Ède dzesii kpɔ be ame aɖewo bɔbɔa woƒe asibidɛwo ɖe megbe le mɔ si mebɔ o nu, alo be woƒe klowo kple abɔta didi wu ame bubuwo sãa? Le ame aɖewo gome la, esia ate ŋu anye nusi dzɔna le dzɔdzɔme nu ko. Gake ɣeaɖewoɣi la, woate ŋu atsɔ ƒunukpeƒetetedɔ sia ƒomevi asɔ kple lãmesẽkuxi aɖewo. Le nɔnɔme mawo me la, dodokpɔ bɔbɔe aɖe li si ɖɔktawo zãna tsɔ nyaa alesi tututu wò ƒunukpeƒewo te ŋu trɔna bɔbɔe. Woyɔe be Beighton ƒe Dzeside . Mina míaƒo nu tso esia ŋu tsitotsito egbea, alo?
Ènya nusi nye ‘Beighton Score’a?
Kpuie ko la, Beighton Score nye dodokpɔ si dzidzea wò ƒunukpeƒewo ƒe asitɔtrɔ le nɔnɔmewo ŋu, alo afisi nàte ŋu aʋuʋu ƒunukpeƒe aɖe. Elɔ dɔwɔna bɔbɔe ʋɛ aɖewo ɖe eme. Le kpɔɖeŋu me, èbɔbɔa wò asibidɛ suea ɖe megbe hekpɔa dzogoe si dzi wòle. Dzesideɖoɖo aɖe li na dodokpɔ sia, si tso 0 va ɖo 9. Zi alesi nèxɔ dzesi geɖee la, zi nenemae wò ƒunukpeƒewo te ŋu trɔna ɖe nɔnɔmewo ŋui. Eɖi nu bɔbɔe, alo?
Dodokpɔ sia léa ŋku ɖe ƒunukpeƒe siawo ŋu koŋ:
- Wò asibidɛ eveawo siaa ƒe gɔme (le axa eveawo dzi) .
- Abɔta eveawo siaa
- Klo eveawo siaa
- Knuckles , si fia asibidɛwo ƒe ƒunukpeƒewo
- Akɔta (akɔta) .
Esiawoe nye nu vevi siwo ŋu woƒe susu nɔa nu ŋu le.
Ɣekaɣie wozãa ‘Beighton Score’?
Beighton Score nye dodokpɔ si wozãna le ɖoɖo nu si wozãna le afisiafi si kpena ɖe ame ŋu wòkpɔa dɔléle aɖe si woyɔna be Joint Hypermobility Syndrome . Ènya be amehawo katã ƒe 3% lɔƒo xɔ Joint Hypermobility Syndromea?
Le amesiwo le lãmesẽ me ŋutɔ gɔ̃ hã gome la, ƒunukpeƒewo ate ŋu atrɔ ɖe nɔnɔmewo ŋu nyuie, si nye nusi sɔ. Gake ɣeaɖewoɣi la, nɔnɔme sia si woyɔna be Joint Hypermobility Syndrome ate ŋu atso nɔnɔme bubu si gbɔ wòtso gbɔ. Vevietɔ ate ŋu ado ƒome kple Domenyinu ƒe Lãmetsiŋusẽ ƒe Dɔléle (HCTD) . "Kadodo ƒe lãkusi" fia ka siwo léa míaƒe ŋutilã ƒe akpa vovovowo kple ŋutinuwo ɖe wo nɔewo ŋu eye wònaa ŋusẽ wo ko. Dɔléle siawo dzɔna ne gbɔdzɔgbɔdzɔ alo tɔtrɔ aɖe va le esiawo me.
Nɔnɔme vevi siwo dzena le HCTD ƒe hatsotso sia me dometɔ aɖewoe nye:
- Ehlers-Danlos Syndrome (EDS) : Esia ate ŋu agblẽ nu le nuwo abe ŋutigbalẽ, ƒunukpeƒewo, kple ʋukawo ƒe gliwo ene ŋu.
- Marfan Syndrome : Esia ate ŋu agblẽ nu le ŋkuwo, ƒuwo, dzi, kple ʋukawo ŋu.
- Osteogenesis Imperfecta : Le nɔnɔme sia me la, ƒuawo va gblẽna ŋutɔ, si ate ŋu ana ƒuawo nagbã enuenu.
Eyata, ɖewohĩ èse alesi gbegbe ‘Beighton Dzesi’ sia le vevie gɔme, elabena wotu esia ɖe nyatakaka siwo esia na dzi be ɖɔkta ate ŋu anya ne ƒunukpeƒetetedɔ bɔbɔe aɖe le ŋuwò, alo nenye be nu bubu aɖe le ete.
Aleke dodokpɔ sia dzidzea wò ƒunukpeƒewo ƒe asitɔtrɔ le nɔnɔmewo ŋui?
Wò ɖɔkta abɔbɔ wò ƒunukpeƒewo blewuu ahaɖe wo ɖa. Le dzidzenu si nye 0-9 dzi la, àxɔ dzesi ne àte ŋu awɔ nusiwo gbɔna:
Akpa Gbãtɔ: Nusiwo Nàte Ŋu Akpɔ To Wò Ŋutilã Ʋuʋu Me
Esiawoe nye dɔwɔna siwo ɖɔktaa ana nàwɔ, alo woawo ŋutɔwo aʋuʋu wò ƒunukpeƒewo.
- Ðe nàte ŋu abɔbɔ ɖe ŋgɔ, màbɔbɔ wò klowo o, eye nàtsɔ wò asiwo aɖo anyigba keŋkeŋa? (1 point for this) Tsɔe be, ne èbɔbɔ ɖe ŋgɔ eye nèdo asi ɖa la, èle agbagba dzem be yeakpɔe ɖa be yeƒe klowo le dzɔdzɔe eye wò asibidɛwo le asi kam anyigba hã.
- Ne èɖɔ wò abɔtawo ɖo la, ɖe nàte ŋu akeke wo ɖe megbe wu alesi woate ŋu aɖo woe? (Woyɔa esia be ``hyperextending''. Abɔta ɖeka ƒe asixɔxɔ nye dzesi 1, eye abɔta eveawo ƒe asixɔxɔ nye dzesi 2.)
- Azɔ hã, ne èɖɔ klo eveawo ɖo la, ɖe nàte ŋu akeke wo ɖe megbe wòagbɔ woƒe afisi wòle be wòanɔ ŋua? (Esia hã nye ``hyperextend''. Woxɔa klo ɖeka ƒe dzesi 1, eye woxɔa dzesi 2 le klo eveawo siaa me).
- Ðe nàte ŋu abɔbɔ wò asibidɛ si le pinky (asibidɛ suetɔ kekeake si le wò asi dzi) ɖe megbe wu dzidzenu 90a? (teƒe 1 na asibidɛ pinky ɖesiaɖe, dzesi 2 na asibidɛ eveawo).
- Ðe nàte ŋu abɔbɔ wò asibidɛ ɖe megbe ahaka asi wò abɔta ƒe akpa si le ete ŋua? (teƒe 1 na asibidɛ ɖeka, dzesi 2 na asibidɛ eveawo).
Azɔ kpɔ ɖa, ne ètsɔ esiawo ƒo ƒui la, àkpɔ dzesi si sɔ gbɔ wu 9, alo? (1 + 2 + 2 + 2 + 2 = 9) ƒe xexlẽme.
Akpa Evelia: Nyabiase siwo ku ɖe nusiwo me nèto va yi ŋu
Le esia me la, ɖɔktaa biaa nya ʋɛ aɖewo wò tso wò ƒunukpeƒewo ƒe asitɔtrɔ kple ƒunukpeƒewo ƒe vevesese ŋu. Èxɔa dzesi 1 ɖe biabia ɖesiaɖe si ŋu nèɖo be "ɛ̃" ta.
- Ðe nète ŋu tsɔ wò asiwo da ɖe anyigba evɔ mèbɔbɔ klo o kpɔa?
- Ðe nète ŋu ƒo wò asibidɛ hetsɔe ƒo ɖe wò asi ƒe megbe kpɔa?
- Esime nènye ɖevi alo sɔhɛ tsitsi la, ɖe nèdoa dzidzɔ na wò kpɔ be yeabɔbɔ wò ŋutilã ahanɔ etɔtrɔm le xɔ̃wòwo ŋkumea? Ðe nète ŋu wɔ ‘mamãwo’a? (Eyae nye be nànɔ anyi ɖe anyigba eye nàkeke wò afɔwo ɖe axawo dzi).
- Ðe wò abɔta alo klo aɖe vuvu wu zi ɖeka kpɔ, eɖanye ɖevi alo ƒewuivi nènye oa?
- Ðe nèbua ɖokuiwò be yenye "duble-jointed"? (Eyae nye be, ɖe nèsena le ɖokuiwò me be yeƒe ƒunukpeƒewo bɔbɔna wu bubuwoa?)
Aleke nènɔa te ɖe dzesi siawo dzi léa ŋku ɖe ‘Joint Hypermobility Syndrome’ ŋu?
Wò ɖɔkta aƒo wò dzesiwo katã nu ƒu. Àte ŋu axɔ Joint Hypermobility Syndrome ne nusiwo gbɔna dometɔ ɖeka dzɔ:
1. 1. .Ne èxɔ dzesi 4 alo esi wu nenema le ŋutilã ƒe ʋuʋu ƒe mɔnu siwo míeyɔ va yi me, eye nèse veve le ƒunukpeƒe ene alo esi wu nenema me wu ɣleti etɔ̃.
2. Alo, ne èɖo nya siwo wobia tso nuteƒekpɔkpɔ mawo siwo va yi ŋu la dometɔ eve alo esi wu nenema ŋu be "ɛ̃".
Alea koŋue míewɔna kpɔa nɔnɔme sia ƒe susu.
Nukae wòle be nàkpɔ mɔ na ne èle ‘Beighton Score’ dodokpɔa wɔm?
Esia nye dodokpɔ bɔbɔe aɖe ŋutɔ. Wò ɖɔkta agblɔ na wò be nàʋuʋu wò ƒunukpeƒewo le nɔnɔme aɖewo me. Ðewohĩ ahiã be nàmlɔ aba dzi alo anɔ zikpui dzi hafi awɔ dɔ siawo. Aɖabaƒoƒo ʋɛ aɖewo koe dodokpɔ bliboa xɔa, eye màse veve aɖeke o. Eyata naneke meli si ŋu woatsi dzi ɖo o.
Ðe afɔku alo nugbegblẽ aɖewo le dodokpɔ sia mea?
Ao, menye nenema kura o. Womegblɔ afɔku alo nugbegblẽ le ame ŋu le Beighton Score dodokpɔa ŋu o. Enye dodokpɔ si le dedie ŋutɔ.
Nukae nye Beighton ƒe Dzesi ‘nyui’?
‘Beighton Score’ va zua ‘positive’ , si fia be ɖikeke aɖe li be Joint Hypermobility Syndrome ate ŋu anɔ anyi, le nɔnɔme eve siawo me:
- Ne èxɔ dzesi ene (4) alo esi wu nenema tso asitɔtrɔ le nɔnɔmewo ŋu dodokpɔ ƒe dɔwɔna mawo me .
- Alo, ne èxɔ dzesi eve (2) alo esi wu nenema (si fia be "ɛ̃" ƒe ŋuɖoɖo eve alo esi wu nenema) tso nyabiase siwo wobia tso nuteƒekpɔkpɔ siwo su asiwò va yi ŋu me .
Ele bɔbɔe, alo?
Nukae Beighton Score ƒe emetsonuwo fia?
Zi alesi wò dzesiwo loloe la, zi nenemae wò ƒunukpeƒewo ƒe bɔbɔ alo te ŋu trɔna ɖe nɔnɔmewo ŋui. Beighton Score dodokpɔ me tsonu nyui aɖe fia be anɔ eme godoo be Joint Hypermobility Syndrome le ŋuwò .
Gake nu vevi aɖe si dzi wòle be míaɖo ŋkui enye si. Dɔléle sia ate ŋu atso atikewɔwɔ me nɔnɔme bubu siwo gbɔ wòtso gbɔ ɣeaɖewoɣi. Eyata, wò ɖɔkta aƒo nu kpli wò eye wòatso nya me le nusi nàwɔ azɔ ŋu. Zi geɖe la, ahiã be nàgawɔ dodokpɔ aɖewo be nànya nɔnɔme bubu siwo tututu ate ŋu anɔ ŋuwò.
Ðo ŋku edzi be Beighton ƒe Dzeside ɖeɖe mate ŋu akpɔ nɔnɔmewo abe Ehlers-Danlos Dɔléle (EDS), Marfan Dɔléle, alo Osteogenesis Imperfecta ene o. Dodokpɔ siwo kplɔ wo nɔewo ɖo ƒe akpa ɖeka koe wònye si akpe ɖe ŋuwò nànya nusi tututu gbɔ wò dzesiawo tso.
Ɣeyiɣi didi kae wòxɔna hafi míenyaa emetsonuwo?
Esiae nye nu nyuitɔ kekeake! Àte ŋu anya ‘Beighton Score’ ƒe emetsonuwo enumake.Ne èwu dodokpɔa ƒe akpa ɖesiaɖe nu la, ɖɔkta ate ŋu abu akɔnta le dzesiawo ŋu eye wòana dodokpɔa me tsonuawo wò. Eyata, lala aɖeke mele afima o.
Nya kawoe wòle be nàbia wò ɖɔkta tso Beighton Score dodokpɔa ŋu?
Ne èle dodokpɔ sia wɔm la, anyo be nàbia nya siawo tɔgbe wò ɖɔkta, ne ènya dodokpɔa me tsonu vɔ teti:
- Ðe wòhiã be mawɔ dodokpɔ bubu aɖewo le Beighton ƒe Dzesi la megbea?
- Ne Joint Hypermobility Syndrome le ŋuwò la, aleke wodaae?
- Nukae mate ŋu awɔ be nye ƒunukpeƒewo ƒe lãmesẽ nanyo ɖe edzi? (Le kpɔɖeŋu me, kamedede, nuɖuɖu ƒe tɔtrɔ, kple bubuawo)
- Nukae nye mɔkpɔkpɔ na amesi ŋu Joint Hypermobility Syndrome le? Eyae nye be, ɖe mate ŋu anɔ agbe si sɔa? Nu kawoe wòle be malé ŋku ɖo?
Ele vevie ŋutɔ be nàbia nya siawo tɔgbe eye nàse wò nɔnɔmea gɔme nyuie.
Eyata, gbedasi mamlɛtɔ si woatsɔ ayi aƒemee:
Enyo, eyata tso nusiwo me míedzro me la, mele mɔ kpɔm be èkpɔ nusi Beighton ƒe Dzesi nye nyuie. Kpuie ko la:
- Beighton Score nye dodokpɔ bɔbɔe aɖe ŋutɔ si woate ŋu awɔ le wò ɖɔkta ƒe dɔwɔƒe tututu.
- Esia dzidzea alesi wò ƒunukpeƒewo te ŋu trɔna ɖe nɔnɔmewo ŋui.
- Ne èxɔ dzesi si gogo 9 la, efia be wò ƒunukpeƒewo te ŋu trɔna bɔbɔe ŋutɔ.
- Ne dɔléle sia si wokpɔ ɖee fia be Joint Hypermobility Syndrome , le ŋuwò la, ahiã be woado wò kpɔ ake, elabena ɣeaɖewoɣi la, atikewɔwɔ me dɔléle bubu si le ŋuwò gbɔ ate ŋu atso dɔléle sia gbɔ.
- Eyata ele vevie be nàƒo nu kple wò ɖɔkta be nànya afɔɖeɖe nyuitɔ siwo nàwɔ le etsɔme, alo ne ehiã be wogadoe kpɔ.
Ne nyabiase alo dzimaɖitsitsi aɖewo le asiwò ku ɖe wò ƒunukpeƒewo ŋu la, mègavɔ̃ be yeado go kple wò ɖɔkta alo dɔnɔdzikpɔla aƒo nu tso eŋu o. Woakpe ɖe ŋuwò.
` Beighton ƒe dzesi, Ƒunukpeƒetetedɔ ƒe Dɔléle, Ehlers-Danlos ƒe dɔléle, Marfan ƒe dɔléle, Kadodo ƒe lãmekawo ƒe dɔléle











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