Ðe viwòa ƒe ŋutilã le ʋuʋum eye eƒe ŋutilã melɔ̃na oa? Mina míasrɔ̃ nu tso Ðeviwo ƒe Ŋutilãmedɔléle (JDM) ŋu.

Ðe ɖeɖi te viwòa ŋu wu ale si wònɔna ɖaa, ne ele du dzi alo le atrakpuiwo liam gɔ̃ hã? Alo, ɖe teƒe dzĩ/aɖabɛ dzĩwo le eƒe mo alo asiwo ŋua? Ne dzesi siawo le ŋuwò la, mègabu wo be wosɔ o. Esia ate ŋu anye nɔnɔme si bɔ ɖe ɖeviwo dome, gake ame geɖe menya nu tso eŋu o. Mègatsi dzi o, míaƒo nu tso eŋu eme nakɔ.

Nukae nye Ðeviwo ƒe Ŋutilã ƒe Dɔléle (JDM)?

Kpuie ko la, Juvenile Dermatomyositis (JDM) nye dɔléle si me míaƒe dɔlélenutsiŋutete ƒe gbɔdzɔgbɔdzɔ aɖe dzea mía ŋutɔwo ƒe ŋutigbalẽ, lãmekawo, kple ʋukawo dzi. Míeyɔa dɔléle mawo be dɔlélenutsiŋutete ƒe dɔlélewo. Le esia me la, dɔdzẽ nɔa ŋutilãa me. Esia koŋue hea ŋutigbalẽ ƒe ʋuʋudedi kple lãmekawo ƒe gbɔdzɔgbɔdzɔ vɛ . "Ðeviwo" gɔmee nye esia elabena edzea egɔme tso eƒe ɖevime, si nye le ɖevime.

Dɔléle sia ate ŋu ana wòasesẽ na ɖevi be wòafɔ, aƒu du, alia atrakpui, eye wòawɔ gbesiagbedɔwo abe abɔ kɔkɔ kple taɖa tutu ene gɔ̃ hã. Abe dzila ene la, ate ŋu aɖe fu na wò ŋutɔ ne èkpɔ ɖevi wòle avu wɔm alea. Gake nu vevitɔe nye be ne wowɔ atike na ɖevia nyuie la, woate ŋu aɖu dzesi siawo dzi nyuie eye ɖevia ate ŋu anɔ agbe nyuie .

Amekae ate ŋu axɔ dɔléle sia wu?

Zi geɖe la, JDM dzea egɔme tso ɖevi siwo xɔ tso ƒe 5 va ɖo ƒe 10. Ebɔ ɖe nyɔnuviwo me wu ŋutsuviwo. Togbɔ be ate ŋu adze ɖevi ɖesiaɖe dzi hã la, ebɔ ɖe yevu ɖeviwo me wu.

Ame tsitsiwo hã ate ŋu akpɔ dzesi siawo. Gake zi geɖe la, edzena le ƒe 40 kple 50-awo me. Woyɔa esia be Dermatomyositis. Wo ame evea siaa le nɔnɔmewo ƒe hatsotso ɖeka me.

Nukawoe nye JDM ƒe dzesi veviwo?

Ðevia ate ŋu aɖe dɔléle sia ƒe dzesi aɖewo afia le gɔmedzedzea me hafi woakpɔe gɔ̃ hã. Dɔlélea ƒe dzesi vevitɔwoe nye ŋutigbalẽ ƒe tɔtrɔ kple lãmekawo ƒe gbɔdzɔgbɔdzɔ. Mina míalé ŋku ɖe esiawo ŋu ɖe vovo.

Dzesi siwo ate ŋu ado mo ɖa le dɔléle sesẽwo me

Zi geɖe la, nusiawo mebɔ o. Gake ne JDM nu sẽ la, ate ŋu agblẽ nu le ɖevia ƒe gbɔgbɔ kple nu mimi ƒe lãmekawo hã ŋu . Dzesi siawo ate ŋu anye:

• Nuɖuɖu tsina ɣesiaɣi ne wole nu mimim.
• Gbe trɔna, eye wògbɔdzɔna.
• Yagbɔgbɔ sesẽ (Dyspnea).

Nukawoe nye kuxi siwo dona tso eme ne womewɔ atike na wo o?

Mègana esia navɔ̃ o. Esia ku ɖe nusi ate ŋu adzɔ ne mèxɔ atike o ŋu. Ne wozã egbegbe atikewɔmɔnu deŋgɔwo la, woate ŋu axe mɔ ɖe nusiawo dometɔ geɖe nu.

• Calcium ƒe ƒuƒu: Kpe sesẽ siwo le abe kpe ene ate ŋu adzɔ le ŋutigbalẽa te. Esiawo ate ŋu ana wòasesẽ be woaʋuʋu lãmekawo.
• Lãmetsiwo ƒe tete: Lãmetsiwo tena eye woate ŋu anɔ anyi ne ƒunukpeƒewo bɔbɔ gɔ̃ hã .
• Abi: Abi ate ŋu adze ŋutigbalẽa dzi alo le dɔgbowo me.
• Gbɔdzɔgbɔdzɔ sesẽ: Àte ŋu agbɔdzɔ ale gbegbe be màte ŋu agbɔ ya alo ami nu o.

Nukatae JDM sia le dzɔdzɔm? Nuka tae?

Bu eŋu ale: míaƒe ŋutilã le abe mɔ̃ sesẽ ene. Aʋakɔ aɖe si woyɔna be dɔlélenutsiŋutete le eme. Woƒe dɔe nye be woakpɔ mía ta to duta futɔwo abe dɔlékuiwo kple dɔlékuiwo ene dzi dzedze me. Le dɔléle si dɔlékuiwutikewo tsona abe JDM ene me la, asrafoha sia dzea mía ŋutɔwo ƒe lãmenugbagbevi nyuiwo (ŋutilã, lãmeka) dzi dzedze gɔme vodadatɔe.

Womenya nusi tututu gbɔ dɔlélenutsiŋutete ƒe dɔmawɔmawɔ nyuie sia tso haɖe o, gake ɖɔktawo xɔe se be ate ŋu atso domenyiŋusẽfianu ƒe akpa aɖe kple nutoa me ƒe nɔnɔmewo siaa ƒe ƒuƒoƒo gbɔ (le kpɔɖeŋu me, dɔlékui ƒe dɔléle).

Aleke ɖɔkta awɔ anya dɔléle sia pɛpɛpɛ?

Ne èkplɔ viwòa yi ɖɔkta gbɔ la, ado ɖevia kpɔ nyuie gbã, eye wòalé ŋku ɖe nuwo abe ŋutigbalẽ ƒe ʋuʋu kple lãmekawo ƒe ŋusẽ ene ŋu. Tsɔ kpe ɖe eŋu la, woate ŋu awɔ dodokpɔ geɖe atsɔ aɖo kpe dɔlélea dzi.

• Ʋudodokpɔ: Esiawo ate ŋu akpɔ alesi gbegbe dɔdzẽ le ʋua me kple alesi lãmekawo ƒe enzyme siwo dona ne lãmekawo gblẽ. Woate ŋu adi protein tɔxɛwo (autoantibodies) siwo wokpɔna le JDM me hã.
• Electromyography (EMG): Esia bia be woatsɔ elektrikŋusẽnamɔ̃ siwo le abe aŋe ene siwo le sue ŋutɔ ade lãmekawo me eye woadzidze woƒe elektrikŋusẽ ƒe dɔwɔwɔ.
• MRI (Magnetic Resonance Imaging): Dodokpɔ sia zãa magnet gã aɖe tsɔ kpɔa dɔdzẽ kple vuvu le ŋutilãa me nyuie, vevietɔ le lãmekawo me.
• Lãmetsiwo ɖeɖe: Esia bia be woawɔ amekoko sue aɖe atsɔ aɖe lãmeka sue aɖe ŋutɔ ɖa eye woatsɔ nusuekpɔmɔ̃ adoe kpɔ. Esia le vevie ŋutɔ be woatsɔ aɖo kpe edzi nenye be JDM alo lãmekawo ƒe dɔléle bubue (e.g. lãmekawo ƒe dɔmawɔmawɔ nyuie).
• Nailfold capillaroscopy: Wozãa dɔwɔnu tɔxɛ aɖe tsɔ doa ʋuka suesuesue (capillaries) siwo le ɖevia ƒe ɖawo te la kpɔna be wovuvu hã. Woate ŋu akpɔe be tɔtrɔ aɖewo koŋ le ʋuka siawo me le ɖevi siwo ŋu JDM le ŋu.

Nukawoe nye JDM ƒe atikewo?

Taɖodzinu vevitɔ si le JDM-dɔdamɔnu ŋue nye be wòaɖe abi si le ŋutilãa me dzi akpɔtɔ, aɖu dzesiwo dzi, eye wòakpe ɖe ɖevia ŋu wòanɔ agbe nyui. Atikewɔwɔ ate ŋu ana wòaɖe asi le eŋu ɣeyiɣi aɖewo ne dzesiawo nu yi.

Atikewo

• Corticosteroid-tikewo:Esiawoe nye atike ƒomevi vevi siwo wonana gbã. Esiawo ɖea dɔdzẽ dzi kpɔtɔna kabakaba. Wonaa wo le agbɔsɔsɔ gã me le gɔmedzedzea me, eye emegbe woɖea agbɔsɔsɔa dzi kpɔtɔna vivivi ne dzesiawo le ɖiɖim.
• Methotrexate: Atike vevi bubu si wonana kple corticosteroids alo emegbe. Ekpɔa dɔlélenutsiŋutete ƒe dɔwɔwɔ dzi.
• Hydroxychloroquine: Atike sia kpena ɖe ame ŋu ŋutɔ le ŋutigbalẽ ƒe ʋuʋudedi dzi ɖuɖu me.
• Intravenous immunoglobulin (IVIG): Esia bia be woatsɔ dɔlékuiwutike siwo ŋu wokɔ la ana ŋutilãa to ʋuka aɖe me. Esia ate ŋu axe mɔ na dɔlékuiwutike siwo le nu gblẽm le míaƒe ŋutilã ŋu.
• Atike bubuwo: Ne dɔlélea nu sẽ alo mewɔ nu ɖe ​​atike bubuwo ŋu o la, ɖɔkta ate ŋu aŋlɔ atike bubuwo abe cyclosporine kple rituximab ene na wò.

Agbenɔnɔ ƒe tɔtrɔ kple atikewɔwɔ bubuwo

Tsɔ kpe ɖe atikewo zazã ŋu la, nu siawo hã le vevie ŋutɔ.

• Lãmesẽdɔdamɔnu: Lãmesẽdɔwɔla fiaa kamedede siwo ana lãmekawo nado ŋusẽ, aɖe ƒunukpeƒewo ƒe sesẽ dzi akpɔtɔ, eye woana woate ŋu atrɔ ɖe nɔnɔmewo ŋu geɖe wu.
• Ɣe ƒe takpɔkpɔ: Esia le vevie ŋutɔ. Ɣe ƒe keklẽ ate ŋu ana ŋutigbalẽ ƒe ʋuʋudedi nagado gã ɖe edzi. Eyata ele be nàzã ɣe ƒe keklẽŋusẽtike si ƒe SPF nye 30 alo esi wu nenema ɣesiaɣi. Do kposɔ kple ɣe ƒe ŋkumewu. Ƒo asa na ɣe ƒe keklẽ sesẽ ƒe nɔnɔ le ŋdi ga 10 kple fiẽ ga 4 dome.
• Nunyiame nyui: Nuɖuɖu si me nunyiame le si me amagbewo, atikutsetsewo, protein siwo me ami mele o, kple nuku blibowo sɔ gbɔ ɖo ɖuɖu ate ŋu akpe ɖe ame ŋu wòaɖe abi si le ŋutilãa me dzi akpɔtɔ.
• Nuƒoƒo ƒe atikewɔwɔ: Nuƒoƒo ƒe dɔdamɔnufiala fiaa nuɖuɖu kple kamedede siwo me afɔku mele o ɖevi siwo nu mimi sesẽna.

Nukae wòle be míabu tso etsɔme ŋu?

Atike aɖeke meli na JDM o. Gake mègavɔ̃ o. Nya nyuiae nye be ne wowɔ atike na ɖevi geɖe la, woate ŋu anɔ agbe si akpɔ dzidzedze ŋutɔ, si me dzo le.

Ðevi akpa gãtɔ ayi ɖe dɔlélea ƒe tsɔtsɔke me le ƒe eve me tso esime wodze atikewɔwɔ gɔme. Ðewohĩ àte ŋu adzudzɔ atikeawo nono ɣemaɣi. Gake ele be nàyi edzi anɔ nuɖuɖu nyuiwo ɖum, anɔ kame dem, eye nànɔ ametakpɔnu tso ɣe ƒe keklẽ me be dzesiawo nagatrɔ ava o.

Dɔlélea ate ŋu anɔ ɖevi aɖewo ŋu ɣeyiɣi didi aɖe, alo dzesiawo nu ayi eye emegbe woagadze. Gake JDM menye dɔléle si ate ŋu ade ame ƒe agbe afɔku me o. Ne wokpɔ egbɔ nyuie la, woate ŋu akpɔ nɔnɔmea gbɔ nyuie eye ɖeviwo ate ŋu anɔ agbe si sɔ abe ɖevi bubuwo ene.