Ua like anei kou mau puʻupaʻa me ka huʻa? I kēia lā e kamaʻilio kākou e pili ana i ka Medullary Sponge Kidney!

ʻAʻole paha ʻoe i lohe i ka huaʻōlelo 'Medullary Sponge Kidney' ma mua. ʻOiai paha he mea paʻakikī ke wehewehe ʻana, he maʻi hānau maoli ia e pili ana i nā puʻupaʻa. I ka ʻōlelo maʻalahi, ʻo ia kahi e hana ai nā pehu wai liʻiliʻi, i kapa ʻia he cysts, i loko o kou mau puʻupaʻa, ma ka ʻaoʻao waena o nā puʻupaʻa (medulla). E kamaʻilio kākou e pili ana i kēia i kēia lā, ʻeā?

He aha maoli ka Medullary Sponge Kidney?

E nānā mua kākou i ke ʻano o nā puʻupaʻa a pehea lākou e hana ai. E like me kou ʻike, he ʻāpana koʻikoʻi loa nā puʻupaʻa o ka ʻōnaehana mimi i loko o ko kākou kino. Loaʻa i kēlā me kēia puʻupaʻa kahi ʻāpana waena, a mākou e kapa nei ʻo ka medulla. Loaʻa i kēia medulla nā kahawai liʻiliʻi loa i kapa ʻia he mau tubules liʻiliʻi. Hōʻiliʻili kēia mau kahawai i nā huahana ʻōpala i kānana ʻia mai ke koko a hana i ka mimi. A laila hui pū kēia mau kahawai a pili i nā kahawai nui iki i kapa ʻia he mau ducts hōʻiliʻili. Mai kēia mau mea, hele ka mimi i kahi hōʻiliʻili nui ma waenakonu o ka puʻupaʻa, ʻo ia hoʻi ka pelvis renal. Mai laila mai, hele ka mimi ma o nā ureters a i ka ʻōpū mimi, a laila ma o ka urethra e haʻalele i ke kino.

ʻAe, i kēia manawa, ʻo ka mea e hana ʻia i kahi kanaka me ka 'Medullary Sponge Kidney' ʻo ia ka hoʻomohala ʻana o nā cysts liʻiliʻi i nā ducts hōʻiliʻili aʻu i ʻōlelo ai, a pehu kēlā mau ducts a nui aʻe. Ua like lākou me ka huʻa. ʻO ia ke kumu i kapa ʻia ai ʻo 'Sponge Kidney'. Hoʻopilikia pinepine kēia ʻano i nā puʻupaʻa ʻelua, akā i kekahi manawa hiki ke hoʻopilikia i hoʻokahi puʻupaʻa wale nō.

Pehea e ulu ai kēia maʻi puʻupaʻa medullary sponge?

I kēia manawa, he nīnau kāu e pili ana i ka mea e hana ʻia ke hana ʻia kēia mau cysts. Ke hana ʻia kēia mau cysts, ʻaʻole hiki i kēlā mau kahawai maikaʻi (tubules) ke hana pono. A laila, hoʻomaka nā mea e like me ka calcium e waiho i loko o kēia mau kahawai. Kāhea mākou i kēia (nephrocalcinosis). ʻAʻole wale ka calcium, akā hiki i nā mea ʻē aʻe e like me ka phosphate a me ka oxalate ke hōʻiliʻili ma kēia ʻano. I ka hala ʻana o ka manawa, pili pū kēia mau mea i hōʻiliʻili ʻia a hana i nā pōhaku puʻupaʻa .

Hoʻopili kēia mau cysts a me nā pōhaku i ke kahe o ka mimi ma o ke ala urinary, e hoʻonui ana i ka pilikia o nā maʻi urinary tract (UTIs) .

He aha ka ʻokoʻa ma waena o kēia a me ka maʻi Polycystic Kidney?

Ua lohe paha ʻoe i ka Polycystic Kidney Disease (PKD). He maʻi nō hoʻi ia e hana ʻia ai nā cysts i loko o nā puʻupaʻa. No laila he aha ka ʻokoʻa ma waena o nā mea ʻelua?

ʻO ka maʻi puʻupaʻa polycystic (PKD) kahi maʻi genetic i hoʻoilina pinepine ʻia. Hoʻonui ia i nā puʻupaʻa, me nā cysts he nui e hana ana ma ke kino holoʻokoʻa. I kekahi manawa hiki i ka PKD ke alakaʻi i nā pilikia koʻikoʻi.Hiki iā ia ke hoʻoulu i nā pilikia no ke ola holoʻokoʻa. Nui ka poʻe me PKD e loaʻa i ka hāʻule ʻana o nā puʻupaʻa a pono lākou i ka dialysis e hoʻomaʻemaʻe i ko lākou koko.

Eia nō naʻe, he mea kakaikahi loa ka hāʻule ʻana o ka puʻupaʻa i ka poʻe me ka medullary sponge kidney (MSK). ʻO ia ka ʻokoʻa nui.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia maʻi? Pehea ka maʻamau o ia mea?

Ua manaʻo ʻia i kēia manawa ua kū wale kēia ʻano "medullary sponge kidney (MSK). ʻO ia hoʻi, me ke kumu ʻole. Eia naʻe, no ka mea, ʻike ʻia ia i loko o kekahi mau ʻohana, aia paha kekahi hiki ke hoʻoilina. Eia naʻe, ʻaʻole i loaʻa kahi ʻano hoʻoilina maopopo no ia mea.

ʻIke ka hapa nui o ka poʻe ua loaʻa iā lākou ka maʻi ma hope o ka ʻike ʻia ʻana o nā hōʻailona, ​​​​maʻamau i ko lākou mau makahiki 20. Ua ʻōlelo ʻia hoʻi ua ʻoi aku ka nui o ka pilikia o nā wahine ma mua o nā kāne .

He mea maʻamau loa ia, me ka awelika o hoʻokahi i loko o 5,000 poʻe i loaʻa iā MSK. Eia nō naʻe, ʻoi aku ka maʻamau i nā poʻe i loaʻa nā pōhaku puʻupaʻa. ʻO ke ʻano kēia ma waena o 12% a me 20% o ia poʻe e loaʻa paha iā MSK.

Ke kumu nei anei ka puʻupaʻa medullary sponge i ke koko kiʻekiʻe?

E noʻonoʻo paha kekahi inā ʻo kēia "MSK" ke kumu o ke koko kiʻekiʻe a i ʻole ke kaomi. Wahi a ka noiʻi o kēia manawa, ʻaʻohe hōʻike e hōʻike ana i ke "medullary sponge kidney" ke kumu o ke koko kiʻekiʻe.

He aha ke kumu o ka puʻupaʻa medullary sponge?

ʻAʻole maopopo i nā kauka ke kumu e loaʻa ai i kekahi poʻe kēia maʻi. Ua manaʻo ʻia ua hana ʻia e kahi pilikia me ka ulu ʻana o nā puʻupaʻa i ka wā fetal, i ka wā e noho ana ke pēpē i loko o ka ʻōpū .

He aha nā hōʻailona o kēia maʻi?

ʻO ka mea kupanaha, nui ka poʻe me Medullary Sponge Kidney (MSK) ʻaʻole i ʻike i kekahi mau hōʻailona . ʻO ia hoʻi, ola lākou me ka ʻike ʻole he maʻi ko lākou. He hapa liʻiliʻi wale nō, ma kahi o 10%, e loaʻa ai nā hōʻailona.

Inā loaʻa kēlā mau hōʻailona, ​​​​​​e pili pinepine lākou me nā maʻi ʻōpū mimi (UTI) a me nā pōhaku puʻupaʻa. Eia nā hōʻailona nui:

• Koko i loko o ka mimi (hematuria): ʻO ke ʻano kēia e lilo ka mimi i ʻulaʻula, i kekahi manawa ke kala o ka wai kī.
• ʻEha ʻaoʻao: ʻEha e kū ana ma nā ʻaoʻao ʻelua o kou kua, ma lalo o kou pā iwi ʻaoʻao.
• ʻEha i ka wā e mimi ai (dysuria): Hiki ke loaʻa ka wela a me ka ʻeha i ka wā e mimi ai.
• Nā pōhaku puʻupaʻa: He mea kēia i ʻike ʻia e nā poʻe he nui. Hiki ke hele mai me ka ʻeha nui o ke kua.
• Nā maʻi ʻōpū mimi: Hiki ke ʻike ʻia nā hōʻailona e like me ka mimi pinepine a me ke kuni.

Pehea e ʻike ʻia ai ka maʻi medullary sponge kidney?

Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​e hana mua kāu kauka i kahi hoʻokolokolo kino. E nīnau lākou e pili ana i kou mōʻaukala olakino, ka mōʻaukala ʻohana, a me nā hōʻailona āu e ʻike nei.

Inā kānalua kāu kauka he maʻi puʻupaʻa kou, e kauoha paha lākou i kekahi mau hoʻāʻo koko a me ka mimi . E nānā kēia mau mea:

• Aia ke koko i loko o ka mimi?
• Pehea e hana ai nā puʻupaʻa?
• Aia kekahi maʻi ʻōpū mimi?

Eia kekahi, hiki ke hana ʻia nā hoʻokolohua kiʻi kūikawā e nānā i kēlā mau cysts aʻu i ʻōlelo ai i loko o nā puʻupaʻa. ʻO nā ʻano scan maʻamau:

• CT scan: Hoʻohana kēia i nā kukuna X e hana i kahi kiʻi ʻekolu-dimensional (3D) o nā puʻupaʻa.
• ʻO ka Intravenous Pyelogram (IVP): Pili kēia i ka hoʻokomo ʻana i kahi waihoʻoluʻu kūikawā i loko o kou aʻa. A laila, lawe ʻia kekahi mau kiʻi X-ray. Kānana ʻia ka waihoʻoluʻu ma o ke koko mai nā puʻupaʻa a i loko o ka mimi, no laila e hōʻike maopopo ana nā kiʻi X-ray i ke ala o ka mimi. Hiki i kēia ke kōkua i ka ʻike ʻana i nā cysts a me nā wahi i ālai ʻia ai ka mimi.
• ʻO ke scan Ultrasound: Hoʻohana kēia i nā nalu kani e kiʻi i nā kiʻi o nā puʻupaʻa.

Pehea e mālama ʻia ai ka puʻupaʻa medullary sponge?

ʻAʻohe lāʻau lapaʻau kūikawā i kēia manawa no ke kūlana i ʻike ʻia ʻo ka medullary sponge kidney (MSK). ʻO ka mea nui o ka lāʻau lapaʻau ʻo ia ke kāohi a me ka mālama ʻana i nā maʻi urinary tract (UTIs) a me nā pōhaku puʻupaʻa.

ʻO ka lāʻau lapaʻau nui no nā maʻi ʻōpū mimi he antibiotics .

ʻO ka lāʻau no nā pōhaku puʻupaʻa e pili ana i ka nui o ka pōhaku. ʻO ka maʻamau, hele nā ​​​​pōhaku liʻiliʻi ma o ka mimi ma o lākou iho. Hiki i kāu kauka ke ʻōlelo iā ʻoe e inu i ka wai hou aku e kōkua i ka pōhaku e hele wikiwiki. Hiki iā lākou ke kuhikuhi i nā lāʻau ʻeha a me nā lāʻau lapaʻau e hoʻomaha ai i nā ʻiʻo i loko o kou mau ureters.

Pono paha ka mālama hou ʻana i nā pōhaku nui . Eia kekahi mau laʻana:

• ʻO Shock Wave Lithotripsy: He lāʻau lapaʻau ʻaʻole invasive kēia e hoʻohana ana i nā nalu haʻalulu ikehu kiʻekiʻe e wāwahi i nā pōhaku puʻupaʻa. A laila hoʻokuʻu ʻia nā ʻāpana i haki ʻia mai ke kino i loko o ka mimi.
• Ureteroscopy: Pili kēia i ka hoʻohana ʻana i kahi ʻōmole lōʻihi a lahilahi i kapa ʻia he ureteroscope e nānā i loko o kahi o ka pōhaku. Hiki ke hoʻohana ʻia kēia mea hana e wehe i nā pōhaku liʻiliʻi, a i ʻole hiki ke hoʻohana ʻia ka laser e wāwahi i nā pōhaku nui.
• ʻO ka Nephrolithotomy Percutaneous:Hoʻohana nā kauka i kēia ʻano hana ke kūleʻa ʻole nā ​​ʻano hana ʻē aʻe. Pili kēia i ka hana ʻana i kahi ʻoki liʻiliʻi ma ke kua a kuʻi i ka pōhaku puʻupaʻa ma o ia mea a huki iā ia i waho. He ʻoki kino minimally invasive nō hoʻi kēia.

Hiki ke pale ʻia ka medullary sponge kidney?

ʻO ka medullary sponge kidney (MSK) kahi maʻi hānau ʻole me ke kumu ʻike ʻole ʻia, no laila ʻaʻole hiki ke pale ʻia . Eia nō naʻe, hiki iā ʻoe ke hana i nā hana e pale aku ai i nā maʻi urinary tract (UTIs) a me nā pōhaku puʻupaʻa e hiki ke hopena mai ia mea.

Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia:

• Nā lāʻau antibiotic haʻahaʻa e pale aku i nā maʻi mimi hou.
• Hiki i nā lāʻau lapaʻau e like me ka potassium citrate a i ʻole thiazide (ʻike ʻia hoʻi he mau pila wai) ke hōʻemi i nā pae calcium i loko o ka mimi a pale i ke kūkulu ʻia ʻana o nā pōhaku puʻupaʻa.

Hiki i ka hoʻololi ʻana i kāu meaʻai ke kōkua i ka pale ʻana i nā maʻi urinary tract a me nā pōhaku puʻupaʻa:

• Kalikuma: ʻO ka loaʻa ʻana o ka nui o ka kalikuma mai kāu meaʻai e hiki ke kōkua i ka hōʻemi ʻana i ka pilikia o nā pōhaku puʻupaʻa. (Manaʻo paha kekahi poʻe e hoʻonui ka lawe ʻana i ka nui o ka kalikuma i ka pilikia o nā pōhaku, akā ʻaʻole kēia ka hihia. Pono ʻoe e lawe me ke kaulike. E kūkākūkā me kāu kauka.)
• Nā Wai: He mea nui loa ka inu ʻana i ka nui o ka wai . Hoʻoheheʻe kēia i ka mimi a hōʻemi i ka pilikia o ka hoʻokumu ʻia ʻana o nā pōhaku. Kōkua nō hoʻi ia i ka hoʻokahe ʻana i nā bacteria mai loko mai o nā puʻupaʻa. E hoʻāʻo e inu ma ka liʻiliʻi he 2-3 lita o ka wai i ka lā.
• Nā meaʻai protein kiʻekiʻe: ʻO ka hōʻemi ʻana i nā meaʻai protein kiʻekiʻe e like me ka ʻiʻo, ka iʻa, a me nā hua manu e hiki ke kōkua i ka pale ʻana i nā pōhaku puʻupaʻa.
• Paʻakai: He mea nui loa nō hoʻi ka hōʻemi ʻana i ka paʻakai i kāu meaʻai. ʻO ka ʻai nui ʻana i ka paʻakai e hoʻonui ai i ka pilikia o nā pōhaku puʻupaʻa. No laila e makaʻala i ka nui o ka paʻakai āu e hoʻohui ai i kāu meaʻai. ʻO nā mea e like me nā meaʻai i loko o ka pahu a me nā noodles koke he nui ka paʻakai.

Mea nui: E kūkākūkā mau me kāu kauka a meaʻai paha ma mua o ka hana ʻana i kekahi hoʻololi i kāu papaʻai.

He aha ka wā e hiki mai ana o kekahi me ka medullary sponge kidney?

E makaʻu paha ka poʻe he nui i ka lohe ʻana i kēia, akā hiki i ka hapa nui o ka poʻe me Medullary Sponge Kidney (MSK) ke mālama i ka hana maikaʻi o nā puʻupaʻa i ko lākou ola a pau .

Eia nō naʻe, he hapa liʻiliʻi o ka poʻe, ma kahi o 10%, hiki ke loaʻa i ka hāʻule ʻana o nā puʻupaʻa. ʻO nā kumu nui ka pinepine a me nā maʻi urinary tract (UTIs) a me nā pōhaku puʻupaʻa.

ʻO ka ʻeha mau kekahi pilikia kakaikahi e hiki ke loaʻa i nā poʻe e ulu pinepine ana i nā pōhaku puʻupaʻa. Hiki ke kāohi ʻia kēia kūlana ma ka lawe ʻana i nā hana e pale aku ai i nā pōhaku puʻupaʻa.

Hiki i ka medullary sponge kidney (MSK) ke hoʻohaʻahaʻa i nā pae calcium i loko o ke koko. Hiki i kēia ke hoʻonāwaliwali i nā iwi . Hoʻonui kēia i ka pilikia o nā maʻi e pili ana i ka iwi. Eia kekahi laʻana:

• ʻO ka Osteoporosis (kahi maʻi e lahilahi ai nā iwi a palupalu)
• ʻO ka hyperparathyroidism lua (ka hoʻokuʻu nui ʻia ʻana o nā hormones e nā kelepa parathyroid)

I mea e pale ai i kēia ʻano hōʻino iwi lōʻihi, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me ka potassium citrate.

Pehea e ola ai me ka medullary sponge kidney?

E nānā mau kāu kauka i kāu hana puʻupaʻa a hāʻawi i ka mālama kākoʻo e like me ka mea e pono ai. He mea nui e lawe i kāu mau lāʻau lapaʻau e like me ke kauoha, e hahai i kāu papaʻai, a e mālama i kāu mau manawa hoʻopaʻa . Hiki i kēia mau mea ke kōkua i ka pale ʻana i nā maʻi ʻōpū mimi a me nā pōhaku puʻupaʻa.

ʻAʻohe lāʻau lapaʻau no ka Medullary Sponge Kidney (MSK). Akā e like me kaʻu i ʻōlelo ai ma mua, nui ka poʻe me kēia maʻi ʻaʻohe o lākou mau hōʻailona, ​​a ʻaʻole ʻike kekahi iā lākou. Ke kū mai nā hōʻailona, ​​​​​​ua hoʻokumu pinepine ʻia lākou e ka maʻi urinary tract a i ʻole ka pōhaku puʻupaʻa. He mea hiki ke mālama ʻia kēia mau mea ʻelua. Hiki iā ʻoe ke pale aku i nā maʻi urinary tract a me nā pōhaku puʻupaʻa ma ka hoʻololi ʻana i kāu meaʻai a me kou nohona. Inā he mau nīnau a hopohopo paha kāu, mai kānalua e kamaʻilio me kāu kauka .

Leka Lawe-Home

ʻAe, ke lana nei koʻu manaʻo ua maopopo iā ʻoe i kēia manawa ke ʻano o ka 'Medullary Sponge Kidney' a mākou i kamaʻilio ai. E hoʻomanaʻo hou kākou i nā mea nui loa:

• He kūlana hānau kēia kahi e ulu ai nā cysts liʻiliʻi ma ka ʻaoʻao waena o nā puʻupaʻa (medulla).
• ʻAʻohe hōʻailona o ka hapa nui o ka poʻe. Inā loaʻa, no ka maʻi ʻaʻai mimi (UTIs) a i ʻole nā ​​pōhaku puʻupaʻa.
• ʻAʻohe lāʻau lapaʻau kūikawā no kēia, akā hiki ke mālama maikaʻi ʻia nā hōʻailona a me nā pilikia.
• He mea nui loa ia e pale aku i nā pōhaku puʻupaʻa a me nā maʻi ʻōpū mimi. No ka hana ʻana i kēia, e inu i ka wai he nui, e makaʻala i kāu mea e ʻai ai, a e hahai i nā ʻōlelo a kāu kauka.
• Hiki i ka hapa nui o nā kānaka ke mālama i ka hana maikaʻi o nā puʻupaʻa i ko lākou ola a pau . He mea kākaʻikahi ka hāʻule ʻana o nā puʻupaʻa.
• Inā he mau nīnau kāu e pili ana i kēia, e ʻike pono i ke kauka .

Mai hopohopo, hiki i nā poʻe he nui ke ola maʻamau a olakino me kēia maʻi!

`ʻO ka Medullary Sponge Kidney, ka maʻi Cacchi-Ricci, maʻi puʻupaʻa, nā pōhaku puʻupaʻa, nā maʻi ʻōnaehana mimi, nā cysts puʻupaʻa, ka maʻi puʻupaʻa hānau, nā cysts puʻupaʻa, nephrocalcinosis, hematuria, olakino puʻupaʻa Sinhala