Ua ʻike mākou a pau ua hoʻonohonoho ʻia nā ʻāpana koʻikoʻi o ko mākou kino, e like me ka puʻuwai, nā māmā, ke akepaʻa, a me ka ʻōpū, ma kekahi ʻano. ʻO ka maʻamau, ua hoʻonohonoho ʻia kēia mau ʻāpana ma nā ʻaoʻao like, ma ke ʻano like, e like me nā mea ʻē aʻe a pau. Akā, ua manaʻo paha ʻoe, he mea kakaikahi loa, hiki ke hoʻohuli loa ʻia nā ʻāpana o ke kanaka i lalo, e like me ke kiʻi aniani? I kēia lā, e kamaʻilio mākou e pili ana i kēlā ʻano ʻē, akā ʻo ka hapa nui o ka manawa he mea ʻino ʻole. Ua kapa ʻia kēia (Situs Inversus) i ka ʻepekema lapaʻau.
He aha kēia (Situs Inversus)? E hoʻomaopopo maʻalahi kākou.
I ka ʻōlelo maʻalahi, ʻo Situs Inversus kahi maʻi genetic laha ʻole kahi e kū pono ai nā ʻōpū o kou umauma a me kou ʻōpū, e like me ke kiʻi aniani, ma mua o ke kino kanaka maʻamau.
E nānā kākou i ke ʻano o ko kākou mau kino. Hoʻomohala ʻia kēlā me kēia ʻano kino ma ke ʻano hema-ʻākau. Kāhea mākou i kēia kūlana maʻamau (Situs Solitus) . No ka laʻana, ua hoʻohuli ʻia ka piko o ka puʻuwai i ka hema, ke akepaʻa i ka ʻākau, ka ʻōpū a me ka spleen i ka hema.
Eia nō naʻe, ʻo ke kū'ē loa kēia no kekahi me (Situs Inversus) . ʻO ia hoʻi:
- Hiki ke loaʻa ka atrium hema o ka puʻuwai a me ka māmā hema ma ka ʻaoʻao ʻākau o ka umauma.
- Inā ʻoe e nānā i ka ʻōpū, aia paha ke akepaʻa a me ka ʻōpū ma ka ʻaoʻao hema ma kahi o ka ʻākau.
- Aia paha ka ʻōpū a me ka ʻōpū ma ka ʻaoʻao ʻākau ma kahi o ka hema.
Ke hoʻohuli ʻia ke kino holoʻokoʻa ma kēia ʻano, ua kapa ʻia ʻo ia ʻo (Situs Inversus Totalis) . Hiki i kēia ke hana hoʻokahi me ka ʻole o nā pilikia ʻē aʻe. Eia nō naʻe, i kekahi manawa ʻike ʻia kēia ʻano me nā kīnā hānau ʻē aʻe a i ʻole me kahi hui pū ʻana o nā hōʻailona (syndrome). ʻO (Situs Inversus) ka mea maʻamau i waena o ka poʻe me ke ʻano i kapa ʻia ʻo (Primary Ciliary Dyskinesia) . Eia kekahi, ma kahi o 5% a 10% o ka poʻe me (Situs Inversus) hiki ke loaʻa nā kīnā puʻuwai hānau (Congenital Heart Defect) .
He aha nā ʻano nui o Situs Inversus?
ʻElua ʻano nui o Situs Inversus . ʻO lākou kēia:
1. Dextrocardia me Situs Inversus: ʻO kēia ka manawa e kū pono ana ka piko o kou puʻuwai i ka ʻaoʻao ʻākau o kou umauma. Ke kū pono nei hoʻi ke koena o kou mau kino i kekahi ʻaoʻao.
2. Levocardia me Situs Inversus: Ma kēia ʻano, kuhikuhi pinepine ʻia ka piko o ka puʻuwai i ka hema. Eia nō naʻe, ua hoʻohuli ʻia nā ʻāpana ʻē aʻe o ka ʻōpū i kēlā ʻaoʻao. He ʻano kakaikahi iki kēia ʻano, a ʻoi aku ka nui o ka hele pū ʻana me nā maʻi puʻuwai ʻē aʻe.
Ma waho aʻe o kēia, inā he ʻano ʻē aʻe i ka ulu ʻana o nā ʻōpū ma ka ʻaoʻao hema a ʻākau paha, ua kapa ʻia ia (Situs Ambiguous).ʻO ka mea e hana ʻia ma kēia hihia, ʻoiai ua kau ʻia kekahi mau ʻōkana ma ke ʻano ʻē, ʻaʻole ia e hahai i kahi ʻano maopopo. ʻO ia hoʻi, hiki ke kau ʻia nā ʻōkana ma ke ʻano haunaele iki ma nā wahi.
Pehea ka maʻamau o kēia ʻano (Situs Inversus)?
ʻAʻole ʻo Situs Inversus kahi maʻi maʻamau loa. Ua hōʻike ʻia e pili ana i hoʻokahi i loko o 10,000 mau kānaka. Eia kekahi, ʻoi aku ka maʻamau o kēia maʻi i nā kāne ma mua o nā wahine.
Pehea e hana ʻia ai kēia (Situs Inversus)?
ʻO ke kumu nui o Situs Inversus ka loli ʻana o nā genes, i kapa ʻia ʻo ka mutation genetic . Aia kekahi mau ʻano genes e kōkua i nā ʻōkana o ko mākou kino e kau ʻia ma nā ʻaoʻao kūpono. Hoʻokumu ʻia ʻo Situs Inversus e kahi mutation i loko o hoʻokahi a ʻoi aku paha o kēia mau genes. Ua ʻike nā kānaka ʻepekema a hiki i kēia manawa ma mua o 100 mau genes e hiki ke hana i nā hemahema i ka hoʻoholo ʻana i nā ʻaoʻao o ke kino. No ka laʻana, hiki ke kapa ʻia nā genes e like me `(ANKS3)`, `(NODAL)`, `(DNAH9)`.
Ua hoʻoilina ʻia kēia maʻi ma ke ʻano autosomal recessive . ʻO ke ʻano kēia, no ke keiki e loaʻa i kēia maʻi, pono nā mākua ʻelua e hoʻoilina i ka gene mutated. I ka ʻōlelo maʻalahi, pono nā mākua ʻelua e lawe i kēia gene, akā ʻaʻole paha lākou e loaʻa i ke ʻano (Situs Inversus) .
No ke aha i loaʻa ai ka Situs Inversus? He aha nā kumu pilikia?
ʻOiai ke kumu kikoʻī o Situs Inversus he genetic, aia kekahi mau mea pilikia e hiki ke kōkua i ia. Eia nā mea:
- Loaʻa kahi moʻolelo ʻohana o ka maʻi puʻuwai hānau (pili i ka biologically).
- Loaʻa kahi moʻolelo ʻohana o nā ʻano maʻi ʻole cardiac (pili biologically).
- Loaʻa i ka makuahine ka maʻi diabetes mellitus .
- Ke hoʻohana nei i kekahi mau mea hoʻopau ʻū i ka wā hāpai.
- Ka hoʻohana ʻana i nā huahana paka (e like me nā cigarette) i ka wā hāpai.
- Loaʻa kahi pae haʻahaʻa socioeconomic.
He aha nā hōʻailona o ka Situs Inversus?
He mea kupaianaha ka nui o ka poʻe me Situs Inversus ʻaʻohe o lākou mau hōʻailona! ʻAe, inā paha e huli hewa ana kou mau kino, inā e hana pono ana lākou, hiki iā ʻoe ke hele i kou ola holoʻokoʻa me ka ʻole o ka ʻike ʻana i kekahi ʻokoʻa a i ʻole nā pilikia. ʻAʻole paha ʻoe e ʻike he maʻi kou.
Eia nō naʻe, inā loaʻa iā ʻoe kekahi maʻi a kūlana paha me Situs Inversus , hiki ke ʻike ʻia nā hōʻailona e pili ana i kēlā maʻi. Eia kekahi laʻana:
- Inā he mau kīnā puʻuwai kou, hiki iā ʻoe ke loaʻa nā pilikia e pili ana i ka puʻuwai (e like me ka paʻakikī o ka hanu ʻana, ka ʻeha o ka umauma).
- Inā loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo Primary Ciliary Dyskinesia , hiki i ka mucus ke hōʻiliʻili i loko o nā māmā a hoʻoulu i ka bronchitis mau loa.Hiki ke loaʻa ka bronchitis mau (ka ʻū mau, ka phlegm) a me ka sinusitis ( ka maʻi sinus).
ʻO ka Ciliary Dyskinesia mua he kūlana wale nō ia kahi e hana pono ʻole ai nā ʻano lauoho lahilahi (cilia) i loko o ko kākou mau ala ea. ʻO kā lākou hana ka hoʻokuke ʻana i nā mea e like me ka mucus i luna a i waho o nā māmā. Ke hana ʻole kēia mau mea, hōʻiliʻili ka mucus a hoʻoulu i nā maʻi.
Pehea e ʻike ʻia ai ka Situs Inversus?
I ka manawa pinepine, e ʻike koke kāu kauka iā Situs Inversus i ka wā e mālama ʻia ai ʻoe no kekahi maʻi ʻē aʻe.
I kekahi manawa, ke hoʻolohe kāu kauka i kou puʻuwai (me ka stethoscope), kānalua paha ʻo ia i kēia kūlana. ʻO ka puʻuwai o ke kanaka maʻamau ka mea i lohe maopopo ʻia ma ka ʻaoʻao hema o ka umauma, kokoke i ka wahi haʻahaʻa loa o ka puʻuwai. Akā inā loaʻa iā ʻoe ka dextrocardia (ka puʻuwai i huli i ka ʻaoʻao ʻākau ) me Situs Inversus , ʻo ka puʻuwai ka mea i lohe maopopo ʻia ma ka ʻaoʻao ʻākau o ka umauma.
Hoʻohana nā kauka i nā hoʻokolohua kiʻi like ʻole e hōʻoia i ka hōʻailona a hoʻoholo pono i nā ʻōpū i hoʻopilikia ʻia. ʻO kēia mau mea:
- Hoʻokolohua X-ray (X-ray)
- ʻO ke kiʻi ʻana o ka ultrasound
- CT scan (Computed Tomography - CT scan)
- MRI scan (Magnetic Resonance Imaging - MRI scan)
Hiki i kēia mau hoʻokolohua ke ʻike maopopo i ke ʻano o ke kau ʻana o nā ʻōpū.
Pehea e mālama ʻia ai ka Situs Inversus?
ʻOiai ʻaʻole ʻike ka hapa nui o ka poʻe he Situs Inversus ko lākou, a ʻaʻole ia e hōʻike i kekahi mau hōʻailona a pilikia paha, ʻaʻole ia e koi i kekahi lāʻau lapaʻau kikoʻī. ʻOiai inā hewa kou mau kino, inā e hana pono ana lākou, ʻaʻole pono ʻoe i ke ʻoki kino e hoʻihoʻi iā lākou i ka ʻaoʻao ʻākau.
Eia nō naʻe, inā he maʻi a maʻi ʻē aʻe kāu e pili ana i kēia ʻano, e mālama kāu kauka i kēlā mau hōʻailona.
He mea nui loa kēia: Inā ʻike ʻoe he Situs Inversus kou, he mea nui e hoʻomaopopo i kāu mau kauka a pau.
E noʻonoʻo i kēia ʻano. ʻO ka maʻamau, ʻo ka appendicitis ke kumu o ka ʻeha ma ka ʻaoʻao ʻākau haʻahaʻa o kou ʻōpū. Akā inā aia kāu appendix ma kēlā ʻaoʻao, hiki iā ʻoe ke ʻeha ma ka ʻaoʻao hema haʻahaʻa o kou ʻōpū. Inā ʻaʻole ʻike kāu kauka i kou kūlana Situs Inversus , hiki iā ia ke manaʻo ʻaʻole ka ʻeha ma kou ʻaoʻao hema he appendicitis, a hiki ke hoʻopaneʻe i ka mālama ʻana i ka pilikia. Hiki i kēia ke lilo i pilikia nui.
No laila, inā loaʻa iā ʻoe kekahi maʻi i ka wā e hiki mai ana, he mea nui loa kēia ʻike no nā kauka e hana i kahi hōʻailona pololei. Eia kekahi, he mea nui e ʻike nā kauka āpau i kou kūlana ma mua o ka hana ʻana i kekahi ʻoki kino a i ʻole kekahi hana lapaʻau ʻē aʻe. I ka hana ʻana i ke ʻoki kino ma kekahi me (Situs Inversus) , pono paha nā kauka ʻoki kino e lōʻihi a hoʻolālā paha i kahi ʻokoʻa.
Hiki ke pale ʻia ka Situs Inversus?
Hoʻokumu ʻia ka Situs Inversus e kahi loli genetic kakaikahi. No laila, ʻaʻohe mea hiki iā mākou ke hana i kēia manawa e pale aku ai i kēia maʻi.
He aha ke kūlana o ke ola o kekahi me ka (Situs Inversus)?
Hiki i ka hapa nui o ka poʻe me Situs Inversus ke manaʻo e ola i kahi ola maʻamau. ʻAʻole paha ʻoe e ʻike he maʻi kou, a hiki iā ʻoe ke ola me ka ʻole o nā hōʻailona a i ʻole nā pilikia. Eia nō naʻe, inā pili kou maʻi me kahi pilikia olakino ʻē aʻe a kīnā paha, e hilinaʻi kāu prognosis i ke kūlana kumu a me kāna mālama ʻana.
Hiki i nā kānaka me Situs Inversus ke hāpai?
ʻAe, hiki i nā wahine me Situs Inversus ke hāpai maʻamau a hoʻopau i kā lākou hāpai ʻana me ka ʻole o nā hanana kūikawā. ʻAʻole kēia kūlana e hoʻopilikia i ka hāpai ʻana.
He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?
Ke ʻike ʻoe he Situs Inversus kou, nui paha kāu mau nīnau. He mea maʻamau kēlā. Hiki iā ʻoe ke nīnau i kāu kauka e like me:
- "No ke aha i huli ai koʻu mau ʻāpana kino penei?"
- "Ua loaʻa iaʻu ka Pūnaewele Inversus Totalis a i ʻole ʻo Situs Inversus Ambiguous ?"
- "Ua pili anei koʻu kūlana (Situs Inversus) i kekahi maʻi a kīnā paha?"
- "Pono anei iaʻu kekahi hana kūikawā no kēia?"
- "He aha kaʻu mea e makaʻala nui ai i ka wā e hiki mai ana?"
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)
No laila, ʻo (Situs Inversus) kahi maʻi genetic laha ʻole kahi e kau ʻia ai nā ʻōpū o ko kākou kino, aia ma ka umauma a me ka ʻōpū, ma ke ʻaoʻao ʻē aʻe mai ko lākou kūlana maʻamau, e like me ke kiʻi aniani. Ke lohe ʻoe i kēia, e hopohopo iki paha ʻoe, "Auē, ʻaʻole i kūpono koʻu mau ʻōpū?" Akā, i ka hapanui o nā hihia, ʻaʻole kēia e hōʻeha.
ʻAʻole paha ʻoe e loaʻa i kekahi mau hōʻailona, a hana maʻamau paha kou mau kino. I kekahi manawa hiki ke pili kēia ʻano me nā pilikia olakino ʻē aʻe. Inā pēlā, e mālama kāu kauka i kēlā ʻano. Eia nō naʻe, ʻaʻohe lāʻau lapaʻau kikoʻī e pono ai no ke ʻano ponoʻī, i kapa ʻia ʻo Situs Inversus .
ʻO ka mea nui loa, ʻo ia ka hoʻomaopopo ʻana i kāu mau kauka a me nā mea lawelawe olakino a pau he Situs Inversus kou. He mea nui paha kēia ʻike no ka ʻike pololei a me ka mālama palekana.
No laila, he mea nui e makaʻala i kēia. Inā he mau nīnau hou aku kāu e pili ana i kēia, mai kānalua e kamaʻilio me kāu kauka.
ʻO Situs Inversus, Situs Inversus, Nā kino ma kēlā ʻaoʻao, Nā maʻi genetic, Puʻuwai ma ka ʻākau, Dextrocardia, Levocardia, Ciliary Dyskinesia mua, Nā maʻi puʻuwai hānau











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