E noʻonoʻo i kahi kūlana kahi hiki ʻole i kekahi ke ʻai a ale paha i ka meaʻai ma muli o kekahi maʻi a ma hope paha o ke ʻoki ʻana. Pehea ʻoe e hāʻawi ai i ke kino i ka meaʻai e pono ai i ia manawa? ʻAʻole hiki iā ʻoe ke ʻae i ke kino e nāwaliwali. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi ʻano lapaʻau kūikawā i hoʻohana ʻia i ia mau hihia a me kahi lāʻau lapaʻau e pono ai no ia mea.
He aha kēia Cysteine?
I ka ʻōlelo maʻalahi, ʻo ka cysteine he waikawa amino e pono ai no ke kūkulu ʻana i nā protein i loko o ko mākou kino. E like me ka pono o nā piliki e kūkulu i hale, pono nā protein e kūkulu a mālama i nā cell a me nā ʻiʻo i loko o ko mākou kino. ʻO kēia mau waikawa amino nā poloka kūkulu kumu o kēlā mau protein.
Hoʻohana pinepine ʻia kēia inikini cystine i kahi lāʻau i kapa ʻia ʻo Parenteral Nutrition . ʻO ka pōkole no kēia ʻo (PN) . ʻOiai he ʻano lapaʻau kēia, he maʻalahi loa ke ʻano. ʻO ia hoʻi , ua hāʻawi pololei ʻia ke kino i ka meaʻai e pono ai ma o kahi aa koko, me ka hoʻohana ʻole ʻana i ka ʻōnaehana hoʻoheheʻe. Hoʻohui ʻia ʻo Cysteine ma ke ʻano he mea nui i ka hopena meaʻai i hāʻawi ʻia ma kēia ʻano. Ma Sri Lanka, hiki ke ʻike ʻia kēia lāʻau lapaʻau ma lalo o ka inoa inoa `(ELCYS)`.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka hāʻawi ʻana i kēia lāʻau lapaʻau
No ka mea he lāʻau lapaʻau kūikawā kēia, he mea nui loa ia e ʻike kāu kauka i kou mōʻaukala olakino piha. Inā loaʻa iā ʻoe kekahi o kēia mau kūlana, e haʻi i kāu kauka ma mua o ka hoʻomaka ʻana i ka lāʻau lapaʻau.
- Inā he maʻi puʻuwai kou .
- Inā he maʻi kou e pili ana i ka puʻupaʻa .
- Inā he maʻi kou i ke akepaʻa .
- Inā he maʻi hoʻoilina kou i loaʻa i ka wā hānau a hoʻopilikia i ke ʻano o ka wāwahi ʻana o ke kino i ka meaʻai ('inborn error of metabolism') .
- Inā ua loaʻa iā ʻoe kahi maʻi allergy a i ʻole kahi hopena maʻamau ʻole i ka cysteine, nā waikawa amino ʻē aʻe, nā lāʻau lapaʻau ʻē aʻe, nā meaʻai, nā dyes, a i ʻole nā mea mālama.
- Inā hāpai ʻoe a i ʻole e hoʻāʻo nei e hāpai .
- Inā he makuahine hānai waiū ʻoe .
Ma muli o kēia ʻike, e hoʻoholo ke kime lapaʻau inā kūpono kēia lāʻau iā ʻoe a pehea e hāʻawi ʻia ai.
Pehea e hāʻawi ʻia ai kēia lāʻau i ke kino?
ʻAʻole hāʻawi ʻia kēia lāʻau lapaʻau ma kāna iho. Hoʻomākaukau ʻia ia ma ke ʻano he ʻāpana o kahi hopena meaʻai kūikawā i loaʻa nā meaʻai koʻikoʻi he nui o ke kino, e like me ke kō, nā huaora, a me nā minelala. A laila hoʻokomo mālie ʻia ka hopena i loko o ke kino ma o kahi aʻa, e like me ka saline.
Hāʻawi pinepine ʻia kēia lāʻau lapaʻau ma lalo o ka nānā ʻana o ke kauka ma kahi haukapila a i ʻole ke keʻena lapaʻau . Eia nō naʻe, i kekahi mau hihia, ma muli o ke kūlana o ka mea maʻi, hiki i nā kauka ke ʻōlelo aku e hāʻawi ʻia kēia lāʻau lapaʻau ma ka home.
Inā pono ʻoe e hoʻohana i kēia lāʻau lapaʻau ma ka home, e hāʻawi ʻia ʻoe i ke aʻo kūpono no ka hoʻomākaukau ʻana a me ka hāʻawi ʻana iā ia. He mea nui e hahai pololei i kēlā mau kuhikuhi.
Aia kekahi mea nui e hoʻomanaʻo ai i ka wā e hoʻohana ai i kēia lāʻau lapaʻau ma ka home: ke hoʻolei pono ʻana i nā nila a me nā syringe i hoʻohana ʻia.
- Mai hoʻolei i kēia mau mea i loko o ka ʻōpala maʻamau.
- Pono e waiho ʻia kēia mau mea i loko o kahi pahu palekana kūikawā (pahu ʻoi) no ka hoʻolei ʻana.
- Inā ʻaʻohe āu, e nīnau i kāu kauka pehea e loaʻa ai.
Pono e mālama pono ʻia i ka hāʻawi ʻana i kēia lāʻau lapaʻau i nā keiki, no laila inā ʻoe e hāʻawi ana i kēia lāʻau i kahi keiki, e kamaʻilio me kāu kauka e pili ana i ia mea.
He aha ka mea e hana ai inā hoʻonui ʻia ka nui o ka lāʻau lapaʻau?
Hāʻawi pinepine ʻia kēia ma lalo o ka nānā ʻana o ke kauka, no laila ua haʻahaʻa ka pilikia o ka overdose. Eia nō naʻe, inā manaʻo ʻoe ua lawe nui ʻoe i kēia lāʻau lapaʻau, e kelepona koke aku i ke Kikowaena ʻIke Poisons National ma ka Halemai Lahui ʻo Colombo . A i ʻole e hele i ka ʻOihana Pilikia (ETU) o ka haukapila kokoke loa. Mai lawe māmā i kēia ʻano mea.
He aha nā hopena ʻaoʻao e hiki mai ana?
E like me nā lāʻau lapaʻau āpau, hiki i kēia ke hana i nā hopena ʻaoʻao i kekahi poʻe. Akā, ʻaʻole i loaʻa i nā kānaka a pau. E nānā kākou i kēlā mau hopena ʻaoʻao. Hiki iā ʻoe ke hoʻomaopopo maʻalahi i kēia mai ka papa ma lalo nei.
| ʻAno o ka hopena ʻaoʻao | Nā hōʻailona āu e ʻike ai |
|---|---|
| Nā hopena ʻaoʻao e pono e hōʻike koke ʻia i kāu kauka a i ʻole nā limahana kahu maʻi | |
| Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, lehelehe, alelo a i ʻole ka puʻu, paʻakikī ke hanu. |
| ʻAʻa koko | ʻEha wāwae, pehu a mehana paha, paʻakikī ka hanu ʻana, ʻeha umauma. |
| Nā pilikia o ka ʻōpū gall | ʻEha nui o ka ʻōpū, nausea, luaʻi, kuni. |
| ʻEha o ke akepaʻa | ʻEha ma ka ʻaoʻao ʻākau o luna o ka ʻōpū, nalowale ka makemake i ka ʻai, nausea, nā ʻōpala māmā, ka mimi melemele ʻeleʻele a ʻeleʻele paha, ka melemele o nā maka a i ʻole ka ʻili (jaundice), a me ka manaʻo luhi ʻē. |
| Ka pae waikawa kiʻekiʻe i loko o ke koko | Paʻakikī ka hanu ʻana, nāwaliwali kūikawā, ʻeha poʻo, puʻuwai wikiwiki a ʻano ʻole paha, nausea, luaʻi. |
| Ka nui o ka ammonia i loko o ke koko | Ka nāwaliwali maʻamau ʻole, ka huikau, ka nalowale o ka makemake, ka nausea, ka luaʻi ʻana, nā hopu ʻana. |
| Nā mea i maʻa mau ʻole i ka nui, akā pono e hōʻike ʻia i ke kauka inā hoʻomau lākou | |
| Ka holoi ʻana | ʻUlaʻula ka ʻili a mehana. |
| ʻO ka ʻoluʻolu ʻole ma kahi i hoʻokomo ʻia | ʻEha, ʻulaʻula, a pehu paha ma ke aʻa koko kahi i hāʻawi ʻia ai ka inikini. |
ʻAʻole i loko o kēia papa inoa nā hopena ʻaoʻao āpau. Inā ʻike ʻoe i kekahi mea ʻē, e haʻi koke i kāu kauka.
Pehea ʻoe e mālama ai a hoʻolei aku i ka lāʻau lapaʻau?
E hāʻawi kāu hui lapaʻau iā ʻoe i nā kuhikuhi no ka mālama ʻana i kēia lāʻau. E hahai pono i kēlā mau kuhikuhi. E mālama iā ia mai ka hiki ʻana aku o nā keiki liʻiliʻi a me nā holoholona . Mai hoʻohana i ka lāʻau i pau ka lāʻau.
E nīnau i kāu kauka a i ʻole ka haukapila kahi āu e mālama ʻia nei no nā ʻōlelo kūpono e pili ana i ka hoʻolei ʻana i nā lāʻau lapaʻau i pau ka manawa a i ʻole nā lāʻau i makemake ʻole ʻia.
Leka Lawe-Home
- ʻO Cysteine kahi waikawa amino koʻikoʻi i hoʻohui ʻia i kahi hopena meaʻai kūikawā i hāʻawi ʻia ma o kahi vein ke hiki ʻole ke lawe ʻia ka meaʻai e ka waha.
- Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui e haʻi i kāu kauka e pili ana i kou mau maʻi allergies a pau.
- E ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe kekahi mau hopena koʻikoʻi e like me ka paʻakikī o ka hanu ʻana, ka ʻeha o ka umauma, ka ʻeha nui o ka ʻōpū, a i ʻole ka melemele o nā maka a i ʻole ka ʻili.
- Inā ʻoe e mālama ana ma ka home, e hoʻolei pono i nā nila a me nā syringe i hoʻohana ʻia. Mai hoʻolei iā lākou i loko o ka ʻōpala.
- He lāʻau lapaʻau kūikawā kēia, no laila e hahai mau i ka ʻōlelo aʻo a kāu kauka.











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