Tsɔe be kasia asrã sesẽ aɖe dze dziwò. Le ɣeyiɣi ma ke me la, ʋuʋudedi siwo biã, siwo le ʋuʋum vie, eye wole veve sem la te dzedze le wò ŋutilã, abɔwo, kple afɔwo dzi. Eɖea dzi ɖi ŋutɔ, eye wò ŋutilã sena le eɖokui me abe ɖe wòle veve sem ene. Vɔvɔ̃ anɔ ame aɖe ne ekpɔ nane si le abe esia ene, alo? "Nukae dzɔ kasia?" Ðewohĩ àsusui be. Egbea, míele nu ƒom tso nɔnɔme aɖe si hea dzesiwo abe esia ene vɛ, si mebɔ vie le míaƒe dukɔa me o, gake ele vevie ŋutɔ be woanya nu tso eŋu. Woyɔa esia be Sweet Syndrome le atikewɔwɔ me.
Kpuie ko la, nukae nye Sweet Syndrome?
Sweet Syndrome nye ŋutigbalẽ ƒe dɔléle si xɔa abi. Ƒã ŋutɔ. Dzesi vevitɔe nye dzoxɔxɔ ƒe gɔmedzedze kpata eye ʋuʋudedi alo ʋuʋudedi si le veve sem le ŋutilãa ŋu, vevietɔ le abɔwo, afɔwo, akɔta, kɔ, alo mo. Atikewɔwɔ me ŋkɔ bubu aɖe hã le eŋu, si nye Acute Febrile Neutrophilic Dermatosis . Ŋkɔa ɖi nya sesẽ vie, alo? Mina míana wòanɔ bɔbɔe.
- Acute: Esia fia be esia nye nusi dzea egɔme kpata.
- Febrile: gɔmee nye "kple dzoxɔxɔ."
- Neutrophilic: Esia fia be ʋumenugbagbevi ɣi ƒomevi aɖe si woyɔna be ‘Neutrophil’, si nye lãmenugbagbevi ƒomevi aɖe le míaƒe ŋutilã ƒe dɔlélenutsiŋutete me, le eme. Àte ŋu akpɔ lãmenugbagbevi siawo ƒe ƒuƒoƒo gã aɖe le ʋuʋudedi siawo me.
- Dermatosis: fia ŋutigbalẽdɔléle.
Eyata ne míagblɔe kpuie ko la, esia nye ŋutigbalẽ ƒe dɔléle si lãmenugbagbevi siwo woyɔna be neutrophils hena vɛ si va kpata kple dzoxɔxɔ.
Ɣeaɖewoɣi la, Sweet’s Syndrome ate ŋu adzɔ kple atikewɔwɔ me nɔnɔme bubuwo. Le kpɔɖeŋu me, wokpɔ nɔnɔme sia le kansa, dɔgbo me dɔlékuiwo, alo le fufɔɣi me. Ate ŋu adzɔ hã abe atike aɖewo siwo míezãna ƒe nugbegblẽ le ame ŋu ene.
Ðe nɔnɔme sia bɔa? Amekawoe le afɔku me?
Ao, Sweet Syndrome nye dɔléle si mebɔ kura o . Ame ʋɛ aɖewo koe wokpɔ dɔlélea le le xexeame katã. Eyata mehiã be nàtsi dzodzodzoe ne èse eŋu nya o.
Togbɔ be nɔnɔme sia ate ŋu adze ame sia ame dzi hã la, ebɔ ɖe nyɔnu siwo xɔ tso ƒe 30 va ɖo ƒe 50. Gake ema mefia be mate ŋu adze le ŋutsuwo alo ƒe bubuwo me o.
Nukae hea Sweet Syndrome vɛ?
Le nyateƒe me la, ɖɔktawo mekpɔ nusi koŋ gbɔ esia tso haɖe o. Esia fia be zi geɖe la, edzɔna susu aɖeke manɔmee. Gake ɖɔktawo nɔa te ɖe alesi wòdzɔnae dzi daa nɔnɔme sia ɖe hatsotso vevi etɔ̃ me. Ƒomedodo sia kpena ɖe ame ŋu ŋutɔ le atikewɔwɔ hã me.
| Ƒomevi | Numeɖeɖe bɔbɔe |
|---|---|
| Klasik (ƒomevi si sɔ) . | Esiae nye ƒomevi si bɔ wu. Ate ŋu adzɔ le kadodo me kple atikewɔwɔ ƒe nɔnɔme bubu. Le kpɔɖeŋu me, ŋɔti alo gbɔgbɔtsixe ƒe dɔléle (abe dzamezã alo dzamezã ene), dɔgbo ƒe dɔléle (abe aɖuɖɔtoe ene), alo le fufɔɣi. |
| Dɔléle vɔ̃ɖi (si do ƒome kple kansa ƒe nɔnɔmewo) . | Ɣeaɖewoɣi la, dɔléle sia ate ŋu adzɔ kple kansa ƒomevi aɖe. Wokpɔa esia vevietɔ le kansa siwo do ƒome kple ʋu, le kpɔɖeŋu me , Acute Myeloid Leukemia . Gake esia mefia be kansa le amesiame si xɔ Sweet Syndrome la ŋu o. Esia le vevie ŋutɔ. |
| Atike vɔ̃ɖiwo zazã | Atike siwo míezãna dometɔ aɖewo hã ate ŋu ahe nɔnɔme sia vɛ. Dɔlékuiwutike aɖewo, vevesesenutsitikewo (NSAIDs), kple vevietɔ atike aɖe si woyɔna be G-CSF (Granulocyte Colony-Stimulating Factor) (esia nye atike si nana neutrophil cells ƒe wɔwɔme dzina ɖe edzi le ŋutilã me) ate ŋu ahe esia vɛ. |
Nukawoe nye dzesi vevitɔwo?
Zi geɖe la, Sweet Syndrome ƒe dzesiwo dzena kpata, le ŋkeke ʋɛ aɖewo ko me. Na míalé ŋku ɖe nusiwo wonye ŋu.
- Ŋutilã ƒe tɔtrɔ: Esiae nye dzesi vevitɔ si dze ƒã wu.
- Vevesese, ʋuʋudedi alo ʋuʋudedi siwo dzena zi ɖeka le mo, kɔ, abɔ, afɔ, alo akɔta.
- Kuku siawo dzea egɔme abe ʋuʋudedi suesuesuewo ene, vivivi la, wova lolona, eye woate ŋu aƒo ƒu awɔ abi gã aɖe gɔ̃ hã.
- Ɣeaɖewoɣi la, tsi si le abe ʋuʋudedi ene ate ŋu ayɔ ʋuʋudedi siawo me.
- Abi ate ŋu adzɔ le nu me hã.
- Asrã: Asrã sesẽ, si zi geɖe wua Celsius 38 (100.4 Fahrenheit) , dzɔna.
- Kuxi siwo bɔ:
- Ŋutilã ƒe vevesese kple lãmekawo ƒe vevesese.
- Ƒunukpeƒewo ƒe vevesese.
- Taɖuame.
- Sese le eɖokui me be ɖeɖi te ye ŋu ŋutɔ eye agbe mele ye si o (Ðeɖiteameŋu).
- Zi geɖe la, nye ŋutilã sena le eɖokui me be yeƒe lãme mesẽ o.
Ðe esia ate ŋu ahe kuxi bubuwo vɛa?
Ẽ, ɣeaɖewoɣi la, menye ŋutigbalẽ me koe Sweet Syndrome dzɔna o. Ate ŋu akpɔ ŋusẽ ɖe ŋutinu bubu siwo le ŋutilãa me hã dzi. Gake ema hã mebɔ kura o.
Ŋkuwoe wògblẽa nu le wu.
- Ŋku ƒe dziku ate ŋu adzɔ.
- Ate ŋu adzɔ be ŋkua ƒe nyaƒoɖeamenu ate ŋu adzi ɖe edzi eye wòana ŋkua naxɔ ŋkudɔ .
- Nuveviwɔame ate ŋu adzɔ le ŋkume ƒe ŋkume ƒe ŋkume hã.
Tsɔ kpe ɖe eŋu la, ƒã ŋutɔ la, ate ŋu agblẽ nu le lãmekawo, ayikuwo, alo lãkusiwo hã ŋu. Esia tae wòle vevie be nàyi ɖɔkta gbɔ ne dzesiawo dze ko.
Aleke ɖɔkta wɔna dea dzesi esia?
Ne èyi ɖɔkta gbɔ kple dzesi siawo tɔgbe la, nu gbãtɔ si wòawɔe nye be wòaɖo to wò dzesiwo nyuie eye wòalé ŋku ɖe wò ŋutilã ŋu nyuie, vevietɔ ʋuʋudedi siwo le wò ŋutigbalẽ ŋu.
Emegbe, woate ŋu awɔ dodokpɔ geɖe atsɔ aɖo kpe dɔlélea dzi.
- Skin Biopsy: Esiae nye dodokpɔ vevitɔ kekeake. Woɖea lãkusi sue aɖe ŋutɔ tso ŋutigbalẽa ƒe abi la me hedoa eŋu le nusuekpɔmɔ̃ me. Ne Sweet’s Syndrome le eme la, lãkusia ƒe kpɔɖeŋua aɖe neutrophils gbogbo aɖewo afia.
- Ʋudodokpɔ: Wowɔa ʋudodokpɔ be woatsɔ akpɔe ɖa be ʋumenugbagbevi ɣiwo (vevietɔ neutrophils) kple dɔdzẽ ƒe dzesiwo dzi ɖe edzi hã.
Tsɔ kpe ɖe eŋu la, ɖɔktaa abia nya wò tso dɔlékui ɖesiaɖe si nèxɔ nyitsɔ laa, atike siwo zãm nèle, kple atikewɔwɔ ƒe nɔnɔme bubuwo ŋu.
Aleke wowɔa atike nɛ?
Nya nyuiae nye be atikewɔmɔnu siwo kpɔa dzidzedze na Vivi ƒe Dɔlélea li.
Ɣeaɖewoɣi la, nɔnɔme sia te ŋu nyona ɖe edzi vivivi atike aɖeke manɔmee. Gake esi wònye be dzesiawo nu sẽ eye kuxiwo ate ŋu ado mo ɖa ta la, zi geɖe la, ɖɔktawo ŋlɔa atike nɛ.
Atike vevitɔe nye atikewo ƒe hatsotso aɖe si woyɔna be corticosteroids . Wonaa esiawo abe atikekuiwo ene. Atike siwo wozãna wue nye atikewo abe Prednisone ene .
Steroid-tike siawo wɔa dɔ to ŋutilãa ƒe dɔlélenutsiŋutete ƒe dɔwɔwɔ fũ akpa kple eƒe dɔdzẽ dzi ɖuɖu me. Asrã, vevesese, kple ŋutigbalẽ ƒe ʋuʋu nu ayi kaba le ŋkeke ʋɛ aɖewo megbe tso esime wodze atike siawo zazã gɔme.
- Nusi gbɔ wòtsona la dada:
- Ne atike aɖe gbɔe Sweet Syndrome tso la, dzesiawo nu ayi ne wonya dzudzɔ atikeawo zazã ko.
- Azɔ hã, ne dɔlékui alo atikewɔwɔ me nɔnɔme bubu aɖe (abe kansa ene) gbɔe esia tso la, ele vevie be woada dɔléle ma si gbɔ wòtso.
Nukae nàte ŋu akpɔ mɔ na le atikewɔwɔ vɔ megbe?
Le ame geɖe gome la, ŋutigbalẽ ƒe abi siwo Sweet Syndrome hena vɛ la hayana keŋkeŋ evɔ womegblẽa abi ɖi o . Esia nye nu nyui aɖe. Gake ne abiawo haya vɔ la, ŋutigbalẽa ƒe amadede ate ŋu atrɔ vie le teƒe mawo (abe teƒe yibɔ alo blɔ ene) si ate ŋu anɔ anyi ɣleti ʋɛ aɖewo. Le ɣeyiɣi aɖe megbe la, esia nu ayi vivivi.
Zi geɖe la, dzesiawo nɔa anyi kwasiɖa ʋɛ aɖewo alo ɣleti ɖeka, gake ne wowɔ atike na wo la, wohayana kaba. Ne atikewɔwɔ me dɔléle bubu aɖe li si gbɔ wòtso la, ɣeyiɣi si woatsɔ ahaya ate ŋu adidi vie wu.
Nu vevitɔe nye be dɔléle sia mexɔa ame o. Eyae nye be wometsɔa asikaka ame ŋu alo to mɔ bubu aɖeke dzi tso ame ɖeka gbɔ yia ame bubu gbɔ o.
Ɣekaɣie wòle be makpɔ ɖɔkta?
Esia nye nyabiase vevi aɖe ŋutɔ.
Ne èkpɔ dzesi siwo ŋu míeƒo nu tsoe le nyati sia me dometɔ aɖe, vevietɔ dzoxɔxɔ si nu sẽ kpata si kpe ɖe ʋuʋudedi dzĩ alo ʋuʋudedi siwo le veve sem le wò ŋutigbalẽ ŋu ŋu la , mègaŋe aɖaba ƒu edzi be enye “nusi sɔ.” Kpɔ wò ɖɔkta gbɔ kaba ale si nàte ŋui godoo.
Ne wokpɔ dɔlélea kaba eye wodze atikewɔwɔ si hiã gɔme la, woate ŋu aɖu dzesiawo dzi kaba eye woaxe mɔ ɖe kuxi siwo ate ŋu ado mo ɖa nu.
Gbedasi si Wotsɔ Yi Aƒeme
- Sweet Syndrome nye dɔléle si mebɔ o si naa ʋuʋudedi dzĩ siwo le veve sem le ŋutigbalẽa ŋu, eye asrã kpata kpena ɖe eŋu.
- Zi geɖe la, nu aɖeke meli si koŋ gbɔ esia tsona o, gake ate ŋu atso dɔlékui aɖewo, atikewo, alo atikewɔwɔ ƒe nɔnɔme bubu aɖewo gbɔ.
- Esia menye dɔléle si xɔa ame me o, eyata mehiã be woavɔ̃ o.
- Ðɔkta ƒe ŋutilãdodokpɔ kple ŋutigbalẽ ƒe lãmenugbagbeviwo ɖeɖe le vevie hafi woate ŋu anya dɔlélea.
- Woate ŋu atsɔ atike siwo woyɔna be corticosteroids aɖu nɔnɔme sia dzi dzidzedzetɔe ŋutɔ.
- Ne wò ŋutɔ alo ame aɖe si nènya kpɔ dzesi siawo la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake.











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