Ke manaʻo nei ʻoe i kekahi manawa e kuʻi wikiwiki ana kou puʻuwai me ke kumu ʻole? Ke manaʻo nei ʻoe ua holo wale aku ʻoe? Ke manaʻo nei ʻoe e kuʻi ana kou umauma, ua pōkole kou hanu, ua poniuniu ʻoe, a ua uliuli kou mau maka? Inā ua loaʻa iā ʻoe kēia mau ʻike, ʻo kekahi o nā kumu paha ke ʻano a mākou e kamaʻilio nei i kēia lā i kapa ʻia ʻo Wolff-Parkinson-White Syndrome. Mai makaʻu inā he paʻakikī iki ke kani ʻana o ka inoa. E kamaʻilio kākou e pili ana i kēia me ka maʻalahi, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.
He aha maoli ka Wolff-Parkinson-White (WPW) Syndrome?
I ka ʻōlelo maʻalahi, ʻo ka WPW Syndrome kahi loli liʻiliʻi i ke ʻano o ka hele ʻana o nā hōʻailona uila i loko o ko kākou puʻuwai. He kūlana ia e kū nei i ka wā hānau.
E noʻonoʻo e like me kahi pamu liʻiliʻi. I mea e hana ai kēia pamu i ka mele kūpono, pono ia e loaʻa nā hōʻailona uila. ʻO ka maʻamau, hele wale kēia mau hōʻailona ma ke ala hoʻokahi i loko o ka puʻuwai. Ma kēia ala he hui liʻiliʻi i kapa ʻia ʻo ka AV node . Kōkua kēia hui i nā ʻāpana o luna o ka puʻuwai (atria) a me nā ʻāpana o lalo (nā keʻena ventricular) e ʻaelike ma kahi hoʻonohonoho pololei.
Akā, i loko o ka puʻuwai o kekahi me ka WPW Syndrome, aia kekahi ala kōkua ma waho aʻe o ke ala uila maʻamau. Ua like kēia me kahi "pōkole pōkole" hiki ke hoʻohana ʻia e kāpae i kahi alanui nui ma ke kūlanakauhale.
ʻO kēia ala keu, e kāpae ana i ka AV node e kāohi ana i ka wikiwiki, e ʻae i nā hōʻailona uila e hele wikiwiki loa i nā keʻena haʻahaʻa o ka puʻuwai, ʻo ia hoʻi nā ventricles. Hoʻoulu kēia i nā keʻena puʻuwai e ʻūlū ma mua o ka maʻamau. I ka lāʻau lapaʻau, kapa mākou i kēia preexcitation . ʻO kēia mau hōʻailona wikiwiki a maʻamau ʻole e hoʻoulu ai i ka puʻuwai e kuʻi wikiwiki koke. Hoʻohana mākou i nā inoa e like me "supraventricular tachycardia - SVT" a i ʻole "atrial fibrillation - AFib" no kēia mau ʻano kuʻi puʻuwai wikiwiki.
E hoʻomanaʻo, ʻaʻole ka WPW Syndrome he nāwaliwali i loko o kou puʻuwai. He loli liʻiliʻi wale nō ia i loko o ka ʻōnaehana uila o ka puʻuwai.
ʻAʻole maʻamau loa kēia ʻano. Hoʻopilikia ia ma waena o 1 a me 3 i loko o 1,000 mau kānaka ma ka honua holoʻokoʻa. ʻOi aku ka maʻamau i nā poʻe me nā kīnā puʻuwai hānau ʻē aʻe, e like me ka maʻi ʻano ʻē aʻe ʻo Ebstein.
He aha nā hōʻailona o ka WPW Syndrome?
ʻAʻole nā kānaka a pau me ka WPW Syndrome e loaʻa nā hōʻailona. ʻAʻole paha e ʻike kekahi poʻe he maʻi ko lākou no ke koena o ko lākou ola. Akā inā loaʻa nā hōʻailona, loaʻa pinepine lākou i ka wā e wikiwiki loa ai ka puʻuwai.
No ke aha kēia e hana ʻia ai? Ke kuʻi wikiwiki ka puʻuwai, ʻaʻole lawa ka manawa o kona mau keʻena e hoʻopiha ai me ke koko. ʻO ka hopena, ʻaʻole hiki i ka puʻuwai ke pamu i ke koko lawa i ke kino. ʻO kēia ka manawa e ʻike ʻia ai kēia mau hōʻailona.
E nānā kākou i nā hōʻailona nui ma ka papa ma lalo nei.
| Hōʻailona | He wehewehe maʻalahi |
|---|---|
| Nā Palpitations o ka Puʻuwai | He manaʻo koke o ka ʻūmiʻi o ka umauma, me he mea lā e paʻi ana kou puʻuwai mai loko mai o kou umauma. Hiki ke hana ʻia kēia i ka wā e noho wale ana, e hoʻoikaika kino ana, ma lalo o ke kaumaha, a ma hope paha o ka lawe ʻana i kahi mea hoʻoulu e like me ke kofe. |
| Pōʻino | Manaʻo poniuniu. Hiki ke hana ʻia kēia ʻano ke loaʻa ʻole ke koko i ka lolo. |
| Ka nawaliwali a i ʻole ka manaʻo nāwaliwali | Polū nā maka, nāwaliwali a nalowale paha ka ʻike. |
| Luhi a nāwaliwali paha | Me he mea lā ʻaʻohe ola o kou kino, luhi mau i nā manawa a pau. |
| Pōkole o ka hanu | Manaʻo ua pio ka hanu a i ʻole ka pilikia o ka hanu ʻana. |
| Kaomi a paʻa paha o ka umauma | Ka manaʻo o ka ʻūmiʻi a i ʻole ke kaumaha ma ka umauma. |
He aha ke kumu o ka WPW Syndrome?
No ka hapa nui o nā kānaka, ʻaʻohe kumu kikoʻī i loaʻa no ka WPW Syndrome. ʻO ke ʻano kēia, hiki wale mai ia ma ke ʻano ulia pōpilikia. Akā no kahi poʻe liʻiliʻi loa, hiki ke hana ʻia ke kūlana e nā kumu genetic. ʻO kekahi kumu, ʻo ia nā loli i loko o kahi gene i kapa ʻia ʻo PRKAG2 . Hiki ke hoʻoili ʻia kēia mau loli genetic mai kēlā hanauna a i kēia hanauna.
He aha nā pilikia e hiki ke hana ma muli o kēia ʻano?
Noho ka hapa nui o ka poʻe me ka WPW Syndrome i nā ola maʻamau. Eia nō naʻe, inā ʻaʻole mālama ʻia, hiki ke loaʻa nā pilikia i kekahi manawa. Mai hopohopo , he mea kakaikahi loa kēia. A aia nā lāʻau lapaʻau kūpono i loaʻa i kēia lā e hiki ke pale aku iā lākou.
- Nā ulia i hoʻokumu ʻia e ka nalowale ʻana o ka ʻike: Inā nalowale koke kou ʻike, hiki iā ʻoe ke hāʻule a ʻeha.
- Nā ʻano ʻē aʻe o ka puʻuwai puʻuwai: ʻO ka pilikia o ka hoʻomohala ʻana i nā ʻano ʻē aʻe o ka puʻuwai puʻuwai, e like me ka atrial fibrillation, hiki ke hoʻonui.
- Nā ʻano ʻino weliweli o ka puʻuwai: He mea kākaʻikahi loa, hiki ke hana ʻia kahi kūlana weliweli i kapa ʻia ʻo "Ventricular fibrillation".
- Make koke ʻana o ka puʻuwai: ʻO kēia ka pilikia koʻikoʻi a kakaʻikahi loa o ka maʻi WPW. ʻO kekahi o nā pahuhopu nui o ka mālama ʻana, ʻo ia ka hoʻopau loa ʻana i kēia pilikia.
Pehea e ʻike ai nā kauka i kēia maʻi?
Inā loaʻa iā ʻoe nā hōʻailona i ʻōlelo ʻia ma luna, ʻo ka mea mua a kāu kauka e hana ai, ʻo ia ke hana i kahi ECG (electrocardiogram). He hoʻāʻo maʻalahi loa kēia a ʻeha ʻole.
Hiki i kahi ECG ke hoʻopaʻa i ka hana uila o ka puʻuwai. Hōʻike kahi ECG o kekahi me ka maʻi WPW i kahi ʻano kikoʻī i hoʻokumu ʻia e ke ala uila keu. Kāhea mākou i kēia ʻano ʻo "WPW pattern."
- ʻAno WPW: ʻOiai inā loaʻa iā ʻoe kēia ʻano kikoʻī ma kāu ECG, inā ʻaʻohe ou hōʻailona, e ʻōlelo wale kāu kauka he ʻano WPW kou.
- ʻO WPW Syndrome: Inā ʻike ʻoe i nā hōʻailona e like me ka ʻeha o ka umauma me kēia ʻano ma kāu ECG, a laila e hoʻoholo kāu kauka he WPW Syndrome kou.
Ma waho aʻe o ka ECG, hiki i kāu kauka ke kuhikuhi i kekahi mau hoʻokolohua ʻē aʻe.
- Echocardiogram (Echo): He scan ultrasound kēia o ka puʻuwai. Kōkua ia e ʻike inā e hana pono ana ke ʻano o ka puʻuwai, nā keʻena, a me nā valves.
- Haʻawina Electrophysiology: He hoʻokolohua paʻakikī iki kēia. Ma kēia, hoʻokomo ʻia nā uea lahilahi (catheters) i loko o ka puʻuwai, ua palapala ʻia nā ala uila o ka puʻuwai, a ua hoʻoholo ʻia kahi kikoʻī o ke ala keu.
- Hoʻāʻo koʻikoʻi hoʻoikaika kino: Hana ʻia ʻoe e holo ma luna o ka treadmill a hoʻohana ʻia kahi ECG e nānā i ke ʻano o ka loli o ka hana a me ke ʻano o kou puʻuwai i kou hoʻoikaika kino ʻana.
- Ka nānā ʻana i ka wā e hele ana (Holter monitor):Hoʻokomo ʻia kahi mea liʻiliʻi ma kou kino e hoʻopaʻa ana i kou helu puʻuwai no 24 mau hola a ʻoi aku paha. Kōkua kēia i ka ʻike ʻana i nā loli i loko o kou ʻano puʻuwai i kou hele ʻana i kāu mau hana maʻamau o kēlā me kēia lā.
He aha nā lāʻau lapaʻau no ka WPW Syndrome?
Aia nā lāʻau lapaʻau kūpono loa no ka WPW Syndrome. Na kāu kauka e hoʻoholo i ka lāʻau lapaʻau kūpono loa nāu ma muli o ke ʻano o kāu mau hōʻailona, ka pinepine o lākou e kū mai ai, a me nā hopena o kāu mau hoʻokolohua.
| ʻAno Lapaʻau | Wehewehena |
|---|---|
| Nā lāʻau antiarrhythmic | Hiki i nā lāʻau lapaʻau e kaohi ana i ka puʻuwai wikiwiki ke hōʻemi i ke alapine (frequency) o nā hōʻailona. |
| Nā Hana Hoʻololi Vagal | Ke wikiwiki ka helu o kou puʻuwai, aia kekahi mau mea maʻalahi hiki iā ʻoe ke hana ma ka home e kōkua iā ia e hoʻi i ka maʻamau. Eia kekahi laʻana, ke kuʻi nui ʻana a i ʻole ka holoi ʻana i kou maka me kahi kāwele anu. E aʻo aku kāu kauka iā ʻoe pehea e hana ai i kēia mau mea. |
| Ka hoʻololi ʻana o ke kāʻei | I kahi pilikia, ʻo ia hoʻi, inā hoʻomau ka wikiwiki o ka puʻuwai, he ʻano hana e hoʻihoʻi i ka puʻuwai i ka maʻamau ma o ka hāʻawi ʻana i kahi haʻalulu uila liʻiliʻi i ka umauma ma ka haukapila. |
| ʻO ka hoʻopau ʻana o ka catheter | ʻO kēia ka lāʻau lapaʻau maikaʻi loa a mau loa no ka WPW Syndrome. Ma kēia, hoʻokomo ʻia kahi uea lahilahi (catheter) i loko o ka puʻuwai ma o kahi kīʻaha koko ma ka ʻūhā, loaʻa ke ala uila keu, a hoʻopau ʻia me ka ikehu radiofrequency a i ʻole cryoablation. He lāʻau lapaʻau kēia i ʻoi aku ma mua o 94% ka holomua. Ma hope o kēia, hiki ke ho'ōla loa ʻia ka maʻi. |
| ʻOki ʻoki kino | He ʻano hana e hoʻohana wale ʻia inā ʻaʻole holo pono ke ʻano ablation catheter a i ʻole inā pono kekahi ʻoki puʻuwai ʻē aʻe. |
Āhea wau e ʻike ai i ke kauka?
Inā loaʻa iā ʻoe ka WPW Syndrome, he mea nui loa ia e ʻike ʻoe i kāu kauka no nā nānā maʻamau (follow-up). E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou hele ʻana mai. Eia kekahi, inā ʻike ʻoe i kekahi mau loli i kāu mau hōʻailona a i ʻole e loaʻa kekahi mau hōʻailona hou, e hoʻomaopopo koke i kāu kauka.
I ke ola ʻana me ke kūlana e like me kēia, i kekahi manawa e makaʻu iki paha ʻoe a hopohopo. He mea maʻamau loa ia. I nā manawa e like me kēia, ma kahi o ka hūnā ʻana iā ia iho i loko, ʻo ke kamaʻilio ʻana me kekahi āu e hilinaʻi ai, a i ʻole he kākāʻōlelo, hiki ke maikaʻi loa no kou olakino noʻonoʻo.
I ka manawa hea e hele ai i ka ETU no ka mālama ʻana i ka pilikia
Inā ʻike ʻoe i nā hōʻailona ma lalo nei, e hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa .
- Inā loaʻa iā ʻoe ka ʻeha nui o ka umauma .
- Ka mae ʻana.
- Inā hoʻomau ka wikiwiki o kou puʻuwai no nā minuke he nui a ʻaʻole i emi iho ma hope o ka hana ʻana i nā Vagal Maneuvers a kāu kauka i kauoha ai.
Inā nalowale ʻoe i ka ʻike, ʻaʻole paha ʻoe e hiki ke kōkua iā ʻoe iho. No laila he mea nui e hoʻomaopopo i kou ʻohana a me nā hoaaloha āu e noho pū ai e pili ana i kou kūlana. Ma kēlā ala, e ʻike lākou i ka mea e hana ai i kahi pilikia.
Pehea lā koʻu wā e hiki mai ana me kēia kūlana?
ʻO ka hapa nui o ka poʻe me ka WPW Syndrome e loaʻa ana ka lāʻau kūpono e ola maʻamau a olakino . ʻO ka Catheter Ablation, ma ke ʻano kūikawā, hiki ke ho'ōla loa i ke kūlana a pale iā ʻoe mai ka pilikia o ka make koke ʻana o ka puʻuwai.
Pono paha ʻoe e makaʻala i kekahi mau mea i kou ola o kēlā me kēia lā. Eia kekahi laʻana, ʻoi aku ka maikaʻi o ka pale ʻana i nā mea e hiki ai ke hoʻoikaika i kou puʻuwai.
- ʻAila
- Kafeina (kofe, kekahi kī, kekahi mau mea inu palupalu)
- Nā mea hoʻonāukiuki e like me ka nicotine (puhi paka)
- Hoʻoikaika kino ikaika a paʻakikī (e nīnau i kāu kauka i nā hoʻomaʻamaʻa palekana nou)
Inā loaʻa i kāu keiki ka WPW Syndrome ...
Ma ke ʻano he makua, e makaʻu paha ʻoe ke ʻike ʻoe ua loaʻa i kāu keiki kēia maʻi. He mea maʻamau kēlā. ʻO ka mea nui loa, ʻo ke kamaʻilio ākea me ke kauka o kāu keiki a nīnau i kāu mau nīnau a pau.
Eia kekahi laʻana, e kiʻi i nā kuhikuhi maopopo no ka palekana o kāu keiki e pāʻani i nā haʻuki a i ʻole ka mea e hana ai inā piʻi ka helu o ko lākou puʻuwai ma ke kula. Hiki i ke kauka ke kōkua iā ʻoe e wehewehe i ke kūlana ma kahi ʻōlelo a kāu keiki e maopopo ai.
Hiki ke weliweli ka inoa ʻo WPW Syndrome. Akā e hoʻomanaʻo, he ʻano ia e hiki ke mālama ʻia, a i ka hapa nui o nā hihia, e ho'ōla loa ʻia. Eia kāu kauka a me ka hui lapaʻau e kōkua iā ʻoe. No laila, mai kānalua e nīnau i kāu mau nīnau.
Leka Lawe-Home
- ʻO ka Wolff-Parkinson-White (WPW) Syndrome kahi maʻi hānau ʻia i hoʻokumu ʻia e ke alo o kahi ala uila keu i loko o ka puʻuwai.
- Hiki ke ʻike koke ʻia nā hōʻailona e like me ka puʻuwai wikiwiki, ka poniuniu, a me ka nalowale o ka ʻike. Eia naʻe, ʻaʻole ʻike nā kānaka a pau i nā hōʻailona.
- ʻO ka hoʻāʻo nui e ʻike ai i kēia maʻi ʻo ia ka ECG.
- Mai hopohopo! Aia nā lāʻau lapaʻau kūpono loa no kēia. Hiki i kahi lāʻau lapaʻau i kapa ʻia ʻo Catheter Ablation ke ho'ōla loa i kēia maʻi ma mua o 94% o nā hihia.
- Inā loaʻa iā ʻoe ka ʻeha o ka umauma, ka nāwaliwali, a i ʻole ka puʻuwai wikiwiki mau, e hele koke i ka ETU o ka haukapila.
- E kamaʻilio ākea me kāu kauka e pili ana i kāu mau hōʻailona a me ka lāʻau lapaʻau. Me ka lāʻau lapaʻau kūpono a me nā hoʻololi ʻana i ke ʻano o ka nohona, hiki iā ʻoe ke ola i kahi ola olakino piha.











💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo