Ua ʻike anei ʻoe he ʻano ʻē ke kala o nā niho o kekahi poʻe, he uliuli-hina paha, a he melemele-ʻeleʻele paha? A i ʻole he mau niho nāwaliwali loa kou a haki a mae paha ke ʻai ʻoe i kahi mea liʻiliʻi? Manaʻo paha ʻoe he mea maʻamau kēlā. Eia nō naʻe, hiki nō hoʻi kēia ma muli o kahi kūlana kakaikahi e kū mai ana i ka wā o ka ulu ʻana o ka niho i kapa ʻia ʻo `(Dentinogenesis Imperfecta)`. E kamaʻilio iki kākou e pili ana i kēia i kēia lā, ʻae?
He aha ka `(Dentinogenesis Imperfecta)`? E hoʻomaopopo maʻalahi kākou, ʻeā?
I ka ʻōlelo maʻalahi, ʻo `(Dentinogenesis Imperfecta)` kahi pilikia e kū mai ana i ka wā e hoʻokumu ʻia ai nā niho, ʻo ia hoʻi, i ka wā e ulu ai nā niho. ʻO ka mea e hana ʻia ma kēia hihia, ʻo ia ka nāwaliwali loa o kou mau niho a haki maʻalahi . E like me ka biscuit, inā ʻoe e haki iki, e haki ia. Eia kekahi, he ʻano translucent iki nā niho o ka poʻe me kēia maʻi. ʻO ke kala hoʻi, e like me kaʻu i ʻōlelo ai ma mua , he uliuli-hina a he melemele-brown paha .
ʻO kēia kūlana, i kapa ʻia ʻo "Dentinogenesis Imperfecta," hiki ke hoʻopilikia i kou mau niho mua a me kou mau niho paʻa . ʻO ia hoʻi, hiki ke hoʻomaka nā hōʻailona i ka wā ʻōpiopio, a i ʻole hiki ke ʻike ʻia ma hope o ke ola.
E nānā, ke lawe kākou i kahi niho, he mau papa kona. ʻO ka ʻāpana ʻālohilohi a ikaika ma luna ua kapa ʻia ʻo `(Enamel)`. Ma lalo o kēlā `(Enamel)` aia kekahi papa ʻē aʻe, i kapa ʻia ʻo `(Dentin)`. ʻO kēia ʻāpana `(Dentin)` ka mea nui e hāʻawi i ka ikaika a me ke kala o ka niho. ʻO ka mea e hana ʻia ma `(Dentinogenesis Imperfecta)` ʻo ia ka ulu pono ʻole o ka ʻāpana `(Dentin)`. He aha ka mea e hana ʻia a laila? No ka mea ua nāwaliwali ka `(Dentin)`, ʻaʻole i hoʻopili pono ʻia ka `(Enamel)` ma luna i ka niho. ʻO ia ke kumu e maʻalahi ai ka `(Enamel)` a mae wale.
He mea nui: ʻOkoʻa ka `(Dentinogenesis Imperfecta)` mai ka `(Amelogenesis Imperfecta)`. Ma `(Amelogenesis Imperfecta)`, pili pono ka `(Enamel)` o ka niho. Ma `(Dentinogenesis Imperfecta)`, aia ka pilikia ma ka `(Dentin)`.
Ua ʻōlelo ʻia he maʻi laha ʻole kēia. ʻO ka maʻamau, ʻike ʻia kēia maʻi ma kahi o hoʻokahi i loko o 6,000 a 8,000 mau kānaka.
Aia kekahi mau ʻano o ka `(Dentinogenesis Imperfecta)`?
ʻAe, ke kamaʻilio nei mākou e pili ana i ʻekolu ʻano nui o ka `(Dentinogenesis Imperfecta)`. E nānā kākou i ke ʻano o lākou.
1. ʻAno 1 (ʻAno I): He mea kūikawā kēia. No ka mea, loaʻa kēia ʻano me kahi maʻi i kapa ʻia ʻo ʻOsteogenesis Imperfecta. ʻO ka ʻOsteogenesis Imperfecta he maʻi wale nō ia e palupalu ai nā iwi (maʻi iwi brittle). No laila, me nā pilikia niho, loaʻa pū kekahi mau pilikia iwi i kēia poʻe. ʻO ke kumu o kēia, aia kekahi mau loli i nā ʻGenes o nā genes (COL1A1) a i ʻole (COL1A2). Kōkua kēia mau genes ʻelua i ka hana ʻana i ka protein (Collagen) i loko o ko mākou kino.
2. `(Dentinogenesis Imperfecta)` ʻAno 2 (ʻAno II): ʻOi aku ka maʻamau o kēia ʻano ma mua o nā niho paʻa.ʻO ka mea maʻamau ia ma nā niho pēpē. ʻO ka maʻamau, ʻaʻole nui nā maʻi hoʻoilina ʻē aʻe o kēia poʻe. Eia nō naʻe, ua ʻike ʻia i kekahi manawa aia kahi hiki ke loaʻa ka nalowale o ka lohe e pili ana i ka makahiki .
3. ʻAno 3 (ʻAno III): ʻO kēia ke ʻano kakaikahi loa . Hoʻopilikia ia i nā niho paʻa ma mua o nā niho pēpē. Ua hōʻike nā kānaka noiʻi i kēia ʻano ma waena o ka poʻe o ka hanauna Iudaio i kapa ʻia ʻo `(Ashkenazi Jewish)`, a ma kekahi mau ʻohana e noho ana ma ka hema o Maryland.
He aha nā hōʻailona o ka `(Dentinogenesis Imperfecta)`? Pehea e ʻike ai?
E like me kaʻu i ʻōlelo ai ma mua, ʻo nā hōʻailona nui ka hoʻololi ʻana o ke kala a me nā niho nāwaliwali a palupalu . ʻO ka maʻamau, he translucent nā niho, me ke kala melemele-ʻeleʻele a polū-hina paha .
Ma waho aʻe o kēlā, hiki ke ʻike ʻia nā hōʻailona ʻē aʻe e like me:
- ʻO ka nalowale lohi o nā niho pēpē: ʻO ka hāʻule ʻana o nā niho pēpē ma hope o ka manawa maʻamau.
- ʻEnamel Hypoplasia: ʻO ke ʻano kēia ua nalowale pono ka papa enamel ma luna o nā niho.
- ʻO ka Hypermobility Hui: Hiki i kekahi poʻe ke kulou i ko lākou mau hono, e like me ko lākou mau manamana lima a me nā kuʻekuʻe lima, i mua a i mua me ka nui.
- ʻO ke Agenesis niho: ʻO ke ʻano kēia o ka hānau ʻia ʻana me ka ʻole o nā niho.
- Enamel niho nāwaliwali: He nāwaliwali ka enamel a pau koke ia.
E noʻonoʻo, inā he ʻano ʻē ke kala o nā niho pēpē o kahi keiki, he polū ke kala, a haki maʻalahi paha, pono ʻoe e hopohopo no lākou.
No ke aha e hana ʻia ai kēia `(Dentinogenesis Imperfecta)`? He aha ke kumu?
ʻO ke kumu nui o kēia, he loli i loko o kā mākou mau genes. ʻO ka mea nui, ʻo ka loli i loko o ka gene i kapa ʻia ʻo `(DSPP) ` ke kumu o `(Dentinogenesis Imperfecta). Hāʻawi kēia gene `(DSPP)` i nā kuhikuhi e hana i `(Dentin)`, ka papa waena o ko mākou mau niho. No laila, i ka wā e loaʻa ai kahi pilikia me kēia gene, ʻaʻole i hana pono ʻia `(Dentin)`.
Hiki ke hoʻoilina ʻia kēia ʻano hoʻoilina mai nā mākua mai , a i ʻole hiki ke hana ma ke ʻano hūpō ʻole .
ʻO ka poʻe i loaʻa iā Dentinogenesis Imperfecta ʻano 1, e like me kaʻu i ʻōlelo ai ma mua, he mau mutations ko lākou i loko o nā genes COL1A1 a i ʻole COL1A2. ʻO ia nā mutations genetic like i ʻike ʻia i loko o ka poʻe me Osteogenesis Imperfecta (kahi maʻi e hoʻoulu ai i nā iwi palupalu).
Pehea e ʻike ai nā kauka i kēia?
Inā loaʻa iā ʻoe a i ʻole kāu keiki kekahi o kēia mau hōʻailona, pono ʻoe e ʻike mua i kahi kauka niho . E hana mua ʻo ia i kahi hoʻokolokolo kino a nīnau inā ua loaʻa i kekahi o kou ʻohana kekahi o kēia mau maʻi..
Eia kekahi, inā kānalua ʻoe he Dentinogenesis Imperfecta kou, hiki ke hana ʻia nā hoʻokolohua aʻe e hōʻoia i ke kūlana:
- Ke lawe ʻana i nā kiʻi X-ray niho.
- Malia paha hiki iā ʻoe ke hana i kahi CT scan .
Ma ka nānā ʻana i kēia mau kiʻi, hiki i ke kauka ke loaʻa kahi manaʻo maikaʻi o ke kūlana o loko o nā niho, ke ʻano o ka "Dentin".
I kekahi manawa, hiki i kāu kauka ke ʻōlelo aku i ka hoʻāʻo genetic e ʻike pono i nā loli i kāu DNA e kumu ai ka dentinogenesis imperfecta.
He aha nā lāʻau lapaʻau no kēia? (Lāʻau lapaʻau)
ʻO ke kumu nui o ka mālama ʻana no Dentinogenesis Imperfecta ʻo ia ka hoʻoikaika ʻana i nā niho nāwaliwali . Hoʻohana nā kauka niho i nā ʻano hana hoʻihoʻi like ʻole e hana i kēia.
ʻo kahi laʻana:
- Nā Hoʻopiha: E hoʻopiha i nā hakahaka a me nā māwae ma nā niho.
- Veneers: He mau pūpū lahilahi kēia i kau ʻia ma ke alo o ka niho. Hiki iā lākou ke hoʻomaikaʻi i ke ʻano o ka niho.
- Nā Lei Aliʻi: Ua like ka lei aliʻi me kahi pāpale i kau ʻia ma luna o ka niho. Uhi ia i ka niho holoʻokoʻa a hoʻoikaika iā ia.
Hoʻohana kēia mau lāʻau lapaʻau i nā mea kala niho, no laila hiki iā ʻoe ke mālama i kou minoʻaka nani.
Ke loaʻa iā ʻoe ʻo Dentinogenesis Imperfecta, ʻoi aku ka nui o ka nalowale ʻana o nā niho i kou wā ʻelemakule. Inā nalowale kou mau niho, hiki iā ʻoe ke hoʻololi iā lākou me nā implants niho a i ʻole nā dentures .
He aha ke ʻano o ka manaʻolana e hiki iā ʻoe ke loaʻa i kou wā e noho nei me kēia kūlana? (Outlook)
Pili kou manaʻo i kekahi mau kumu:
- Kou mau makahiki i ka wā i ʻike ʻia ai ʻoe ua loaʻa i ka maʻi.
- ʻEhia ka manawa i hoʻomaka ai ʻoe i ka lāʻau lapaʻau.
- He aha ke ʻano o ka Dentinogenesis Imperfecta āu e loaʻa nei?
ʻO ka mea nui, ʻaʻole hiki ke ho'ōla ʻia ʻo Dentinogenesis Imperfecta. Eia nō naʻe, me ka mālama pono ʻana i nā niho a me nā ʻano hoʻomaʻemaʻe waha maikaʻi, hiki iā ʻoe ke kōkua i ka pale ʻana i ka hōʻino hou ʻana i kou mau niho a mālama iā lākou i ikaika. ʻO ka wikiwiki o ka ʻike ʻia ʻana a me ka mālama ʻia ʻana o ke kūlana, ʻoi aku ka maikaʻi o ka hopena.
Hiki ke pale ʻia ka Dentinogenesis Imperfecta?
ʻO ka mea pōʻino, ʻaʻole hiki ke pale ʻia ʻo Dentinogenesis Imperfecta no ka mea ua hoʻokumu ʻia e nā loli genetic i hiki ʻole iā mākou ke kaohi. Eia nō naʻe, ʻo ka hoʻomaka ʻana i ka lāʻau i ka wā hikiwawe loa hiki ke hōʻemi i ka pōʻino lōʻihi i nā niho.
Pehea e mālama ai i koʻu mau niho? (Mālama ponoʻī)
Inā loaʻa iā ʻoe ka `(Dentinogenesis Imperfecta)`, he mea nui ka hoʻomaʻemaʻe waha maikaʻi.He mea nui ka mālama ʻana. No ka hōʻemi ʻana i ka pala a me ka hōʻino ʻana o nā niho, e hana i kēia mau mea:
- E nīnau i kāu kauka niho e pili ana i nā lāʻau lapaʻau fluoride e hoʻoikaika ai i kou mau niho.
- E palaki i kou mau niho ʻelua a ʻekolu paha manawa i ka lā me ka pulupulu niho palupalu a me ka toothpaste fluoride .
- E hoʻēmi i nā meaʻai kō a me nā meaʻawaʻawa.
- E holoi i kou waha me ka wai holoi waha fluoride i hoʻokahi manawa i ka lā.
- E kipa aku i ke kauka niho i nā manawa maʻamau no ka nānā ʻana a me ka hoʻomaʻemaʻe ʻana .
He aha ka mea maikaʻi e ʻai a inu ai ke loaʻa iā ʻoe ka `(Dentinogenesis Imperfecta)`?
ʻO ka mea maikaʻi loa e hana ai, ʻo ia ke koho ʻana i nā meaʻai a me nā mea inu haʻahaʻa i ke kō a me ka waikawa . ʻO ke ʻano kēia o ka hōʻemi ʻana i nā mea inu e like me ka soda, nā hua citrus e like me nā lime, a me nā mea ʻono tōmato i ka hiki. He manaʻo maikaʻi nō hoʻi e hōʻemi i nā meaʻai e pono ai ke nau ʻia a paʻakikī a ʻūlū paha .
Eia kekahi mau meaʻai maikaʻi e ʻai ʻia e kekahi me Dentinogenesis Imperfecta:
- Iʻa i hoʻomoʻa ʻia
- Nā ʻano o nā Casseroles
- Nā mea kanu i moʻa ʻia
- ʻOatmeal
- Pasta me ka mea ʻono i hana ʻia me ka kirīmi
- Hua manu i kāwili ʻia
- Nā Smoothies
He mau meaʻai maʻalahi kēia e ʻai a ʻaʻole hoʻi e hōʻino nui i kou mau niho.
Āhea wau e ʻike ai i ke kauka?
Inā ʻike ʻoe a i ʻole kāu keiki i kekahi mea ʻē a ʻokoʻa paha e pili ana i ko lākou mau niho, ʻoi aku ka maikaʻi o ka haʻi koke ʻana i kāu kauka . E hoʻomanaʻo, hiki ke ʻike ʻia nā hōʻailona o DGI i kēlā me kēia makahiki. Inā ʻike ʻia nā niho pēpē mua o kāu pēpē he uliuli, hina, a ʻeleʻele paha , e ʻike pono i kahi kauka niho pediatric no ka ʻōlelo aʻo.
He aha nā nīnau āu e nīnau ai i ke kauka?
Inā ua ʻike ʻia ʻoe me Dentinogenesis Imperfecta, makemake paha ʻoe e nīnau i kāu kauka i nā nīnau e like me:
- He aha ke ʻano o ka `(DGI)` aʻu?
- He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu?
- ʻEhia ka lōʻihi o nā lāʻau lapaʻau? Pehea ka lōʻihi o nā lāʻau lapaʻau?
- ʻEhia pinepine e pono ai iaʻu e hoʻomaʻemaʻe i koʻu mau niho?
- He aha nā hana pale e hiki iaʻu ke hana e hōʻemi ai i ka ʻino a me ka palaho o nā niho?
ʻO ka mea hope loa... (Leka Lawe-Home)
He mea hoʻonāukiuki maoli ka loaʻa ʻana o nā niho nāwaliwali a haki koke. He mea luhi loa hoʻi ka pono e makaʻala i kēlā me kēia manawa āu e ʻai ai. Ke loaʻa iā ʻoe ka `(Dentinogenesis Imperfecta)`, hilahila paha ʻoe i ke ʻano o kou mau niho. Ma muli o kēia, ʻaʻole paha ʻoe makemake e kū i ke kaiāulu.
Akā, e hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi.Aia nā kauka e hiki ke kōkua iā ʻoe. Hiki iā lākou ke ʻōlelo i nā lāʻau lapaʻau e hoʻoikaika i kou mau niho, hoʻomaikaʻi i kou minoʻaka, a hoʻonui i kou hilinaʻi iā ʻoe iho. No laila, mai hopohopo i kekahi mea, a e hahai i ka ʻōlelo aʻo a kāu kauka.
Ma ka ʻike ʻana i ka maʻi i ka wā mua, ka loaʻa ʻana o ka lāʻau lapaʻau kūpono, a me ka hahai ʻana i nā hana hoʻomaʻemaʻe waha maikaʻi, hiki iā ʻoe ke ola i kahi ola olakino a hauʻoli hoʻi me ke kūlana `(Dentinogenesis Imperfecta).'
` dentinogenesis imperfecta, nā maʻi niho, nā niho nāwaliwali, ka hoʻololi ʻana o ke kala o nā niho, nā maʻi hoʻoilina, ke olakino niho, nā niho pēpē
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