nsɛm bi a ɛhaw wo wɔ w’akwahosan anaa wo ba tebea ho a, wo ne w’akwahosan ho ɔyaresafo nsusuw ho bere nyinaa. Nsuro —sɛ wokɔ so nya nsɛm a, ɛboa wo ma wotra ase yiye wɔ tebea yi mu sɛ Nirogi Lanka mpɔtam hɔfo fã.
Sickle Cell Yare, Mogya a ɛtɔ kɔ nipadua mu, ɛyaw ho haw, Nnompe mu Ntini a Wɔde Ma, Akwahosan Ho Nsɛm
