Ke luhi nei ʻoe i kekahi manawa, ka hanu pōkole, a i ʻole nā wāwae pehu? Hoʻopoina pinepine mākou i kēia mau hōʻailona, me ka manaʻo he luhi maʻamau wale nō ia a i ʻole kekahi mea e hana ʻia ke hana nui mākou. Akā i kekahi manawa, ma hope o kēia mau hōʻailona, aia paha kahi maʻi puʻuwai kakaʻikahi a ʻaʻole maʻamau. ʻO ia kekahi o nā maʻi a mākou e kamaʻilio ai i kēia lā, ʻo ia hoʻi ʻo Restrictive Cardiomyopathy (RCM) . Mai hopohopo, e kamaʻilio maʻalahi mākou e pili ana i kēia a ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.
I ka ʻōlelo maʻalahi, he aha ka Restrictive Cardiomyopathy?
He mea paʻakikī paha kēia inoa, akā e wehewehe kākou a hoʻomaopopo maʻalahi.
He ʻōkana kupaianaha ko kākou puʻuwai. He ʻehā ona keʻena nui. Ua kapa ʻia nā keʻena ʻelua o luna ʻo ka atria , a ʻo nā keʻena nui a ikaika ʻelua ma lalo ua kapa ʻia ʻo nā ventricles . Hana nā keʻena ʻelua o lalo i ka hana nui o ka pamu ʻana i ke koko ma o ko kākou kino. I mea e hana pono ai kēia hana, pono e kīkoʻo pono ʻia nā ʻiʻo i loko o nā keʻena, e hoʻopiha ʻia me ke koko, a laila e ʻūlū ikaika e hoʻokuke i ke koko i mua.
E noʻonoʻo i kahi pōpō laholio hou loa. Pehea kona palupalu? Pēlā e pono ai nā hunaola o ka puʻuwai olakino. Pono lākou e pehu maikaʻi ke komo mai ke koko, lawe i ke koko i loko, a laila e ʻūlū maikaʻi ke pono e hoʻopuka ʻia.
I loko o kahi maʻi i kapa ʻia ʻo Restrictive Cardiomyopathy , lilo nā paia ʻiʻo o kēia mau cell i paʻakikī . E like me kahi ʻāpana laholio kahiko i hoʻomaloʻo ʻia i ka lā. Ma muli o kēia paʻakikī, ʻaʻole hiki i nā cell ke kīkoʻo pono a piha i ke koko. ʻO ke ʻano kēia, ʻaʻole hiki iā lākou ke lawe i ka nui o ke koko e komo mai ana i loko o ka puʻuwai. Ke emi ka nui o ke koko e komo mai ana i loko o ka puʻuwai, emi pū ka nui o ke koko e pamu ʻia i ke kino. ʻO kēia ka pilikia nui o kēia maʻi.
No ka hui kēia maʻi o nā maʻi ʻiʻo puʻuwai i kapa ʻia ʻo Cardiomyopathy . Eia nō naʻe, ua manaʻo ʻia ʻo ia ke ʻano kakaikahi loa i waena o lākou. Ma kahi o 5% wale nō o nā maʻi Cardiomyopathy āpau e ʻeha nei i kēia maʻi.
Pehea kou manaʻo no kēia maʻi? (Nā hōʻailona)
I nā pae mua o kēia maʻi, ʻaʻole paha ʻoe e ʻike i kekahi mau hōʻailona. Akā i ka hala ʻana o ka manawa, i ka emi ʻana o ke kahe koko i ka puʻuwai, hoʻomaka nā hōʻailona o ka hāʻule ʻana o ka puʻuwai e ʻike ʻia. Hiki ke ʻike ʻia kēia mau mea i hoʻokahi manawa a i ʻole he mau manawa i ka manawa hoʻokahi.
E nānā kākou i kēlā mau hōʻailona ma ka papa ma lalo nei.
| Hōʻailona | He wehewehe maʻalahi |
|---|---|
| Ka paʻakikī o ka hanu ʻana (Dyspnea) | Hiki paha iā ʻoe ke manaʻo i ka hanu pōkole, ʻoiai ke hana nei i nā hana māmā, ka hele wāwae, a i ʻole ka moe ʻana. Hiki ke hana ʻia kēia e ka hōʻiliʻili ʻana o ka wai i loko o nā māmā ke hiki ʻole i ka puʻuwai ke pamu pono i ke koko. |
| Ka pehu ʻana o nā wāwae, nā kuʻekuʻe wāwae, a me nā wāwae (Edema) | Ma muli o ka nāwaliwali o ka hana pamu o ka puʻuwai, hoʻomaka ka wai e hōʻiliʻili ma nā ʻāpana haʻahaʻa o ke kino. Hiki iā ia ke hoʻoulu i ka pehu. |
| Luhi nui a me ka luhi (Fatigue) | Ke emi nei ka nui o ke koko e hoʻolako ana i nā ʻōkana o ke kino me ka oxygen a me nā meaʻai e pono ai lākou, no laila ke luhi mau nei ʻoe a ʻaʻole hiki ke hana i kekahi mea. |
| Nā Palpitations | Hiki paha iā ʻoe ke manaʻo e piʻi koke ana kou puʻuwai, ke kuʻi nei kou umauma, a i ʻole e manaʻo paha ʻoe ua hala kahi kuʻi. |
| Pōʻino a i ʻole ka nawaliwali | Hiki ke hana ʻia kēia kūlana e ka emi ʻana o ke kahe koko i ka lolo, ʻoiai ke kū koke ʻana. |
| ʻEha umauma | Hiki ke loaʻa ka ʻeha a me ka paʻa o ka umauma i ka wā e hoʻoikaika kino ai a i ka wā e hoʻomaha ai paha. |
ʻO ka mea nui, hiki ke ʻike ʻia kēia mau hōʻailona ma nā ʻano maʻi ʻē aʻe he nui. No laila, inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau mea, ʻo ka mea maikaʻi loa e hana ai, ʻaʻole e hopohopo a ʻike i ke kauka no ka ʻōlelo aʻo.
No ke aha e hana ai kēia? (Nā kumu)
ʻO ka hapa pinepine, ʻike ʻia ka Restrictive Cardiomyopathy ma ke ʻano he hopena ʻaoʻao o kekahi maʻi lapaʻau ʻē aʻe. ʻO ia hoʻi, hōʻino kekahi maʻi i ka ʻiʻo o ka puʻuwai a hoʻolilo iā ia i mea ʻoʻoleʻa. I kekahi manawa, ʻaʻohe kumu kikoʻī e loaʻa.
Eia kekahi o nā kumu nui:
- Amyloidosis: ʻO kēia ka wā e waiho ʻia ai kahi protein ʻano ʻē i hana ʻia e ke kino (amyloid) i loko o nā ʻōkana like ʻole, me ka puʻuwai. Ke waiho ʻia kēia protein i loko o ka puʻuwai, lilo nā paia o ka ʻiʻo puʻuwai i mānoanoa a paʻakikī.
- ʻO Sarcoidosis: He ʻano kēia e hana ʻia ai nā puʻupuʻu liʻiliʻi o nā hunaola mumū (granulomas) ma nā ʻāpana like ʻole o ke kino. Ke hana ʻia kēia mau mea i loko o ka puʻuwai, hiki iā lākou ke hōʻino i ka ʻiʻo o ka puʻuwai a hoʻopaʻakikī.
- Hemochromatosis: He kūlana kēia kahi e hōʻiliʻili ai ke kino i ka hao nui loa, hiki ke hōʻiliʻili i loko o nā ʻōpū e like me ka puʻuwai. Hiki i kēia ke hōʻino i ka puʻuwai.
- Nā maʻi pili pili: ʻO nā kūlana e like me ka scleroderma hiki ke hoʻopaʻakikī i ka ʻiʻo o ka puʻuwai.
- ʻO kekahi mau lāʻau lapaʻau maʻi kanesa: ʻO kekahi mau lāʻau anti-cancer (chemotherapy) a me ka radiation therapy hiki ke hōʻino i ka ʻiʻo puʻuwai ma ke ʻano he hopena ʻaoʻao.
Pehea e ʻike ai ke kauka i kēia?
Ke haʻi aku ʻoe i kāu kauka e pili ana i kāu mau hōʻailona, ʻo ka mea mua āna e hana ai, ʻo ia ke nānā pono iā ʻoe. E hoʻolohe lākou i kou puʻuwai, e ana i kou koko, a e nānā inā ua pehu kou mau wāwae.
A laila, ua ʻōlelo ʻia kekahi mau hoʻokolohua e hōʻoia i ka hōʻoia pololei a ʻike i ke kumu.
| Hoʻāʻo | He aha ka mea e manaʻo ʻia mai kēia? |
|---|---|
| ʻEchocardiogram | ʻO kēia ka hoʻāʻo koʻikoʻi loa. Ua like ia me ke scan ultrasound o ka puʻuwai. Hiki iā ia ke ʻike maopopo inā ua piha pono nā keʻena o ka puʻuwai i ke koko a inā ua mānoanoa a paʻakikī paha ko lākou mau paia. |
| Nā hoʻāʻo koko a me ka mimi | Hiki i kēia ke kōkua i ka loaʻa ʻana o ke kumu. No ka laʻana, hiki ke hoʻohana ʻia kahi hoʻāʻo koko e nānā i kahi maʻi e like me ka hemochromatosis. |
| X-ray umauma, CT Cardiac, MRI Puʻuwai | Hiki i kēia ʻano scan ke hāʻawi i ka ʻike hohonu e pili ana i ka nui, ke ʻano, a me ke ʻano o ka puʻuwai. |
| ʻO ka Biopsy Myocardial | I kekahi mau hihia, lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo puʻuwai a nānā ʻia ma lalo o kahi microscope. He mea nui loa kēia e hōʻoia i ke kumu pololei, e like me ka amyloidosis a i ʻole sarcoidosis. |
| Nā hoʻokolohua ʻē aʻe | Hiki nō hoʻi ke hana ʻia nā hoʻokolohua e like me ka ECG (Electrocardiogram) a me ka Exercise Stress Test inā pono. |
He aha nā lāʻau lapaʻau no kēia?
ʻAʻohe lāʻau lapaʻau kūikawā no ka Restrictive Cardiomyopathy. ʻElua mau pahuhopu nui i ka lāʻau lapaʻau:
1. Ke mālama ʻana i ka maʻi kumu i hoʻokumu ai i kēia kūlana.
2. E kāohi i nā hōʻailona e kū nei a e maʻalahi ke ola.
ʻo kahi laʻana:
- Inā loaʻa kēia maʻi i ka sarcoidosis , hiki ke hāʻawi ʻia nā lāʻau lapaʻau e like me corticosteroids no ia.
- Inā ma muli o ka hemochromatosis (hao overload), hana ʻia kahi lāʻau i kapa ʻia ʻo therapeutic phlebotomy e wehe i kekahi koko e wehe i ka hao keu mai ke kino.
- Aia i kēia manawa nā lāʻau hou no kekahi mau ʻano amyloidosis .
Eia kekahi, hiki i kāu kauka ke ʻōlelo i kēia mau mea e kōkua ai i ka hoʻokele ʻana i nā hōʻailona o ka hāʻule ʻana o ka naʻau:
- Diuretics: Ua kapa pinepine ʻia kēia mau mea he 'nā pila wai'. Kōkua lākou i ke kino e hoʻopau i ka wai keu ma o ka mimi, hiki ke kōkua i ka hōʻemi ʻana i ka pehu ʻana o nā wāwae a me ka pōkole o ka hanu.
- Nā lāʻau lapaʻau kaohi puʻuwai: Inā ʻaʻole kūpono kou puʻuwai, hiki ke hāʻawi ʻia nā lāʻau lapaʻau e like me nā beta-blockers a i ʻole nā mea pale calcium channel e kaohi iā ia.
- Nā lāʻau lapaʻau koko.
Pono paha kekahi mau maʻi me ka maʻi koʻikoʻi i kahi hoʻoili puʻuwai . Paipai pū nā kauka i ka mālama palliative , kahi e kōkua ai i ka mea maʻi e ʻoluʻolu a hōʻemi i ka ʻoluʻolu ʻole i hoʻokumu ʻia e nā hōʻailona.
Pehea lā kākou e ola ai me kēia kūlana?
He mea maʻamau ka makaʻu ke ʻike ʻoe ua loaʻa iā ʻoe kēia maʻi. Eia nō naʻe, me ka mālama lapaʻau kūpono a me nā hoʻololi liʻiliʻi i kou nohona, hiki iā ʻoe ke hōʻemi i ke kaumaha ma kou puʻuwai a ola i kahi ola maikaʻi aʻe.
Nā loli o ke ʻano o ka nohona
- Kaohi ʻana i ka paʻakai: E hōʻemi i ka nui o ka paʻakai āu e hoʻohui ai i kāu meaʻai. Hiki i ka paʻakai ke hoʻonui i ka paʻa ʻana o ka wai i loko o ke kino, e alakaʻi ai i ka pehu a me ka paʻakikī o ka hanu ʻana. He kiʻekiʻe ka paʻakai i nā meaʻai i loko o ka pahu, nā mea ʻono i kūʻai ʻia ma ka hale kūʻai, a me nā sausage.
- ʻAi olakino: E ʻai i nā mea kanu hou, nā huaʻai, a me nā meaʻai waiwai i ka fiber. E hōʻemi i nā momona holoholona, nā mea ʻono, a me nā huahana palaoa.
- Hoʻoikaika Kino: E nīnau i kāu kauka i ke ʻano o ka hoʻoikaika kino kūpono iā ʻoe. ʻAʻole paha kūpono ka hoʻoikaika kino nui, akā, ua maikaʻi pinepine ka hoʻoikaika kino māmā e like me ka hele wāwae.
- E hōʻemi i ke kaumaha: ʻAʻole maikaʻi ke kaumaha no ka puʻuwai. E hoʻomaha i kou manaʻo me nā mea e like me ka noʻonoʻo ʻana, nā hoʻomaʻamaʻa hanu, a me ke komo ʻana i kahi hana leʻaleʻa āu e makemake ai.
E hoʻomanaʻo mau e hahai pono i nā ʻōlelo a kāu kauka. E lawe i kāu lāʻau i ka manawa kūpono. Inā he mau hopohopo kāu, mai makaʻu e kamaʻilio me kāu kauka.
I ka manawa hea e pono ai ʻoe e ʻike koke i ke kauka?
Inā loaʻa iā ʻoe ka Restrictive Cardiomyopathy, aia kekahi mau hōʻailona āu e makaʻala pono ai. He pilikia paha kēia.
Inā ʻike ʻoe i kekahi o nā hōʻailona ma lalo nei, e hele koke i ka haukapila Emergency Department (ETU) kokoke loa:
- ʻEha nui a ʻeha koke paha ka umauma
- Paʻakikī koke a koʻikoʻi ka hanu ʻana
- Ka nawaliwali a nalowale paha o ka ʻike
Hiki i kēia ke lilo i mau hōʻailona o ke kaumaha nui ma ka puʻuwai, no laila ʻo ka ʻimi ʻana i ka lāʻau lapaʻau me ka hoʻonele ʻole i ka manawa hiki ke hoʻōla i ke ola.
Leka Lawe-Home
- ʻO ka Restrictive Cardiomyopathy kahi maʻi laha ʻole kahi e paʻakikī ai nā ʻiʻo o nā keʻena haʻahaʻa (nā keʻena) o ka puʻuwai a ʻaʻole hiki ke hoʻopiha pono i ke koko.
- ʻO ka paʻakikī o ka hanu ʻana, ka pehu ʻana o nā wāwae, ka luhi nui, a me ka puʻuwai kū ʻole i ka maʻamau kekahi o nā hōʻailona nui.
- ʻO ke kumu o kēia maʻi he pinepine ia he maʻi lapaʻau ʻē aʻe e like me Amyloidosis a i ʻole Sarcoidosis.
- ʻO ke kumu nui o ka mālama ʻana, ʻo ia ke kaohi ʻana i nā hōʻailona a me ka mālama ʻana i ke kumu.
- Hiki iā ʻoe ke ola i kahi ola olakino ma ka hahai ʻana i ka papaʻai haʻahaʻa paʻakai, ka hoʻoikaika kino e like me ka ʻōlelo a kāu kauka, a me ka lawe ʻana i kāu mau lāʻau lapaʻau i kuhikuhi ʻia i ka manawa kūpono.
- Inā loaʻa iā ʻoe ka ʻeha nui o ka umauma, ka paʻakikī o ka hanu ʻana, a i ʻole ka nāwaliwali, e hele koke i ka ʻOihana Pilikia (ETU) o ka haukapila.
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