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Ua loli anei kou puʻuwai e like me kēia? E kamaʻilio kākou e pili ana i ka Hypertrophic Cardiomyopathy (HCM)!

Ua loli anei kou puʻuwai e like me kēia? E kamaʻilio kākou e pili ana i ka Hypertrophic Cardiomyopathy (HCM)!

Ua lohe paha ʻoe i kahi maʻi puʻuwai kahi e mānoanoa ai ka ʻiʻo puʻuwai, he mea paʻakikī iki? I kekahi manawa, ʻaʻole paha ʻoe e ʻike he loaʻa iā ʻoe, no ka mea, ʻaʻohe hōʻailona o kekahi poʻe. Akā, he mea nui e makaʻala i ia mea no ka mea e hoʻopilikia ia i ka puʻuwai. I kēia lā, e kamaʻilio mākou e pili ana i kēia maʻi i kapa ʻia ʻo hypertrophic cardiomyopathy, a i ʻole `HCM' i waena o nā kauka. Mai hopohopo, e kamaʻilio maʻalahi mākou e pili ana i ia mea, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.

E nānā mua kākou i ke ʻano o HCM?

I ka ʻōlelo maʻalahi, ʻo ka hypertrophic cardiomyopathy (HCM) kahi maʻi paʻakikī e hoʻopilikia i nā ʻiʻo o kou puʻuwai. Hiki ke hana ʻia e kekahi mau mea nui:

  • Ka mānoanoa o ka ʻiʻo puʻuwai: ʻO nā keʻena haʻahaʻa o ka puʻuwai, a mākou e kapa nei he ventricles, he mau paia mānoanoa.
  • ʻOʻoleʻa o ka ventricle hema: ʻOʻoleʻa ke keʻena nui ma ka ʻaoʻao hema o ka puʻuwai (ventricle hema), e lilo ana i mea elastic, e like me ka laholio.
  • Nā loli o ka valve mitral: Hiki ke hana i nā loli i ka hana o ka valve mitral, kahi valve koʻikoʻi i loko o ka puʻuwai.
  • Nā loli kelepona: Loaʻa kekahi mau ʻano ʻē i loko o nā pūnaewele ʻiʻo puʻuwai (nā loli kelepona).

Hiki i kēia mau mea ke hoʻopilikia i ka hana o ka puʻuwai.

Pehea ka hopena o kēia maʻi HCM i kou kino?

ʻĀ, e nānā kākou i ka mea a kēia mau hoʻololi e hana ai i ke kino.

Ka mānoanoa o ka myocardium

ʻO kēia ka hōʻailona nui i ʻike ʻia ma HCM. ʻO ka hapa pinepine, ʻike ʻia kēia mānoanoa ma ka paia e hoʻokaʻawale ana i nā ʻaoʻao hema a me ka ʻākau o ka puʻuwai, i kapa ʻia ʻo `(septum).` E noʻonoʻo, i ka wā e mānoanoa ai kēia septum ma waena o nā keʻena haʻahaʻa o ka puʻuwai `(ventricles)`, hiki iā ia ke ālai i ke ala e holo ai ke koko mai ka ventricle hema a i ka aorta, ke kīʻaha koko nui e lawe ana i ke koko ma ke kino holoʻokoʻa. Kāhea mākou i kēia `(outflow tract obstruction)`. A laila pono ka puʻuwai e hana ikaika e pamu i ke koko ma mua o kēia ālai. ʻO ke ʻano o HCM e ālai ana i ke ala e holo ai ke koko ua kapa ʻia ʻo `(Hypertrophic Obstructive Cardiomyopathy - HOCM)`.

I kekahi manawa, hiki ke mānoanoa nā ʻāpana ʻē aʻe o ka puʻuwai, e like me ka apex, ka ventricle ʻākau, a i ʻole ka ventricle hema holoʻokoʻa. I kēia mau hihia, ʻaʻole i ālai ʻia ke kahe o ke koko. Eia nō naʻe, ua hoʻemi ʻia ka nui o ke koko e hiki i ka ventricle ke lawelawe. Ua kapa ʻia kēia ʻo Hypertrophic Nonobstructive Cardiomyopathy.

ʻOʻoleʻa o ka Ventricular Hema

Ke mānoanoa ka ʻiʻo o ka puʻuwai, ʻo nā loli i loko o kēlā mau cell e hoʻomaha pono ʻole ai ka ventricle hema a piha i ke koko. He aha ka mea e hana ʻia? No ka mea, ʻaʻole i nui ke koko i loko o ke keʻena, ʻaʻole i nui ke koko momona oxygen i hoʻouna ʻia i nā ʻāpana ʻē aʻe a me nā ʻiʻo o ke kino. Hoʻonui pū kēia paʻakikī i ke kaomi i loko o ka puʻuwai, a hiki iā ʻoe ke ʻike i nā hōʻailona e like me:

  • ʻEha umauma
  • Pōkole o ka hanu
  • Pōʻino a i ʻole ka nawaliwali
  • Manaʻo e like me ka wikiwiki o kou puʻuwai (palpitations)

Nā Hoʻololi o ka Valve Mitral

E like me ka mea i ʻōlelo ʻia ma mua, i ka wā e ālai ʻia ai ke ala kahe o ka ventricle hema, ʻaʻole paha e hana pono ka valve mitral i loko o ka puʻuwai. Hiki i kēia ke ālai i ke kahe o ke koko a hoʻonui i ke kaomi i loko o ka ventricle hema.

ʻO ke kumu o kēia pani ʻana, ʻo ia ka paʻi ʻana o ka valve mitral i ka septum mānoanoa. Ke hana ʻia kēia, ʻaʻole e pani pono ka valve mitral a hiki i ke koko ke hoʻi hou i loko o ka atrium hema.

Nā Hoʻololi Kelepona

Inā ʻoe e nānā pono ma lalo o kahi microscope, ʻaʻole i hoʻonohonoho pono ʻia nā ʻiʻo puʻuwai o ke kanaka me HCM ma kahi laina pololei, akā ma kahi ʻano haunaele iki. Hiki i kēia maʻi ke hoʻololi i nā hōʻailona uila e hele ana ma nā keʻena haʻahaʻa o ka puʻuwai, e hana ana i kahi ʻano puʻuwai ʻē i kapa ʻia ʻo ventricular arrhythmia. Hiki i kēia ke lilo i mea weliweli.

Pehea ka maʻamau o kēia kūlana i kapa ʻia ʻo HCM?

Ua manaʻo ʻia he 1.5 miliona mau kānaka ma ʻAmelika Hui Pū ʻIa wale nō, a i ʻole hoʻokahi i loko o 500 mau kānaka, i loaʻa iā HCM. ʻOi aku ka maʻamau o kēia ma mua o kahi maʻi e like me "(Multiple Sclerosis)". No laila, ʻaʻole ia he mea laha ʻole.

I ka makahiki hea e ulu pinepine ai ʻo HCM?

ʻO ka hapa nui o ka manawa, ʻike ʻia kēia maʻi puʻuwai i nā poʻe ʻōpio, ma kahi o ka makahiki he ʻumikumamāwalu a iwakālua paha. Eia nō naʻe, hiki ke hoʻomaka i kēlā me kēia makahiki.

Inā loaʻa iaʻu ʻo HCM, aia kekahi pilikia o ka hāpai ʻana?

Pono paha ʻoe i ka mālama olakino kūikawā, e like me ka echocardiography maʻamau. Eia nō naʻe, ʻoi aku ka nui o kou hāpai ʻana i kahi hāpai olakino a me ka hānau maʻamau. Eia nō naʻe, he mea nui e kūkākūkā i kēia me kāu kauka ma mua o kou hāpai ʻana a kūkākūkā i nā pilikia. E haʻi pū kāu kauka iā ʻoe i nā lāʻau lapaʻau no HCM hiki iā ʻoe ke hoʻomau i ka lawe ʻana i ka wā hāpai. Pono paha ʻoe e loaʻa kahi pacemaker a i ʻole implantable cardioverter defibrillator (ICD) i hoʻokomo ʻia inā pono i ka wā hāpai.

He aha ke kumu o ka HCM?

Aia kekahi mau kumu e hiki ai ke hana i ka HCM:

  • ʻO ka Genetics: ʻO kēia ke kumu nui. He maʻi ka HCM i hiki ke hoʻoili ʻia mai nā mākua a i nā keiki. ʻO ke ʻano kēia he kīnā i loko o nā genes e kāohi ana i nā ʻano o ka ʻiʻo puʻuwai. Aia kekahi mau ʻano genes e hoʻoulu ai i ka HCM. ʻOiai inā he kīnā genetic, ʻaʻole e loaʻa i nā kānaka a pau o ka ʻohana ka maʻi ma ke ʻano like. Loaʻa paha i kekahi poʻe ka gene HCM akā ʻaʻole loa e loaʻa ka maʻi.
  • Ke koko kiʻekiʻe: ʻO ke koko kiʻekiʻe i loaʻa no ka manawa lōʻihi hiki ke lilo i kumu o kēia.
  • Ka ʻelemakule: Aia kahi hiki ke hana ʻia kēia ʻano i kou wā ʻelemakule.
  • Nā hihia i ʻike ʻole ʻia ke kumu:I kekahi manawa, ʻaʻohe kumu kūpono e loaʻa ai no HCM.

He aha nā hōʻailona e hiki i kekahi me HCM ke ʻike?

Hiki i kekahi poʻe me HCM ke ʻike i nā ʻano hōʻailona like ʻole, aʻo kekahi poʻe ʻaʻohe hōʻailona iki. ʻO nā hōʻailona maʻamau:

  • ʻEha umauma: Hana pinepine kēia i ka wā e hoʻoikaika kino ai, akā hiki ke hana i kekahi manawa i ke kū wale ʻana a ma hope paha o ka ʻai ʻana.
  • Ka pōkole o ka hanu a me ka luhi: ʻO kēia mau hōʻailona, ​​ʻoiai ke luhi ʻoe, he mea maʻamau ia i nā pākeke. ʻO kēia ma muli o ka hoʻonui ʻia o ke kaomi ma ka atrium hema a me nā māmā.
  • Nāwaliwali a i ʻole ka nawaliwali (syncope): Hiki ke hana ʻia kēia e nā ʻano puʻuwai ʻē (arrhythmias) a i ʻole nā ​​pane ʻē o nā kīʻaha koko i ka wā o ka hoʻoikaika kino. I kekahi manawa, ʻaʻole hiki ke loaʻa ke kumu.
  • Palpitations: Hiki ke hana ʻia kēia e kahi ʻano puʻuwai ʻē, e like me ka atrial fibrillation (atrial flutter) a i ʻole ka ventricular tachycardia (ventricular tachycardia). Ma kahi o 25% o ka poʻe me HCM he atrial fibrillation. Hoʻonui kēia i ka pilikia o nā ʻōpū koko a me ka hāʻule ʻana o ka puʻuwai.
  • Ka pehu ʻana o nā aa koko ma ke kino haʻahaʻa a i ʻole ka ʻāʻī.

He aha nā pilikia olakino ʻē aʻe e pili pū ana me HCM?

He nui ka poʻe me HCM e ola maʻamau a ʻaʻohe pilikia olakino nui. ʻAʻole pono kekahi e lawe i ka lāʻau lapaʻau. Eia nō naʻe, inā ʻaʻohe ou hōʻailona, ​​​​hiki i kāu kauka ke aʻo iā ʻoe ʻaʻole e hana i ka hoʻoikaika kino.

Eia nō naʻe, hiki i kekahi poʻe me HCM ke loaʻa i nā maʻi puʻuwai e hoʻopōkole ai i ko lākou ola a i ʻole e hōʻemi i ko lākou ʻano ola. ʻO nā mea nui:

Ka Paʻa koke ʻana o ka Puʻuwai a me ka Make koke ʻana o ka Puʻuwai

ʻO ka hopu koke ʻana o ka puʻuwai ka nalowale koke ʻana o ka hana o ka puʻuwai ma muli o ka wikiwiki o ka puʻuwai (e.g., Ventricular Tachycardia). I kēia hihia, pono ka mālama ʻana i ka pilikia, e like me ka CPR a me ka defibrillation, i ka wā e hoʻomaka ai nā hōʻailona. Inā ʻaʻole hāʻawi pono ʻia kēia lāʻau, hiki ke make koke ka puʻuwai.

ʻO ka hapa nui o ka poʻe me HCM he haʻahaʻa ka pilikia o ka make koke ʻana o ka puʻuwai. Eia nō naʻe, ʻo HCM ke kumu nui o ka make koke ʻana o ka puʻuwai i ka poʻe ma lalo o 35 mau makahiki. Ua lohe paha ʻoe ua pili pū ʻia ʻo HCM i ka make koke ʻana o kekahi mau mea pāʻani ʻōpio.

Ka hāʻule ʻana o ka puʻuwai

ʻOiai ua loaʻa iā ʻoe ka `(Heart Failure)`, ʻaʻole ia he manaʻo ua "hāʻule" kou puʻuwai a ua oki ka hana. ʻO ia hoʻi, ʻaʻole e hoʻopuehu pono ana kou puʻuwai i ke koko. ʻO nā hōʻailona o ka `(Heart Failure)` penei:

  • Pōkole o ka hanu.
  • Manaʻo luhi i ka wā e hana ai (luhi).
  • Ka pehu ʻana o nā kuʻekuʻe wāwae, nā wāwae, a me ka ʻōpū.
  • Pono e mimi i ka pō i ka wā e hoʻomaha ana.
  • Pōniuniu, huikau, paʻakikī i ka noʻonoʻo ʻana, maule.
  • Ke manaʻo nei e kuʻi wikiwiki ana kou puʻuwai (palpitations).
  • ʻO ka ʻū maloʻo a ʻeha loa.
  • Manaʻo piha, pehu, nalowale ka makemake e ʻai, a ʻeha paha ka ʻōpū.

Pehea e ʻike ai i ka HCM? (Diagnosis)

Ua ʻike ʻia ʻo HCM ma muli o kēia mau mea:

  • Mōʻaukala lapaʻau: E nīnau aku kāu kauka iā ʻoe e pili ana i kāu mau hōʻailona a inā paha ua loaʻa i kekahi o kou ʻohana nā maʻi like.
  • Hoʻokolohua kino: E hoʻolohe ke kauka i kou puʻuwai a me kou mau māmā. Hiki i ka poʻe me HOCM ke lohe i kahi kani puʻuwai ʻē (heart murmur).
  • Nā hoʻāʻo: ʻO ka echocardiogram (echo) ka hoʻāʻo nui i hoʻohana ʻia no ka ʻike ʻana i ka HCM. Hiki i kēia ke kōkua i ka ʻike ʻana inā ua mānoanoa nā paia o ka puʻuwai.

Aia kekahi mau hoʻokolohua ʻē aʻe:

  • Nā hoʻāʻo koko.
  • ʻElectrocardiogram (ECG).
  • X-ray umauma.
  • Hoʻāʻo leo koʻikoʻi o ka hoʻoikaika kino.
  • Ka hoʻokomo ʻana o ke catheter puʻuwai.
  • Kiʻi hoʻohālikelike magnetic (MRI).

He aha nā lāʻau lapaʻau no HCM?

E hoʻoholo kāu kauka i ka lāʻau lapaʻau kūpono iā ʻoe ma muli o nā kumu aʻe:

  • Aia kekahi mea e ālai ana i ke ala e puka ai ke koko mai ka puʻuwai aku (e emi ana ke ala e kahe ai ke koko)?
  • Pehea e hana ai kou puʻuwai?
  • Kou mau hōʻailona.
  • Kou mau makahiki a me kou ʻano hana ikaika.
  • Loaʻa iā ʻoe nā ʻano puʻuwai ʻē aʻe (arrhythmias)?

ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka hōʻemi a pale ʻana paha i nā hōʻailona a me ka hoʻemi ʻana i ka pilikia o nā pilikia e like me ka hāʻule ʻana o ka puʻuwai a me ka make koke ʻana o ka puʻuwai.

Hiki ke hana i kēia mau mea ma ke ʻano he lāʻau lapaʻau:

  • E ʻike i nā pilikia a hoʻomau i ke kipa ʻana i ke kauka.
  • Nā loli o ke ʻano o ka nohona.
  • Nā lāʻau lapaʻau.
  • Nā kaʻina hana lapaʻau kūikawā.

Pehea e hoʻoholo ai i ka HCM?

ʻOiai ʻo HCM kahi maʻi e hiki ke hoʻoili ʻia mai kēlā hanauna a kēia hanauna, inā loaʻa i kekahi o kou mau mākua, nā kaikaina, a i ʻole nā ​​​​keiki (ʻo ia hoʻi, he hoahānau mua) ka maʻi, he mea nui e hoʻāʻo ʻia.

ʻO ka hana mua, ʻo ia ke nānā ʻia kou puʻuwai e kahi Electrocardiogram (ECG) a me kahi Echocardiogram (echo). Inā hōʻike kēia mau hoʻokolohua i nā hōʻailona o HCM, pono ʻoe e ʻike i ke kauka loea i kēia maʻi (cardiologist).

I kekahi manawa, ʻoiai inā he moʻolelo ʻohana kou o HCM, maʻamau paha kāu mau hopena hoʻāʻo. Inā pēlā, ʻōlelo nā kauka e hana ʻoe i kahi echo a me ECG i kēlā me kēia ʻekolu makahiki a hiki i kou 30, a laila i kēlā me kēia ʻelima makahiki.

ʻO wai ka mea i ʻoi aku ka nui o ka make ʻana o ka puʻuwai ma muli o HCM?

ʻO ka hapa nui o ka poʻe me HCM he haʻahaʻa ka pilikia o ka make koke ʻana o ka puʻuwai. Eia nō naʻe, he nui ka poʻe me HCM i loaʻa ka pilikia nui. He mea nui e ʻike inā loaʻa iā ʻoe kēia ʻano. Hiki i kāu kauka ke haʻi iā ʻoe i ka mea hiki iā ʻoe ke hana e hōʻemi i kou pilikia.

ʻO ka poʻe i ʻoi aku ka nui o ka make ʻana o ka puʻuwai ma muli o HCM:

  • ʻO nā kānaka me ka mōʻaukala ʻohana o ka make koke ʻana o ka puʻuwai.
  • ʻO ka poʻe i loaʻa ka syncope i nā manawa he nui i ko lākou wā ʻōpiopio.
  • ʻO nā kānaka i loaʻa ka pane koko kūpono ʻole i ka hoʻoikaika kino.
  • ʻO nā kānaka me ka mōʻaukala mua o nā puʻuwai wikiwiki loa (arrhythmia).
  • ʻO ka poʻe me nā hōʻailona koʻikoʻi a me ka hana puʻuwai maikaʻi ʻole.

E kamaʻilio me kāu kauka e pili ana i kou pilikia pilikino. Inā he ʻelua a ʻoi aku paha mau kumu pilikia no ka make koke ʻana, hiki i kāu kauka ke ʻōlelo aku i nā lāʻau antiarrhythmic (nā lāʻau lapaʻau e kaohi ana i nā ʻano puʻuwai maʻamau ʻole) a i ʻole kahi implantable cardioverter defibrillator (ICD) e hōʻemi i kou pilikia.

He aha nā lāʻau lapaʻau i hoʻohana ʻia e mālama i ka HCM?

Hoʻomaopopo nā kauka i nā lāʻau lapaʻau like ʻole e kāohi i kāu mau hōʻailona a pale i nā pilikia hou aʻe. ʻO nā lāʻau lapaʻau e like me nā "Beta blockers" a me nā "calcium channel blockers" e hoʻomaha i ka ʻiʻo o ka puʻuwai, e kōkua ana iā ia e hoʻopiha me ke koko a hoʻomaʻamaʻa i ke koko me ka ʻoi aku ka maikaʻi. Hiki i nā lāʻau lapaʻau ʻē aʻe ke kāohi i kou helu puʻuwai a hōʻemi paha i ka pilikia o nā ʻano puʻuwai maʻamau ʻole (arrhythmias).

Hiki ke ʻōlelo ʻia iā ʻoe ʻaʻole e lawe i kekahi mau lāʻau lapaʻau, no ka laʻana nitrates (nāna e hoʻohaʻahaʻa i ke koko) a i ʻole digoxin (ka mea e hoʻonui ai i ka ikaika o ka puʻuwai).

I kekahi manawa pono ʻoe e lawe i nā lāʻau antibiotic a lawe i nā hana ʻē aʻe e hōʻemi i ka pilikia o kahi maʻi hoʻoweliweli ola i kapa ʻia ʻo bacterial endocarditis.

He aha nā kaʻina hana lapaʻau kūikawā i hoʻohana ʻia e mālama ai iā HCM?

Aia kekahi mau ʻano hana e mālama ai i ka Hypertrophic Obstructive Cardiomyopathy (HOCM), kahi kūlana e hoʻopilikia ai i ke kahe koko:

ʻO ka myectomy Septal

He hana ʻoki kino kēia. I loko o ka myectomy septal, wehe ke kauka ʻoki kino i kahi ʻāpana liʻiliʻi o kou paia septal mānoanoa. Hoʻonui kēia i ke ala kahe mai ka ventricle hema a i ka aorta. Manaʻo wale nā ​​​​kauka i kēia ʻoki kino inā ʻaʻole kōkua ka lāʻau lapaʻau. Hoʻoponopono pinepine kēia i ka pilikia o ka valve mitral.

ʻO ka hoʻopau ʻana i ka ʻEthanol

Ua kapa ʻia hoʻi kēia he `(septal ablation)`. Hoʻohana ʻia kēia ʻano hana no ka poʻe hiki ʻole ke hana i ke ʻoki ʻana `(septal myectomy)` i ʻōlelo ʻia ma mua. Ma kēia, loaʻa i ke kauka kahi aʻa coronary liʻiliʻi e hoʻolako ana i ke koko i ka ʻaoʻao o luna o kou septum. A laila hoʻokomo ʻo ia i kahi catheter balloon i loko o kēlā aʻa a hoʻopiha iā ia. A laila, hoʻokomo ʻo ia i kahi `(contrast agent)` dye e ʻike i kahi kikoʻī o ka paia septal mānoanoa e ālai ana i ke kahe koko.

Ke loaʻa ka wahi, hoʻokomo ke kauka i kahi liʻiliʻi o ka waiʻona maʻemaʻe ma o ke catheter. Pepehi ka waiʻona i nā ʻāpana, a i nā mahina e hiki mai ana e emi hou ka septum i kona nui maʻamau. Hoʻonui kēia i ke ala no ke kahe ʻana o ke koko.

ʻO ka Implantable Cardioverter Defibrillator (ICD)

Hiki i kahi implantable cardioverter defibrillator (ICD) ke kōkua i nā poʻe me nā arrhythmias e hoʻoweliweli ana i ke ola a i ʻole ka make koke ʻana o ka puʻuwai. He mea liʻiliʻi ka ICD i hoʻokomo ʻia ma lalo o kou ʻili. Hoʻopili ʻia ia i kou puʻuwai e nā uwea. Ke nānā mau nei ka ICD i kou mele puʻuwai. Ke ʻike ʻo ia i kahi puʻuwai wikiwiki loa a ʻano ʻē, hāʻawi ia i kahi haʻalulu uila liʻiliʻi akā ikaika i ka puʻuwai, e hoʻoulu ai iā ia e kuʻi maʻamau hou. E haʻi aku kāu kauka iā ʻoe inā kūpono kahi ICD iā ʻoe.

Ka Hoʻokele ʻana i ka Pōʻino o ka Puʻuwai

Aia kekahi mau ala e mālama ai i ka hāʻule ʻana o ka puʻuwai, mai nā loli o ke ʻano o ka nohona a hiki i nā lāʻau lapaʻau e hōʻemi ana i nā hōʻailona a kōkua i ka hana pono ʻana o ka ʻiʻo o ka puʻuwai.

Pehea e hiki ai iaʻu ke hoʻomaikaʻi i koʻu ola maikaʻi me HCM?

Inā he mau hōʻailona kou a ʻaʻole paha, inā ua ʻike ʻia ʻoe me HCM, a inā loaʻa i kekahi o kou ʻohana, aia kekahi mau mea hiki iā ʻoe ke hana e mālama i ke olakino o kou puʻuwai i kona maikaʻi loa:

  • E kaupalena i nā wai a me ka paʻakai (sodium): Inā loaʻa iā ʻoe nā hōʻailona o ka hāʻule ʻana o ka puʻuwai, pono paha ʻoe e kaupalena i kāu lawe ʻana i ka wai a me ka paʻakai. E noi i kāu kauka no nā alakaʻi kikoʻī e pili ana i kāu ʻai, me ka waiʻona a me ka caffeine.
  • E hoʻomaʻamaʻa me ke akahele: E kamaʻilio kāu kauka me ʻoe e pili ana i ka hoʻomaʻamaʻa kino kūpono iā ʻoe. Hiki i nā poʻe he nui me HCM ke hana i nā hana aerobic hoʻokūkū ʻole. ʻAʻole ʻōlelo nā kauka i ka hāpai kaumaha a i ʻole nā ​​​​haʻuki ikaika kiʻekiʻe.
  • E ʻike pinepine i kāu kauka: Inā loaʻa iā ʻoe ʻo HCM, pono ʻoe e ʻike pinepine i kāu cardiologist e nānā i kou kūlana.
  • E hōʻemi i kou pilikia o ka maʻi: Inā loaʻa iā ʻoe ʻo HCM, e aʻo aku kāu kauka iā ʻoe e hana i nā hana e hōʻemi i kou pilikia o ka loaʻa ʻana o kahi maʻi i kapa ʻia ʻo "infective endocarditis".

Pehea e hiki ai iā ʻoe ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i ka Infective Endocarditis?

ʻOi aku ka nui o ka poʻe me HCM e loaʻa i kahi maʻi bacteria i kapa ʻia ʻo "bacterial endocarditis" a i ʻole "infective endocarditis".

ʻO ka bacterial endocarditis kahi maʻi o kou mau valves puʻuwai a i ʻole ka uhi o kou puʻuwai (endocardium). Hana ʻia ia i ka wā e komo ai nā germs (ʻoi aku ka bacteria, akā i kekahi manawa fungi a me nā microorganisms ʻē aʻe) i loko o kou koko a hoʻouka i ka uhi o kou puʻuwai a i ʻole nā ​​valves. Hiki i kēia ke hana i nā valves e mānoanoa, perforated, a i ʻole scarred. ʻO ka hopena pinepine kēia i kahi valve puʻuwai leaky. Inā ʻaʻole mālama pono ʻia, hiki ke make.

Hiki iā ʻoe ke hana i kēia mau hana e hōʻemi i kēia pilikia:

  • E mālama pono i kou mau niho a me kou ʻāʻī: E ʻike i ke kauka niho i kēlā me kēia ʻeono mahina, e palaki i kou mau niho i kēlā me kēia lā, e floss, a e nānā i ke kūpono o kāu toothpaste.
  • E ʻike i ke kauka inā loaʻa iā ʻoe nā hōʻailona o kahi maʻi:
  • Ke kuni ma luna o 100 degere Fahrenheit, ka hou ʻana, a i ʻole ke anuanu.
  • ʻŌhūhū ʻili.
  • ʻEha, palupalu, ʻulaʻula, a pehu paha.
  • He ʻeha a ʻoki paha i hoʻōla ʻole ʻia, a i ʻole he ʻeha ʻulaʻula, wela, a ke kahe nei ka pus.
  • ʻEha ka ʻāʻī, paʻa ka ʻāʻī, a i ʻole ka ʻeha i ka wā e moni ai.
  • Ka hoʻokuʻu ʻana o ka sinus, ka ihu paʻa, ka ʻeha poʻo, a i ʻole ka ʻeha ma nā iwi papālina o luna.
  • ʻO ka ʻū maloʻo a phlegm paha e mau ana ma mua o ʻelua lā.
  • Nā kiko keʻokeʻo ma ka waha a i ʻole ke alelo.
  • Ka luaʻi, ka luaʻi ʻana, a i ʻole ka maʻi pākī.

Mai hoʻokaʻulua i ka ʻimi ʻana i ka lāʻau lapaʻau. ʻAʻole ke anu a me ka maʻi palū e hoʻoulu ai i ka endocarditis. Eia nō naʻe, hiki i nā maʻi ʻē aʻe me nā hōʻailona like ke hoʻoulu i ka endocarditis. No laila, e palekana a e ʻike i kāu kauka.

  • E lawe i nā lāʻau antibiotic pale ma mua o kekahi mau kaʻina hana lapaʻau a me nā niho. E kamaʻilio me kāu kauka e pili ana i ke ʻano o nā lāʻau antibiotic āu e lawe ai, ka nui, a me nā ʻano kaʻina hana āu e lawe ai.
  • E mālama i kahi kāleka hōʻike bacterial endocarditis i loaʻa mai ka American Heart Association.

ʻO ka mea hope loa, eia kāu e ʻōlelo ai (Leka Lawe-Home)

Noho ka hapa nui o ka poʻe me HCM i nā ola maʻamau a hauʻoli. Aia kekahi mau lāʻau lapaʻau i loaʻa no ka poʻe i loaʻa nā hōʻailona a i ʻole ka poʻe i pilikia i ka loaʻa ʻana o nā pilikia koʻikoʻi. Aia kou prognosis i ka maikaʻi o ka hana ʻana o kou puʻuwai, nā hōʻailona āu e loaʻa ai, a me ka maikaʻi o kāu pane ʻana a me ka hahai ʻana i kāu hoʻolālā lapaʻau.

E nīnau i kāu kauka e pili ana i kou mau pilikia a me nā mea hiki iā ʻoe ke hana e hoʻomaikaʻi i kou ʻano ola a pale i nā maʻi. Inā ua ʻike ʻia ʻoe me HCM a loaʻa nā hōʻailona a manaʻo paha he maʻi, e ʻike koke i kāu kauka. E hoʻomanaʻo, hiki iā ʻoe ke ola i kahi ola maikaʻi me kēia maʻi!


`Hypertrophic cardiomyopathy, HCM, maʻi puʻuwai, hoʻonui ʻia o ka puʻuwai, ʻeha umauma, pōkole o ka hanu, make koke o ka puʻuwai

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ua loli anei kou puʻuwai e like me kēia? E kamaʻilio kākou e pili ana i ka Hypertrophic Cardiomyopathy (HCM)!

Ua loli anei kou puʻuwai e like me kēia? E kamaʻilio kākou e pili ana i ka Hypertrophic Cardiomyopathy (HCM)!

Ua lohe paha ʻoe i kahi maʻi puʻuwai kahi e mānoanoa ai ka ʻiʻo puʻuwai, he mea paʻakikī iki? I kekahi manawa, ʻaʻole paha ʻoe e ʻike he loaʻa iā ʻoe, no ka mea, ʻaʻohe hōʻailona o kekahi poʻe. Akā, he mea nui e makaʻala i ia mea no ka mea e hoʻopilikia ia i ka puʻuwai. I kēia lā, e kamaʻilio mākou e pili ana i kēia maʻi i kapa ʻia ʻo hypertrophic cardiomyopathy, a i ʻole `HCM' i waena o nā kauka. Mai hopohopo, e kamaʻilio maʻalahi mākou e pili ana i ia mea, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.

E nānā mua kākou i ke ʻano o HCM?

I ka ʻōlelo maʻalahi, ʻo ka hypertrophic cardiomyopathy (HCM) kahi maʻi paʻakikī e hoʻopilikia i nā ʻiʻo o kou puʻuwai. Hiki ke hana ʻia e kekahi mau mea nui:

  • Ka mānoanoa o ka ʻiʻo puʻuwai: ʻO nā keʻena haʻahaʻa o ka puʻuwai, a mākou e kapa nei he ventricles, he mau paia mānoanoa.
  • ʻOʻoleʻa o ka ventricle hema: ʻOʻoleʻa ke keʻena nui ma ka ʻaoʻao hema o ka puʻuwai (ventricle hema), e lilo ana i mea elastic, e like me ka laholio.
  • Nā loli o ka valve mitral: Hiki ke hana i nā loli i ka hana o ka valve mitral, kahi valve koʻikoʻi i loko o ka puʻuwai.
  • Nā loli kelepona: Loaʻa kekahi mau ʻano ʻē i loko o nā pūnaewele ʻiʻo puʻuwai (nā loli kelepona).

Hiki i kēia mau mea ke hoʻopilikia i ka hana o ka puʻuwai.

Pehea ka hopena o kēia maʻi HCM i kou kino?

ʻĀ, e nānā kākou i ka mea a kēia mau hoʻololi e hana ai i ke kino.

Ka mānoanoa o ka myocardium

ʻO kēia ka hōʻailona nui i ʻike ʻia ma HCM. ʻO ka hapa pinepine, ʻike ʻia kēia mānoanoa ma ka paia e hoʻokaʻawale ana i nā ʻaoʻao hema a me ka ʻākau o ka puʻuwai, i kapa ʻia ʻo `(septum).` E noʻonoʻo, i ka wā e mānoanoa ai kēia septum ma waena o nā keʻena haʻahaʻa o ka puʻuwai `(ventricles)`, hiki iā ia ke ālai i ke ala e holo ai ke koko mai ka ventricle hema a i ka aorta, ke kīʻaha koko nui e lawe ana i ke koko ma ke kino holoʻokoʻa. Kāhea mākou i kēia `(outflow tract obstruction)`. A laila pono ka puʻuwai e hana ikaika e pamu i ke koko ma mua o kēia ālai. ʻO ke ʻano o HCM e ālai ana i ke ala e holo ai ke koko ua kapa ʻia ʻo `(Hypertrophic Obstructive Cardiomyopathy - HOCM)`.

I kekahi manawa, hiki ke mānoanoa nā ʻāpana ʻē aʻe o ka puʻuwai, e like me ka apex, ka ventricle ʻākau, a i ʻole ka ventricle hema holoʻokoʻa. I kēia mau hihia, ʻaʻole i ālai ʻia ke kahe o ke koko. Eia nō naʻe, ua hoʻemi ʻia ka nui o ke koko e hiki i ka ventricle ke lawelawe. Ua kapa ʻia kēia ʻo Hypertrophic Nonobstructive Cardiomyopathy.

ʻOʻoleʻa o ka Ventricular Hema

Ke mānoanoa ka ʻiʻo o ka puʻuwai, ʻo nā loli i loko o kēlā mau cell e hoʻomaha pono ʻole ai ka ventricle hema a piha i ke koko. He aha ka mea e hana ʻia? No ka mea, ʻaʻole i nui ke koko i loko o ke keʻena, ʻaʻole i nui ke koko momona oxygen i hoʻouna ʻia i nā ʻāpana ʻē aʻe a me nā ʻiʻo o ke kino. Hoʻonui pū kēia paʻakikī i ke kaomi i loko o ka puʻuwai, a hiki iā ʻoe ke ʻike i nā hōʻailona e like me:

  • ʻEha umauma
  • Pōkole o ka hanu
  • Pōʻino a i ʻole ka nawaliwali
  • Manaʻo e like me ka wikiwiki o kou puʻuwai (palpitations)

Nā Hoʻololi o ka Valve Mitral

E like me ka mea i ʻōlelo ʻia ma mua, i ka wā e ālai ʻia ai ke ala kahe o ka ventricle hema, ʻaʻole paha e hana pono ka valve mitral i loko o ka puʻuwai. Hiki i kēia ke ālai i ke kahe o ke koko a hoʻonui i ke kaomi i loko o ka ventricle hema.

ʻO ke kumu o kēia pani ʻana, ʻo ia ka paʻi ʻana o ka valve mitral i ka septum mānoanoa. Ke hana ʻia kēia, ʻaʻole e pani pono ka valve mitral a hiki i ke koko ke hoʻi hou i loko o ka atrium hema.

Nā Hoʻololi Kelepona

Inā ʻoe e nānā pono ma lalo o kahi microscope, ʻaʻole i hoʻonohonoho pono ʻia nā ʻiʻo puʻuwai o ke kanaka me HCM ma kahi laina pololei, akā ma kahi ʻano haunaele iki. Hiki i kēia maʻi ke hoʻololi i nā hōʻailona uila e hele ana ma nā keʻena haʻahaʻa o ka puʻuwai, e hana ana i kahi ʻano puʻuwai ʻē i kapa ʻia ʻo ventricular arrhythmia. Hiki i kēia ke lilo i mea weliweli.

Pehea ka maʻamau o kēia kūlana i kapa ʻia ʻo HCM?

Ua manaʻo ʻia he 1.5 miliona mau kānaka ma ʻAmelika Hui Pū ʻIa wale nō, a i ʻole hoʻokahi i loko o 500 mau kānaka, i loaʻa iā HCM. ʻOi aku ka maʻamau o kēia ma mua o kahi maʻi e like me "(Multiple Sclerosis)". No laila, ʻaʻole ia he mea laha ʻole.

I ka makahiki hea e ulu pinepine ai ʻo HCM?

ʻO ka hapa nui o ka manawa, ʻike ʻia kēia maʻi puʻuwai i nā poʻe ʻōpio, ma kahi o ka makahiki he ʻumikumamāwalu a iwakālua paha. Eia nō naʻe, hiki ke hoʻomaka i kēlā me kēia makahiki.

Inā loaʻa iaʻu ʻo HCM, aia kekahi pilikia o ka hāpai ʻana?

Pono paha ʻoe i ka mālama olakino kūikawā, e like me ka echocardiography maʻamau. Eia nō naʻe, ʻoi aku ka nui o kou hāpai ʻana i kahi hāpai olakino a me ka hānau maʻamau. Eia nō naʻe, he mea nui e kūkākūkā i kēia me kāu kauka ma mua o kou hāpai ʻana a kūkākūkā i nā pilikia. E haʻi pū kāu kauka iā ʻoe i nā lāʻau lapaʻau no HCM hiki iā ʻoe ke hoʻomau i ka lawe ʻana i ka wā hāpai. Pono paha ʻoe e loaʻa kahi pacemaker a i ʻole implantable cardioverter defibrillator (ICD) i hoʻokomo ʻia inā pono i ka wā hāpai.

He aha ke kumu o ka HCM?

Aia kekahi mau kumu e hiki ai ke hana i ka HCM:

  • ʻO ka Genetics: ʻO kēia ke kumu nui. He maʻi ka HCM i hiki ke hoʻoili ʻia mai nā mākua a i nā keiki. ʻO ke ʻano kēia he kīnā i loko o nā genes e kāohi ana i nā ʻano o ka ʻiʻo puʻuwai. Aia kekahi mau ʻano genes e hoʻoulu ai i ka HCM. ʻOiai inā he kīnā genetic, ʻaʻole e loaʻa i nā kānaka a pau o ka ʻohana ka maʻi ma ke ʻano like. Loaʻa paha i kekahi poʻe ka gene HCM akā ʻaʻole loa e loaʻa ka maʻi.
  • Ke koko kiʻekiʻe: ʻO ke koko kiʻekiʻe i loaʻa no ka manawa lōʻihi hiki ke lilo i kumu o kēia.
  • Ka ʻelemakule: Aia kahi hiki ke hana ʻia kēia ʻano i kou wā ʻelemakule.
  • Nā hihia i ʻike ʻole ʻia ke kumu:I kekahi manawa, ʻaʻohe kumu kūpono e loaʻa ai no HCM.

He aha nā hōʻailona e hiki i kekahi me HCM ke ʻike?

Hiki i kekahi poʻe me HCM ke ʻike i nā ʻano hōʻailona like ʻole, aʻo kekahi poʻe ʻaʻohe hōʻailona iki. ʻO nā hōʻailona maʻamau:

  • ʻEha umauma: Hana pinepine kēia i ka wā e hoʻoikaika kino ai, akā hiki ke hana i kekahi manawa i ke kū wale ʻana a ma hope paha o ka ʻai ʻana.
  • Ka pōkole o ka hanu a me ka luhi: ʻO kēia mau hōʻailona, ​​ʻoiai ke luhi ʻoe, he mea maʻamau ia i nā pākeke. ʻO kēia ma muli o ka hoʻonui ʻia o ke kaomi ma ka atrium hema a me nā māmā.
  • Nāwaliwali a i ʻole ka nawaliwali (syncope): Hiki ke hana ʻia kēia e nā ʻano puʻuwai ʻē (arrhythmias) a i ʻole nā ​​pane ʻē o nā kīʻaha koko i ka wā o ka hoʻoikaika kino. I kekahi manawa, ʻaʻole hiki ke loaʻa ke kumu.
  • Palpitations: Hiki ke hana ʻia kēia e kahi ʻano puʻuwai ʻē, e like me ka atrial fibrillation (atrial flutter) a i ʻole ka ventricular tachycardia (ventricular tachycardia). Ma kahi o 25% o ka poʻe me HCM he atrial fibrillation. Hoʻonui kēia i ka pilikia o nā ʻōpū koko a me ka hāʻule ʻana o ka puʻuwai.
  • Ka pehu ʻana o nā aa koko ma ke kino haʻahaʻa a i ʻole ka ʻāʻī.

He aha nā pilikia olakino ʻē aʻe e pili pū ana me HCM?

He nui ka poʻe me HCM e ola maʻamau a ʻaʻohe pilikia olakino nui. ʻAʻole pono kekahi e lawe i ka lāʻau lapaʻau. Eia nō naʻe, inā ʻaʻohe ou hōʻailona, ​​​​hiki i kāu kauka ke aʻo iā ʻoe ʻaʻole e hana i ka hoʻoikaika kino.

Eia nō naʻe, hiki i kekahi poʻe me HCM ke loaʻa i nā maʻi puʻuwai e hoʻopōkole ai i ko lākou ola a i ʻole e hōʻemi i ko lākou ʻano ola. ʻO nā mea nui:

Ka Paʻa koke ʻana o ka Puʻuwai a me ka Make koke ʻana o ka Puʻuwai

ʻO ka hopu koke ʻana o ka puʻuwai ka nalowale koke ʻana o ka hana o ka puʻuwai ma muli o ka wikiwiki o ka puʻuwai (e.g., Ventricular Tachycardia). I kēia hihia, pono ka mālama ʻana i ka pilikia, e like me ka CPR a me ka defibrillation, i ka wā e hoʻomaka ai nā hōʻailona. Inā ʻaʻole hāʻawi pono ʻia kēia lāʻau, hiki ke make koke ka puʻuwai.

ʻO ka hapa nui o ka poʻe me HCM he haʻahaʻa ka pilikia o ka make koke ʻana o ka puʻuwai. Eia nō naʻe, ʻo HCM ke kumu nui o ka make koke ʻana o ka puʻuwai i ka poʻe ma lalo o 35 mau makahiki. Ua lohe paha ʻoe ua pili pū ʻia ʻo HCM i ka make koke ʻana o kekahi mau mea pāʻani ʻōpio.

Ka hāʻule ʻana o ka puʻuwai

ʻOiai ua loaʻa iā ʻoe ka `(Heart Failure)`, ʻaʻole ia he manaʻo ua "hāʻule" kou puʻuwai a ua oki ka hana. ʻO ia hoʻi, ʻaʻole e hoʻopuehu pono ana kou puʻuwai i ke koko. ʻO nā hōʻailona o ka `(Heart Failure)` penei:

  • Pōkole o ka hanu.
  • Manaʻo luhi i ka wā e hana ai (luhi).
  • Ka pehu ʻana o nā kuʻekuʻe wāwae, nā wāwae, a me ka ʻōpū.
  • Pono e mimi i ka pō i ka wā e hoʻomaha ana.
  • Pōniuniu, huikau, paʻakikī i ka noʻonoʻo ʻana, maule.
  • Ke manaʻo nei e kuʻi wikiwiki ana kou puʻuwai (palpitations).
  • ʻO ka ʻū maloʻo a ʻeha loa.
  • Manaʻo piha, pehu, nalowale ka makemake e ʻai, a ʻeha paha ka ʻōpū.

Pehea e ʻike ai i ka HCM? (Diagnosis)

Ua ʻike ʻia ʻo HCM ma muli o kēia mau mea:

  • Mōʻaukala lapaʻau: E nīnau aku kāu kauka iā ʻoe e pili ana i kāu mau hōʻailona a inā paha ua loaʻa i kekahi o kou ʻohana nā maʻi like.
  • Hoʻokolohua kino: E hoʻolohe ke kauka i kou puʻuwai a me kou mau māmā. Hiki i ka poʻe me HOCM ke lohe i kahi kani puʻuwai ʻē (heart murmur).
  • Nā hoʻāʻo: ʻO ka echocardiogram (echo) ka hoʻāʻo nui i hoʻohana ʻia no ka ʻike ʻana i ka HCM. Hiki i kēia ke kōkua i ka ʻike ʻana inā ua mānoanoa nā paia o ka puʻuwai.

Aia kekahi mau hoʻokolohua ʻē aʻe:

  • Nā hoʻāʻo koko.
  • ʻElectrocardiogram (ECG).
  • X-ray umauma.
  • Hoʻāʻo leo koʻikoʻi o ka hoʻoikaika kino.
  • Ka hoʻokomo ʻana o ke catheter puʻuwai.
  • Kiʻi hoʻohālikelike magnetic (MRI).

He aha nā lāʻau lapaʻau no HCM?

E hoʻoholo kāu kauka i ka lāʻau lapaʻau kūpono iā ʻoe ma muli o nā kumu aʻe:

  • Aia kekahi mea e ālai ana i ke ala e puka ai ke koko mai ka puʻuwai aku (e emi ana ke ala e kahe ai ke koko)?
  • Pehea e hana ai kou puʻuwai?
  • Kou mau hōʻailona.
  • Kou mau makahiki a me kou ʻano hana ikaika.
  • Loaʻa iā ʻoe nā ʻano puʻuwai ʻē aʻe (arrhythmias)?

ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka hōʻemi a pale ʻana paha i nā hōʻailona a me ka hoʻemi ʻana i ka pilikia o nā pilikia e like me ka hāʻule ʻana o ka puʻuwai a me ka make koke ʻana o ka puʻuwai.

Hiki ke hana i kēia mau mea ma ke ʻano he lāʻau lapaʻau:

  • E ʻike i nā pilikia a hoʻomau i ke kipa ʻana i ke kauka.
  • Nā loli o ke ʻano o ka nohona.
  • Nā lāʻau lapaʻau.
  • Nā kaʻina hana lapaʻau kūikawā.

Pehea e hoʻoholo ai i ka HCM?

ʻOiai ʻo HCM kahi maʻi e hiki ke hoʻoili ʻia mai kēlā hanauna a kēia hanauna, inā loaʻa i kekahi o kou mau mākua, nā kaikaina, a i ʻole nā ​​​​keiki (ʻo ia hoʻi, he hoahānau mua) ka maʻi, he mea nui e hoʻāʻo ʻia.

ʻO ka hana mua, ʻo ia ke nānā ʻia kou puʻuwai e kahi Electrocardiogram (ECG) a me kahi Echocardiogram (echo). Inā hōʻike kēia mau hoʻokolohua i nā hōʻailona o HCM, pono ʻoe e ʻike i ke kauka loea i kēia maʻi (cardiologist).

I kekahi manawa, ʻoiai inā he moʻolelo ʻohana kou o HCM, maʻamau paha kāu mau hopena hoʻāʻo. Inā pēlā, ʻōlelo nā kauka e hana ʻoe i kahi echo a me ECG i kēlā me kēia ʻekolu makahiki a hiki i kou 30, a laila i kēlā me kēia ʻelima makahiki.

ʻO wai ka mea i ʻoi aku ka nui o ka make ʻana o ka puʻuwai ma muli o HCM?

ʻO ka hapa nui o ka poʻe me HCM he haʻahaʻa ka pilikia o ka make koke ʻana o ka puʻuwai. Eia nō naʻe, he nui ka poʻe me HCM i loaʻa ka pilikia nui. He mea nui e ʻike inā loaʻa iā ʻoe kēia ʻano. Hiki i kāu kauka ke haʻi iā ʻoe i ka mea hiki iā ʻoe ke hana e hōʻemi i kou pilikia.

ʻO ka poʻe i ʻoi aku ka nui o ka make ʻana o ka puʻuwai ma muli o HCM:

  • ʻO nā kānaka me ka mōʻaukala ʻohana o ka make koke ʻana o ka puʻuwai.
  • ʻO ka poʻe i loaʻa ka syncope i nā manawa he nui i ko lākou wā ʻōpiopio.
  • ʻO nā kānaka i loaʻa ka pane koko kūpono ʻole i ka hoʻoikaika kino.
  • ʻO nā kānaka me ka mōʻaukala mua o nā puʻuwai wikiwiki loa (arrhythmia).
  • ʻO ka poʻe me nā hōʻailona koʻikoʻi a me ka hana puʻuwai maikaʻi ʻole.

E kamaʻilio me kāu kauka e pili ana i kou pilikia pilikino. Inā he ʻelua a ʻoi aku paha mau kumu pilikia no ka make koke ʻana, hiki i kāu kauka ke ʻōlelo aku i nā lāʻau antiarrhythmic (nā lāʻau lapaʻau e kaohi ana i nā ʻano puʻuwai maʻamau ʻole) a i ʻole kahi implantable cardioverter defibrillator (ICD) e hōʻemi i kou pilikia.

He aha nā lāʻau lapaʻau i hoʻohana ʻia e mālama i ka HCM?

Hoʻomaopopo nā kauka i nā lāʻau lapaʻau like ʻole e kāohi i kāu mau hōʻailona a pale i nā pilikia hou aʻe. ʻO nā lāʻau lapaʻau e like me nā "Beta blockers" a me nā "calcium channel blockers" e hoʻomaha i ka ʻiʻo o ka puʻuwai, e kōkua ana iā ia e hoʻopiha me ke koko a hoʻomaʻamaʻa i ke koko me ka ʻoi aku ka maikaʻi. Hiki i nā lāʻau lapaʻau ʻē aʻe ke kāohi i kou helu puʻuwai a hōʻemi paha i ka pilikia o nā ʻano puʻuwai maʻamau ʻole (arrhythmias).

Hiki ke ʻōlelo ʻia iā ʻoe ʻaʻole e lawe i kekahi mau lāʻau lapaʻau, no ka laʻana nitrates (nāna e hoʻohaʻahaʻa i ke koko) a i ʻole digoxin (ka mea e hoʻonui ai i ka ikaika o ka puʻuwai).

I kekahi manawa pono ʻoe e lawe i nā lāʻau antibiotic a lawe i nā hana ʻē aʻe e hōʻemi i ka pilikia o kahi maʻi hoʻoweliweli ola i kapa ʻia ʻo bacterial endocarditis.

He aha nā kaʻina hana lapaʻau kūikawā i hoʻohana ʻia e mālama ai iā HCM?

Aia kekahi mau ʻano hana e mālama ai i ka Hypertrophic Obstructive Cardiomyopathy (HOCM), kahi kūlana e hoʻopilikia ai i ke kahe koko:

ʻO ka myectomy Septal

He hana ʻoki kino kēia. I loko o ka myectomy septal, wehe ke kauka ʻoki kino i kahi ʻāpana liʻiliʻi o kou paia septal mānoanoa. Hoʻonui kēia i ke ala kahe mai ka ventricle hema a i ka aorta. Manaʻo wale nā ​​​​kauka i kēia ʻoki kino inā ʻaʻole kōkua ka lāʻau lapaʻau. Hoʻoponopono pinepine kēia i ka pilikia o ka valve mitral.

ʻO ka hoʻopau ʻana i ka ʻEthanol

Ua kapa ʻia hoʻi kēia he `(septal ablation)`. Hoʻohana ʻia kēia ʻano hana no ka poʻe hiki ʻole ke hana i ke ʻoki ʻana `(septal myectomy)` i ʻōlelo ʻia ma mua. Ma kēia, loaʻa i ke kauka kahi aʻa coronary liʻiliʻi e hoʻolako ana i ke koko i ka ʻaoʻao o luna o kou septum. A laila hoʻokomo ʻo ia i kahi catheter balloon i loko o kēlā aʻa a hoʻopiha iā ia. A laila, hoʻokomo ʻo ia i kahi `(contrast agent)` dye e ʻike i kahi kikoʻī o ka paia septal mānoanoa e ālai ana i ke kahe koko.

Ke loaʻa ka wahi, hoʻokomo ke kauka i kahi liʻiliʻi o ka waiʻona maʻemaʻe ma o ke catheter. Pepehi ka waiʻona i nā ʻāpana, a i nā mahina e hiki mai ana e emi hou ka septum i kona nui maʻamau. Hoʻonui kēia i ke ala no ke kahe ʻana o ke koko.

ʻO ka Implantable Cardioverter Defibrillator (ICD)

Hiki i kahi implantable cardioverter defibrillator (ICD) ke kōkua i nā poʻe me nā arrhythmias e hoʻoweliweli ana i ke ola a i ʻole ka make koke ʻana o ka puʻuwai. He mea liʻiliʻi ka ICD i hoʻokomo ʻia ma lalo o kou ʻili. Hoʻopili ʻia ia i kou puʻuwai e nā uwea. Ke nānā mau nei ka ICD i kou mele puʻuwai. Ke ʻike ʻo ia i kahi puʻuwai wikiwiki loa a ʻano ʻē, hāʻawi ia i kahi haʻalulu uila liʻiliʻi akā ikaika i ka puʻuwai, e hoʻoulu ai iā ia e kuʻi maʻamau hou. E haʻi aku kāu kauka iā ʻoe inā kūpono kahi ICD iā ʻoe.

Ka Hoʻokele ʻana i ka Pōʻino o ka Puʻuwai

Aia kekahi mau ala e mālama ai i ka hāʻule ʻana o ka puʻuwai, mai nā loli o ke ʻano o ka nohona a hiki i nā lāʻau lapaʻau e hōʻemi ana i nā hōʻailona a kōkua i ka hana pono ʻana o ka ʻiʻo o ka puʻuwai.

Pehea e hiki ai iaʻu ke hoʻomaikaʻi i koʻu ola maikaʻi me HCM?

Inā he mau hōʻailona kou a ʻaʻole paha, inā ua ʻike ʻia ʻoe me HCM, a inā loaʻa i kekahi o kou ʻohana, aia kekahi mau mea hiki iā ʻoe ke hana e mālama i ke olakino o kou puʻuwai i kona maikaʻi loa:

  • E kaupalena i nā wai a me ka paʻakai (sodium): Inā loaʻa iā ʻoe nā hōʻailona o ka hāʻule ʻana o ka puʻuwai, pono paha ʻoe e kaupalena i kāu lawe ʻana i ka wai a me ka paʻakai. E noi i kāu kauka no nā alakaʻi kikoʻī e pili ana i kāu ʻai, me ka waiʻona a me ka caffeine.
  • E hoʻomaʻamaʻa me ke akahele: E kamaʻilio kāu kauka me ʻoe e pili ana i ka hoʻomaʻamaʻa kino kūpono iā ʻoe. Hiki i nā poʻe he nui me HCM ke hana i nā hana aerobic hoʻokūkū ʻole. ʻAʻole ʻōlelo nā kauka i ka hāpai kaumaha a i ʻole nā ​​​​haʻuki ikaika kiʻekiʻe.
  • E ʻike pinepine i kāu kauka: Inā loaʻa iā ʻoe ʻo HCM, pono ʻoe e ʻike pinepine i kāu cardiologist e nānā i kou kūlana.
  • E hōʻemi i kou pilikia o ka maʻi: Inā loaʻa iā ʻoe ʻo HCM, e aʻo aku kāu kauka iā ʻoe e hana i nā hana e hōʻemi i kou pilikia o ka loaʻa ʻana o kahi maʻi i kapa ʻia ʻo "infective endocarditis".

Pehea e hiki ai iā ʻoe ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i ka Infective Endocarditis?

ʻOi aku ka nui o ka poʻe me HCM e loaʻa i kahi maʻi bacteria i kapa ʻia ʻo "bacterial endocarditis" a i ʻole "infective endocarditis".

ʻO ka bacterial endocarditis kahi maʻi o kou mau valves puʻuwai a i ʻole ka uhi o kou puʻuwai (endocardium). Hana ʻia ia i ka wā e komo ai nā germs (ʻoi aku ka bacteria, akā i kekahi manawa fungi a me nā microorganisms ʻē aʻe) i loko o kou koko a hoʻouka i ka uhi o kou puʻuwai a i ʻole nā ​​valves. Hiki i kēia ke hana i nā valves e mānoanoa, perforated, a i ʻole scarred. ʻO ka hopena pinepine kēia i kahi valve puʻuwai leaky. Inā ʻaʻole mālama pono ʻia, hiki ke make.

Hiki iā ʻoe ke hana i kēia mau hana e hōʻemi i kēia pilikia:

  • E mālama pono i kou mau niho a me kou ʻāʻī: E ʻike i ke kauka niho i kēlā me kēia ʻeono mahina, e palaki i kou mau niho i kēlā me kēia lā, e floss, a e nānā i ke kūpono o kāu toothpaste.
  • E ʻike i ke kauka inā loaʻa iā ʻoe nā hōʻailona o kahi maʻi:
  • Ke kuni ma luna o 100 degere Fahrenheit, ka hou ʻana, a i ʻole ke anuanu.
  • ʻŌhūhū ʻili.
  • ʻEha, palupalu, ʻulaʻula, a pehu paha.
  • He ʻeha a ʻoki paha i hoʻōla ʻole ʻia, a i ʻole he ʻeha ʻulaʻula, wela, a ke kahe nei ka pus.
  • ʻEha ka ʻāʻī, paʻa ka ʻāʻī, a i ʻole ka ʻeha i ka wā e moni ai.
  • Ka hoʻokuʻu ʻana o ka sinus, ka ihu paʻa, ka ʻeha poʻo, a i ʻole ka ʻeha ma nā iwi papālina o luna.
  • ʻO ka ʻū maloʻo a phlegm paha e mau ana ma mua o ʻelua lā.
  • Nā kiko keʻokeʻo ma ka waha a i ʻole ke alelo.
  • Ka luaʻi, ka luaʻi ʻana, a i ʻole ka maʻi pākī.

Mai hoʻokaʻulua i ka ʻimi ʻana i ka lāʻau lapaʻau. ʻAʻole ke anu a me ka maʻi palū e hoʻoulu ai i ka endocarditis. Eia nō naʻe, hiki i nā maʻi ʻē aʻe me nā hōʻailona like ke hoʻoulu i ka endocarditis. No laila, e palekana a e ʻike i kāu kauka.

  • E lawe i nā lāʻau antibiotic pale ma mua o kekahi mau kaʻina hana lapaʻau a me nā niho. E kamaʻilio me kāu kauka e pili ana i ke ʻano o nā lāʻau antibiotic āu e lawe ai, ka nui, a me nā ʻano kaʻina hana āu e lawe ai.
  • E mālama i kahi kāleka hōʻike bacterial endocarditis i loaʻa mai ka American Heart Association.

ʻO ka mea hope loa, eia kāu e ʻōlelo ai (Leka Lawe-Home)

Noho ka hapa nui o ka poʻe me HCM i nā ola maʻamau a hauʻoli. Aia kekahi mau lāʻau lapaʻau i loaʻa no ka poʻe i loaʻa nā hōʻailona a i ʻole ka poʻe i pilikia i ka loaʻa ʻana o nā pilikia koʻikoʻi. Aia kou prognosis i ka maikaʻi o ka hana ʻana o kou puʻuwai, nā hōʻailona āu e loaʻa ai, a me ka maikaʻi o kāu pane ʻana a me ka hahai ʻana i kāu hoʻolālā lapaʻau.

E nīnau i kāu kauka e pili ana i kou mau pilikia a me nā mea hiki iā ʻoe ke hana e hoʻomaikaʻi i kou ʻano ola a pale i nā maʻi. Inā ua ʻike ʻia ʻoe me HCM a loaʻa nā hōʻailona a manaʻo paha he maʻi, e ʻike koke i kāu kauka. E hoʻomanaʻo, hiki iā ʻoe ke ola i kahi ola maikaʻi me kēia maʻi!


`Hypertrophic cardiomyopathy, HCM, maʻi puʻuwai, hoʻonui ʻia o ka puʻuwai, ʻeha umauma, pōkole o ka hanu, make koke o ka puʻuwai

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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