Ke ʻike nei hoʻi ʻoe i ka luhi koke, ka piʻi koke ʻana o ke kaumaha, a i kekahi manawa ka huikau? Hoʻopoina pinepine mākou i kēia mau mea, me ka manaʻo he mea maʻamau lākou. Akā i kekahi manawa aia paha ke kumu ma hope o kēia āu i noʻonoʻo ʻole ai. I kēia lā, e kamaʻilio kākou e pili ana i kahi ʻāpana liʻiliʻi akā koʻikoʻi loa o ko mākou kino, nā kelepa adrenal, a me nā pilikia e kū mai ana mai ia mau mea.
He aha kēia mau kelepa adrenal?
I ka ʻōlelo maʻalahi, ʻo nā kelepa adrenal he ʻelua mau kelepa ʻano triangular i loaʻa ma luna o ko kākou mau puʻupaʻa, e like me ʻelua mau pāpale liʻiliʻi. ʻOiai he liʻiliʻi ko lākou nui, hana lākou i kahi hana koʻikoʻi loa i loko o ko kākou kino. ʻO ia hoʻi, hana lākou i nā hormones e kōkua i ka mālama ʻana i ke kaulike i loko o ko kākou kino.
E noʻonoʻo i kēia ʻano: ua like ko kākou kino me kahi ʻenekini paʻakikī. I mea e hana pono ai kēia ʻenekini, pono iā ia ka nui kūpono o nā mea like ʻole. Pēlā nō, kōkua kēia mau hormones i ka hoʻomalu ʻana i kā kākou metabolism, ke koko, ka ʻōnaehana pale, a me ke ʻano o kā kākou hana ʻana me ke kaumaha.
ʻEkolu mau ʻano nui o nā hormones i hana ʻia e kēia mau kelepa:
- ʻO Cortisol: He hormone koʻikoʻi e kōkua iā mākou e hoʻoponopono i ke kaumaha.
- Adrenaline: ʻO ka hormone e hoʻomākaukau ai i ko mākou kino no kahi pilikia.
- ʻAldosterone: He hormone e kaohi i ko mākou koko a me ka pae o ka paʻakai a me ka wai i loko o ke kino.
ʻIke ʻia nā kūlana e pili ana i ka ʻōpū adrenal ke hana nui ʻia kēia mau hormones a nele paha .
He aha nā maʻi maʻamau o nā kelepa adrenal?
Aia kekahi mau kūlana. E hoʻomaopopo pono kākou i nā mea nui. No ka maʻalahi o ka hoʻomaopopo ʻana, e kau wau i kēia ma kahi papa .
| Kūlana | I ka ʻōlelo maʻalahi, ʻo kēia ka mea e hana ʻia. |
|---|---|
| ʻO ka maʻi o Addison | ʻAʻole hana ke kino i ka lawa o nā hormones cortisol a/a i ʻole aldosterone. |
| ʻO ka maʻi Cushing | Hoʻonui nui ʻia o ka nui o ka hormone cortisol i loko o ke kino. |
| ʻO ka Hyperplasia Adrenal Congenital (CAH) | ʻO ka nele a i ʻole ka nele o nā enzymes e pono ai no ka hana ʻana i nā hormones i ka wā hānau. |
| ʻO ka Hyperaldosteronism | Ka hana nui ʻana o ka hormone aldosterone i loko o ke kino. |
| Hoʻopilikino ʻana | Ka hana nui ʻana o nā hormones kāne i loko o ke kino. ʻIke maopopo ʻia kēia i nā wahine a me nā keikikāne ma mua o ka wā ʻōpiopio. |
Eia kekahi, hiki ke hana ʻia nā kūlana e nā puʻupuʻu i loko o nā kelepa adrenal. Akā, mai hopohopo, ʻo ka hapa nui o kēia mau puʻupuʻu he maʻi ʻaʻole ia he maʻi kanesa (benign). Eia nō naʻe, i kekahi mau hihia kakaikahi, hiki ke loaʻa pū kekahi maʻi kanesa (adrenocortical carcinoma).
He aha nā hōʻailona o kēia mau maʻi?
Pili nā hōʻailona i ka hormone haʻahaʻa a kiʻekiʻe paha. E nānā kākou i nā hōʻailona e kū mai ana ke loli kēlā me kēia pae hormone.
Inā kiʻekiʻe nā pae cortisol (e like me ka Cushing's syndrome)
| Hōʻailona | Wehewehena |
|---|---|
| Ka hoʻonui ʻana o ke kino o luna | Lilo ka maka, ka ʻāʻī, a me ka ʻōpū i mea nui aʻe ʻoiai he lahilahi nā lima a me nā wāwae. |
| Luhi nui | Luhi loa ke manaʻo nei ʻoiai me ka hana ʻole ʻana i kekahi mea. |
| Ke koko kiʻekiʻe a me ka maʻi diabetes | Hoʻonui ʻia ke koko a me nā pae kō. |
| Nā loli ʻili | Ka lahilahi o ka ʻili, ka maʻalahi o ka palapū mai kahi ʻeha liʻiliʻi. ʻIke ʻia nā māka ākea a poni ma ka ʻōpū. |
Inā kiʻekiʻe ka pae o ka aldosterone
- Ke koko kiʻekiʻe
- Nā pae potassium haʻahaʻa o ke koko (Hypokalemia)
- Manaʻo nāwaliwali i ke kino
- ʻEha ʻiʻo a me nā ʻūmiʻi (muscle spasms)
Inā piʻi aʻe ka nui o ka hormone kāne (i nā wahine)
Inā loaʻa kēia ʻano i nā wahine a i nā keikikāne ma mua o ka wā ʻōpiopio, hoʻomaka nā ʻano kāne e puka mai.
- Ka ulu ʻana o ka lauoho maka
- Ka nalowale o ka lauoho (ʻōhule)
- ʻAkika
- Ka hoʻonui ʻana i ka leo (e like me ka leo kāne)
- Ka ulu ʻana o nā ʻiʻo
ʻO ka mea nui, hiki ke ʻike ʻia kēia mau hōʻailona i nā maʻi ʻē aʻe. No laila, inā loaʻa iā ʻoe kēia mau hōʻailona, he mea nui loa ia e ʻike i ke kauka no ka hōʻoia kūpono.
No ke aha e loaʻa ai kēia mau maʻi?
Aia paha kekahi mau kumu no kēia.
- Ka hana nui ʻana a i ʻole ka hana ʻole ʻia ʻana o nā hormones e nā kelepa adrenal iā lākou iho.
- ʻO kahi pilikia me kekahi kelepa ʻē aʻe, e like me ke kelepa pituitary i loko o ko mākou lolo, hiki ke hoʻopilikia i ka hana o nā kelepa adrenal.
- ʻO kekahi mau lāʻau lapaʻau a mākou e lawe ai (no ka laʻana, nā lāʻau steroid) hiki ke hoʻololi i nā pae hormone.
- I kekahi manawa hiki ke loaʻa kēia mau maʻi ma muli o nā hoʻololi genetic .
I ka manawa pinepine, ʻaʻole hiki i nā kauka ke ʻōlelo pololei i ke kumu e loaʻa ai i kekahi poʻe kēia mau maʻi a ʻo kekahi ʻaʻole.
Pehea e ʻike ʻia ai a mālama ʻia ai ka maʻi?
Ke hele ʻoe i ke kauka, e nīnau mua ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona a hana i kahi hoʻokolokolo kino. A laila, e kauoha ʻo ia i kekahi mau hoʻokolohua e nānā i nā pae hormone i loko o kou koko, mimi, a me ka lawai.
Inā he kānalua no nā puʻupuʻu, hiki ke hana ʻia nā scan e like me ka CT scan (Computed Tomography) a i ʻole MRI scan (Magnetic Resonance Imaging) .
I ka hapanui o nā hihia, pono ʻoe e kūkākūkā me kahi endocrinologist.
Aia nā koho lapaʻau i kou kūlana kikoʻī. Pono paha kekahi mau kūlana i ka lāʻau lapaʻau e hoʻoponopono i nā pae hormone. I nā hihia kahi i loaʻa ai nā puʻupuʻu , pono paha ke ʻoki kino a i ʻole ka radiation therapy .
ʻO ka mea maikaʻi loa, inā ʻike mua ʻia kēia mau kūlana a mālama pono ʻia , hiki ke mālama pono ʻia a alakaʻi i ke ola maikaʻi.
Āhea ʻoe e ʻike ai i ke kauka?
Inā ua ʻike ʻia ʻoe me ka maʻi adrenal gland a i ʻole, e makaʻala i nā hōʻailona ma lalo nei. Inā loaʻa iā ʻoe kekahi o kēia mau mea, e ʻike i ke kauka.
| E makaʻala i kēia mau hōʻailona. |
|---|
| Ka pohō kaumaha me ke kumu ʻole. |
| ʻOi aku ka nui o ka ʻaoʻao o luna o ke kino. |
| Manaʻo luhi loa e hoʻopau i ka hana o ka lā. |
| Loaʻa ka ʻeha mau a nui paha. |
| Nā loli o ka ʻili (ʻeha maʻalahi, nā māka kīkoʻo). |
| Nā loli maʻamau ʻole i ka ulu ʻana o ka lauoho o ke kino. |
Āhea ʻoe e hele ai i ka Emergency Treatment Unit (ETU)?
Inā loaʻa iā ʻoe kahi maʻi e hoʻohaʻahaʻa ai i nā pae cortisol, e like me ka maʻi ʻo Addison, hiki iā ʻoe ke loaʻa i kahi maʻi hoʻoweliweli i ke ola i kapa ʻia ʻo ka pilikia adrenal . ʻO kēia ka manawa e hāʻule koke ai nā pae cortisol o ke kino i kahi haʻahaʻa weliweli.
Inā ʻike ʻia nā hōʻailona ma lalo nei, e hele koke i ka ʻOihana Pōpilikia (ETU) o ka haukapila kokoke loa.
| Pilikia! (Nā Hōʻailona Pilikia) |
|---|
| ʻEha koke a nui ma ke kino haʻahaʻa (ʻōpū, kua, wāwae). |
| Ka luaʻi nui a me ka maʻi pākī. |
| Manaʻo nāwaliwali loa. |
| Ka huikau a me ka nalowale o ka ʻike (huikau). |
| Haʻahaʻa ke kō koko (Hypoglycemia). |
| Haʻahaʻa loa ke koko. |
Inā loaʻa iā ʻoe ka lawa ʻole o ka adrenal, e nīnau i kāu kauka e pili ana i kahi glucocorticoid injectable hiki ke hoʻohana ʻia i kahi pilikia. He mea nui e hoʻomaopopo ʻia ʻoe a me kou ʻohana e pili ana i ke ʻano o ka lawe ʻana.
Leka Lawe-Home
- He ʻāpana koʻikoʻi nā kelepa adrenal e mālama ana i ke kaulike hormonal i loko o ko mākou kino.
- Inā hoʻonui ʻia a hoʻemi ʻia paha nā hormones i loko o kēia mau kelepa, hiki ke ʻike ʻia nā hōʻailona like ʻole.
- Inā he mau hōʻailona kānalua kāu, mai kuhi a e ʻike pono i ke kauka.
- Hiki ke mālama pono ʻia ka nui o kēia mau maʻi me ka ʻike mua ʻana a me ka mālama kūpono.
- Inā kū mai nā hōʻailona ulia pōpilikia (e like me ka pilikia adrenal), e hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila me ka hoʻokaʻulua ʻole.
- E hoʻomaopopo pono i kou kūlana olakino. Mai makaʻu e nīnau i kāu kauka.











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