Ua puka mai nā ʻōpū o kāu pēpē? E aʻo kākou e pili ana i kēia mea i kapa ʻia ʻo cloacal exstrophy!

Pehea ka makaʻu o ka makuahine a i ʻole ka makuakāne inā ʻike lākou ʻaʻole i hana pono ʻia ka ʻōpū o kahi pēpē hānau hou a ua puka mai kekahi o nā ʻōpū i loko? He mea paʻakikī loa ke noʻonoʻo. Akā, mai hopohopo. ʻOiai he maʻi kakaikahi loa kēia, aia kahi lāʻau lapaʻau no ia mea. E kamaʻilio kākou e pili ana i kēia maʻi i kapa ʻia ʻo Cloacal Exstrophy ma ke ʻano maʻalahi hiki iā ʻoe ke hoʻomaopopo.

He aha kēia exstrophy cloacal?

I ka ʻōlelo maʻalahi, ʻo Cloacal Exstrophy kahi kīnā hānau e kū mai ana i ka wā e hana pono ʻole ai ka paia ʻōpū o ka pēpē i ko lākou ulu ʻana i loko o ka ʻōpū. E noʻonoʻo, no ka mea, ʻaʻole i pani pono ka ʻaoʻao haʻahaʻa o ka ʻōpū, ua uhi ʻia ka ʻōpū mimi o ka pēpē a me kekahi hapa o ka colon, a i ʻole nā ​​​​​​kikowaena ʻē aʻe, e kahi membrane liʻiliʻi a kū i waho o ke kino. He mea paʻakikī loa kēia ke ʻike. Hoʻopilikia pū kēia ʻano i nā ʻāpana o ka pēpē.

Ua kapa ʻia hoʻi kēia he ʻano maʻi urinary congenital . ʻO ia hoʻi, he pilikia ia e kū mai ana i ka wā e noho ana ke pēpē i loko o ka ʻōpū. Akā, mai hopohopo, ma hope o kekahi mau ʻoki hoʻoponopono , e hoʻomaka ana mai ka hānau ʻana a mau no kekahi manawa, ʻo ka hapa nui o nā keiki me kēia maʻi e hoʻomau i ke ola maʻamau a hauʻoli.

Pehea kēia e pili ai i ka pēpē? He aha ka paʻakikī OEIS?

Ua ʻike ʻia hoʻi ʻo Cloacal Exstrophy ʻo ia ka OEIS complex a i ʻole OEIS syndrome no ka mea ua hele pū ʻia me kekahi mau pilikia ʻē aʻe. E nānā kākou i ke ʻano o lākou:

He aha ka ʻOmphalocele?

Hana ʻia kēia ke hui pono ʻole ʻia nā ʻiʻo ʻōpū o ka pēpē, kokoke i ka pihi ʻōpū, e hana ana i kahi puka. Ma o kēia puka, e puka mai ana ka ʻōpū mimi, ka ʻōpū nui, a i kekahi manawa nā ʻāpana ʻē aʻe, e like me ke akepaʻa. Akā, ʻaʻole e puka wale mai kēia mau ʻāpana, ua uhi ʻia lākou e kahi membrane pale.

He aha ka exstrophy?

ʻO kēia ka manawa e huli ai ka paia o ka ʻōpū mimi o ke pēpē i waho ma kahi o loko. Ua kapa ʻia kēia he bladder exstrophy . He pālahalaha ka ʻōpū mimi ma kahi o ka poepoe, a hiki ke māhele ʻia i ʻelua. Eia kekahi, ʻaʻole pili pono nā ʻiʻo ʻōpū a me nā iwi pelvic, a i ʻole nā ​​​​iwi a puni ka pūhaka. ʻO ka hopena, ua hohola ʻia ka pelvis ma nā ʻaoʻao ʻelua, e like me ka puke i wehe ʻia.

He aha ka anus imperforate?

I kēia hihia, ʻaʻole i hana pono ʻia ka anus o ke pēpē, ka puka e hele ai mākou i ka ʻōpala. Ua ālai ʻia paha, a ʻaʻohe puka e like me ia. He pōkole loa ka colon, a ua pili paha ia i ka ʻōpū mimi.

He aha nā kīnā o ke kuamoʻo?

Ma kahi o ʻekolu o nā pēpē ʻehā me ka cloacal exstrophyAia paha kekahi maʻi i kapa ʻia ʻo spina bifida, kahi e pani pono ʻole ai nā iwi o ka iwi kuamoʻo, e hoʻoulu ai i ka ʻeke piha wai a puni ke kaula kuamoʻo (me nā aʻalolo paha) e puka i waho ma waena o ka hakahaka.

Mea nui: Loaʻa paha i kahi pēpē kēia mau mea a pau, a i ʻole kekahi wale nō o lākou. E nānā pono nā kauka i kēia mau mea a pau.

He hopena anei kēia i nā ʻōpū moekolohe?

ʻAe, hoʻopilikia pū ka Cloacal Exstrophy i nā ʻōpū o ke pēpē.

• Inā he keikikāne: Hiki ke pālahalaha ka penis, pōkole, a māhele ʻia paha i nā ʻaoʻao ʻākau a me hema.
• Inā he kaikamahine: Hiki ke māhele ʻia ka clitoris i ʻelua ʻāpana, hoʻokahi ma ka ʻākau a hoʻokahi ma ka hema. Loaʻa paha he ʻelua puka o ka vagina.

Pehea ka maʻamau o kēia ʻano?

He maʻi laha ʻole kēia. Ma ke ʻano kikoʻī, hoʻopilikia ia ma kahi o hoʻokahi i loko o 250,000 a hoʻokahi i loko o 400,000 mau pēpē i hānau ʻia. Eia kekahi, ʻelua a ʻekolu paha manawa ka nui o ka loaʻa ʻana o kēia maʻi i nā keikikāne ma mua o nā kaikamahine.

He aha nā ʻano o ka exstrophy-epispadius complex (EEC)?

ʻO ka cloacal exstrophy kekahi o kahi hui o nā kīnā hānau i kapa ʻia ʻo Exstrophy-Epispadias Complex (EEC) . ʻO ka ʻoiaʻiʻo, ʻo ia ke ʻano koʻikoʻi loa o ka hui. Hiki i kahi pēpē ke loaʻa i hoʻokahi wale nō maʻi i loko o kēia hui, a i ʻole hiki iā lākou ke loaʻa i kekahi mau mea i ka hui pū ʻana.

ʻO nā kūlana ʻē aʻe ma ka māhele EEC:

• Epispadias: Ma kēia ʻano, ʻaʻole i hana pono ʻia ka urethra o ke pēpē, ka ʻōmole e lawe ana i ka mimi i waho o ke kino.
• ʻO ka exstrophy bladder: Ma kēia ʻano, huli ka ʻōpū o ke pēpē i loko i waho.

He aha ke kumu o ka exstrophy cloacal?

ʻAʻole maopopo loa i nā kauka ke kumu e loaʻa ai kēia ʻano i kekahi mau pēpē, akā manaʻoʻiʻo lākou e hana ia ke haehae a haki paha kahi ʻiʻo i kapa ʻia ʻo ka membrane cloacal i ka trimester mua o ka hāpai ʻana.

ʻO ka cloaca kahi e hui pū ai ka ʻōnaehana hānau keiki o ka pēpē, ka ʻōnaehana hoʻoheheʻe ʻana, a me ka ʻōnaehana mimi. ʻO ka maʻamau, ua hoʻokaʻawale ʻia nā ʻōpū o kēia mau ʻōnaehana mai kekahi i kekahi e kēia membrane cloacal. No laila, ke haki kēia membrane, ʻaʻole i hana piha ʻia ka paia o ka ʻōpū. ʻAʻole ulu pono nā ʻōpū, a hiki paha ke pili pono kekahi i kekahi. I ka hopena, puka mai kekahi mau ʻōpū ma kahi hakahaka i loko o ka ʻōpū.

He aha nā hōʻailona o kēia maʻi?

Hiki ke ʻike koke ʻia nā hōʻailona o ka cloacal exstrophy ma hope o ka hānau ʻana. Hiki i kāu pēpē ke ʻike i kēia mau mea:

• Ua puka mai nā ʻōkana mai loko mai o kahi lua i loko o ka ʻōpū, i loko o kahi ʻano like me ke ʻeke.
• Aia kahi ʻano like me ka ʻeke e puka mai ana mai kahi hakahaka ma ke kua o ka iwi kuamoʻo (ʻo Spina Bifida kēia).
• Me he mea lā ua māhele ʻia ka penis a i ʻole ka vagina i ʻelua.

Pehea e ʻike ai nā kauka i kēia?

Hiki ke ʻike pinepine ʻia ka cloacal exstrophy i ka wā o ka ultrasound prenatal i ka wā hāpai. Hiki i kāu kauka ke ʻōlelo aku i kahi MRI fetal scan. Hiki i kēia ke hāʻawi i nā kiʻi maopopo o nā ʻōpū o kāu pēpē. Hiki i kēia mau scan ke hōʻike i nā mea e like me:

• ʻAʻole kahe pono ka mimi mai ka ʻōpū mimi mai.
• Ua hoʻokaʻawale ʻia nā iwi pubic mai kekahi i kekahi.
• ʻOi aku ka liʻiliʻi ma mua o ka nui maʻamau o nā ʻāpana kino.
• ʻO ka omphalocele ke ʻano o ka hoʻopaʻa ʻia ʻana o ke kaula umbilical ma lalo loa i loko o ka ʻōpū o ke pēpē.

Ma hope o ka hānau ʻana o kāu pēpē, hiki i kāu kauka ke kauoha i kahi scan MRI , kahi ultrasound ʻōpū , a i ʻole nā ​​​​scan kiʻi ʻē aʻe. Hiki i kēia mau mea ke loiloi i ka hana o nā ʻōkana a me ke koʻikoʻi o ka maʻi. Ma ka hoʻohana ʻana i kēia ʻike āpau, e hoʻomohala kāu kauka i ka hoʻolālā lapaʻau maikaʻi loa no kāu pēpē.

Pehea e mālama ai i ka Cloacal exstrophy?

Pono kēlā me kēia keiki hānau hou me ka cloacal exstrophy i ke ʻoki kino . ʻO kēia ʻoki kino e pili ana i ke kau ʻana i nā ʻōpū e puka mai ana i loko o ke kino a me ka pani ʻana i nā hakahaka ma ka ʻōpū a me ke kua. E loaʻa paha i kāu pēpē kekahi mau ʻoki kino i loko o kekahi mau makahiki. Ua kapa ʻia kēia he hana hou i hoʻonohonoho ʻia .

Ka lāʻau lapaʻau hānau

Hoʻomaka nā lāʻau lapaʻau e like me kēia i ka wā e hānau ai ke pēpē:

• Ke hana hou ʻana i ka ʻōpū mimi, hoʻihoʻi i nā ʻōpū i loko o ka ʻōpū, a me ka pani ʻana i ka hakahaka ma ka ʻōpū.
• Ke hana ʻana i kahi stoma . He lua kēia ma ka ʻōpū e hiki ai i ka ʻōpala ke hele mai loko mai o ka ʻōpū nui. Hōʻiliʻili ʻia kēia ʻōpala i loko o kahi ʻeke ma waho (ʻeke colostomy). Hiki ke lilo kēia ʻeke colostomy i mea manawa pōkole, a hiki i ka hana ʻia ʻana o nā ʻoki ʻē aʻe.
• Ke pani nei i ka hakahaka ma ka iwi kuamoʻo.

Ka mālama ʻana i ka wā kamaliʻi

Ke ʻōpiopio iki aʻe ke pēpē, ʻo ia hoʻi, i ka wā kamaliʻi, hana ʻia ka lāʻau lapaʻau penei:

• Hana ʻia kahi ʻoki iwi (osteotomy) e ʻoki ai i nā iwi pelvic. ʻAe kēia i ka pelvis e pani maʻalahi a hāʻawi i ke kākoʻo maikaʻi aʻe no ka ʻōpū mimi i ka wā e ulu ana ka pēpē.
• Ke hoʻonohonoho hou ʻia nei nā ʻōpū hānau a me ke ala mimi.
• Hoʻokumu ʻia kahi puka anal. Inā lawa ka lōʻihi o ke kolona, ​​hiki i ke kauka ke hana i kahi ʻoki pull-through e hoʻopili ai i ke kolona i ka anus. A laila pani ʻia ka stoma. ʻAʻole pono hou ka pēpē i kahi ʻeke colostomy.

He aha nā pilikia e hiki ke kū mai mai kēia maʻi?

Ma hope o ke ʻoki ʻana, ola ka hapa nui o nā keiki me ka cloacal exstrophy i nā ola piha a piha . Pono paha kekahi mau keiki i ke ʻoki hou aku i ko lākou wā ʻelemakule.

Hiki i ka cloacal exstrophy ke hana i nā kūlana pilikia ma lalo nei:

• Ka hānau ʻole ʻana.
• Maʻi puʻupaʻa, nā maʻi puʻupaʻa, nā pōhaku puʻupaʻa, a me ka hāʻule ʻana o ka puʻupaʻa.
• ʻO ka hana moekolohe, ka hana erectile, a pēlā aku.
• ʻO ka hoʻōki ʻana o ka mimi a me ka hoʻōki ʻana o ka fecal.

Nā mea e nīnau aku ai i kāu kauka

Hiki iā ʻoe ke nīnau i ke kauka o kāu pēpē i nā mea e like me:

• Aia kaʻu pēpē i ka nui o ka pilikia o nā pilikia olakino ʻē aʻe?
• He aha ka lāʻau lapaʻau maikaʻi loa no ka Cloacal exstrophy?
• ʻEhia mau ʻoki kino e pono ai kaʻu pēpē?
• He aha nā pilikia e pono iaʻu e makaʻala ma hope o ke ʻoki ʻana?
• He aha nā mea e loaʻa ai i kaʻu keiki aʻe ka Cloacal Exstrophy?

He mea maʻamau ke makaʻu a hopohopo ke ʻike ʻoe ua loaʻa i kāu pēpē ka Cloacal Exstrophy, a i ʻole OEIS syndrome. Akā e hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi.

ʻO ka mea nui loa e hoʻomanaʻo

He mea maʻamau ka manaʻo kaumaha a me ka makaʻu ke ʻike ʻoe ua loaʻa i kāu pēpē ka Cloacal Exstrophy. Akā , mai hopohopo . Ua mākaukau kāu mau kauka a me ka hui lapaʻau e kōkua iā ʻoe a me kāu pēpē. Pono kāu pēpē i kekahi mau ʻoki kino ma hope koke o ka hānau ʻana, a laila nā ʻoki kino hou aʻe e hoʻoponopono hou i nā kino.

Akā ʻo ka mea maikaʻi loa, me ka mālama kūpono ʻana, ʻo ka hapa nui o nā keiki i hānau ʻia me kēia maʻi e ola maʻamau a hauʻoli . E kamaʻilio me kāu kauka e pili ana i nā nīnau a hopohopo paha āu e loaʻa ai. E wehewehe lākou i nā mea āpau iā ʻoe.

ʻO ka Cloacal Exstrophy, nā kīnā hānau, OEIS Complex, Omphalocele, Bladder Exstrophy, ʻoki kino pediatric