Ðe "nyitsu ƒe ŋku" ƒe nɔnɔme le wò ŋkuwo mea? Mina míasrɔ̃ nu tso (Bull's Eye Maculopathy) sia ŋu!

Efɔ̃a? Egbea míele nu ƒom tso ŋku ƒe nɔnɔme aɖe si womenya tututu o, gake wòle vevie ŋutɔ ŋu. Ɣeaɖewoɣi la, míaƒe ŋkuwo te ŋu trɔa alesi míekpɔa nui evɔ míenya o. Èse nɔnɔmetata aɖe si le abe taɖodzinu ene le taɖodzinu ƒe ʋuƒo dzi kpɔa? Emae nye nusi dzɔna le nɔnɔme sia si woyɔna be Bull's Eye Maculopathy'' me. Ŋkɔa ɖi nusi wɔ nuku vie, alo? Gake mègatsi dzi o, mina míaƒo nu tso eŋu tsitotsito eye míaƒo nu tso eŋu bɔbɔe.

Nukae nye Bull ƒe Ŋku ƒe Dɔléle''? Ne míagblɔe kpuie ŋutɔ la...

Bull’s Eye Maculopathy nye dɔléle si mebɔ kura o si nana lãmenugbagbevi siwo le ŋku ƒe ŋkume, si nye ŋkume ƒe akpa vevitɔ kekeake, gbɔdzɔna vivivi eye ne míagblɔe tututu la, wogblẽna.

Bu eŋu kpɔ, ne wò ŋku le abe fotoɖemɔ̃ ene la, ŋkume ƒe ŋkume le abe film alo sensor si le fotoɖemɔ̃a megbe ene. Woléa nɔnɔmetata siwo míekpɔna la ɖe afima. Le ŋkua ƒe titina tututu la, teƒe sue aɖe gake wòle vevie ŋutɔ si kpena ɖe mía ŋu míekpɔa nuwo nyuie ŋutɔ eye wòdzena nyuie. Emae nye nusi woyɔna be macula. Macula sia kpena ɖe mía ŋu míekpɔa nu nyuiwo nyuie, abe ne míele agbalẽ aɖe xlẽm, le ŋku lém ɖe ame ƒe mo ŋu, alo ne míetsɔ ka tsɛ aɖe kpe ɖe eŋu ene.

Eyata, le Bull's Eye Maculopathy'' me la, ne lãmenugbagbevi siwo le macula'' sia me gblẽ la, ne ɖɔkta do ŋkua ƒe eme kpɔ la, wokpɔa asigɛ siwo ƒe amadede trɔ ƒe nɔnɔme aɖe le macula'' ma me. Exɔ ŋkɔ elabena edze abe asigɛ siwo le atidada ƒe taɖodzinu (nyitsu ƒe ŋku ƒe nɔnɔme) dzi ene. Nɔnɔme sia ate ŋu ana ame nabu nu tegbee.

Woate ŋu anyi dɔléle sia ƒe dome (i.e., atso dziwòlawo gbɔ to domenyiŋusẽfianuwo dzi). Ðɔktawo yɔa Bull's Eye Maculopathy'' ƒe domenyiŋusẽfianu sia ɣeaɖewoɣi be Benign Concentric Annular Macular Dystrophy (BCAMD)''. Ate ŋu adzɔ hã le ŋkudɔ bubuwo ta alo atike aɖewo zazã ɣeyiɣi didi ƒe nugbegblẽ le ame ŋu .

Nukpɔkpɔ ƒe kuxi ɖesiaɖe ate ŋu ado vɔvɔ̃ na ame. Gake wò ɖɔkta ate ŋu akpe ɖe ŋuwò nàke ɖe nusi gbɔ wòtso ŋu eye wòana atike kple kpekpeɖeŋu si nèhiã be nàte ŋu anɔ te ɖe nɔnɔmea nu la wò.

Ŋusẽ kawoe Bull’s Eye Maculopathy ate ŋu akpɔ ɖe nukpɔkpɔ dzi?

Lãmenugbagbevi siwo kpena ɖe mía ŋu míekpɔa nuwo ƒe gbegblẽ gbɔe Bull’s Eye Maculopathy tsona. Eyata, esia ate ŋu akpɔ ŋusẽ ɖe wò titinakpɔkpɔ dzi le agbɔsɔsɔ vovovowo me.

• Ate ŋu asesẽ na ame aɖewo be woakpɔ nya nyuiwo tsitotsito.
• Ðewohĩ màte ŋu ade vovototo amadedewo me nyuie o, alo wò amadedewo ƒe dzedzeme dzi aɖe akpɔtɔ.
• Nukpɔkpɔ ate ŋu aɖiɖi le zã me.
• Esi nukpɔkpɔ le titina le gbɔdzɔgbɔdzɔm la , ate ŋu asesẽ be woaxlẽ agbalẽwo, aku ʋuwo, eye woakpɔ nuwo le ŋgɔ tẽ.
• Dɔléle sia ate ŋu adze ŋku ɖeka ko alo ŋku evea siaa dzi.

Gake zi geɖe la, amesiwo ŋu Bull’s Eye Maculopathy le la mekpɔa kuxi gã aɖeke le woƒe ŋku ƒe nukpɔkpɔ le gota gome o - si nye nusi woate ŋu akpɔ tso woƒe ŋku ƒe dzogoe dzi. Gake esi wònye be zi geɖe la, nɔnɔme sia nyea nɔnɔme si yia ŋgɔ ta la, nukpɔkpɔ ate ŋu agblẽ ɖe edzi le ɣeyiɣi aɖe megbe .

Amekae le afɔku gã me be wòaxɔ Bull's Eye Maculopathy''?

Afɔku nye nane si dzia dɔléle aɖe xɔxɔ ƒe mɔnukpɔkpɔ ɖe edzi. Afɔku geɖewo li na Bull's Eye Maculopathy:

• Ne Bull's Eye Maculopathy'' (domenyiŋusẽfianu ƒe ŋutinya) le ƒomea me .
• Ŋkudɔ bubuwo abe ŋku ƒe dɔmawɔmawɔ nyuie ene ƒe amesinɔnɔ .
• Domenyiŋusẽfianu aɖewo , le kpɔɖeŋu me, Batten dɔléle alo Stargardt dɔléle.
• Atike aɖewo zazã ɣeyiɣi didi, vevietɔ esiwo wozãna tsɔ daa dɔléle siwo dɔlélenutsiŋutete wɔna (ne míagblɔe bɔbɔe la, dɔléle siwo tsoa dɔlélenutsiŋutete gbɔ nye nɔnɔme siwo me wò ŋutilã ŋutɔ ƒe dɔlélenutsiŋutete dzea wò ŋutɔ wò lãmenugbagbevi siwo le lãmesẽ me dzi).

Aleke gbegbee nɔnɔme sia bɔe?

Le nyateƒe me la, Bull’s Eye Maculopathy nye dɔléle si mebɔ kura o. Le kpɔɖeŋu me, le United States gɔ̃ hã la, ame ʋɛ aɖewo koe dɔléle sia le. Eyata, mègatsi dzodzodzoe ne ède dzesi tɔtrɔ aɖewo le wò ŋkumekpɔkpɔ me o.

Nukae nye nusiwo hea Bull's Eye Maculopathy'' vɛ?

Susu geɖewo li siwo tae esia ate ŋu anɔ dzɔdzɔm ɖo:

1. Domenyiŋusẽfianu:

Bull’s Eye Maculopathy, si wogayɔna be BCAMD, nye dɔléle si nye autosomal dominant. Kpuie ko la, ne domenyiŋusẽfianu si trɔ le dzila ɖesiaɖe si na dɔlélea la, mɔnukpɔkpɔ 50% li be wo vi nanyi dɔlélea dome. Domenyiŋusẽfianu siawo nye míaƒe DNA ƒe akpa aɖewo siwo dzraa nyatakakawo ɖo ɖe míaƒe ŋutilã me.

2. Dɔléle bubuwo:

Ŋkudɔ bubuwo abe cone-rod dystrophy alo retinitis pigmentosa ene hã ate ŋu ahe Bull’s Eye Maculopathy vɛ. Azɔ hã, abe alesi míegblɔe va yi ene la, amesiwo ŋu domenyiŋusẽfianu ƒe dɔlélewo abe Batten dɔléle alo Stargardt ƒe dɔléle ene le hã le afɔku me be woaxɔ nɔnɔme sia.

3. Aɖi si le eme:

Nu aɖewo, vevietɔ atike aɖewo, ate ŋu agblẽ nu le lãmenugbagbevi siwo le wò ŋku ƒe titina (macula) ŋu. Le kpɔɖeŋu me, atikewo abe chloroquine alo hydroxychloroquine, siwo wozãna tsɔ daa dɔlélewo abe ƒunukpeƒetetedɔ alo lupus ene zazã ɣeyiɣi didi ate ŋu ahe Bull’s Eye Maculopathy vɛ.

Azɔ hã, amesiwo wòle be woado ʋu na wo enuenu ate ŋu axɔ dɔléle aɖe si woyɔna be hemochromatosis (iron overload). Esia ate ŋu agblẽ nu le wò ŋku ƒe ŋkume hã ŋu.

Aleke atike si nye (Hydroxychloroquine) hea (Bull ƒe Ŋku ƒe Dɔléle) vɛ?

Eŋutinunyalawo menya alesi tututu esia dzɔna haɖe o. Gake numekukuwo ɖee fia be atike la ate ŋu abla ɖe lãmenugbagbevi siwo le wò ŋkume eye wòakpɔ ŋusẽ ɖe alesi lãmenugbagbevi mawo wɔa dɔe dzi. Zi geɖe la, esia dzɔna ne èno atike la ƒe agbɔsɔsɔ gbogbo aɖe ɣeyiɣi didi. Esia tae ɖɔktawo kafui be woado ŋkume na amesiwo le atike siawo nom edziedzi.

Nukae nye Bull's Eye Maculopathy'' ƒe dzesiwo?

Nɔnɔme sia gblẽa nu le nukpɔkpɔ ŋu koŋ. Dzesiawo ate ŋu anye:

• Nukpɔkpɔ si me mekɔ o alo si me afu le.
• Teƒe dovivitiwo alo vɔvɔli dovivitiwo kpɔkpɔ le wò nukpɔkpɔ ƒe akpaa dzi.
• Amadedewo nyanya sesẽ alo amadedewo ƒe ŋkumaʋumaʋu keŋkeŋ.
• Nuwo abe ka siwo le tsia dzi le ŋkume (ŋku ƒe tsiƒuƒu) kpɔkpɔ alo kekeli ƒe keklẽ kpɔkpɔ.
• Nukpɔkpɔ si bɔbɔ ŋutɔ .

Ðo ŋku edzi be mègasusu be Bull’s Eye Maculopathy le ye ŋu le esi dzesi siawo dometɔ ɖeka alo eve le ye ŋu ta ko o. Esiawo ate ŋu anye ŋku ƒe dɔléle bubuwo ƒe dzesiwo hã. Eyata ele vevie be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo.

Aleke Bull's Eye Maculopathy'' dzena le ŋkua me?

Esia menye nusi nàte ŋu ade dzesii ne èkpɔ ahuhɔ̃e me o. Ŋkudɔdala aɖe atsɔ dɔwɔnu tɔxɛ aɖe si woyɔna be ŋkumekpɔmɔ̃ alé ŋku ɖe wò ŋkume kple ŋkume ƒe ŋkume ŋu akpɔe ɖa be ele ŋuwò alo mele ŋuwò o.

Zi geɖe la, "nyitsu ƒe ŋku" ƒe nɔnɔme sia dzena abe titina goglo si do viviti ene eye asigɛ geɖe siwo ƒe amadede le keklẽm ƒo xlãe. Titina si do viviti la tsi tre ɖi na ŋku ƒe ŋkume ƒe akpa si sɔ. Kplɔ̃ siwo ƒo xlãe la mesɔ o. Kplɔ̃ siawo ate ŋu anye aŋutiɖiɖi, pink, alo aŋutiɖiɖi si me kɔ. Amadede vovovo siawo tsoa nukpɔkpɔ ƒe titina (macula) ƒe gbegblẽ alo gbegblẽ gbɔ.

Aleke wokpɔa Bull’s Eye Maculopathy ƒe dɔlélea?

Wò ɖɔkta ate ŋu awɔ ŋkudɔ geɖe atsɔ anya ne Bull’s Eye Maculopathy le ŋuwò. Wo dometɔ aɖewoe nye:

• Nukpɔkpɔ ƒe ŋutete dodokpɔ: Esia nye dodokpɔ be nàkpɔ alesi nàte ŋu akpɔ nu nyuie. Woabia tso asiwò be nàxlẽ ŋɔŋlɔdzesiwo ƒe nɔnɔmetata si woɖo ɖe ɖoɖo nu (Snellen ƒe nɔnɔmetata'') alo ŋkuléleɖenuŋu si ƒe ŋɔŋlɔdzesiwo ƒe lolome to vovo. Woado wò nukpɔkpɔ kpɔ kple ŋku eveawo kple ŋku ɖeka si wotu ɖe vovo.
• Nukpɔkpɔ ƒe dodokpɔ:Esia alé ŋku ɖe wò titinakpɔkpɔ kple gotagome nukpɔkpɔ ŋu. Ate ŋu ana nànya hã ne ŋkuagbãtɔ aɖewo le ŋuwò. Woate ŋu abia tso asiwò be nàlé ŋku ɖe fli siwo le fli me ŋu, alo woabia tso asiwò be nàsi akaɖiwo alo aʋuʋu wò asiwo akpɔ afisi nàte ŋu akpɔ nu le ŋgɔwò kple axawo.
• Amadedewo ƒe nukpɔkpɔ dodokpɔ: Wofia nɔnɔmetata si wotsɔ amadede ƒe dzesiwo wɔ eye xexlẽdzesi le titina (amadede ƒe agbalẽvi dodokpɔ). Ne mète ŋu kpɔ xexlẽdzesia o la, ɖewohĩ amadede ƒe ŋkuʋuʋu le ŋuwò. Àte ŋu azã mɔ̃ aɖe si woyɔna be anomaloscope hã atsɔ akpɔ alesi nèkpɔa kekeli kple amadedewo ƒe keklẽ.
• Ŋkudɔdamɔnu: Esia bia be woatsɔ ŋkumeɖonu akeke ŋkume ƒe ŋkume. Emegbe wozãa ŋkumekpɔmɔ̃ tsɔ léa ŋku ɖe wò ŋkume ƒe ŋkume, ŋkume ƒe ŋkume ƒe ŋkume, ŋkume ƒe ŋkume ƒe ŋkume, ŋkume ƒe ŋkume ƒe ŋkume ƒe ŋkume, ŋkume ƒe lãkusi, kple ʋuka siwo ƒo xlã wò ŋu. Wogayɔa dodokpɔ sia be fundoscopy.
• Optical coherence tomography (OCT) dodokpɔ: Esia nye dodokpɔ si me vevesese aɖeke mele o. Ezãa kekeli ƒe ƒutsotsoewo tsɔ ɖea wò ŋkume ƒe ƒuƒoƒo siwo le wò ŋku ƒe titina, siwo le akpa etɔ̃ (3D) me tsitotsito ŋutɔ. Dodokpɔ sia ate ŋu ade dzesi nusiwo gblẽ kple esiwo gblẽ le ŋku ƒe ŋkume ŋu kaba eye wòadze ƒã wu dodokpɔ bubuwo.
• Fundus autofluorescence imaging (FAF) dodokpɔ: Esia nye nɔnɔmetatawo ɖeɖe ƒe mɔnu yeye aɖe. Ezãa akaɖi blɔ tsɔ léa ŋku ɖe lãmenugbagbevi siwo me amadede le siwo le wò ŋkume ƒe ŋkume ŋu. Lãmenugbagbevi aɖewo xɔa kekeli sia alo ɖenɛ fiana le mɔ si to vovo na bubuwo tɔ nu. Esia kpena ɖe ɖɔktaa ŋu wòkpɔnɛ nenye be nu gblẽ le ŋkume ƒe ŋkume ŋu alo gblẽ nu le eŋu.

Ðe woate ŋu ada Bull’s Eye Maculopathy keŋkeŋa?

Nublanuitɔe la, womekpɔ atike blibo aɖeke na Bull's Eye Maculopathy'' o.

Aleke wodaa Bull’s Eye Maculopathy ƒe dɔléleae?

Fifia la, atike aɖeke meli si ate ŋu ana nukpɔkpɔ si bu le Bull's Eye Maculopathy. ta la nagaɖo anyi o.Ke hã, ne atike aɖe alo iron si sɔ gbɔ ɖe ŋutilã me (aɖi) gbɔe nɔnɔmea tso la, ne wodzudzɔ atike la alo iron ƒe agbɔsɔsɔ dzi ɖuɖu ate ŋu axe mɔ ɖe dɔlélea nu alo aɖu edzi be wòagagblẽ ɖe edzi o.

Zi geɖe la, atikewɔwɔ ƒe taɖodzinu vevitɔe nye be wòakpe ɖe dɔnɔwo ŋu woanɔ agbe kple nɔnɔmewo abe ŋku ƒe ʋuʋu kple amadede ƒe ŋkumaʋumaʋu ene. Wò ɖɔkta ate ŋu aɖo aɖaŋu na wò be:

• Mɔ̃ɖaŋununya si kpena ɖe ame ŋu: Le kpɔɖeŋu me, videodzidzenu, nukpɔkpɔmɔ̃, alo screen reader.
• Glasses alo ŋkumeɖonu siwo wotsɔna kpɔa ŋkume.
• Nukpɔkpɔ si mebɔ o ƒe ɖɔɖɔɖo alo dɔwɔwɔ ƒe atikewɔwɔ: Esiawo fiaa mɔnu kple aɖaŋu vovovowo wò be nàwɔ gbesiagbedɔwo kple ŋkumekpɔkpɔ dzi ɖeɖe kpɔtɔ.
• Nukpɔkpɔ ƒe kpekpeɖeŋunuwo: Nuwo abe asidzinu siwo lolona, ​​didiƒekpɔmɔ̃, alo kekeli ƒe ŋkumekpɔnu ene.

Nukae nye mɔkpɔkpɔ na amesi ŋu Bull's Eye Maculopathy'' le?

Zi geɖe la, nukpɔkpɔ ƒe bu si Bull’s Eye Maculopathy hena vɛ la nɔa anyi ɖaa eye ate ŋu anɔ ŋgɔ yim le ɣeyiɣi aɖe megbe . Gake abe alesi míegblɔe va yi ene la, ne aɖi aɖe gbɔe ŋku ƒe nugbegblẽ tso la, aɖinu la ƒoƒo asa na ate ŋu akpe ɖe ame ŋu be nɔnɔmea nagagblẽ ɖe edzi o.

Ðe mɔ aɖe li si dzi woato axe mɔ ɖe Bull's Eye Maculopathy'' nua?

Le nyateƒe me la, mɔ aɖeke meli si dzi woato axe mɔ ɖe Bull's Eye Maculopathy'' ƒe dzɔdzɔ nu o.

Gake esi wònye be afɔku le atike aɖewo (e.g., hydroxychloroquine) me be woahe nɔnɔme sia vɛ ta la, ne wozã atike mawo ɣeyiɣi didi la, ŋkudodokpɔ edziedzi abe alesi ɖɔkta ɖo aɖaŋue ene ate ŋu akpe ɖe ame ŋu woade dzesi nusiwo gblẽ le ame ŋu kaba eye woaxe mɔ ɖe dɔlélea nu be wòagagblẽ ɖe edzi o.

Nya kawoe wòle be mabia nye ɖɔkta tso Bull's Eye Maculopathy'' ŋu?

Ne Bull's Eye Maculopathy'' le ŋuwò la, àteŋu abia wò ɖɔkta nya aɖewo abe:

• "Ðɔkta, ɖe atike aɖewo li siwo zãm mele fifia siwo ate ŋu ana nɔnɔme sia nagado gã ɖe edzia?"
• "Ðe nunyiame aɖewo li siwo ate ŋu akpe ɖe ŋunye nye ŋku ƒe nukpɔkpɔ nanyo ɖe edzia?"
• "Aleke mate ŋu awɔ dɔ le nye gbesiagbegbenɔnɔ me kple ŋku ƒe bublu sia? Mɔ kawoe nye esiwo dzi mato akpɔ kpekpeɖeŋu le ema me?"
• "Aleke mawɔ anya ne egakpɔtɔ le dedie nam be maku ʋu?"
• "Ðe nye ŋku ƒe bublu sia nɔa anyi ɖaa?"
• "Aleke wòanya wɔ be nye ŋkumekpɔkpɔ agblẽ ɖe edzi?"

Bull’s Eye Maculopathy nye dɔléle si mebɔ o. Ne ède dzesi tɔtrɔ aɖewo le wò ŋkumekpɔkpɔ me la, anɔ eme be nɔnɔme sia gbɔe wòtso o. Ke hã, mègaŋe aɖaba ƒu nukpɔkpɔ ƒe kuxi aɖeke dzi o. Togbɔ be wò ŋkumakpɔmakpɔ ate ŋu ado vɔvɔ̃ na ame eye wòate ɖe ame dzi hã la, mɔ aɖewo li siwo dzi nàto anɔ te ɖe enu. Wò ɖɔkta ate ŋu aɖo wò ɖe ŋkuléleɖenuŋu, kpekpeɖeŋunadɔwo, kple atikewɔwɔ siwo nèhiã la gbɔ.

Ne ède dzesi tɔtrɔ aɖewo le wò ŋkume, ŋku ƒe nukpɔkpɔ si me kɔ o, alo dzesi yeye bubuwo la, yi ɖɔkta gbɔ enumake. Nuka kee ɖanye nusi gbɔ wò ŋkumekpɔkpɔ ƒe kuxiwo tso o, atikewɔwɔ kaba ate ŋu ana nukpɔkpɔ ƒe kuxiwo nagbɔdzɔ, atɔ te, eye ɖewohĩ atrɔe gɔ̃ hã.

Nu vevitɔ kekeake siwo dzi wòle be woaɖo ŋkui (Take-Home Message) .

Enyo, eyata mina míaƒo nu tso nu siwo ŋu míeƒo nu tsoe egbea siwo ŋu nàte ŋu akpɔ be wole vevie la dometɔ aɖewo ŋu kpuie:

• Bull's Eye Maculopathy nye ŋkudɔ si mebɔ kura o si me nukpɔkpɔ ƒe titina (macula) le ŋkua me gblẽna, si wɔnɛ be eƒe nɔnɔme le abe "nyitsu ƒe ŋku" ene.
• Esia ate ŋu ana be nukpɔkpɔ le titina nagbɔdzɔ. Esia ate ŋu akpɔ ŋusẽ ɖe nuwo abe agbalẽwo xexlẽ kple mowo nyanya ene dzi.
• Esia ate ŋu atso domenyiŋusẽfianu, dɔléle bubuwo, kple atike aɖewo zazã ɣeyiɣi didi gbɔ .
• Womekpɔ atike si ŋu kakaɖedzi le na nɔnɔme sia haɖe o. Gake mɔ aɖewo li siwo dzi míato akpe ɖe ŋuwò nàɖu dzesiawo dzi eye wòana agbea nanɔ bɔbɔe.
• Ne ède dzesi tɔtrɔ aɖewo le wò nukpɔkpɔ me la, ele vevie be nàyi ŋkudɔdala gbɔ enumake. Ne wokpɔ dɔlélea kaba hedae la, ate ŋu akpe ɖe ame ŋu be nɔnɔmea nagagblẽ ɖe edzi o.

Wò agbanɔamedzie wònye be nàlé be na wò ŋkuwo. Ŋku siwo le lãmesẽ me nye kekeli gã aɖe le agbe me.