Ke manaʻo pinepine nei ʻoe ua piha ʻoe ma hope o ka ʻai ʻana, ʻeha ka ʻōpū, a he ʻōpala ʻala ʻaila paha? Hiki paha iā ʻoe ke emi ke kaumaha me ke kumu ʻole. ʻAʻole kēia he mau hōʻailona e hoʻowahāwahā ʻia. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi maʻi i kapa ʻia ʻo Exocrine Pancreatic Insufficiency, a i ʻole EPI no ka pōkole, hiki ke hana i kēia mau hōʻailona.
I ka ʻōlelo maʻalahi, he aha ka EPI?
ʻAe, e ʻōlelo kākou penei. Loaʻa iā kākou kahi ʻōkana i kapa ʻia ʻo ka pancreas i loko o ko kākou ʻōpū. ʻO kāna hana nui ka hana ʻana i nā enzymes , kahi ʻano kemika kūikawā e kōkua iā kākou e hoʻoheheʻe i ka meaʻai a kākou e ʻai ai. Hele kēia mau enzymes i loko o ko kākou ʻōpū liʻiliʻi a wāwahi i ka meaʻai a kākou e ʻai ai, ʻoiai nā aila a me nā momona, i hiki i ko kākou kino ke omo iā lākou.
I kēia manawa, ʻo ka mea e hana ʻia i kahi kanaka me EPI, ʻaʻole lawa ka hana ʻana o ka pancreas i nā enzymes. He aha ka mea e hana ʻia a laila? ʻAʻole i hoʻoheheʻe pono ʻia ka meaʻai. ʻAʻole omo ke kino i nā meaola e pono ai, ʻoiai ka momona a me nā huaora momona-soluble (e like me nā huaora A, D, E, a me K). Hoʻopilikia kēia i nā pilikia e like me ka ʻōpū ʻeha a me ka pohō kaumaha.
Akā, mai hopohopo. Aia nā lāʻau lapaʻau maikaʻi loa no kēia i kēia manawa. Inā loaʻa iā ʻoe ka lāʻau lapaʻau kūpono, hiki iā ʻoe ke ola hou i kahi ola maʻamau.
He aha nā kumu o ka EPI?
ʻO ke kumu nui o EPI kekahi ʻano hōʻino i ka pancreas. Hiki i kēia ke loaʻa i kekahi mau kumu.
- ʻO ka pancreatitis pinepine: Ua kapa ʻia kēia e nā kauka he pancreatitis mau loa . ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka hoʻomaka ʻana o nā enzymes i hana ʻia i loko o ka pancreas e hana i loko o ka pancreas ma mua o ko lākou hiki ʻana i ka ʻōpū liʻiliʻi. Hōʻino kēia i ka pancreas ponoʻī. ʻOi aku ka kiʻekiʻe o kēia pilikia i ka poʻe e inu nui ana i ka waiʻona. Eia kekahi, hiki i nā mea e like me ke kiʻekiʻe o ka momona koko (Triglycerides) a me nā ʻōnaehana pale nāwaliwali ke hoʻopilikia i kēia.
- ʻOki kino: Hiki ke hana ʻia kēia ʻano ma ke ʻoki ʻana ma ka pancreas, ka ʻōpū, a i ʻole nā naʻau.
- Nā maʻi hānau: Hiki i kekahi mau maʻi hoʻoilina ke hana i ka EPI.
- ʻO Cystic Fibrosis: Hoʻopuka ka poʻe me kēia maʻi i ka mucus mānoanoa a pipili i loko o ko lākou kino. Hoʻopili kēia mucus i nā ducts pancreatic, e pale ana i nā enzymes mai ka puka ʻana i waho.
- ʻO Shwachman-Diamond Syndrome: He maʻi hoʻoilina nō hoʻi kēia. I kēia kūlana, nalowale nā pūnaewele e hana ana i nā enzymes i loko o ka pancreas.
- Nā maʻi ʻē aʻe: Loaʻa i kekahi poʻe ka pilikia o ka hoʻomohala ʻana i ka EPI ma muli o nā maʻi ʻē aʻe o ka ʻōnaehana hoʻoheheʻe, e like me ka maʻi a Crohn a me ka maʻi Celiac.
Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe ka EPI? He aha nā hōʻailona?
I nā pae mua, ʻaʻohe paha he mau hōʻailona, akā i ka wā i hōʻino ʻia ai ka pancreas a emi iho kona hiki ke omo i ka momona, hoʻomaka mālie nā hōʻailona e ʻike ʻia.
ʻO ka mea nui loa, ʻo ia ke ʻimi i ke kōkua lapaʻau i ka wā e ʻike ai ʻoe i kēia mau hōʻailona, ma mua o ka noʻonoʻo ʻana, "He ʻeha ʻōpū wale nō ia."
Aia ma ka papa ma lalo nei nā hōʻailona maʻamau.
| ʻAno o ka hōʻailona | Wehewehena |
|---|---|
| Nā hōʻailona o ka ʻōnaehana hoʻoheheʻe |
|
| Nā hōʻailona i hoʻokumu ʻia e ka nele o nā huaora |
Pehea e ʻike pono ai ke kauka i kēia maʻi?
Ke hele ʻoe e ʻike i ke kauka, e nīnau ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona a laila e kauoha ʻo ia i kekahi mau hoʻokolohua e hōʻoia i ka maʻi.
Nā nīnau e nīnau aku ai i ke kauka
- He ʻeha kou ma kou ʻōpū luna?
- He ʻala ʻino anei ka ʻōpala a he ʻano ʻaila paha? He paʻakikī anei ke holoi aku?
- Loaʻa iā ʻoe ka maʻi pākī a i ʻole ka pehu?
- Ua emi anei kou kaumaha i kēia mau lā iho nei?
Nā hoʻokolohua e ʻōlelo ʻia paha
Aia nā ʻano hoʻāʻo like ʻole no kēia.
| ʻAno hoʻāʻo | He aha ka ho'āʻo ʻana o kēia? |
|---|---|
| Nā hoʻāʻo koko | Nānā ia i nā pae huaora o ke kino a inā paha e hana ana ka pancreas i nā enzymes. Hiki iā ia ke nānā i nā kumu ʻē aʻe, e like me ka maʻi celiac. |
| Nā Hoʻāʻo Noho | ʻO kahi hoʻāʻo fecal 3 lā e ana i ka nui o ka momona i loko o ka ʻōpala. Nānā pū kahi hoʻāʻo fecal elastase-1 no nā pae o kahi enzyme koʻikoʻi i hana ʻia e ka pancreas. |
| Nā Hoʻāʻo Kiʻi | Kōkua kēia i ka ʻike inā ua pehu ka pancreas.
|
He aha nā lāʻau lapaʻau?
ʻO ka lāʻau lapaʻau nui a maikaʻi loa no EPI ʻo ia ka Pancreatic Enzyme Replacement Therapy (PERT) . I ka pōkole, ʻo ia ka lawe ʻana i nā lāʻau e pani i nā enzymes a kāu pancreas e hana ʻole nei.
- Pehea e lawe ai i nā papa PERT: Pono e lawe ʻia kēia mau papa i ka wā ʻai . Inā lawe ʻia ma mua o ka ʻai ʻana, e haʻalele nā enzymes i ka ʻōpū ma mua o ka hiki ʻana o ka meaʻai. Inā lawe ʻia ma hope o ka ʻai ʻana, e hōʻea lohi nā enzymes ma hope o ka hoʻomaka ʻana o ka meaʻai e ʻeli. No laila, pono e lawe ʻia kēia mau papa me nā meaʻai nui a me nā meaʻai māmā .
- Nā lāʻau lapaʻau e hōʻemi ai i ka waikawa ʻōpū: I kekahi manawa, hiki i ka waikawa ʻōpū kiʻekiʻe ke hoʻopau i kēia mau pila enzyme ma mua o ko lākou hana ʻana. No ka hoʻōki ʻana i kēia, hiki i kāu kauka ke kuhikuhi i kahi lāʻau lapaʻau e like me 'Proton pump inhibitors' (e.g. omeprazole) a i ʻole 'H2 blockers' (e.g. famotidine).
- Nā lāʻau hoʻopau ʻeha:Inā he ʻeha, hiki iā ʻoe ke lawe i kahi lāʻau hoʻopau ʻeha maʻamau e like me Paracetamol ma ke ʻōlelo aʻo a kāu kauka. Inā koʻikoʻi ka ʻeha, hiki ke kuhikuhi ʻia nā lāʻau ikaika. Eia nō naʻe, hiki i kēlā mau lāʻau ke hoʻopili, no laila pono e hoʻohana ʻia me ke akahele loa a ma lalo o ke aʻo ʻana a ke kauka.
Eia kekahi, he mea nui loa hoʻi e mālama i ka maʻi kumu (e like me ka Chronic Pancreatitis, Cystic Fibrosis) i hoʻoulu ai i ke kūlana EPI.
Pehea ʻoe e mālama ai iā ʻoe iho?
Me ka lāʻau lapaʻau, he mea nui loa kou nohona a me kāu mau ʻano ʻai i ka kaohi ʻana i kēia maʻi.
- E ʻai i kekahi mau meaʻai liʻiliʻi: Ma kahi o ka ʻai ʻana i ʻekolu mau meaʻai nui i ka lā, e ʻai i nā meaʻai liʻiliʻi ma kahi o ʻeono manawa i ka lā. E maʻalahi kēia i ka ʻeli ʻana.
- E pale i ka waiʻona a me ka puhipaka: Hoʻoikaika ka waiʻona i ke kino e omo i ka momona a hōʻino pū i ka pancreas. He mea ʻino nō hoʻi ka puhipaka i ka pancreas.
- E lawe i nā wikamina: ʻOiai ʻaʻole hiki i ke kino ke omo pono iā lākou, pono ʻoe e lawe i nā wikamina e like me nā wikamina A, D, E, a me K ma waho. No kēia, e kuhikuhi kāu kauka i nā wikamina a me nā ana kūpono.
- E ʻimi i ka ʻōlelo aʻo mai kahi meaʻai meaʻai: He mea nui loa ia e ʻimi i ka ʻōlelo aʻo mai kahi meaʻai meaʻai e hoʻomākaukau ai i kahi meaʻai momona e kūpono iā ʻoe.
ʻAʻole he maʻi ka EPI e hopohopo ai. Me ka mālama kūpono a me ke ʻano o ka nohona, hiki iā ʻoe ke kāohi iā ia a ola i kahi ola maʻamau. ʻO ka mea nui loa, ʻo ia ke kamaʻilio mau me kāu kauka a hahai pololei i kāna mau kuhikuhi.
Leka Lawe-Home
- ʻO ka EPI kahi maʻi ʻōnaehana hoʻoheheʻe e hana ʻia ke hana ʻole ka pancreas i nā enzymes lawa.
- ʻO ka ʻeha o ka ʻōpū, ka ʻōpala ʻaila, ka maʻi kahe, a me ka pohō kaumaha nā hōʻailona nui. Mai hoʻowahāwahā i kēia mau mea.
- Hiki ke ʻike pololei ʻia ka maʻi ma o ke koko, ka ʻōpala, a me nā hoʻokolohua scan.
- Hiki ke mālama pono ʻia kēia maʻi me nā pila enzyme i kapa ʻia ʻo PERT.
- He mea nui loa e pale loa i ka waiʻona a me ka puhipaka a e ʻai i ka meaʻai kaulike.
- Inā kū mai kekahi mau pilikia, e kamaʻilio me kāu kauka ma kahi o ka hoʻoholo ʻana i kāu iho.











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