Ðe thalassemia le ŋuwò alo viwòa? Mina míaƒo nu tso Beta Thalassemia ŋu

Ðe nèsena le ɖokuiwò me ɣesiaɣi be ɖeɖi te ye ŋu eye yeƒe lãme gbɔdzɔa? Ɣeaɖewoɣi la, míesusuna be nu siawo sɔ, gake dɔléle aɖe si do ƒome kple ʋu ate ŋu anɔ wo megbe. Beta Thalassemia nye dɔléle si tso dzidzime yi dzidzime le míaƒe domenyiŋusẽfianuwo me, gake woate ŋu adae. Vɔvɔ̃ kple ɖikeke le ame geɖe me le esia ŋu. Eyata egbea, mina míaƒo nu tso esia ŋu eme nakɔ eye wòanɔ bɔbɔe.

Kpuie ko la, nukae nye beta thalassemia?

Ele bɔbɔe ŋutɔ. Lãmenugbagbevi siwo woyɔna be ʋumenugbagbevi dzĩwo le míaƒe ʋu me. Lãmenugbagbevi siawo ƒe dɔe nye be woatsɔ ɔksidzin ayi míaƒe ŋutilã ƒe akpawo katã. Protein tɔxɛ aɖe li si kpena ɖe ʋumenugbagbevi dzĩwo ŋu wowɔa dɔ sia nyuie, si woyɔna be hemoglobin .

Fifia, le amesi ŋu beta thalassemia le gome la, ŋutilãa mewɔa protein sia si woyɔna be hemoglobin wòde edeƒe o. Nukae dzɔna ɣemaɣi? Ʋumenugbagbevi dzĩawo mete ŋu wɔa woƒe dɔ nyuie o, eye wogblẽna kabakaba.

Ne ʋumenugbagbevi dzĩ siwo le lãmesẽ me mesɔ gbɔ o la, ŋutilãa mekpɔa ɔksidzin si wòhiã o. Míeyɔa nɔnɔme sia be ʋusɔgbɔdɔ . Ʋusɔgbɔdɔ ate ŋu ana nàse le ɖokuiwò me be ɖeɖi te ye ŋu, gbɔdzɔgbɔdzɔ, eye gbɔgbɔtsixe tsia ƒowò. Ne nɔnɔme sia yi edzi la, ate ŋu agblẽ nu le míaƒe ŋutilã ƒe ŋutinu veviwo hã ŋu.

Nukawoe nye beta thalassemia ƒomevi veviwo?

Beta thalassemia ƒomevi vevi etɔ̃e li, le woƒe sesẽme nu. Ele vevie ŋutɔ be míase nya sia gɔme pɛpɛpɛ.

Nukae nye dɔléle sia ƒe dzesiwo?

Dzesiawo ate ŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ, le thalassemia ƒomevi si le ŋuwò kple alesi wòsẽe nu.

• Ðewohĩ dzesi aɖeke manɔ amesi ŋu thalassemia minor le ŋu o.
• Ame siwo ŋu thalassemia intermedia kple major le ate ŋu akpɔ dzesi siwo gbɔna la dometɔ ɖeka alo esi wu nenema:
• Ŋutilã si le ɣie: Ŋutilãa dzena abe ɖe wòle ɣie eye eƒe amadede trɔna le ʋu ƒe anyimanɔmanɔ ta.
• Ðeɖiteameŋu kple gbɔdzɔgbɔdzɔ si gbɔ eme: Sese le eɖokui me be kuviawɔwɔ, ɖeɖiteameŋu ɣesiaɣi.
• Ƒodo ƒe ʋuʋu: Ƒodoa dona ɖe ŋgɔ le ŋutinuwo abe aklã kple dɔgbo ene ƒe lolome ta.
• Aɖuɖɔ si ƒe amadede nye viviti: Aɖuɖɔ ƒe amadede va zua viviti.
• Tsitsi ƒe megbetsitsi: Ðeviwo ƒe ŋutilã ƒe tsitsi dzɔna blewu wu ɖevi bubuwo.
• Mo ƒe ƒu ƒe gbagbã: Le nɔnɔme sesẽ aɖewo me la, mo ƒe ƒuwo ƒe nɔnɔme trɔna.
• Jaundice: Ŋutilã ƒe ɣie kple ŋku ƒe ɣie.

Aleke woawɔ anya dɔléle sia?

Zi geɖe la, wokpɔa dɔléle sia le ƒe 6 va ɖo 12. Woate ŋu ade dzesii le vome ne èyi ɖɔkta gbɔ le ʋusɔgbɔdɔ ƒe dzesiwo ta, alo le ʋudodokpɔ si wowɔna edziedzi le susu bubu ta me.

Ɣeaɖewoɣi ne èkpɔ ʋusɔgbɔdɔ la, àsusui vodadatɔe be iron ƒe anyimanɔmanɔ gbɔe wòtso. Ne èna iron-tikewo le ɣeyiɣi sia tɔgbe me la, ate ŋu agblẽ nu le thalassemia dɔnɔ ŋu. Eyata ele vevie ŋutɔ be woayi ʋumenugbagbeviɣidɔdala gbɔ hafi anya dɔlélea nyuie.

Esi wònye be eƒua du le ƒomewo me ta la, ate ŋu adzɔ be ame siwo ŋu thalassemia le nanɔ wò ƒomea alo ƒometɔwo me. Azɔ hã, dɔléle sia bɔ ɖe amesiwo tso dukɔwo abe Asia, Titina Ɣedzeƒe, Italy, kple Greece ene me wu.

Dodokpɔ vevi siwo wozãna tsɔ dea dzesi dɔlélea dometɔ aɖewoe nye:

• Ʋu Xexlẽme Blibo (CBC): Esia léa ŋku ɖe ʋumenugbagbevi dzĩwo, ʋumenugbagbevi ɣiwo, kple ʋumenugbagbevi dzĩwo ƒe xexlẽme, woƒe lolome, kple woƒe tsitsi le wò ʋu me ŋu.
• Hemoglobin electrophoresis: Wozãa esia tsɔ nyaa hemoglobin ƒomevi siwo tututu le wò ʋu me kple agbɔsɔsɔ si le wò ʋu me.
• Dodokpɔwo na vidada funɔwo: Ne thalassemia carrier state le vidada funɔ aɖe ŋu la, woate ŋu awɔ dodokpɔwo abe Chorionic villus sampling (CVS) alo Amniocentesis ene atsɔ anya nenye be vidzĩ si le vidzidɔa me hã ŋue wògblẽ nu le.

Nukawoe nye atikewɔmɔnuawo?

Atike si nàxɔ anɔ te ɖe wò thalassemia ƒomevi kple eƒe sesẽ dzi.

• Le amesiwo ƒe nɔnɔmewo mesẽ o gome (Sue): Ðewohĩ mahiã be woawɔ atike na wo o.
• Le amesiwo ƒe nɔnɔme le titina gome: Ɣeaɖewoɣi, abe ne dɔléle alo dɔlékui aɖe dze ame dzi ene la, ate ŋu ahiã be woado ʋu na wo.
• Le amesiwo ƒe nɔnɔme sesẽ (Gãtɔ): Esi ʋusɔgbɔdɔ sesẽ le ame siawo ŋu ta la, ele vevie be woado ʋu na wo edziedzi .

Ʋudodo enuenu ate ŋu ana iron naƒo ƒu ɖe ŋutilãa me madzemadzee. Woyɔa esia be ``Iron overload.'' Iron sia si sɔ gbɔ ate ŋu aƒo ƒu ɖe ŋutinuwo abe dzi kple aklã ene me eye wòagblẽ nu le wo ŋu. Be woaxe mɔ ɖe esia nu la, wowɔa atike aɖe tsɔ ɖea iron si sɔ gbɔ ɖe ŋutilãa me ɖa. Woyɔa esia be iron chelation therapy . Wodoa esia abe atikekui alo atikekui ene.

Tsɔ kpe ɖe eŋu la, àte ŋu azã atikewɔmɔnu siwo gbɔna abe alesi wò ɖɔkta gblɔe ene:

• Amekoko si wowɔna tsɔ ɖea aɖuɖɔ ɖa.
• Ƒumeŋuɖui dodo na ame .
• Egbegbe atikewɔwɔwo abe domenyiŋusẽfianu ƒe atikewɔwɔ ene.

Aleke woawɔ anɔ agbe le lãmesẽ me kple thalassemia?

Togbɔ be agbenɔnɔ kple thalassemia ate ŋu asesẽ hã la, nu geɖe li nàte ŋu awɔ atsɔ alé be na ɖokuiwò.

Nu siwo nàte ŋu awɔ

• Nuɖuɖu si naa lãmesẽ: Ƒo atikutsetse kple amagbe geɖe wu. Gake bia wò ɖɔkta nenye be ele be nàɖo seɖoƒe na nuɖuɖu siwo me iron sɔ gbɔ ɖo (lã, tɔmelã, amagbe aɖewo, kple nuku siwo me iron sɔ gbɔ ɖo) .
• Kamedede edziedzi: Ƒo ɖokuiwò ɖe kamedede fafɛ abe azɔlizɔzɔ kple gasɔdodo ene me.
• Wɔ ɖe wò ɖɔkta ƒe mɔfiamewo dzi: Wɔ ɖe ŋkeke siwo dzi nàdo ʋu kple atike nono ƒe ɖoɖowɔɖiwo dzi pɛpɛpɛ. Kpɔ wò ɖɔkta le ŋkeke siwo woɖo ɖi dzi.
• Takpɔ ɖokuiwò tso dɔlékuiwo me: Klɔ asi enuenu. Te ɖa tso ame siwo le dɔ lém gbɔ.
• Do atike: Na atikewɔmɔnu siwo katã wò ɖɔkta kafu, abe dzamezã ƒe atike ene, ɖe game dzi.
• Bu wò susu ƒe lãmesẽ ŋu kpɔ: Esesẽna be wò ɖeka nàto mɔzɔzɔ sia me. Ðo dze kple wò ƒometɔwo kple xɔlɔ̃wo. Ne ehiã la, di tagbɔdɔdala alo susuŋutinunyala ƒe kpekpeɖeŋu.

Aɖaŋuɖoɖo na dɔnɔdzikpɔlawo

Ne wòe nye ɖevi alo ƒometɔ aɖe si ŋu thalassemia le dzikpɔla la, wò akpa si nèwɔna le vevie ŋutɔ.