Ðe viwòa ƒe ƒodo vuvu abe lãgbalẽŋudɔwɔnu enea? Mina míaƒo nu tso Prune Belly Syndrome ŋu!

Ne míelé ŋku ɖe vidzĩ si wodzi yeyee ƒe ƒodo ŋu la, zi geɖe la, míekpɔnɛ be ele blɔ ŋutɔ eye wòyɔ fũ, alo? Gake bu eŋu kpɔ, ɣeaɖewoɣi, le vome, míekpɔnɛ be ŋutigbalẽ si le vidzĩa ƒe ƒodo ŋu la vuvu ŋutɔ, abe prune ene. Ne èkpɔ esia, abe vidada alo vifofo ene la, vɔvɔ̃ ate ŋu anɔ ŋuwò ŋutɔ eye wòatsi dzodzodzoe. "Oo, nukae dzɔ ɖe vinyea dzi?" Ðewohĩ àsusui. Le nyateƒe me la, esia nye nɔnɔme si mebɔ kura o. Egbea míele nu ƒom tso nɔnɔme si mebɔ o si ate ŋu ahe esia vɛ ŋu, si nye Prune Belly Syndrome . Mègatsi dzi o, míaƒo nu tso nusianu ŋu bɔbɔe eye eme nakɔ.

Kpuie ko la, nukae nye Prune Belly Syndrome?

Prune Belly Syndrome nye dɔléle si mebɔ o si wodzina. Exɔ ŋkɔa elabena vidzĩ ƒe ƒodo ƒe ŋutigbalẽ le abe lãgbalẽ si wotsɔ lãgbalẽ wɔe ene. Dzesi vevi etɔ̃ le eŋu. Esia tae woyɔnɛ ɣeaɖewoɣi be ‘Triad Syndrome’. Wogayɔnɛ be ‘Eagle-Barrett Syndrome’ tsɔ dea bubu ɖɔkta siwo ke ɖe eŋu ŋu.

Nu vevi etɔ̃ siawoe nye:

1. Ƒodo ƒe lãmeka siwo gbɔdzɔ alo womele o: Lãmetsi aɖewo le míaƒe ƒodo me siwo kpena ɖe mía ŋu be eƒe nɔnɔme nɔa anyi eye wokpɔa ŋutinu siwo le eme, abe dɔgbowo ene, ta. Le vidzĩ siwo ŋu dɔléle sia le gome la, lãmeka siawo metsina nyuie o. Ɣeaɖewoɣi la, womewɔa wo kura o. Esia tae ŋutigbalẽ si le ƒodoa dzi la dzena abe ɖe wòle ʋuʋum eye wòle ʋuʋum ene.

2. Vidzidɔ siwo meɖiɖi o: Le vidzĩ ŋutsu gome la, zi geɖe la, vidzidɔa nɔa ŋutilãa godo le vidzidɔa me. Gake le vidzĩ siwo ŋu dɔléle sia le gome la, vidzidɔa nɔa ƒodoa me. Womeɖiɖi o.

3. Aɖuɖɔtoe me kuxiwo: Esiae nye nɔnɔmea ƒe akpa si nu sẽ wu. Vidzĩa ƒe ayikuwo, tsinyegoe, kple mɔ̃ siwo doa ka kplii (dziɖuɖɔtoewo) metsi bliboe o. Esia ate ŋu ahe kuxi sesẽwo vɛ le aɖuɖɔtoe me.

Tsɔ kpe ɖe dzesi vevi etɔ̃ siawo ŋu la, kuxi vovovowo ate ŋu anɔ vidzĩ aɖewo ŋu le dzi, lãkusi, dɔgbo, kple ƒunukpeƒewo hã ŋu.

Aleke gbegbee nɔnɔme sia bɔe?

Esia nye nɔnɔme si mebɔ kura o. Edzea vidzĩ yeye siwo ade ɖeka le 30,000 va ɖo 40,000 ɖesiaɖe me dzi. Nusi le etɔxɛe nye be ŋutsuviwo ŋue wogblɔa dɔléle siawo ƒe 95% le . Esia le alea elabena ŋutsuviwo koe vidzidɔ si meɖina o ƒe kuxi si ŋu míeƒo nu tsoe va yi la gblẽa nu le eŋu.

Dzesi kawoe ate ŋu akpe ɖe ŋuwò nànya ne dɔléle sia le viwòa ŋu?

Wogblɔ be dzesi siwo wu 50 ye le Prune Belly Syndrome ŋu. Gake dzesi siawo ate ŋu ato vovo tso vidzĩ ɖeka gbɔ yi bubu gbɔ. Vidzĩ aɖewo ate ŋu agblẽ nu le wo ŋu vevie ŋutɔ, evɔ bubuwo ya masẽ nenema gbegbe o. Wò ɖɔkta ado viwòa kpɔ eye wòawɔ dodokpɔ siwo hiã atsɔ aɖo kpe esia dzi kakaɖedzitɔe.

Mina míalé ŋku ɖe kplɔ̃ si le ete ŋu akpɔ nusiwo nye dzesi siwo bɔ wu.

Nukatae esia dzɔna ɖe vidzĩwo dzi?

Ne míagblɔe tututu la, ɖɔktawo mekpɔ nusi tututu gbɔ esia tso haɖe o, gake nufiafia vovovowo li.

Ame bubuwo xɔe se be esi ƒodo ƒe lãmekawo metsina nyuie le gɔmedzedzea me o tae kuxi sia doa mo ɖa. Ame bubuwo gblɔna be ɖewohĩ domenyiŋusẽfianu aɖe gbɔe wòtso. Woka nya ta tso nɔnɔme sia ŋu le nɔviwo hã dome. Azɔ hã, ɖevi aɖewo siwo ƒe domenyiŋusẽfianu ƒe dɔmawɔmawɔ nyuie abe `Trisomy 18 (Edwards Syndrome)` kple `Trisomy 21 (Down Syndrome)` hã ​​toa Prune Belly Syndrome sia me.

Kuxi kawoe ate ŋu ado mo ɖa le nɔnɔme sia ta?

Prune Belly Syndrome ƒe sesẽme nɔ te ɖe kuxi bubu siwo do ƒome kplii dzi, vevietɔ alesi gbegbe aɖuɖɔtoea gblẽe.

Kuxi siwo bɔ wue nye:

• Dɔmeɖui: Dɔgbo ƒe lãmeka siwo gbɔdzɔ nana wòsesẽna be woatutu wo sesĩe ale gbegbe be woate ŋu ato aɖuɖɔ me.
• Ƒu ƒe dɔmawɔmawɔ nyuie: nuwo abe akɔta ƒe ʋuʋu, asiwo, asibidɛwo, alo afɔbidɛwo ƒe gbagbã.
• Aɖuɖɔtoe me dɔlékuiwo xɔxɔ enuenu: Dɔlékuiwo ate ŋu adze ame dzi bɔbɔe elabena womele aɖuɖɔ me tom nyuie o. Dɔlékui siawo ate ŋu agblẽ nu le ayikuwo ŋu.
• Vidzidzimakpɔmakpɔ: Ne vidzidɔa mete ŋu ɖiɖi o la, ate ŋu agblẽ nu le vidzidzi ƒe ŋutete ŋu le etsɔme. Afɔku hã li be woaxɔ dɔdzẽ le vidzidɔ me.
• Aklã ƒe Ʋuʋudedi: Ðewohĩ aklãa matsi nyuie o le esi teƒe aɖeke mele vidzidɔa me o ta.
• Ayikuwo ƒe Dɔmawɔmawɔ nyuie: Esiae nye kuxi sesẽtɔ kekeake. Kuxi siwo yia edzi le aɖuɖɔtoe me ate ŋu ana ayiku nawɔ dɔ nyuie vivivi.

Aleke wokpɔa dɔléle sia dzea sii?

Zi geɖe la, woate ŋu ade dzesi nɔnɔme sia kaba le wò fufɔɣi to fugboe ƒe ultrasound scan dzi.Ðɔktawo asusu esia ne scan la ɖee fia be vidzĩa ƒe tsinyegoe lolo ŋutɔ alo ayikuawo vuvu. Scan la ate ŋu aɖee afia hã be ƒodo ƒe lãmeka aɖeke mele vidzĩa ŋu o.

Ne wodzi vidzĩa vɔ la, ɖɔkta ate ŋu asusu esia le vidzĩa ƒe gotagome dzedzeme nu, i.e. ƒodoa ƒe dzedzeme si le fli me. Emegbe, wowɔa dodokpɔ vovovowo tsɔ ɖoa ​​kpe dɔlélea dzi eye wokpɔa alesi gbegbe ŋutinuwo gblẽe.

Dodokpɔ kawoe wowɔna?

• Ʋudodokpɔ: Srɔ̃ nu tso ayiku ƒe dɔwɔwɔ ŋu.
• Ultrasound Scan: Kpɔ ŋutinu siwo le ƒodoa me, abe ayiku kple tsinyegoe ene, ƒe nɔnɔme ɖa.
• X-ray: Be woatsɔ akpɔe ɖa be kuxi aɖeke le ƒunukpeƒewo ŋu hã.
• CT Scan alo MRI Scan: Na ŋutinuwo ƒe nɔnɔmetata si me kɔ wu, si me kɔ wu.
• VCUG (Voiding Cystourethrogram): Esia nye X-ray dodokpɔ tɔxɛ aɖe. Esia bia be woado tsi tɔxɛ aɖe ɖe tsinyegoea me ahalé ŋku ɖe tsi si le sisim to eme ŋu esime vidzĩa le aɖuɖɔ tom. Esia kpena ɖe ame ŋu wònya ne aɖuɖɔ le sisim le megbe (reflux).

Nukawoe nye atike siwo wozãna na esia?

Prune Belly Syndrome ƒe atikewɔwɔ to vovo tso vidzĩ ɖeka gbɔ yi bubu gbɔ. Elabena menye vidzĩ ɖesiaɖee wògblẽa nu le le mɔ ɖeka nu o. Zi geɖe la, eŋutinunyalawo ƒe ƒuƒoƒo aɖe, abe ɖeviwo ƒe dɔdalawo, ɖeviwo ƒe tsinyegoeŋutinunyalawo, kple aɖuɖɔtoedɔdalawo ene, wɔa dɔ ɖekae wɔa atikewɔwɔ ƒe ɖoɖo nyuitɔ kekeake na viwòa.

Ne wole nya me tsom le atikewɔwɔ ŋu la, wobua nu siawo ŋu:

• Vidzĩa ƒe lãmesẽ bliboa.
• Vidzĩa ƒe ƒexɔxɔ.
• Alesi dɔlélea nu sẽe kple ŋutinu siwo gblẽ.
• Vidzĩa ƒe ŋutete be wòado dzi le amekoko kple atikewɔwɔ me.
• Miaƒe nukpɔsusuwo kple didiwo abe dzilawo ene.

Gake ahiã be woawɔ dɔ na vidzĩ geɖe zi geɖe. Woɖoe be woawɔ amekoko siawo be woado ŋusẽ ƒodo ƒe gli, aɖiɖi vidzidɔa ɖe anyi, eye woaɖɔ kuxi siwo le aɖuɖɔtoeme ŋu ɖo.

Amekoko ƒomevi vevi geɖewo li siwo wowɔna:

• Vesicostomy: Esia bia be woawɔ dɔ sue aɖe le ƒodo ƒe akpa si le ete ayi tsinyegoea me. Esia wɔnɛ be aɖuɖɔ dona tẽ. Esia ate ŋu aɖe ayikuwo ƒe gbegblẽ dzi akpɔtɔ.
• Orchiopexy: Esia bia be woawɔ dɔ na vidzidɔ siwo le ƒodoa me la ayi anyime ayi ɖe vidzidɔa me eye woaɖɔ wo ɖo.
• Cystoplasty: Esia nye amekoko si sesẽ vie wu. Ebia be woagbugbɔ tsinyegoea atu keŋkeŋ.

Le nɔnɔme sesẽ aɖewo me la, ne ayikuawo do kpo dɔwɔwɔ keŋkeŋ la, .Ate ŋu ahiã hã be woado ayiku na ame.

Aleke ɖevi siawo ƒe etsɔme anɔ?

Menya be nya sia sese sesẽ vie. Gake ele vevie be nànya nyateƒea. Ðevi siawo ƒe agbenɔƒe nɔ te ɖe alesi dɔlélea nu sẽe dzi. Nublanuitɔe la, vidzĩ siwo ade 10% va ɖo 25% kuna le vidzidɔ me alo kuna le kuxiwo ta le wo dzidzi ƒe kwasiɖa ʋee gbãtɔwo me.

Gake, akpa aɖe si me kɔ la li. Ðevi siwo ŋu Prune Belly Syndrome le dometɔ siwo ade 40%, togbɔ be kuxi suesuesuewo le woƒe aɖuɖɔtoe ŋu hã la, woléa ayiku ƒe dɔwɔwɔ nyuie me ɖe asi eye wonɔa agbe si sɔ ƒe akpa gãtɔ.

30% bubuwo ate ŋu ahiã be woado ayiku na wo le woƒe agbemeɣeyiɣi aɖe me. Vevietɔ wu la, ele be amesiame si ŋu dɔléle sia le nanɔ atikewɔlawo ƒe dzikpɔkpɔ te le eƒe agbemeŋkekewo katã me. Ele vevie be woalé ŋku ɖe aɖuɖɔtoea ŋu edziedzi be woaɖe nusiwo gblẽ le ayikuawo ŋu dzi akpɔtɔ.

Aleke nàlé be na viwòa kple ɣeyiɣi si nàyi ɖɔkta gbɔ?

Ne wokpɔe be Prune Belly Syndrome le viwòa ŋu la, nu vevitɔ kekeakee nye be nàdi ɖɔkta bibi aɖe si nya nu tso dɔlélea ŋu. Aɖe nu sia nu me na wò eye wòafia mɔ wò le ale si nàlé be na viwòa ŋu.

Afɔku le Aɖuɖɔtoe me Dɔlékuiwo (UTI) me na ɖevi siawo ŋutɔ. Eyata ne ède dzesi aɖuɖɔtoedɔléle ƒe dzesi suetɔ kekeake gɔ̃ hã la, ele be nàƒo ka na wò ɖɔkta enumake.

Ne ède dzesi dzesi siawo dometɔ aɖe la, mègahe ɖe megbe o. Di atikewɔlawo ƒe aɖaŋuɖoɖo enumake. Azɔ hã, ele vevie be nàyi atikewɔƒewo le ɣeyiɣi siwo woɖo ɖi dzi eye nàna woado viwòa kpɔ, abe alesi ɖɔktaa kafui ene.