Ua loaʻa anei iā ʻoe ka ʻū no kekahi mau lā? Malia paha me ka ʻū iki? Manaʻo pinepine mākou i kēia mau mea he mau hōʻailona o ke anu. Akā i kekahi manawa ma hope o kēia mau hōʻailona liʻiliʻi aia paha kekahi mea ʻē aʻe e pono ai mākou e makaʻala. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi māmā i lohe ʻole ʻia e ka poʻe he nui, akā he mea nui e ʻike. ʻO ia ka Lung Carcinoid Tumors. Mai makaʻu i kou lohe ʻana i kēia inoa a me ka huaʻōlelo "tumor". E hoʻomaopopo pono kākou i kēia.
He aha nā puʻupuʻu carcinoid o ka māmā?
I ka ʻōlelo maʻalahi, he ʻano puʻupuʻu kanesa kēia e hana ʻia ana i loko o nā māmā. Akā, ʻaʻole ia he ʻano huhū a laha wikiwiki paha e like me kā mākou e manaʻo ai ke lohe mākou i ka huaʻōlelo "maʻi kanesa." Hoʻomohala kēia mau puʻupuʻu mai kahi ʻano kūikawā o ke kelepona i loko o ko mākou mau māmā i kapa ʻia ʻo "Neuroendocrine cells."
E noʻonoʻo i kēia mau pūnaewele "Neuroendocrine" e like me nā ʻelele liʻiliʻi i loko o ko kākou kino. Hiki iā lākou ke loaʻa nā leka e like me nā pūnaewele nerve, a, e like me nā pūnaewele endocrine, hana i nā hormones e pili ana i kēlā mau leka e kāohi i nā hana like ʻole i loko o ke kino. I loko o nā māmā, kōkua kēia mau pūnaewele i ka hoʻokele ʻana i nā mea e like me ka nui o ka ea a kākou e hanu ai a me ke kahe ʻana o ke koko.
No laila, no kekahi kumu, ke hoʻomaka kēia mau ʻāpana e māhelehele me ke kāohi ʻole ʻia, e hoʻokumu ʻia kahi puʻupuʻu ma laila. ʻO kēia ka mea a mākou e kapa nei he `(Carcinoid Tumor)`. Hiki i kēia mau puʻupuʻu ke hoʻokumu ʻia ma nā wahi o ke kino, e like me ke ala ʻai a me nā puʻupaʻa. Akā ma kahi o ka hapakolu o lākou e hoʻokumu ʻia i loko o nā māmā.
ʻElua ʻano nui o kēia mau nati.
He mea nui loa kēia e ʻike, no ka mea, ʻokoʻa ke ʻano o ka lāʻau a me ke ʻano o ka maʻi ma muli o ke ʻano.
1. Nā ʻōpū Carcinoid maʻamau
ʻO kēia ke ʻano maʻamau . He 90% ia o nā puʻupuʻu carcinoid māmā i ʻike ʻia. ʻO ka mea maikaʻi loa, ulu mālie kēia mau puʻupuʻu a kākaʻikahi ka neʻe ʻana i nā wahi ʻē aʻe o ke kino. No laila, hiki ke mālama pono ʻia.
2. Nā ʻōpū Carcinoid Atypical
ʻAʻole maʻamau kēia ʻano. Hiki iā ia ke ulu wikiwiki iki ma mua o ke ʻano maʻamau. ʻOi aku ka nui o ka laha ʻana i nā ʻāpana ʻē aʻe o ke kino. Ua ʻike ʻia hoʻi he kiʻekiʻe aʻe ka pilikia o ka hoʻomohala ʻana i kēia ʻano "(Atypical)" i waena o ka poʻe puhi paka.
ʻO ka mea nui, ʻoiai ke ʻano, he ʻokoʻa loa kēia mau mea mai nā maʻi kanesa māmā maʻamau a pane maikaʻi i ka lāʻau lapaʻau.
He aha nā hōʻailona o kēia?
ʻO ka hapa nui o ka manawa, ʻoiai ka poʻe me nā cysts "Typical" , ʻaʻole ʻike ka nui o ka poʻe i kekahi mau hōʻailona.Loaʻa pinepine kēia mau mea i ka wā o ka X-ray umauma no kekahi kumu ʻē aʻe. Eia nō naʻe, hiki i kekahi poʻe ke ʻike i kēia mau hōʻailona:
E hōʻike wau i kēia mau ʻano ma kahi papa e maʻalahi ai ke hoʻomaopopo.
| ʻAno hiʻohiʻona | Wehewehena |
|---|---|
| Nā hōʻailona maʻamau e pili ana i ka māmā | |
| Kuke | ʻO ka ʻū pinepine, i kekahi manawa me ka mucus liʻiliʻi a i ʻole ke koko. |
| ʻEha umauma | ʻEha, ʻoiai i ka wā e hanu hohonu ai. |
| Ka paʻakikī o ka hanu ʻana (dyspnea) | Ua ʻike ʻia ka ʻeha ʻoiai ke hana ʻana i nā hana maʻamau. |
| He leo hū i ka wā e hanu ana | ʻO ka wheezing he leo i lohe ʻia i ka wā e hanu ana i waho, e like me ke kani o ka poʻe asthma. |
| Nā hōʻailona e pili ana me ka Carcinoid Syndrome | |
| Pehu nui | ʻO kahi kūlana i hoʻokumu ʻia e nā hormones e like me ka serotonin i hana ʻia e ka puʻupuʻu. |
| ʻUlaʻula o ka maka a me ka ʻāʻī | ʻUlaʻula koke a me ka ʻulaʻula o ka maka a me ka ʻāʻī. |
| Piʻi ke kaumaha me ke kumu ʻole | Hiki ke pili kēia i nā hopena o nā hormones. |
ʻO kēia mau hōʻailona, i kapa ʻia ʻo 'Carcinoid Syndrome', hiki mai no ka mea ua hana ka puʻupuʻu i nā hormones he nui ma mua o ka mea e pono ai ke kino a hoʻohui iā lākou i ke koko. Eia nō naʻe, ʻike pinepine ʻole ʻia kēia.
No ke aha i hoʻokumu ʻia ai kēia mau puʻupuʻu? He aha nā kumu pilikia?
ʻAʻole maopopo loa i nā kānaka ʻepekema ke kumu e hoʻomaka koke ai kēia mau pūnaewele "neuroendocrine" e māhelehele me ka ʻole o ke kāohi ʻia, akā ua ʻike lākou he ʻoi aku ka nui o ka pilikia o kekahi poʻe i ka loaʻa ʻana o ke kūlana.
- Nā kumu hoʻoilina: Aia kekahi ʻano hoʻoilina laha ʻole i kapa ʻia ʻo "Multiple Endocrine Neoplasia type 1 (MEN1). ʻOi aku ka nui o ka pilikia o ka poʻe me kēia ʻano i ka loaʻa ʻana o nā ʻōpū carcinoid.
- Puhipaka: Hiki i ka puhipaka ke kōkua i ka ulu ʻana o nā ʻōpū, ʻoiai hoʻi nā ʻōpū "atypical".
- Kāne: ʻOi aku ka nui o ka pilikia o nā wahine i ka loaʻa ʻana o kēia maʻi.
- Makahiki: ʻOiai he mea maʻamau ia i waena o ka poʻe ma waena o 45 a me 55 mau makahiki, hiki ke loaʻa kēia ʻano i kekahi o kēlā me kēia makahiki, ʻoiai nā keiki ʻōpio.
Pehea e ʻike ai i ka maʻi?
ʻAe, e ʻōlelo kākou he loaʻa iā ʻoe kēia mau hōʻailona. Ke hele ʻoe e ʻike i ke kauka, e nīnau mua ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, a laila e nānā i kou mau māmā me ka stethoscope. A laila e kauoha paha ʻo ia i kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
1. Kiʻi: ʻO ka hana mua he X-ray umauma . Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā he mea ʻē i loko o nā māmā. Hiki ke hana ʻia kahi CT scan (Computed Tomography scan) e hoʻoholo maopopo i ka nui a me kahi o ka puʻupuʻu.
2. Nā hoʻāʻo koko a me ka mimi: Kōkua kēia mau hoʻāʻo e ʻike inā aia kekahi mau hormones i hana ʻia e kēia mau puʻupuʻu i loko o ke koko a i ʻole ka mimi.
3. Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi loa e hōʻoia i ka maʻi 100%. ʻO ka mea i hana ʻia ma ʻaneʻi, ʻo ia ke lawe ʻana i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka puʻupuʻu a nānā iā ia ma lalo o kahi microscope. Hiki i kēia ke haʻi pololei inā he "Typical" a i ʻole "Atypical" ka puʻupuʻu. ʻO ke ʻano maʻamau i hoʻohana ʻia e loaʻa ai kēia ʻāpana o ka ʻiʻo, ʻo ia ka bronchoscopy . Maanei, ua hoʻokomo ʻia kahi paipu lahilahi a palupalu me kahi kāmela i hoʻopili ʻia ma ka waha a i ʻole ka ihu i loko o nā ala ea o nā māmā a loaʻa kahi ʻāpana o ka puʻupuʻu.
Pehea e mālama ʻia ai?
E hilinaʻi kāu hoʻolālā lapaʻau i ke ʻano, ka nui, kahi o ka puʻupuʻu, a me kou olakino holoʻokoʻa. I ka hapanui o nā hihia, hiki ke ho'ōla loa ʻia kēia mau puʻupuʻu.
ʻoki kino
ʻO ka lāʻau lapaʻau nui a kūleʻa loa no kēia, ʻo ia ka wehe ʻoki ʻana i ka puʻupuʻu.
- ʻO ka Wedge Resection: Ka wehe ʻana i ka puʻupuʻu wale nō a me kahi ʻāpana liʻiliʻi o ka māmā a puni ia.
- Lobectomy: Wehe ʻana i kahi lobe, a i ʻole kahi ʻāpana nui, o ka māmā.
- Pneumonectomy: Kākaʻikahi loa, inā pono, ka wehe ʻana i kahi māmā holoʻokoʻa.
I ka wā o ke ʻoki ʻana, ua wehe ʻia kekahi mau lymph node kokoke i ka puʻupuʻu a ua nānā ʻia e ʻike inā ua pālahalaha nā hunaola kanesa iā lākou.
Nā lāʻau lapaʻau ʻē aʻe
Inā ʻaʻole hiki ke wehe loa ʻia ka puʻupuʻu, a inā ua pālahalaha aku i nā wahi ʻē aʻe, pono paha nā lāʻau ʻē aʻe.
- Lapaʻau Radiation: Ke luku ʻana i nā hunaola kanesa me ka hoʻohana ʻana i nā kukuna ikehu kiʻekiʻe.
- Lāʻau lapaʻau: Hoʻohana ʻia nā lāʻau lapaʻau e like me `(Octreotide)` e kāohi i nā hōʻailona o `Carcinoid Syndrome`, a hoʻohana ʻia nā lāʻau lapaʻau e like me `(mTOR inhibitors)` e kāohi i ka ulu ʻana o ka puʻupuʻu.
- Kemoterapia: No ka mea, lohi pinepine ka ulu ʻana o kēia mau ʻōpū, ʻaʻole hoʻohana pinepine ʻia ka chemotherapy, ka mea e pepehi ai i nā ʻāpana e māhele wikiwiki ana. Eia nō naʻe, pono paha i kekahi manawa no nā ʻōpū e ulu wikiwiki ana o ke ʻano "atypical".
Hiki ke ho'ōla loa ʻia kēia maʻi?
He nīnau kēia a ka poʻe he nui. Ua kānalua iki nā kauka e hoʻohana i ka huaʻōlelo "ho'ōla piha ʻia" i ka wā e kamaʻilio ai e pili ana i ka maʻi kanesa, no ka mea, he manawa liʻiliʻi mau nō ia e hoʻi hou mai ai.
Eia nō naʻe, hiki ke mālama ʻia a ho'ōla ʻia nā ʻōpū carcinoid maʻamau . ʻO ka pilikia o ka hoʻi hou ʻana ma hope o ka mālama ʻana he emi ma mua o 4%. ʻO ia hoʻi, ʻaʻole e loaʻa hou ka 96 o 100 poʻe.
ʻOi aku ka paʻakikī o ka mālama ʻana i nā puʻupuʻu atypical. Pono paha lākou i ka hui pū ʻana o nā lāʻau lapaʻau. Ma keʻano holoʻokoʻa, 89% o ka poʻe i ʻike ʻia me kēia maʻi (me nā ʻano ʻelua) e ola kino maikaʻi ana ma hope o 5 mau makahiki. He hopena maikaʻi loa kēia no kahi ʻano maʻi kanesa.
Āhea ʻoe e ʻimi ai i ke aʻo lapaʻau? Āhea ʻoe e hele ai i ka ETU?
ʻO ka mea nui loa, ʻo ia ka mālama ʻana i kou kino. He mea nui e hana koke i nā kūlana aʻe.
| Manawa kūpono | He aha e hana ai |
|---|---|
| E ʻike i kāu kauka. | |
Inā loaʻa iā ʻoe nā hōʻailona hou a i ʻole e ʻoi aku ka ʻino:
| |
| E hele koke i ka Emergency Treatment Unit (ETU). | |
Inā loaʻa iā ʻoe kēia mau hōʻailona koʻikoʻi:
| |
Leka Lawe-Home
- He ʻano maʻi kanesa laha ʻole nā puʻupuʻu carcinoid māmā e ulu ana i loko o nā māmā. Akā, he ʻokoʻa loa lākou mai nā maʻi kanesa māmā maʻamau.
- ʻO ke ʻano maʻamau (maʻamau) e ulu lohi loa a hiki ke ho'ōla loa ʻia me ka lāʻau lapaʻau .
- ʻAʻole ʻike ka nui o ka poʻe i kekahi mau hōʻailona , no laila mai hoʻowahāwahā i nā mea e like me ke kuʻi mau a i ʻole ka hanu ʻana.
- ʻO ka lāʻau lapaʻau nui, ʻo ia ka wehe ʻana i ka puʻupuʻu me ke ʻoki kino .
- Inā he mau makaʻu a kānalua paha kou e pili ana i kēia maʻi, ʻo ka mea maikaʻi loa e hana ai, ʻo ia ke kamaʻilio ākea me kāu kauka . E hāʻawi ʻo ia iā ʻoe i ka ʻike a me ke alakaʻi āpau āu e pono ai.
- Inā ʻoe e puhipaka, ʻo ka haʻalele ʻana i ka puhipaka ke ala maikaʻi loa e pale aku ai iā ʻoe iho mai nā maʻi he nui e pili ana i ka māmā.











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