Ua hoʻomaka koke anei kāu keiki liʻiliʻi e neʻe i ko lākou mau lālā a me ke kino ma nā ʻano ʻē? Ke ʻōhumu nei ʻo ia i kekahi manawa i ka wā e kamaʻilio ana? A i ʻole ke ʻike nei ʻoe iā ia e minoʻaka koke ana a hana i nā helehelena? Ma ke ʻano he makua, he mea maʻamau iā ʻoe ke makaʻu nui i ka ʻike ʻana i kēia mau mea. Akā aia paha ke kumu no kēia mau mea a pau. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi. ʻO ia ke ʻano i kapa ʻia ʻo 'Sydenham Chorea'.
He aha ka ʻōlelo ʻo Sydenham Chorea?
I ka ʻōlelo maʻalahi, ʻo 'Sydenham Chorea' kahi maʻi neʻe o ka ʻōnaehana nerve i loaʻa i nā keiki. Hoʻokumu kūikawā ʻia ia e kahi maʻi bacteria i kapa ʻia ʻo '(Group A beta-hemolytic Streptococcus)'. ʻAe, ʻae, ua kuhi pololei ʻoe, ʻo ia ka bacteria like e hoʻoulu ai i ka ʻāʻī strep a me ka fiva rheumatic.
I kēia manawa, ke noʻonoʻo nei paha ʻoe, "Pehea lā e hiki ai kēia me ka maʻi ʻāʻī?" Eia ka mea e hana nei... Aia ka ʻōnaehana pale o ko mākou kino e pale iā mākou mai ka maʻi. Eia naʻe, ke komo kēia bacteria '(Streptococcus)' i ke kino, huikau iki kekahi mau ʻōnaehana pale o nā keiki. ʻO ia hoʻi, ma kahi o ka hoʻouka wale ʻana i ka bacteria, hoʻomaka hewa ia e hoʻouka i kekahi mau ʻāpana olakino o ka lolo. He ʻoiaʻiʻo loa kēia no nā ʻāpana o ka lolo e kaohi ana i ka neʻe ʻana.
ʻO ke ʻano o ka huaʻōlelo Helene "Chorea" ʻo ia hoʻi "hula." No laila, ua loaʻa ka inoa mai ka neʻe ʻana a me ka neʻe ʻana o nā lālā i makemake ʻole ʻia, wikiwiki, a ʻaʻole like me ka hula ʻana o kēia mau keiki. I kekahi mau hihia koʻikoʻi, hiki i kēia mau neʻe ʻana ke hoʻopilikia i nā hana o kēlā me kēia lā o ke keiki.
ʻIke pinepine ʻia kēia ʻano i nā keiki ma hope o ka loaʻa ʻana o ka "strep throat" a i ʻole ka "rheumatic fever." ʻO kēia ke ʻano maʻamau o ka chorea i nā keiki i hoʻokumu ʻia e nā kumu o waho.
Pehea ka maʻamau o kēia ʻano?
ʻO kaʻoiaʻiʻo, ma nā ʻāina i hoʻomohala ʻia e like me ʻAmelika ʻĀkau a me ʻEulopa, ua haʻahaʻa loa ka nui o Sydenham Chorea i kēia manawa. ʻO ke kumu o kēia, ʻo ia ka hāʻawi koke ʻia ʻana o nā antibiotics no nā maʻi ʻāʻī ma kēlā mau ʻāina. Eia nō naʻe, ma nā ʻāina e ulu ana e like me ko kākou, hiki ke ʻike ʻia kēia ʻano maʻi no ka mea i kekahi manawa he ʻokoʻa nā ʻano lapaʻau a ʻaʻole i loaʻa i nā kānaka a pau ka lāʻau lapaʻau koke.
ʻO wai ka mea i ʻoi aku ka paʻakikī ke hoʻomohala i kēia?
ʻIke pinepine ʻia ia i nā keiki ma waena o 5 a me 15 mau makahiki. ʻOi aku ka maʻamau o ia i nā kaikamahine ma mua o nā keikikāne. He mea kākaʻikahi loa ia i nā keiki ma lalo o 5 mau makahiki a i ʻole i nā pākeke.
He aha nā pilikia ʻē aʻe e hiki ai i kēia ke hana?
Aia nā keiki me Sydenham Chorea i ka pilikia no kahi maʻi i kapa ʻia ʻo PANDAS (Pediatric Autoimmune Neuropsychiatric Disorders Associated with Streptococcal Infections). ʻO PANDAS kahi maʻi neuropsychiatric autoimmune e pili ana i nā maʻi streptococcal. Eia nō naʻe, aia nō ka manaʻo kūʻē ma waena o nā kauka e pili ana i ka mea inā paha ʻo ka maʻi strep ke kumu o ka PANDAS. Hiki i nā keiki me PANDAS ke ʻike i nā hōʻailona e like me:
- Nā loli o ke ʻano a me ka nele o ka nānā.
- Nā hiʻohiʻona obsessive-compulsive.
- Nā neʻe a i ʻole nā leo koke a kūlohelohe ʻole (tics).
ʻAʻole wale kēlā, akā hiki i ka pane a ko mākou ʻōnaehana pale i kēia maʻi streptococcus ke hoʻopilikia i nā ʻōpū ʻē aʻe, e like me ka ʻili, nā hono, a me ka puʻuwai. Eia kekahi laʻana:
- ʻO ka ʻāʻī o ke kino
- Ka mumū ʻana o ka uhi o loko o ka puʻuwai (endocarditis)
- Maʻi valve puʻuwai
He mea nui: ʻO kēia ke kumu e ʻōlelo ʻia ai e nānā ʻia kahi keiki me Sydenham Chorea e ke kauka cardiologist.
He aha ke kumu maoli o ka maʻi ʻo Sydenham Chorea?
E like me kā mākou i ʻōlelo ai, ʻo ke kumu nui o kēia he pane maʻamau ʻole o ka ʻōnaehana pale i kahi maʻi bacteria me ka `(Group A beta-hemolytic Streptococcus)`. I ka ʻōlelo maʻalahi, hoʻouka hewa kā mākou mau koa pale ponoʻī (nā cell immune) i nā ʻāpana o ko mākou lolo ponoʻī. ʻOi aku ka wahi o ka lolo e kaohi ana i ka neʻe ʻana. I loko o ke koko o ka poʻe me `Sydenham Chorea`, ua loaʻa nā `(antibodies)` kūikawā (antibodies) i loko o ke koko o ka poʻe i loaʻa iā `Sydenham Chorea`.
He aha nā hōʻailona o ka maʻi ʻo Sydenham Chorea?
Hiki ke ʻike ʻia kēia mau hōʻailona ma nā wahi āpau o ke kino o ke keiki. I kekahi manawa ʻike koke ʻia lākou a hiki ke ʻoi aku ka ʻino ke luhi ke keiki.
Nā ʻano kino:
- Ke neʻe nei a ke kuʻi nei nā lālā a me ke kino me ka ʻole o ka manaʻo, me ka wikiwiki, a me ka manaʻo ʻole. Ke ʻike ʻoe i kēia, me he mea lā ua hoʻomaha ʻole a kolohe ke keiki.
- Hiki ʻole i ka hana, hāʻule nā mea mai nā lima mai.
- Ka paʻakikī ke paʻa ʻana i kahi mea ma kou lima.
- Ke hamo pū nei i kou mau lima.
- Hoʻomaha ʻole.
- Nā loli koke i ka helehelena o ka helehelena (e like me ka ʻūmiʻi iki ʻana).
- Ke kuʻia a me ka hāʻule ʻana i ka wā e hele ana.
Nā pilikia ʻōlelo:
- Ke ʻōhumu ʻana o ka ʻōlelo, ke kūpikipikiʻō ʻana.
- Ka pahū koke ʻana o nā huaʻōlelo, ka hoʻōho ʻana, a pēlā aku.
Nā ʻano noʻonoʻo a me nā naʻau:
- Hopohopo, makaʻu.
- Paʻakikī i ka noʻonoʻo ʻana.
E noʻonoʻo, i ka hoʻi ʻana mai o kekahi keiki i kapa ʻia ʻo Amila mai ke kula mai, ʻike kona makuahine ua ʻoi aku ka palaka o kāna kākau lima ma mua o ka mea maʻamau, a haʻalulu kona mau lima i kāna kākau ʻana. ʻOiai ma ka papa, ʻaʻole ʻo ia e noho mālie i ka wā e ʻōlelo ai ke kumu e hele ana ʻo ia, hula wale nō ʻo ia. I kona hoʻi ʻana mai i ka home, ʻaʻole hiki iā ia ke hoʻokomo pono i ka laiki i loko o kona waha me ka puna a ninini ʻia i waho. Inā ʻike ʻoe i kahi mea e like me kēia, pono ʻoe e ʻimi i ke kōkua lapaʻau.
Āhea e hoʻomaka ai nā hōʻailona?
He ʻano kūikawā kēia. ʻAʻole ʻike koke ʻia nā hōʻailona ma hope o ka maʻi ʻāʻī (strep throat) a i ʻole ka fiva rumatika. ʻAʻole paha e hoʻomaka kekahi mau keiki e hoʻomohala i kēia mau hōʻailona o 'Sydenham Chorea' a hiki i ka piha ʻana o 6 mau mahina .
Pehea ʻoe e ʻike ai i kēia?
E nīnau ke kauka i kāu keiki e pili ana i kā lākou mau hōʻailona a nīnau inā ua loaʻa iā lākou nā maʻi Streptococcus beta-hemolytic Group A ma mua. ʻO ke ʻano kēia e nīnau lākou inā ua loaʻa iā lākou kahi ʻeha puʻu, kahi maʻi ʻili, a i ʻole ka ʻeha hui.
A laila, hiki ke hana ʻia kahi hoʻāʻo koko e nānā i nā antibodies i ka bacteria strep. Hiki i kēia ke kōkua nui i ka hana ʻana i kahi hōʻailona. Inā ua hōʻoia ʻia kāu keiki he Sydenham Chorea, hiki ke hana ʻia kahi hoʻāʻo puʻuwai (ʻo ka maʻamau he echocardiogram) e nānā i ka hōʻino ʻia o nā valves puʻuwai a i ʻole nā kūlana e like me ka endocarditis.
Pehea e mālama ʻia ai ka Sydenham Chorea?
ʻO ka lāʻau lapaʻau maikaʻi loa no kāu keiki e hilinaʻi ʻia i ke koʻikoʻi o nā hōʻailona. I kekahi manawa, inā he akahai loa nā hōʻailona, ʻaʻole pono kekahi lāʻau lapaʻau kūikawā. Eia nō naʻe, e hoʻomau ke kauka i ka nānā ʻana i ke keiki.
Ka mālama ʻana i ka `Sydenham Chorea` waena a koʻikoʻi:
Hiki i nā keiki me nā ʻōuli maʻamau a koʻikoʻi ke pōmaikaʻi mai ka lāʻau lapaʻau.
- Nā lāʻau lapaʻau ʻano steroid: Kōkua kēia i ka wehe ʻana i nā antibodies i hana hewa ʻia mai ke kino.
- Nā lāʻau lapaʻau ʻē aʻe: I kekahi manawa pono paha nā lāʻau lapaʻau hou aʻe. ʻOiai ke hoʻohana nui ʻia nei kēia mau lāʻau lapaʻau no nā kūlana ʻē aʻe, hiki ke hoʻohana palekana ʻia no Sydenham Chorea. ʻO lākou kekahi:
- Nā lāʻau hoʻōla i ka ʻōhū: ʻO nā laʻana e like me nā lāʻau lapaʻau e like me ka valproic acid a me ka carbamazepine. Kōkua kēia i ka hoʻopaʻa ʻana i nā impulses nerve.
- Nā lāʻau antipsychotics: No ka laʻana, haloperidol. Hiki i kēia ke kāohi i nā tics, e like me nā neʻe ʻana o ka ʻūlū a me nā uē koke.
- Nā mea hoʻopau Dopamine: ʻO kahi laʻana o kēia he lāʻau i kapa ʻia ʻo Tetrabenazine. Kāohi kēia i nā neʻe ʻana me ka makemake ʻole.
E hoʻomanaʻo, loaʻa kēia mau lāʻau lapaʻau a pau ma ke kauoha wale nō. Mai hoʻohana i kēia mau lāʻau lapaʻau me ka ʻole o ke aʻo ʻana a ke kauka.
Hiki ke pale ʻia kēia kūlana?
ʻAe, i kekahi ʻano. ʻO ka mālama kūpono a me ka manawa kūpono (antibiotics) no ka "Strep throat" (maʻi ʻāʻī) a me ka "rheumatic fever" (rheumatic fever) hiki ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i ka "Sydenham Chorea".
A pēlā nō hoʻi,Inā loaʻa i kāu keiki ka Sydenham Chorea, hiki i nā kauka ke ʻōlelo aku i ka hoʻomau ʻana i nā antibiotics a hiki i ka wā makua o ke keiki (a hiki paha i ka 21 makahiki a ʻoi aku paha) e pale aku i nā maʻi strep hou a hoʻemi i ka pilikia o ka maʻi puʻuwai. ʻO ka pahuhopu lōʻihi ka pale ʻana i ka hōʻino mau loa i nā valves puʻuwai e hiki ke hopena mai ka maʻi puʻuwai.
He aha ka wā e hiki mai ana no nā keiki me ka `Sydenham Chorea`? (Prognosis)
E hauʻoli paha ʻoe i ka lohe ʻana i kēia. Hoʻōla piha ka hapa nui o nā keiki i loko o 3 a 6 mau mahina. Eia nō naʻe, he kakaikahi loa paha e loaʻa nā hōʻailona a hiki i 2 mau makahiki.
ʻO kekahi mea ʻē aʻe, i kekahi manawa hiki i kēia mau hōʻailona ke hoʻi hou mai ma hope o ke ola, ʻoiai ke lawe nā wahine i nā pila hoʻomalu hānau i loaʻa ka hormone `(estrogen)` a hāpai paha. No laila, inā ua loaʻa iā ʻoe ʻo `Sydenham Chorea` ma mua, he mea nui loa ia e hoʻomaopopo i kāu kauka e pili ana i ia mea.
Pehea ke ola o kēlā me kēia lā me kēia kūlana?
ʻO nā keiki me nā hōʻailona waena a koʻikoʻi paha e paʻakikī iā lākou ke hana i nā hana o kēlā me kēia lā. E noʻonoʻo i ka nui o kēia mau neʻe ʻana i makemake ʻole ʻia e hoʻopilikia i nā hana kula, ka pāʻani, a me ka launa pū ʻana me nā hoaaloha. ʻO kekahi o nā pilikia o ka noho ʻana me Sydenham Chorea, hiki ke hiki koke mai nā hōʻailona a hiki ke hoʻonui a emi iho i ka lā. Hiki i kēia ke paʻakikī i ke komo ʻana i nā hana maʻamau o ka wā kamaliʻi.
ʻO Sydenham Chorea kahi maʻi neurological i loaʻa i ka maʻi me ka Group A beta-hemolytic Streptococcus. ʻO ia ka mea maʻamau ma nā ʻāina e ulu ana, kahi i loaʻa ʻole ai i nā keiki ka lāʻau antibiotic kūpono no nā maʻi strep. ʻOiai ma hope o ka mālama ʻana i kūleʻa, hiki i kahi helu liʻiliʻi o nā keiki ke loaʻa i nā maʻi puʻuwai a me nā pilikia ʻē aʻe ma hope o ke ola. Eia nō naʻe, hoʻōla piha ka hapa nui o nā keiki a ʻaʻole loaʻa i nā pilikia.
E hoʻomanaʻo ma ke ʻano he hōʻuluʻulu manaʻo (Leka Lawe-Home)
- ʻO ka Sydenham Chorea kahi maʻi neʻe i hoʻokumu ʻia e kahi pane kūpono ʻole o ka ʻōnaehana pale o ko mākou kino i kahi bacteria (streptococcus) e hoʻoulu ai i nā maʻi ʻāʻī a me ka fiva rumatika.
- ʻIke pinepine ʻia kēia i waena o nā keiki ma waena o nā makahiki 5-15, ʻoiai nā kaikamahine.
- Hiki ke ʻike ʻia nā hōʻailona e like me ka neʻe ʻana o nā lālā me ka makemake ʻole, ka ʻōlelo ʻana me ka ʻole o ka lohe ʻana, a me nā loli o ke ʻano.
- ʻO ka mālama pono ʻana i nā maʻi ʻāʻī i ka manawa koke e hiki ke kōkua i ka pale ʻana i kēia.
- Hoʻōla piha ka hapa nui o nā keiki, akā hiki i kekahi ke loaʻa i nā pilikia e like me ka maʻi puʻuwai, no laila he mea nui ka nānā ʻana i ke kauka no ka manawa lōʻihi.
- Inā loaʻa i kāu keiki kekahi o kēia mau hōʻailona, mai hopohopo a e ʻike koke i ke kauka kūpono. Hiki i ka ʻike koke ʻana a me ka mālama ʻana ke kōkua i kāu keiki e hoʻōla koke.
Inā he mau nīnau hou aku kāu e pili ana i kēia, e kamaʻilio me kāu kauka ʻohana a kauka keiki paha. E hiki iā lākou ke hāʻawi iā ʻoe i nā wehewehe hou aku a me ke kōkua.
`ʻO ka chorea a Sydenham, ka ʻāʻī strep, ka fiva rumatika, nā maʻi neurological, nā maʻi neʻe, pediatrics, nā antibiotics











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