Ua manaʻo paha ʻoe ua mae koke kekahi ʻaoʻao o kou helehelena, a ua huki ʻia paha ke kihi o kou waha i lalo? A i ʻole ua ʻike ʻoe i kahi pehu liʻiliʻi i loko o kou pepeiao me ka ʻeha nui? Ke noʻonoʻo nei paha ʻoe i ka mea e hana nei. I kēia lā e kamaʻilio mākou e pili ana i kahi kūlana kūikawā e hiki ai ke hana i nā hōʻailona like, akā ʻaʻole i kamaʻilio nui ʻia i loko o ke kaiāulu. ʻO ia ka Ramsay Hunt Syndrome .
He aha ka Ramsay Hunt Syndrome?
I ka ʻōlelo maʻalahi, ʻo Ramsay Hunt Syndrome kahi pilikia o nā maʻi viral e like me ka chickenpox a i ʻole herpes zoster (i ʻike ʻia hoʻi he shingles). Ua ʻike ʻia hoʻi ʻo ia ʻo Herpes Zoster Oticus a me Ramsay Hunt Syndrome type 2. Ua kapa ʻia ʻo ia ma hope o James Ramsay Hunt, he luna koa ʻAmelika a he neurologist nāna i wehewehe mua i ke ʻano i ka makahiki 1907.
Ke hoʻomanaʻo nei ʻoe i ka loaʻa ʻana o ka moa i kou wā kamaliʻi? ʻO ka maʻi e hoʻoulu ai i ka moa ua kapa ʻia ʻo ka Varicella-Zoster Virus . ʻAʻole e nalowale loa kēia maʻi ma hope o ka moa. Hiki iā ia ke moe i loko o kou mau aʻalolo no nā makahiki. I kekahi lā, no kekahi kumu (pinepine i ka wā e nāwaliwali ai kou ʻōnaehana pale), hoʻāla hou kēia maʻi moe. ʻO ia ka manawa e loaʻa ai iā ʻoe ʻo Herpes Zoster, a i ʻole shingles.
I kēia manawa, inā hoʻāla hou kēia Varicella-Zoster Virus a hoʻopilikia i kou aʻalolo maka , a laila ʻo ia ka manawa e kū mai ai kahi maʻi i kapa ʻia ʻo Ramsay Hunt Syndrome. ʻO ka mea nui e hana ʻia ma kēia, ʻo ia ka paralysis o ke aʻalolo maka, ʻo ia hoʻi ka paralysis maka a me ka ʻeha nui i ka pepeiao. Eia kekahi, hiki ke ʻike ʻia kahi ʻulaʻula ʻeha ma ka pepeiao, ka maka, a i loko paha o ka waha.
Iā wai kēia e hana nei?
ʻO ka Ramsay Hunt Syndrome, kahi maʻi e hiki ke hoʻopilikia i kekahi mea i loaʻa i ka chickenpox a i ʻole shingles, ʻo ia ka mea maʻamau i nā poʻe ma luna o 60 mau makahiki . He mea kākaʻikahi ia i nā keiki ʻōpio, akā ua hōʻike ʻia nā hihia i nā keiki ʻōpio i ʻekolu mau makahiki.
ʻO ka poʻe me nā ʻōnaehana pale kino nāwaliwali (e like me ka poʻe me ka maʻi HIV, nā maʻi kanesa, a me nā mea i loaʻa i ka hoʻoili ʻana o nā kino) ua ʻoi aku ka nui o ka pilikia o ka loaʻa ʻana o ke ʻano. ʻOi aku ka koʻikoʻi o ko lākou mau hōʻailona ma mua o ka heluna kanaka maʻamau, a ʻaʻole lākou e ola piha.
Pehea ka maʻamau o ka Ramsay Hunt Syndrome?
He ʻano maʻi laha ʻole kēia. Wahi a nā helu helu ma ʻAmelika Hui Pū ʻIa, hoʻopilikia ia ma kahi o 5 o kēlā me kēia 100,000 poʻe i kēlā me kēia makahiki.
Eia nō naʻe, manaʻoʻiʻo kekahi poʻe noiʻi no ka mea i kekahi manawa ʻaʻole i ʻike ʻia a i ʻole ua kuhihewa ʻia ka maʻi, he mea paʻakikī ke ʻōlelo pololei i ka nui o ka poʻe i loaʻa maoli iā ia.
ʻO Ramsay Hunt Syndrome ka lua o ke kumu maʻamau o ka maʻi lolo o ke aʻalolo maka, e helu ana ma kahi o 7% o nā hihia maʻi lolo o ke aʻalolo maka. ʻO Bell's Palsy ke kumu maʻamau o ka maʻi lolo o ke aʻalolo maka.
No ke aha i kū mai ai ʻo Ramsay Hunt Syndrome?
E like me kā mākou i ʻōlelo ai ma mua, ʻo ke kumu nui o ka Ramsay Hunt Syndrome ka hoʻāla hou ʻana o ka Varicella-Zoster Virus , ka mea e hoʻopilikia ai i ke aʻalolo maka, ka mea e lawe i ka manaʻo i kou maka, ke alelo, a me ka pepeiao o loko. ʻO kēia ka maʻi like e hoʻoulu ai i ka chickenpox a me ka shingles.
Ke loaʻa iā ʻoe ka maʻi puʻupuʻu i kou wā kamaliʻi, ʻaʻole e nalowale loa ka maʻi. Hiki iā ia ke moe i loko o kou mau aʻalolo no nā makahiki. Kāhea mākou i kēia maʻi he "moe." A laila, i kekahi lā, no kekahi kumu, e ala hou mai ka maʻi. ʻO ia ka manawa e loaʻa ai iā ʻoe ka herpes zoster, a i ʻole shingles. Hele ka maʻi ma nā olonā aʻalolo i ka ʻili, e hana ana i nā pehu ʻeha. I kekahi manawa, hiki i ka maʻi ke hoʻopilikia i ke aʻalolo maka, e hana ana i ka Ramsay Hunt Syndrome. ʻAʻole maopopo i nā mea noiʻi ke kumu e hoʻopilikia ai ka maʻi i ke aʻalolo maka wale nō.
He aha nā hōʻailona o kēia?
I loko o ka Ramsay Hunt Syndrome, ma muli o ka lālā o ke aʻalolo maka i hoʻopilikia ʻia, hiki iā ʻoe ke ʻike i ka nāwaliwali a i ʻole ka ʻoʻoleʻa ma kekahi ʻaoʻao o kou maka .
Nā hiʻohiʻona helehelena
- Paʻakikī i ka pani ʻana i ka maka: ʻAʻole paha ʻoe e hiki ke pani pono i ka maka ma ka ʻaoʻao i hoʻopilikia ʻia.
- ʻAʻole hiki ke ʻūmiʻi: ʻOiai inā ʻoe e hoʻāʻo e hāpai i kou lae a ʻūmiʻi, ʻaʻole paha e neʻe kēlā ʻaoʻao.
- Paʻakikī ke hōʻike ʻana i nā hiʻohiʻona helehelena: He mea paʻakikī paha ke hana i nā mea e like me ka minoʻaka a me ka ʻūʻū.
- Ke kuʻi ʻana a i ʻole ka lolo o kekahi ʻaoʻao o ka maka: Hiki i ka ʻaoʻao i hoʻopilikia ʻia o ka maka ke kuʻi i lalo, a hiki paha ke lilo i maʻi lolo loa.
- ʻŌlelo pahee: Hiki ke hoʻokiʻekiʻe ʻia ka waha i kekahi ʻaoʻao, e paʻakikī ai ke haʻi ʻana i nā huaʻōlelo.
- Paʻakikī i ka ʻai ʻana: He paʻakikī paha ke mālama i ka meaʻai i loko o kou waha a nau iā ia. Hiki paha iā ʻoe ke paʻakikī i ka moni ʻana i ka wai.
Hoʻopilikia pinepine ka Ramsay Hunt Syndrome i nā aʻalolo ma kekahi ʻaoʻao o ka maka, no laila ʻike pinepine ʻia nā hōʻailona ma kēlā ʻaoʻao o ka maka.
Nā hōʻailona e pili ana i ka pepeiao a me nā hōʻailona ʻē aʻe
Ma waho aʻe o nā hiʻohiʻona o ka helehelena, aia kekahi mau hōʻailona ʻē aʻe:
- He ʻulaʻula ʻeha a puni ka pahu pepeiao, ke kahawai pepeiao, a me ka lobe pepeiao.
- Nā pehu piha i ka wai i loko o ke kahawai pepeiao a ma waho o ka pepeiao.
- ʻEha o ke alelo, ka puʻu, a me ke kaupaku o ka waha ma ka ʻaoʻao i hoʻopilikia ʻia.
- ʻEha nui ka pepeiao.
- Tinnitus: He manaʻo o ke kani mau ʻana i loko o nā pepeiao.
- Hyperacusis: He manaʻo e kani nui ana nā leo maʻamau.
- Ka nalowale o ka lohe ma kekahi ʻaoʻao: Hiki ke emi a nalowale loa paha ka lohe ma ka pepeiao i hoʻopilikia ʻia.
- Nā maka maloʻo a me ka waha.
- Ka leo haʻalulu.
- Ka nalowale ʻana o ka ʻike o ka ʻono.
- Hopohopo pilikanaka ma muli o nā loli o ka helehelena.
Hiki i kekahi poʻe ke loaʻa i ka vertigo , ʻo ia hoʻi kahi manaʻo wahaheʻe e wili ana nā mea a puni lākou, a i ʻole e wili ana lākou iho.
He maʻi laha anei ka Ramsay Hunt Syndrome?
Aia kekahi mea nui e hoʻomaopopo ai ma ʻaneʻi. ʻAʻole laha ka Ramsay Hunt Syndrome ponoʻī. Eia nō naʻe, ʻo ka loaʻa ʻana o ke ʻano maʻi, ʻo ia hoʻi, aia ka Varicella-Zoster Virus (VZV) i loko o kou kino. Hiki ke hoʻoili ʻia kēlā maʻi i kekahi kanaka ʻē aʻe inā pili lākou me ke kahe mai nā pehu ma ka ʻili o ka mea maʻi.
Inā laha ka maʻi ma kēia ʻano, hiki i ke kanaka ke loaʻa i ka maʻi moa , ʻoiai inā ʻaʻole i loaʻa i ke kanaka ka maʻi moa ma mua a ʻaʻole paha i loaʻa i ka lāʻau pale moa. Eia kekahi, hiki i ka poʻe me nā ʻōnaehana pale i hoʻopilikia ʻia ke loaʻa i nā pilikia olakino koʻikoʻi mai ka loaʻa ʻana o kēia maʻi.
No laila, inā loaʻa iā ʻoe ʻo Ramsay Hunt Syndrome, pono ʻoe e pale i ka launa pū ʻana me kekahi mau hui o ka poʻe a maloʻo a ʻili nā pehu o kou mau ʻōpū. ʻO kēia mau mea:
* ʻO ka poʻe i loaʻa ʻole i ka maʻi moa a i ʻole ʻaʻole i loaʻa i ka lāʻau pale maʻi moa.
* Nā kānaka me nā ʻōnaehana pale maʻi nāwaliwali.
* Nā pēpē hānau hou.
* Nā wahine hāpai.
Pehea ʻoe e ʻike ai i kēia?
E hana mua kāu kauka i kahi hoʻokolohua kino e ʻike ai i ka Ramsay Hunt Syndrome. E nīnau ʻo ia e pili ana i kou mōʻaukala olakino a me nā hōʻailona, ʻoiai ke nānā ʻana i kahi ʻulaʻula a nāwaliwali paha ma kou maka.
Eia nō naʻe, no ka mea, ʻaʻole i ʻike mau ʻia nā hōʻailona o kēia maʻi i ka manawa like, hiki i kekahi manawa ke paʻakikī ke ʻike. No laila, hiki i kāu kauka ke hana i kahi hoʻokolohua hoʻokolohua e hōʻoia i ka ʻike. Hiki i kēia ke pili i ka lawe ʻana i kahi laʻana o kou lawai, kahi laʻana koko, a i ʻole kahi laʻana o ka wai mai kahi pehu a nānā iā ia ma lalo o kahi microscope e ʻike inā loaʻa iā ia ka Varicella-Zoster Virus.
ʻOiai ʻaʻole pono mau, hiki i kāu kauka ke ʻōlelo aku i kahi scan MRI (Magnetic Resonance Imaging - MRI scan) . Hiki i kēia ke kōkua i ka hōʻoia ʻana ʻaʻole i hoʻokumu ʻia kāu mau hōʻailona e kekahi maʻi ʻē aʻe.
He aha nā lāʻau lapaʻau?
Hoʻohana ʻia nā lāʻau lapaʻau like ʻole e mālama ai i ka Ramsay Hunt Syndrome.
Lapaʻau lapaʻau
Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me:
- Lāʻau lapaʻau antiviral: E mālama i ka maʻi a hōʻemi paha i nā hōʻailona. Eia kekahi laʻana, nā lāʻau lapaʻau e like me Acyclovir a i ʻole Valacyclovir .
- Corticosteroids: E hōʻemi i ka pehu ʻana o ke aʻalolo. No ka laʻana, nā lāʻau lapaʻau e like me Prednisone .
- Hoʻopau ʻeha: Hoʻēmi i ka ʻeha.
- Nā lāʻau lapaʻau no ka Vertigo: Aia nā lāʻau lapaʻau like ʻole e hiki ke hōʻoluʻolu i nā hōʻailona o ka vertigo.
- Lāʻau lapaʻau anti-seizure: Nā lāʻau lapaʻau e like me ka carbamazepine e mālama i ka ʻeha aʻalolo mau (i kapa ʻia ʻo postherpetic neuralgia ).
Nā mea hiki iā ʻoe ke hana ma ka home
Hiki iā ʻoe ke hoʻohana i kahi ʻūlū anu e hōʻemi i ka ʻeha. Eia kekahi, inā ʻaʻole hiki iā ʻoe ke pani pono i kou maka, aia kahi manawa kūpono e hōʻino ai i ka maka. Ma muli o ka wehe mau ʻana o ka maka, hiki ke hōʻino ʻia ka cornea . No kēia, hiki iā ʻoe ke kau i kahi ʻūlū maka . Hiki iā ʻoe ke hoʻohana i nā waimaka hana a i ʻole nā mea hoʻoluʻu maka e pale ai i nā maka maloʻo.
Inā ua lolo loa ka maka, hiki i ke kauka ke ʻōlelo aku i kahi hana ʻoki kino . Kōkua kēia ʻoki kino i ka hoʻomaha ʻana i ke kaomi ma nā aʻalolo maka.
ʻEhia ka lōʻihi e ho'ōla ai?
ʻO ka manawa e hoʻōla ai mai ka Ramsay Hunt Syndrome e pili ana i ke koʻikoʻi o kou maʻi lolo maka. Inā he liʻiliʻi ka pōʻino o ke aʻalolo a olakino maikaʻi ʻoe, hiki ke hoʻomaikaʻi ʻia nā hōʻailona i loko o kekahi mau pule a i kekahi mau mahina . Eia nō naʻe, hiki i ka hoʻōla piha ʻana ke hala a hiki i hoʻokahi makahiki.Hiki ke lōʻihi ka manawa. Inā koʻikoʻi ka hōʻino ʻana i ke aʻalolo maka, ʻoi aku ka haʻahaʻa o ka manawa e hoʻōla piha ai.
He mea nui loa: ʻOiai hiki i nā lāʻau antiviral ke kōkua, ʻoi aku ka kiʻekiʻe o ka manawa e hoʻōla piha ai inā hoʻomaka ʻia ka lāʻau i loko o ʻekolu lā o nā hōʻailona . Ua hōʻike ʻia ka ʻike mua ʻana a me ka hoʻomaka mua ʻana o ka lāʻau antiviral e hoʻomaikaʻi i nā hopena lōʻihi. Ma kahi o 70% o ka poʻe me Ramsay Hunt Syndrome e hoʻi hou i ka hana maka piha a kokoke paha i ka piha. Eia nō naʻe, ʻoiai me ka lāʻau mua, hiki ke loaʻa ka maʻi lolo mau loa o ka maka a i ʻole ka nalowale o ka lohe i kekahi manawa.
Hiki paha kēia ke hana hou?
ʻOiai he mea kakaikahi loa ia, e like me ka maʻi herpes zoster (shingles), hiki i ka Ramsay Hunt Syndrome ke hoʻi hou mai . ʻO kēia no ka mea e noho mau ana ka Varicella-Zoster Virus i loko o kāu ʻōnaehana nerve a mau loa aku.
He aha nā pilikia e hiki ke hana?
ʻO ka Ramsay Hunt Syndrome kahi pilikia o ka hoʻoulu hou ʻana o nā aʻalolo e hoʻoulu ai i ka ulu pono ʻole o nā aʻalolo. Hiki i kēia ke hana i nā hopena maʻamau ʻole i kekahi mau neʻe ʻana. No ka laʻana, ke minoʻaka ʻoe, e pani paha ka maka i hoʻopili ʻole ʻia.
ʻO nā pilikia ʻē aʻe paha:
- Ka hōʻino ʻana o ke kino ma muli o ka nalowale ʻana o ka neʻe ʻana o ka maka.
- Hoʻololi i ka ʻono .
- Hiki i nā ʻeha corneal, nā ʻōpala, a me nā maʻi ke hōʻino i nā maka a alakaʻi i ka nalowale o ka ʻike.
- Nā ʻūmiʻi ʻiʻo maka .
- Hopohopo pilikanaka.
Inā hoʻopilikia pū ka maʻi i nā aʻalolo ʻē aʻe i loko o kou lolo a i ʻole ke kaula kuamoʻo, hiki ke loaʻa nā pilikia hou aʻe. ʻO kēia mau mea:
- Ka huikau.
- Hiamoe.
- Nā ʻeha poʻo.
- Ka nāwaliwali i kou mau lima a me kou mau wāwae.
- ʻEha o ke aʻalolo.
Aia kekahi mau maʻi ʻē aʻe i ʻike ʻia e James Ramsay Hunt?
Ua wehewehe kekahi kauka i kapa ʻia ʻo James Ramsay Hunt ma ka liʻiliʻi he ʻekolu mau ʻano o ka maʻi. ʻO ka lua o ke ʻano a mākou e kamaʻilio nei, ʻo ia ka maʻi Ramsay Hunt type 2, ʻo ia ka mea kaulana loa o kēia. ʻOiai ua kapa ʻia nā ʻano ʻelua ʻē aʻe ma muli ona, ʻaʻole lākou e pili i kēia ʻano lua.
- ʻO ka maʻi Ramsay Hunt type 1 kahi maʻi neurological laha ʻole e hoʻoulu ai i ka hopu ʻana, ka haʻalulu, ka nalowale o ka hana o ke kino, a me ke kīnā noʻonoʻo.
- ʻO ka Ramsay Hunt syndrome type 3 kahi maʻi neurological e hoʻopilikia ai i ke aʻalolo ulnar ma ka poho lima.
ʻO ka mea nui a mākou e hoʻomanaʻo ai, ʻo ia
ʻO Ramsay Hunt Syndrome kahi maʻi e hiki ke hana ma ke ʻano he pilikia o ka herpes zoster (shingles). Hiki iā ia ke hana i nā pehu ʻeha, ka ʻeha nui, a me ka maʻi lolo o ka maka. Inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona, e ʻike koke i ke kauka. ʻO ka wikiwiki o kou ʻike ʻia ʻana a me ka mālama ʻia ʻana, ʻoi aku ka maikaʻi o kou manawa e hoʻōla piha ai.
Hiki paha iā ʻoe ke noʻonoʻo e kiʻi i ka lāʻau pale herpes zoster (shingles) e pale aku i nā maʻi ahulau i ka wā e hiki mai ana. E kamaʻilio me kāu kauka e pili ana i kēia a aʻo hou aʻe. E noho olakino!
ʻO Ramsay Hunt Syndrome, ka maʻi palupalu o ka maka, ka moa, ka herpes zoster, ka shingles, ka ʻeha pepeiao, ka maʻi viral











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