I kekahi manawa loaʻa iā ʻoe nā puʻupuʻu liʻiliʻi a me nā puʻupuʻu ma kou kino holoʻokoʻa, ʻeā? ʻO ka hapa nui o ka manawa, ʻaʻole mākou e nānā nui iā lākou. Manaʻo mākou, "He cyst wale nō paha kēia" a i ʻole "He puʻupuʻu momona paha." Akā i kekahi manawa he mea maikaʻi ke hopohopo iki e pili ana i nā mea e like me kēia. I kēia lā, e kamaʻilio mākou e pili ana i kahi ʻano puʻupuʻu kakaʻikahi loa, akā he mea nui loa e makaʻala. Kāhea mākou i kēia mau Solitary Fibrous Tumors (SFTs) .
He aha maoli ka Solitary Fibrous Tumor (SFT)?
I ka ʻōlelo maʻalahi, ʻo SFT kahi ʻano puʻupuʻu e hana ʻia ana i loko o nā ʻiʻo palupalu o ko mākou kino. ʻOiai hiki iā lākou ke hana ma nā wahi āpau o ke kino, ʻike pinepine ʻia lākou i loko o ka uhi pale a puni ko mākou mau māmā.
ʻElua ʻano o kēia mau nati SFT.
1. Lohi loa ka ulu ʻana o kekahi a ʻaʻole e laha i nā wahi ʻē aʻe (ʻaʻole maʻi kanesa - benign) .
2. ʻO ke ʻano ʻē aʻe he maʻi kanesa/malignant, kahi e ulu wikiwiki loa a hiki ke laha i nā ʻāpana ʻē aʻe o ke kino .
ʻO ka mea nui, ʻo ka hapa nui o kēia mau puʻupuʻu SFT ʻaʻole ia he maʻi kanesa . Eia nō naʻe, ʻōlelo nā kauka he mea maikaʻi ke wehe ʻana i kēia mau puʻupuʻu, ma o ke ʻoki ʻana a i ʻole nā ʻano lapaʻau ʻē aʻe.
He aha ka inoa o kēia i ka wā kahiko?
I ka wā ma mua, ua manaʻo nā kauka ua ulu wale kēia mau puʻupuʻu i loko o ka lua o ka umauma. ʻO ia ke kumu i kapa ʻia ai lākou he "benign fibrous tumors of the pleura." Maanei, ʻo `(pleura)` e pili ana i ka membrane lahilahi e uhi ana i loko o ko mākou paia umauma a pale i ko mākou mau māmā. Hoʻopuka pū kēia membrane i ka lubricant e pono ai ko mākou mau māmā e neʻe maʻalahi i ka wā e hanu ai mākou.
Akā i kēia manawa ua ʻike mākou hiki i kēia mau puʻupuʻu ke ulu i nā wahi āpau o ke kino, ʻaʻole wale ma ka umauma, e like me ke akepaʻa, ka lolo, a me ka ʻāʻī. No laila, ʻaʻole hoʻohana nui ʻia kēlā inoa kahiko.
He ʻelua mau mea like ʻole ʻo SFT a me Pleural Mesothelioma?
ʻAe, he ʻelua kūlana ʻokoʻa loa kēia.
- ʻO ka Mesothelioma Pleural: He maʻi ʻaʻai kēia e ulu ana i loko o ka ʻili o nā māmā (pleura). ʻO ke kumu nui o kēia, ʻo ia ka hanu ʻana i ka asbestos .
- ʻO ka Solitary Fibrous Tumor (SFT): ʻAʻohe pili o kēia mau SFT me ka asbestos. ʻAʻole lākou e lilo i maʻi kanesa. Eia kekahi, ʻaʻole e like me ka mesothelioma, hiki i nā SFT ke ulu ma nā wahi āpau o ke kino. ʻAʻole ʻike ʻia ke kumu pololei o nā SFT .
ʻO wai ka mea i ʻoi aku ka pilikia o ka hoʻomohala ʻana i kēia mau tumors?
Hiki i ka SFT ke ulu i kēlā me kēia makahiki, akā ʻoi aku ka maʻamau i nā poʻe ma waena o 50 a me 60 mau makahiki.I waena o ka poʻe ʻelemakule, he mea kakaikahi loa kēia ʻano maʻi i waena o nā keiki ʻōpio. ʻO ka ʻoiaʻiʻo, ʻoi aku ka liʻiliʻi ma mua o 2% o nā puʻupuʻu palupalu i hōʻike ʻia he SFTs.
He aha ke kumu o ka SFT?
ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia, akā manaʻoʻiʻo nā kānaka noiʻi ua hui pū ʻia ʻelua o kā mākou mau genes , ʻo NAB2 lāua ʻo STAT6 . ʻO ka manaʻo o kēia manawa, hiki i kēia gene i hoʻololi ʻia ke hoʻonui i ka pilikia o ka hoʻomohala ʻana i ka SFT.
He aha nā hōʻailona e hana ai ʻo SFT?
ʻO kēia mau puʻupuʻu SFT e ulu lohi loa ana. No laila , ʻo ka hapalua o ka poʻe me SFT ʻaʻohe o lākou hōʻailona . Hoʻomaka wale nā hōʻailona e ʻike ʻia ma hope o ka ulu ʻana o ka puʻupuʻu i lawa ka nui e paʻi i nā ʻōpū kokoke, nā iwi, a i ʻole nā ʻiʻo ʻē aʻe.
ʻOkoʻa nā hōʻailona ma muli o kahi o ka puʻupuʻu. E nānā kākou pehea e hana ai.
| Kahi o ka puʻupuʻu a me nā hōʻailona hiki ke loaʻa | |
|---|---|
| I loko o ka lua o ka umauma (mama, pleura) |
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| Ma ka ʻāpana o ka lua maka |
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| E pili ana i nā lua ihu a me nā sinus |
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| Pili i ka lolo |
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| Pili i ke kaula kuamoʻo |
|
| Pili i ke akepaʻa |
|
| Pili i ka thyroid |
|
Pehea e ʻike ai ke kauka he SFT kēia?
ʻOkoʻa nā hoʻokolohua ma muli o kāu mau hōʻailona a me kahi i manaʻo ʻia o ka puʻupuʻu. ʻO nā hoʻokolohua nui:
- Hoʻokolokolo maka: Inā he mau pilikia ʻike maka kou, hiki i nā hoʻokolohua kūikawā e like me ka Optical Coherence Tomography (OCT) ke kōkua i ka hoʻoholo ʻana i ke kumu o kou mau pilikia maka.
- Nā Kiʻi Kiʻi: Hiki ke hana ʻia kahi X-ray, CT scan, MRI scan, Ultrasound scan , a i ʻole PET scan e ʻike pono i kahi o ka puʻupuʻu a me kona nui.
- Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi a paʻa loa . Lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka puʻupuʻu a nānā ʻia ma lalo o kahi microscope. Hiki i kēia ke hōʻoia 100% inā he maʻi kanesa ka puʻupuʻu a ʻaʻole paha.
Ka hoʻokaʻawale ʻana o ka ʻAhahui Ola Honua (WHO)
Ua hoʻokaʻawale ka World Health Organization (WHO) i nā ʻōpū SFT i nā pae ma muli o ko lākou koʻikoʻi. Pili kēia pae i ka wikiwiki o ka ulu ʻana o ka ʻōpū, ma muli o ke ʻano o nā ʻāpana ma lalo o ka microscope. He ʻokoʻa kēia mai nā pae o ke kanesa.
- Papa I (Papa Haʻahaʻa): ʻO kēia nā ʻano ʻoi aku ka liʻiliʻi o ka huhū. ʻO ka hapa nui o nā pūnaewele e like me nā pūnaewele maʻamau. Ulu lohi loa lākou. ʻAʻole paha lākou e hōʻike i kekahi mau hōʻailona.
- Papa II (Papa Waena): ʻOi aku ka ʻano ʻē o nā pūnaewele ma kēia papa ma mua o nā mea ma ka Papa I. No laila, ʻoi aku ka kiʻekiʻe o ka ulu ʻana. ʻOi aku ka kiʻekiʻe o ka manawa e lilo ai i maʻi ʻaʻai.
- Papa III (Pae kiʻekiʻe): Aia i loko o kēia mau mea nā pūnaewele ʻano ʻē loa. He ʻino kēia mau puʻupuʻu, ulu koke, a ʻoi aku ka nui o ka hoʻi ʻana mai ma hope o ka mālama ʻana, lilo i maʻi ʻaʻai, a laha i nā ʻāpana ʻē aʻe o ke kino.
He aha nā lāʻau lapaʻau no SFT?
ʻO ke ʻoki kino ka lāʻau lapaʻau nui a maikaʻi loa no kahi puʻupuʻu SFT. E ho'āʻo ke kauka e wehe i ka puʻupuʻu holoʻokoʻa ma ke ʻoki kino.
I kekahi mau hihia, ʻaʻole hiki ke hana ʻoki kino ma muli o ka wahi o ka puʻupuʻu. I ia mau hihia, hāʻawi ʻia ka radiation therapy e hoʻēmi i ka puʻupuʻu a luku iā ia. I kekahi manawa, hāʻawi ʻia ka radiation therapy ma mua o ke ʻoki kino e wāwahi i ka puʻupuʻu a maʻalahi ka wehe ʻana.
He aha nā pilikia e hiki mai ana o SFT?
ʻO ka makaʻu nui loa no kekahi me ka SFT, ʻo ia ka lilo ʻana i maʻi kanesa a i ʻole e laha aku i nā wahi ʻē aʻe (maʻi kanesa metastatic). Hiki ke hoʻemi nui ʻia kēia pilikia ma o ke ʻoki ʻana e wehe i ka puʻupuʻu.
Eia nō naʻe, ʻoiai ma hope o ka mālama ʻana, i kekahi manawa hiki i kahi puʻupuʻu SFT ke 'hoʻi hou' . ʻOi aku ka nui o ka manawa e lilo ai kēia ʻano puʻupuʻu i maʻi kanesa.
Hiki ke loaʻa nā pilikia ʻē aʻe ma muli o ka wahi o ka puʻupuʻu.
- Ka lolo ʻana o nā ʻāpana kino
- ʻO ka effusion pleural (hōʻiliʻili wai ma waena o nā membrane māmā)
- Ka hōʻino ʻana i nā aʻalolo e lawe ana i nā leka mai nā maka a i ka lolo (Optic atrophy)
Nānā a i ka manawa hea e ʻike ai i ke kauka?
Hoʻōla piha ka nui o ka poʻe ma hope o ke ʻoki ʻana e wehe i ka puʻupuʻu. Eia nō naʻe, e like me kā mākou i ʻōlelo ai ma mua, he mea kakaikahi loa ka hoʻi ʻana mai o kahi puʻupuʻu a lilo i maʻi kanesa. No laila, e hana kāu kauka i nā scan maʻamau e nānā no kekahi hoʻi hou ʻana.
Inā ʻike ʻoe i kekahi o kēia mau hōʻailona, e ʻike pono i ke kauka:
- ʻEha umauma
- Paʻakikī ka hanu ʻana
- Luhi nui me ke kumu ʻole
- Nā pilikia ʻike
Ke ʻike ʻoe i kāu kauka, mai poina e nīnau i kēia mau nīnau:
- Aia i hea ka puʻupuʻu?
- Hiki ke wehe ʻia kēia me ke ʻoki kino?
- He aha nā hōʻailona e hiki ai ke hoʻi hou mai kahi puʻupuʻu?
- ʻEhia pinepine e pono ai iaʻu ke kiʻi i kahi scan?
- He aha nā pilikia ʻē aʻe e pono iaʻu e hopohopo?
He mea maʻamau ka makaʻu ke ʻike ʻoe he puʻupuʻu kou. Akā e hoʻomanaʻo, ʻoiai he maʻi kakaikahi ka SFT, hiki ke ho'ōla loa ʻia me ka mālama kūpono. ʻO ka mea nui loa, ʻo ia ke ʻimi i ke kōkua lapaʻau i ka wā hikiwawe loa, me ka nānā ʻole i nā hōʻailona.
Leka Lawe-Home
- ʻO nā Solitary Fibrous Tumors (SFTs) kahi ʻano puʻupuʻu kakaikahi e hana ʻia i loko o nā ʻiʻo palupalu o ke kino.
- ʻAʻole ka hapa nui o kēia mau mea he maʻi kanesa (benign), akā hiki i kekahi ke lilo i maʻi kanesa (malignant).
- ʻO ka hapa nui o ka manawa, ʻaʻohe hōʻailona i nā pae mua. Pili nā hōʻailona e ʻike ʻia ma kahi o ka puʻupuʻu.
- ʻO ka lāʻau nui e mālama ai, ʻo ia ka wehe loa ʻana i ka puʻupuʻu ma o ke ʻoki ʻana.
- Ma muli o ka liʻiliʻi o ka pilikia o ka hoʻi hou ʻana mai o ka puʻupuʻu ma hope o ka mālama ʻia ʻana, he mea nui loa ia e hana i nā hoʻokolohua maʻamau e like me ka ʻōlelo a kāu kauka.
- Inā he puʻupuʻu ʻē kou, ʻeha, a i ʻole kekahi hōʻailona ʻē aʻe i loko o kou kino, mai hoʻowahāwahā iā ia a e ʻike koke i ke kauka.











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