Loaʻa iā ʻoe kahi ʻeha lōʻihi a i ʻole kahi puʻupuʻu i loko o ka iwi a i ʻole ke ami i loko o kou kino, ʻoi aku hoʻi ma kou lima, wāwae, ʻūhā, a umauma paha? Ke ʻano nei paha kēia ʻeha e ʻoi aku ka ʻino i ka pō? Inā pēlā, he mea nui loa kēia ʻatikala iā ʻoe. I kēia lā e kamaʻilio mākou e pili ana i kahi ʻano maʻi ʻaʻai iwi kakaʻikahi loa, akā he mea pono ke ʻike e pili ana. ʻO ia ka chondrosarcoma.
He aha ka Chondrosarcoma?
I ka ʻōlelo maʻalahi, ʻo Chondrosarcoma kahi ʻano maʻi kanesa e ulu ana i loko o ke cartilage i loko o ko kākou kino. ʻIke anei ʻoe i ke ʻano o ke cartilage? He ʻiʻo palupalu a ikaika ka Cartilage e hoʻopuni ana i ko kākou mau hono a pale i nā iwi mai ka hamo ʻana kekahi i kekahi. Ua like ia me ka laholio. Mālama kēia cartilage i ko kākou mau hono a kōkua i ka ulu ʻana o nā iwi.
No laila, hiki i kēia maʻi ʻaʻai chondrosarcoma ke ulu i nā wahi āpau o ko mākou kino kahi i loaʻa ai ke cartilage. Akā ʻike pinepine ʻia ia ma:
- Ma nā kuʻekuʻe lima a me nā ʻūhā.
- Ma nā wāwae.
- I loko o ka pelvis.
- I loko o nā iwi ʻaoʻao o ka umauma.
- Ka iwi ma waenakonu o ka lua o ka umauma (sternum).
I kekahi manawa, ʻoiai nā ʻōpū iwi ʻaʻole i maʻi kanesa (benign) ma mua hiki ke lilo i maʻi kanesa a lilo i chondrosarcoma.
He maʻi kanesa laha ʻole kēia. Wahi a nā helu helu ma ʻAmelika Hui Pū ʻIa, loaʻa ia ma kahi o hoʻokahi i loko o 200,000 mau kānaka. ʻOiai hiki ke loaʻa i kēlā me kēia makahiki, ʻoi aku ka maʻamau i nā poʻe ma waena o 40 a me 75 mau makahiki. ʻO ka awelika o ka makahiki o ka ʻike ʻia ʻana ma kahi o 51. ʻO ke ʻano nui o ka lāʻau lapaʻau no kēia, ʻo ia ke ʻoki ʻana e wehe i ke cartilage a me ka iwi kanesa. I kekahi manawa kapa nā kauka i kēia maʻi he sarcoma.
Aia kekahi mau ʻano o ka chondrosarcoma?
ʻAe, aia nā ʻano like ʻole o ka chondrosarcoma. Ua hoʻokaʻawale ʻia kēia mau maʻi kanesa e hana ʻia ana i loko o ke cartilage ma muli o nā pūnaewele e hana ana i ka puʻupuʻu. E nānā kākou i nā ʻano nui.
ʻO ka Chondrosarcoma Kuʻuna
ʻO kēia ke ʻano maʻamau . ʻOi aku ma mua o 85% o nā chondrosarcomas āpau. Loaʻa pinepine ia i nā kānaka ma waena o 50 a me 70 mau makahiki. Loaʻa pinepine ia ma ka femur, humerus, a me ka pelvis. Ulu mālie loa kēia ʻano puʻupuʻu a ʻaʻole hiki ke metastasize.
ʻO Chondrosarcoma i hoʻokaʻawale ʻia
ʻO kēia ʻano he 10% o nā chondrosarcomas āpau. ʻOi aku ka maʻamau i nā poʻe ma luna o 60 mau makahiki. ʻOi aku ka wikiwiki o kona ulu ʻana ma mua o nā ʻano ʻē aʻe. ʻO ka maʻamau, ulu kēia mau puʻupuʻu wikiwiki i ka iwi lima o luna (humerus), iwi ʻūhā (femur), a i ʻole nā iwi pelvic.
Ua kapa ʻia ʻo 'dedifferentiated' no ka mea ua hoʻomaka kekahi o nā cell ma ke ʻano he mau cell chondrosarcoma maʻamau, akā ma hope e loli kekahi mau ʻāpana o ka puʻupuʻu i nā cell sarcoma kiʻekiʻe. ʻO nā sarcoma kiʻekiʻe nā maʻi kanesa e ulu a pālahalaha koke. ʻO nā laʻana e komo pū me ka osteosarcoma, fibrosarcoma, a me ka undifferentiated pleomorphic sarcoma.
ʻO ka Chondrosarcoma Cell Moakaka
ʻO kēia ka helu ʻana ma kahi o 2% o nā chondrosarcomas āpau. Loaʻa pinepine ia i nā kānaka ma waena o 30 a me 50 mau makahiki, akā hiki nō hoʻi ke loaʻa i nā kānaka ma ko lākou mau makahiki iwakālua. ʻO ka mea maʻamau ia ma nā lima a i ʻole nā wāwae, kokoke i kahi hui. Ulu mālie ia a kākaʻikahi ka laha ʻana i nā ʻāpana ʻē aʻe o ke kino.
ʻO ka Chondrosarcoma Mesenchymal
ʻOi aku ka maʻamau o kēia ʻano i nā poʻe ʻōpio ma waena o nā makahiki 19 a me 30. Hoʻomohala pinepine ia ma ka iwi kuamoʻo, nā iwi ʻaoʻao, a i ʻole ka ʻāwae. ʻOi aku ka wikiwiki o ka ulu ʻana o kēia ʻano ma mua o nā ʻano ʻē aʻe a ʻoi aku ka nui o ka laha a me ka hoʻi hou ʻana ma hope o ka mālama ʻana.
ʻO ka extraskeletal myxoid chondrosarcoma kahi ʻano maʻi ʻaʻai mesenchymal. Hoʻomohala ia i loko o nā ʻiʻo palupalu, ʻaʻole ka iwi a i ʻole ke cartilage, o nā lima o luna a me nā wāwae.
He aha nā hōʻailona o ka chondrosarcoma?
Ma muli o ka ulu mālie ʻana o ka hapa nui o nā puʻupuʻu chondrosarcoma, hiki ke hala i nā mahina no ka ʻike ʻia ʻana o nā hōʻailona. ʻO nā hōʻailona maʻamau:
- ʻEha iwi ma kahi ʻāpana kikoʻī o ke kino e hele mai a hele aku, ʻoi aku hoʻi i ka pō.
- He puʻu a puʻu paha e like me ka puʻu i loko o ka iwi, e like me ka lima, ka wāwae, a i ʻole ka iwi ʻaoʻao.
- Luhi .
- Ka pohō kaumaha i manaʻo ʻole ʻia.
Akā he mea nui e hoʻomanaʻo i kēia: He mea kākaʻikahi loa ka maʻi ʻaʻai iwi. Ua like ka nui o nā hōʻailona o ka chondrosarcoma me nā hōʻailona o nā maʻi ʻoi aku ka koʻikoʻi. No laila, ʻoiai he puʻu kou ma kou wāwae, ʻaʻole ia he manaʻo he maʻi ʻaʻai iwi ia.
Eia nō naʻe, inā he puʻupuʻu kou i nalowale ʻole no nā pule ʻelua a ʻoi aku, a inā paha e luhi loa ʻoe i nā manawa a pau, pono ʻoe e ʻike i ke kauka . E nānā ʻo ia i kou olakino holoʻokoʻa a hoʻoholo i ke kumu o kēia mau hōʻailona.
He aha nā kumu o ka Chondrosarcoma?
ʻAʻole ʻike nā kānaka noiʻi i ke kumu kikoʻī o kēia ʻano, akā ua ʻike lākou ua pili ia i kekahi mau maʻi hoʻoilina. ʻO kēia mau mea:
- ʻO ka maʻi Li Fraumeni:ʻOi aku ka nui o ka poʻe me kēia kūlana e hoʻomohala i nā maʻi ʻaʻai, me ka chondrosarcoma.
- ʻO ka maʻi Maffucci a me ka maʻi ʻo Ollier: Hoʻokumu kēia mau maʻi i nā ʻōpū ʻaʻole maʻi kanesa i loko o ke kāʻei, ka iwi, a me ka ʻili.
- ʻO nā osteochondromas he nui i hoʻoilina ʻia: He mau puʻupuʻu he nui kēia, ʻaʻole maʻi kanesa e hana ʻia i loko o nā iwi. Hiki iā lākou ke hoʻopilikia i ka ulu ʻana o ka iwi.
I kekahi mau hihia, manaʻo nā pathologists e aʻo ana i nā loli genetic i ka chondrosarcoma e hiki i nā loli chromosomal i hoʻoilina ʻole ʻia a i ʻole kekahi mau hoʻololi genetic ke kumu o ka loli ʻana o nā cell cartilage.
He aha nā pilikia o kēia maʻi?
ʻO nā ʻano ulu wikiwiki, e like me Mesenchymal Chondrosarcoma a i ʻole Dedifferentiated Chondrosarcoma, hiki ke hoʻoweliweli i ke ola no ka mea hiki iā lākou ke laha koke a hoʻopilikia i nā ʻāpana ʻē aʻe o ke kino.
Pehea e ʻike ʻia ai ka Chondrosarcoma?
E nīnau aku ke kauka iā ʻoe i nā nīnau e pili ana i kāu mau hōʻailona. Eia kekahi laʻana:
- I ka manawa hea ʻoe i ʻike mua ai i kēia mau hōʻailona?
- Ua nui aʻe anei lākou?
- Pehea lākou e pili ai i kou ola o kēlā me kēia lā?
A laila e hana ʻo ia i kahi hoʻokolohua kino a hiki paha ke kauoha i nā hoʻokolohua kiʻi a i ʻole kahi biopsy.
Nā hoʻokolohua kiʻi
Hoʻohana nā kauka i nā hoʻokolohua kiʻi e like me kēia e ʻike ai i ka chondrosarcoma:
- Nā hoʻāʻo X-ray.
- ʻO ke kiʻi CT `(Computered tomography (CT) scan)`.
- ʻO ke kiʻi MRI `(ʻO ke kiʻi resonance magnetic (MRI) scan)`.
- Nānā PET `(Positron emission tomography (PET) scan)`.
- Nānā iwi.
Biopsy
Hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi orthopedist, he kauka hana e nānā a mālama i nā maʻi e like me ke kanesa iwi, no kahi biopsy. Ma laila, lawe kahi pathologist i kahi ʻāpana o ka ʻiʻo mai ka puʻupuʻu kānalua a nānā iā ia ma lalo o kahi microscope. Aia kekahi mau ʻano biopsy:
- Ka huki ʻana me ke kui maikaʻi: Pili kēia i ka lawe ʻana i kahi hāpana ʻiʻo me ka hoʻohana ʻana i kahi kui a me ka syringe.
- Biopsy ʻokiʻoki: Ua ʻoki ʻia ka puʻupuʻu a lawe ʻia kahi hāpana ʻiʻo.
- Biopsy Excisional: Wehe ʻia ka ʻōpū holoʻokoʻa a i ʻole kahi hapa o ka ʻiʻo.
Nānā ke kauka maʻi i kēia hāpana ʻiʻo e ʻike inā he mau hunaola kanesa. Inā he hunaola kanesa nā hunaola, e hoʻoholo pū ʻo ia i ke ʻano o ka puʻupuʻu a me ke ʻano o ka puʻupuʻu.
He aha nā ʻano o ka chondrosarcoma?
ʻO ke ʻano o kahi puʻupuʻu ke ana o ka wikiwiki o ka ulu ʻana a me ka laha ʻana o kahi puʻupuʻu. Ua helu ʻia ʻo Chondrosarcoma mai 1 (I) a i 3 (III):
- ʻO nā chondrosarcomas haʻahaʻa (papa I): Ua kapa ʻia kēia mau mea he mau puʻupuʻu cartilaginous atypical. ʻO kēia nā mea ulu lohi loa a ʻo ka liʻiliʻi loa ka manawa e laha ai.
- ʻO nā chondrosarcomas papa waena (papa II): ʻOi aku ka palahalaha o kēia mau mea.
- ʻO nā chondrosarcomas kiʻekiʻe (papa III): ʻO kēia nā mea e laha nui ai .
He aha nā lāʻau lapaʻau no ka Chondrosarcoma?
ʻO ka hapa nui o ka manawa, pono ʻoe i ke ʻoki kino e wehe i ka chondrosarcoma. ʻO ke ʻano o ke ʻoki kino āu e hana ai e pili ana i kou kūlana. Hoʻokomo pū kēia i ke ʻano o ka chondrosarcoma āu e loaʻa ai, kahi i loaʻa ai ka puʻupuʻu, a me kona ʻano (pehea ka wikiwiki o kona laha ʻana). Aia kekahi mau ʻano ʻoki kino no ka chondrosarcoma:
- Curettage: Ma kēia kaʻina hana, ʻoki ke kauka i ka ʻiʻo kanesa mai ka iwi a hoʻokomo i kahi mea hoʻopili iwi i loko o ka hakahaka.
- ʻO ke ʻoki ʻana i nā lālā: Maanei, wehe ke kauka i ka puʻupuʻu a me ka iwi a me nā ʻiʻo e hoʻopuni ana. A laila, hana ʻia ke ʻoki hana hou e pani i ka iwi a me nā ʻiʻo i wehe ʻia.
I ka manawa kākaʻikahi loa, hiki i kāu orthopedist ke ʻōlelo aku i ke ʻoki kino e wehe i kahi ʻāpana o kou lima a wāwae paha (amputation). I kēia hihia, hiki iā lākou ke ʻōlelo aku i ka hoʻohana ʻana i kahi lālā prosthetic. I nā hihia āpau, pono ʻoe i ka lāʻau lapaʻau kino e hoʻomaikaʻi i kou ikaika, kaulike, a me ka neʻe ʻana.
Inā loaʻa iā ʻoe kahi ʻano chondrosarcoma kakaʻikahi, e like me ka dedifferentiated a mesenchymal chondrosarcoma paha, hiki ke hāʻawi ʻia iā ʻoe ka chemotherapy a i ʻole ka radiation therapy e hoʻēmi i ka puʻupuʻu ma mua o ke ʻoki ʻana a e luku i nā hunaola kanesa i koe ma hope o ke ʻoki ʻana.
Hiki ke pale ʻia ka Chondrosarcoma?
ʻAʻole maoli, ʻaʻole hiki ke pale ʻia kēia mau mea. ʻO kekahi kumu, ʻaʻole maopopo i nā kānaka noiʻi ke kumu o ko lākou ulu ʻana. Akā, hōʻike ka noiʻi he ʻoi aku ka nui o ka pilikia o ka poʻe me kekahi mau kūlana hoʻoilina i ka ulu ʻana o ka chondrosarcoma. No laila, e kamaʻilio me kāu kauka e pili ana i ka mōʻaukala olakino o kou ʻohana. Hiki iā ia ke loiloi i kou pilikia a hāʻawi i nā ʻanuʻu e nānā ai i kou olakino.
He aha kaʻu e manaʻo ai me kēia kūlana?
No ka mea, he nui nā ʻano chondrosarcoma, ʻokoʻa nā hopena i manaʻo ʻia (prognoses) ma muli o ke ʻano. E nīnau i kāu kauka i kāu mea e manaʻo ai ma muli o kou kūlana kikoʻī. E hauʻoli ʻo ia e wehewehe i kēia iā ʻoe.
Hiki ke ho'ōla ʻia ka Chondrosarcoma?
I kekahi mau hihia, hiki ke ho'ōla loa ʻia nā ʻōpū chondrosarcoma maʻamau liʻiliʻi loa a lohi ka ulu ʻana ma o ka wehe ʻana iā lākou ma ke ʻoki ʻana. Ma muli o ke ʻano o ka chondrosarcoma, hiki i ka hoʻohui ʻana i ka chemotherapy ke kōkua i ka ho'ōla ʻana i ka maʻi.
He aha ka nui o ka ho'ōla no ka Chondrosarcoma?
ʻOkoʻa nā helu ola no ka chondrosarcoma ma muli o ke ʻano o ka puʻupuʻu a inā ua pālahalaha ka puʻupuʻu i nā ʻāpana ʻē aʻe o ke kino. Ma ke ʻano holoʻokoʻa, 79% o ka poʻe me ka chondrosarcoma e ola ana i ʻelima mau makahiki ma hope o ka hōʻoia ʻana.
I ka noʻonoʻo ʻana i kēia mau pakeneka, e hoʻomanaʻo i kekahi mau mea:
- He mau kuhi nā helu hoʻōla, ʻaʻole he wānana . He mau kuhi kēia i hoʻokumu ʻia ma nā ʻike o haʻi, a ʻokoʻa loa paha kou kūlana.
- Hoʻokumu ʻia kēia mau kuhi ma luna o nā mea i hana ʻia i ka wā ma mua . No ka laʻana, hoʻokumu ʻia kēia mau pakeneka ma luna o nā mea i hana ʻia i ka poʻe i loaʻa i ka chondrosarcoma ma waena o 2012 a me 2018.
- ʻAʻole haʻi aku nā helu ola iā ʻoe i ka lōʻihi o kou ola ʻana .
Inā he mau nīnau a hopohopo paha kāu e pili ana i ke ʻano o ka helu ho'ōla no kou kūlana, e noi i kāu kauka e wehewehe pehea e pili ai kēlā kuhi i kou kūlana.
Inā loaʻa iaʻu ʻo Chondrosarcoma, pehea wau e mālama ai iaʻu iho?
ʻO ka noho ʻana me ka chondrosarcoma e hoʻomaka pinepine me ka hoʻōla ʻana mai ka lāʻau lapaʻau. Hoʻōla pinepine ʻia ʻo Chondrosarcoma me ke ʻoki kino. I kekahi manawa, pono e wehe ʻia kahi lālā a i ʻole kahi ʻāpana o kahi lālā e wehe i ke kanesa. Ma hope o ka hoʻōla ʻana mai ke ʻoki kino, inā ʻoe e hoʻohana ana i kahi lālā prosthetic, pono ʻoe e hoʻomaka i kahi papahana hoʻōla hou e maʻa ai iā ia.
Pono paha ʻoe i ke kōkua e hoʻololi i nā loli i kou ola o kēlā me kēia lā a i ʻole nā loli i kou helehelena. Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau kino, ʻoihana a noʻonoʻo paha e hiki ke kōkua iā ʻoe e hoʻokele i kēia mau pilikia.
Āhea wau e ʻike ai i ke kauka?
E nīnau i kāu kauka e pili ana i nā loli kino e hōʻike ana i ka hoʻi ʻana mai o ka maʻi kanesa, a me ka manawa e hoʻokaʻaʻike aku ai i kāu kauka inā loaʻa.
He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka e pili ana i kaʻu hōʻailona?
Eia kekahi mau nīnau hiki iā ʻoe ke nīnau i kāu kauka:
- He aha ke ʻano o ka Chondrosarcoma i loaʻa iaʻu?
- He aha nā lāʻau lapaʻau āu e paipai nei?
- No ke aha ʻoe e paipai nei i kēlā lāʻau lapaʻau?
- He aha nā hopena ʻaoʻao o ka lāʻau lapaʻau?
- He aha nā hopena o kēia mau lāʻau lapaʻau?
- Inā wau e lawe i ka lāʻau lapaʻau i ʻōlelo ʻia, hiki i kaʻu chondrosarcoma ke hoʻi hou mai?
He aha ka ʻokoʻa ma waena o ka chondrosarcoma a me ka osteosarcoma?
Hoʻomaka ka Osteosarcoma i loko o nā iwi a loaʻa pinepine i nā keiki. Hoʻomaka ka Chondrosarcoma i loko o ke cartilage a loaʻa pinepine i nā pākeke. Hiki i nā kauka ke hana i ke ʻoki kino no ka chondrosarcoma wale nō, akā no ka osteosarcoma, hoʻohana lākou i ka chemotherapy a me ke ʻoki kino.
ʻO ka mea hope loa, he leka koʻikoʻi
ʻO ka ʻike ʻana i kēia maʻi ʻaʻai iwi laha ʻole, i kapa ʻia ʻo chondrosarcoma, hiki ke lilo i ka hana mua i kahi huakaʻi lōʻihi o ka hoʻōla ʻana. Hoʻomaka pinepine kēlā huakaʻi me ke ʻoki ʻana e wehe i ke kanesa, a ukali ʻia e ka hoʻōla hou ʻana e hoʻōla mai ke ʻoki ʻana a me nā lāʻau lapaʻau ʻē aʻe.
ʻOiai hiki ke mālama pono ʻia kēia maʻi kanesa, e hoʻololi ia i kou ola. Pono paha ʻoe i ke kōkua e hoʻoponopono ai i nā pilikia kino a me ka naʻau. E kamaʻilio me kāu kauka e pili ana i nā pilikia āu e kū nei. Hoʻomaopopo kāu kauka a me kāna hui i kāu mea e hele nei. I kou hoʻomaka ʻana i kēia huakaʻi, e noho pū lākou me ʻoe i kēlā me kēia ʻanuʻu o ke ala. Mai haʻalele i ka manaʻolana!
ʻO Chondrosarcoma, maʻi ʻaʻai iwi, maʻi ʻaʻai cartilage, ʻeha hono, nā puʻupuʻu iwi, mālama ʻana i ke kanesa, ʻoki kino











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