I kekahi manawa, e manaʻo paha ʻoe i kahi mea e like me kahi puʻupuʻu liʻiliʻi ma kekahi wahi o kou kino. A i ʻole e manaʻo paha ʻoe i ke kani ʻana, ka ʻeha, a i ʻole kahi manaʻo ʻē. ʻO kekahi kumu o kēia mau mea he maʻi i kapa ʻia ʻo 'Schwannoma'. He ʻano paʻakikī a weliweli hoʻi ke kani o ka inoa, ʻeā? Akā, mai hopohopo. Ma kēia ʻatikala, e kamaʻilio mākou e pili ana i ke ʻano maoli o kēia, no ke aha e hana ʻia ai, he mea weliweli paha ia, a he aha ka lāʻau lapaʻau.
He aha ka Schwannoma?
I ka ʻōlelo maʻalahi, he puʻupuʻu ka schwannoma. Akā, kū mai ia mai kahi ʻano cell kūikawā i loko o ko mākou kino. Kāhea mākou iā ia he 'nā cell Schwann'.
I kēia manawa, ke noʻonoʻo nei paha ʻoe i ke ʻano o kēia mau 'Schwann cells'. E noʻonoʻo i nā aʻalolo ma loko o ko kākou kino e like me nā uea uila. Lawe kēia mau aʻalolo i nā leka mai ka lolo a i nā ʻāpana a pau o ke kino. Aia kahi ʻūpā palaki a puni kēlā uea uila no ka pale ʻana, ʻeā? Pēlā nō, loaʻa i ko kākou mau aʻalolo kahi ʻūpā a puni lākou e pale aku iā lākou a kōkua iā lākou e lawe wikiwiki i nā leka. Hana ʻia kēlā ʻūpā me nā 'Schwann cells'. No laila, no kekahi kumu, i ka wā e hoʻomaka ai kēia mau cell Schwann e ulu ma waho o ke kaohi, hana ʻia kahi puʻupuʻu ma laila. ʻO ia ka mea a mākou e kapa nei he Schwannoma.
ʻO ka nūhou maikaʻi, ʻaʻole ka hapa nui o kēia mau puʻupuʻu he maʻi kanesa (benign) . ʻO ke ʻano kēia, ʻaʻole lākou e laha i nā ʻāpana ʻē aʻe o ke kino. A ulu pinepine lākou me ka lohi loa, i kekahi manawa i nā makahiki he nui.
Akā, he mea kākaʻikahi loa, ʻo ia hoʻi, he mea kākaʻikahi loa, hiki i kēia mau mea ke lilo i maʻi kanesa (malignant). A laila kapa mākou iā lākou he 'soft tissue sarcoma'. Akā he mea kākaʻikahi loa ia. I ka 90% o nā hihia, aia kēia mau mea ma ke ʻano he puʻupuʻu hoʻokahi.
Ma hea kahi e loaʻa pinepine ai nā Schwannomas?
Hiki i kēia mau puʻupuʻu ke ulu aʻe ma nā wahi āpau o ka 'ʻōnaehana nerve peripheral', ka ʻōnaehana nerve e lawe ana i nā leka mai ko kākou lolo a me ke kaula spinal i ke koena o ke kino.
Akā aia kekahi ʻano kūikawā i ʻike pinepine ʻia. Ua kapa ʻia ʻo ia he 'vestibular schwannoma' . Ua kapa pū kekahi poʻe iā ia he 'acoustic neuroma'. Hoʻomohala kēia i loko o ke aʻalolo e hele ana mai ko mākou lolo a i ko mākou pepeiao, kahi e kōkua ai iā mākou e lohe a kaulike. ʻAʻole pinepine kēia he maʻi kanesa, a he ʻano ulu lohi.
Eia kekahi, hiki iā lākou ke ulu i loko o ke aʻalolo sciatic i ka wāwae, ka brachial plexus ma ka lima, a me nā aʻalolo ma ke kua haʻahaʻa.
He puʻupuʻu lolo anei kēia?
He nīnau kēia a ka poʻe he nui. ʻO ka pane, he nīnau paha ia a ʻaʻole paha. Aia ia i kahi o ka puʻupuʻu.
ʻO nā ʻano a mākou i ʻōlelo ai ma mua, e like me ka 'vestibular schwannoma', e kū mai ana i loko o nā aʻalolo i loko o ka lolo. ʻO ia ke kumu i manaʻo ʻia ai he puʻupuʻu lolo. Akā no ka mea hiki i ka schwannoma ke kū mai ma nā wahi āpau o ke kino, no ka laʻana, ma kahi aʻalolo ma ka lima a i ʻole ka wāwae, ʻaʻole lākou a pau he mau puʻupuʻu lolo.
He aha nā hōʻailona o Schwannoma?
Ma muli o ka ulu lohi ʻana o kēia mau puʻupuʻu, hiki iā lākou ke hala no nā makahiki me ka ʻole o ka hōʻike ʻana i kekahi mau hōʻailona. Inā ʻike ʻia nā hōʻailona, e pili ana lākou i kahi o ka puʻupuʻu a me kona nui.
Aia ma ka papa ma lalo nei kekahi o nā hōʻailona maʻamau.
| Hōʻailona | Wehewehena |
|---|---|
| He puʻupuʻu i ʻike ʻia | I kekahi manawa, hiki iā ʻoe ke ʻike i kahi puʻupuʻu liʻiliʻi ma lalo o kou ʻili, hiki ke ʻeha ke ʻomi ʻoe. |
| Ke kani ʻana a i ʻole ka manaʻo e like me nā ʻanuʻu e holo ana a puni | Ke kaomi ka puʻupuʻu ma luna o ke aʻalolo, hiki iā ʻoe ke manaʻo i kahi ʻano ʻūlū ma kahi e lawe ai ke aʻalolo i nā leka. Ma nā ʻōlelo lapaʻau, ua kapa ʻia kēia ʻo 'paresthesia'. |
| Nāwaliwali o nā ʻiʻo | No ka mea, ʻaʻole hana pono nā ʻiʻo i kāohi ʻia e nā aʻalolo, hiki iā ʻoe ke manaʻo i ka nāwaliwali ma ia wahi. Eia kekahi laʻana, he mea paʻakikī paha ke hopu i kahi mea ma kou lima. |
| ʻEha | Hiki i ke kaomi ʻana o ke aʻalolo ke hoʻoulu i ka ʻeha ʻeleʻele, ʻā, a ʻoi paha. |
Nā hōʻailona kikoʻī e ʻokoʻa ana ma muli o ka wahi o ka puʻupuʻu
- Vestibular Schwannoma: Aia kēia ma ke aʻalolo pepeiao, e hoʻonui ana i ka lohe ma kekahi pepeiao.Hiki nō. Hiki paha iā ʻoe ke ʻike i ke kani ʻana i loko o kou mau pepeiao (tinnitus), ka poniuniu, a me ka nalowale o ke kaulike.
- ʻAʻalolo Maka: Inā loaʻa kahi puʻupuʻu ma kēia wahi, hiki iā ia ke pilikia i ka ale ʻana, ka paʻakikī i ka neʻe ʻana i nā maka, nā loli i ka ʻono, a i ʻole ka maʻi lolo.
- ʻO ke aʻalolo Sciatic: Inā ulu kahi puʻupuʻu ma ke aʻalolo nui e hele ana i ka wāwae, hiki iā ia ke hana i ka ʻeha e hele ana mai ke kua i lalo o ka wāwae, e like me ka ʻeha kua a i ʻole kahi 'pilikia disc' .
No ke aha i hoʻokumu ʻia ai kēia Schwannoma?
ʻO ka ʻoiaʻiʻo, 90% o kēia mau mea e kū pinepine ʻole ana, me ke kumu ʻole . ʻAʻohe kumu i loaʻa.
Eia nō naʻe, he hapa liʻiliʻi loa paha nā kumu hoʻoilina. No ka laʻana, ʻoi aku ka nui o ka poʻe me nā kūlana hoʻoilina e like me Neurofibromatosis 2 (NF2), Schwannomatosis, a i ʻole Carney complex e ulu aʻe ma mua o hoʻokahi o kēia mau puʻupuʻu. Loaʻa i ka poʻe me kēia mau kūlana hoʻoilina kahi kīnā i nā genes e kāohi ana i ka hoʻokumu ʻana o ka puʻupuʻu i loko o ko lākou kino.
Pehea e ʻike ai ke kauka i kēia?
Ke hele ʻoe e ʻike i ke kauka me nā hōʻailona, e nānā ʻo ia iā ʻoe a, inā kānalua lākou i kēia ʻano, e kuhikuhi iā ʻoe no kekahi mau hoʻokolohua kiʻi. I kekahi manawa, hiki ke loaʻa kēia puʻupuʻu ma ka hanana i ka wā o kahi scan i hana ʻia no kekahi kumu ʻē aʻe.
ʻO nā hoʻāʻo nui i hoʻohana ʻia no kēia:
- ʻO ke kiʻi MRI (Magnetic Resonance Imaging): ʻO kēia ka hoʻāʻo maikaʻi loa a maopopo loa e ʻike ai i kahi schwannoma. Hoʻohana ia i kahi kahua magnetic a me nā nalu lekiō e lawe i nā kiʻi maopopo loa o loko o ke kino. Hiki i kahi MRI ke kōkua i ka hoʻoholo ʻana i ka wahi kikoʻī, ka nui, a me ka hopena ma nā aʻalolo kokoke.
- ʻO ke scan CT (Computed Tomography): Hoʻohana kēia i nā kukuna X-ray he nui e lawe i nā kiʻi ʻokiʻoki o ke kino. ʻOiai ʻaʻole maopopo e like me ka MRI, hiki iā ia ke kōkua i ka ʻike ʻana.
- ʻO ke scan Ultrasound: Hoʻohana ʻia kēia e ʻimi i nā mea e like me nā ʻōpū liʻiliʻi, ʻoi aku hoʻi ma lalo o ka ʻili.
- Biopsy: I kekahi manawa, hoʻoholo paha ke kauka e lawe i kahi ʻāpana liʻiliʻi o ka puʻupuʻu me kahi nila a nānā iā ia. Ua kapa ʻia kēia he 'biopsy'. E hōʻoia kēia i ka 100% inā he schwannoma maoli ia a inā paha he mau hunaola kanesa.
He aha nā lāʻau lapaʻau no kēia?
Aia ka lāʻau lapaʻau i kekahi mau kumu. E noʻonoʻo kāu kauka i nā mea e like me kahi o ka puʻupuʻu, kona nui, pehea ka wikiwiki o kona ulu ʻana, a me kāu mau hōʻailona.
ʻEkolu mau koho lapaʻau nui.
1. Nānā (Nānā / "E Nānā a Kali")
Inā ʻaʻole he maʻi kanesa ka puʻupuʻu, e ulu mālie ana, a ʻaʻohe ou hōʻailona hoʻopilikia, e ʻōlelo paha kāu kauka, "E kali wale kākou a ʻike." ʻO ia hoʻi, e hana ʻo ia i nā mea e like me nā scan MRI i nā manawa maʻamau e ʻike ai inā e loli ana ka nui o ka puʻupuʻu. Inā hoʻomaka ka puʻupuʻu e ulu a inā he mau hōʻailona kāu, a laila e hoʻomaka lākou e mālama iā ia.
2. Wehe ʻoki kino (ʻoki kino)
Inā ulu wikiwiki ka puʻupuʻu a inā paha e hoʻopilikia nei nā hōʻailona iā ʻoe, hiki i kāu kauka ke ʻōlelo aku i ke ʻoki kino e wehe iā ia. ʻOiai ke ulu nei kēia mau puʻupuʻu i loko o ka ʻūpā a puni ke aʻalolo, ʻo ka hapa nui o ka manawa hiki ke wehe loa ʻia ka puʻupuʻu me ka ʻole o ka hōʻino ʻana i ke aʻalolo . Eia nō naʻe, i nā hihia e like me 'vestibular schwannoma', aia kahi pilikia o kekahi pohō lohe ma hope o ke ʻoki kino.
3. Hoʻōla Lapaʻau
Ua kapa ʻia kēia he stereotactic radiosurgery (SRS) . Pili kēia i ka hoʻohana ʻana i kahi nui o nā kukuna radiation i kuhikuhi pono ʻia e luku i ka puʻupuʻu. Ua like ia me ke ʻoki kino, akā me ka ʻole o ka hoʻohana ʻana i ka pahi. Hiki i kāu kauka ke paipai i kēia lāʻau lapaʻau inā aia ka puʻupuʻu ma kahi paʻakikī a pilikia paha no ke ʻoki kino (no ka laʻana, kokoke i nā kīʻaha koko koʻikoʻi a i ʻole nā aʻalolo).
ʻO ka mea nui loa, ʻo ia ke koho ʻana o kāu kauka a me kāna hui lapaʻau i ka lāʻau lapaʻau kūpono loa iā ʻoe. No laila, e kamaʻilio me lākou e pili ana i nā nīnau a hopohopo paha āu e loaʻa ai.
Pehea ke kūlana ma hope o ka mālama ʻana?
I ka hapanui o nā hihia, maikaʻi loa ka wānana ma hope o ka mālama ʻana. ʻOiai inā ua wehe loa ʻia ka puʻupuʻu, haʻahaʻa loa ka manawa e hoʻi hou mai ai.
Eia nō naʻe, ʻo ka nui o nā pilikia e hiki mai ana ma hope o ke ʻoki ʻana e pili ana i nā kumu penei:
- Inā nui ka puʻupuʻu
- Inā aia ka puʻupuʻu i loko o ke kino
- Inā aia ka puʻupuʻu ma ke aʻalolo ulnar, he aʻalolo nui ma ka lima
Eia naʻe, ma keʻano holoʻokoʻa, maikaʻi loa ka prognosis no ka schwannoma.
ʻAʻole anei hiki ke pale ʻia kēia?
ʻO ka mea pōʻino, ʻaʻohe ala e pale aku ai i ka hoʻokumu ʻana o nā schwannomas, no ka mea, e like me kā mākou i ʻōlelo ai ma mua, hana pinepine lākou me ka ʻole o ke kumu.
Eia nō naʻe, inā ʻike ʻoe he maʻi genetic ko kekahi o kou ʻohana e like me ka neurofibromatosis 2 (NF2), he manaʻo maikaʻi e kamaʻilio me kāu kauka e pili ana i ia mea. Hiki paha iā ia ke kuhikuhi iā ʻoe no ke aʻoaʻo genetic.
Leka Lawe-Home
- He puʻupuʻu ka schwannoma e ulu ana mai nā pūnaewele Schwann e uhi ana i nā aʻalolo. ʻAʻole ka hapa nui o kēia mau mea he maʻi kanesa (benign) .
- Aia nā hōʻailona ma kahi o ka puʻupuʻu. Aia paha he puʻupuʻu, ʻūlū, ʻeha, a nāwaliwali paha nā ʻiʻo. ʻO ke ʻano e ulu pinepine a puni ka pepeiao hiki ke hoʻopilikia i ka lohe a me ke kaulike.
- ʻAʻole pono mau ka lāʻau lapaʻau. Aia kekahi mau koho e like me ka nānā ʻana i ka puʻupuʻu, ka wehe ʻana i ke ʻoki kino, a i ʻole ka radiation therapy.
- Ma keʻano holoʻokoʻa, maikaʻi loa ka prognosis ma hope o ka mālama ʻana.
- Inā ʻike ʻoe i kahi puʻupuʻu hou ma kou kino, a inā he ʻeha mau a ʻoluʻolu ʻole paha kou ma kekahi wahi, mai hoʻowahāwahā iā ia a e ʻike koke i kāu kauka . Mai hopohopo, ʻaʻole paha he mea koʻikoʻi, akā he mea nui e nānā ʻia.











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