Koj puas paub tej yam no txog sab laug ventricle ntawm koj lub plawv? (Left Ventricular Non-Compaction - LVNC) Cia peb tham!

Niaj hnub no peb yuav tham txog ib qho mob uas nyuaj me ntsis, tab sis tej zaum yuav tseem ceeb heev rau lub plawv. Tej zaum koj yuav tsis tau hnov ​​​​​​txog qhov no ua ntej. Nws hu ua Left Ventricular Non-Compaction (LVNC) raws li cov kws kho mob hu ua. Lub npe yuav zoo li ib qho teeb meem loj, tab sis tsis txhob txhawj, cia peb ua kom yooj yim.

Yog li ntawd, sab laug ventricular tsis muaj zog plawv tsis ua haujlwm (LVNC) yog dab tsi?

Hais yooj yim xwb, qhov no yog ib qho mob uas tshwm sim thaum lub chamber qis ntawm sab laug ntawm peb lub plawv, Left Ventricle, tsis loj hlob zoo. Xav txog nws, feem ntau lub ventricle sab laug ntawm peb lub plawv no yog ib daim nqaij du thiab muaj zog heev. Nws yog qhov tseem ceeb uas tso ntshav mus rau peb lub cev tag nrho. Tab sis rau ib tus neeg uas muaj qhov '(LVNC)' no, lub ventricle sab laug zoo li lub daim txhuam cev, tuab dua me ntsis, thiab teeb tsa zoo li lub vas. Nws muaj qhov xwm txheej zoo li lub roob, zoo li sab hauv ntawm ib lub ncuav mog qab zib.

Feem ntau qhov no suav tias yog mob plawv txij thaum yug los. Qhov no txhais tau tias koj yuav muaj mob no hauv koj lub plawv txij thaum koj yug los. Yog tias tsis kho kom zoo, qhov "(LVNC)" no tuaj yeem ua rau muaj teeb meem loj rau lub plawv, uas yog, mob plawv.

Tus mob LVNC no cuam tshuam li cas rau kev ua haujlwm ntawm lub plawv?

Tam sim no saib seb, sab laug ntawm peb lub plawv muaj ib txoj haujlwm tseem ceeb heev. Nws yog qhov no uas tso cov ntshav uas muaj oxygen ntau los ntawm lub ntsws mus rau tag nrho lub cev. Ib yam li lub tshuab dej. Txawm li cas los xij, thaum qhov xwm txheej '(LVNC)' no tshwm sim, sab laug ventricle, uas zoo li lub daim txhuam cev, tsis tuaj yeem cog lus lossis so kom zoo. Ntawd yog, nws muaj teeb meem hauv kev nruj thiab thawb cov ntshav mus tom ntej, lossis so thiab sau nws nrog cov ntshav dua. Yog li, qhov tshwm sim yog tias txoj haujlwm ntawm kev tso cov ntshav mus rau tag nrho lub cev tsis tshwm sim kom zoo . Qhov no yog vim li cas ntau yam teeb meem pib tshwm sim.

Tus mob no hu ua LVNC tsawg npaum li cas?

Qhov no yog ib qho mob tsis tshua muaj. Raws li cov kws kho mob hais, tsuas yog kwv yees li kaum ob tus neeg hauv ib lab tus neeg thiaj li kuaj pom tias muaj tus mob no txhua xyoo. Txawm li cas los xij, tus lej tiag tiag yuav siab dua . Qhov laj thawj yog vim qee tus neeg tsis muaj tsos mob dab tsi. Tom qab ntawd lawv tsis mus ntsib kws kho mob, thiab yog li ntawd tsis tau txais kev kuaj mob.

Cov tsos mob ntawm LVNC yog dab tsi?

Qhov no yog qhov tseem ceeb tshaj plaws. Ib txhia neeg yuav tsis muaj tsos mob dab tsi li . Txawm li cas los xij, lwm tus tuaj yeem muaj teeb meem plawv loj heev. Piv txwv li, kev tuag tam sim ntawd ntawm lub plawv tuaj yeem tshwm sim. Kwv yees li ob feem peb ntawm cov neeg uas muaj LVNC muaj feem yuav mob plawv tsis ua haujlwm .

Zoo, yog li cia peb saib seb tus neeg uas muaj '(LVNC)' yuav muaj cov tsos mob li cas:

Cov tsos mob uas pom ntau zaus :

• Cov ntshav txhaws tuaj yeem tsim tau. Cov no yog qhov txaus ntshai heev, vim tias yog cov ntshav txhaws no mus rau lub hlwb lossis lub ntsws, nws tuaj yeem yog teeb meem loj.
• Tej zaum koj yuav ua pa nyuaj thaum pw hauv txaj.
• Tsaus muag .
• Lub plawv dhia ceev - Qhov no tuaj yeem zoo li lub nruas ntaus hauv lub hauv siab, lossis zoo li lub plawv dhia ceev.
• Tsis muaj peev xwm tawm dag zog, ua pa luv luv txawm tias siv zog me ntsis los xij (Dyspnea) .
• Lub plawv dhia tsis sib xws (Arrhythmia) .
• O ntawm ob txhais ceg (Lymphedema) - tshwj xeeb tshaj yog nyob rau hauv pob luj taws.
• Ua tsis taus pa / Ua tsis taus pa - Zoo li koj ua tsis taus pa txawm tias siv zog me ntsis los xij.

Vim li cas tus mob LVNC no thiaj tshwm sim? Dab tsi yog cov ua rau muaj?

Feem ntau, qhov mob '(LVNC)' no yog tshwm sim los ntawm kev hloov pauv caj ces (Gene mutation) uas tshwm sim ua ntej koj yug los. Qhov no yog ib qho nyuaj heev. Qhov kev hloov pauv caj ces no tuaj yeem tshwm sim yam tsis muaj laj thawj, lossis nws tuaj yeem tau txais los ntawm koj niam koj txiv. Qhov ntawd txhais tau tias nws tuaj yeem yog ib yam dab tsi uas khiav hauv tsev neeg. Xav txog, qee tsev neeg muaj feem ntau ntawm hom kab mob plawv no.

Tsis tas li ntawd xwb, muaj ib feem pua ​​me me ntawm cov poj niam uas yuav muaj tus kab mob LVNC thawj zaug thaum cev xeeb tub yam tsis muaj laj thawj pom tseeb. Cov kws kho mob xav tias qhov no yuav yog vim muaj kev ntxhov siab ntxiv rau cov leeg nqaij plawv thaum cev xeeb tub. Rau qee tus poj niam, cov tsos mob no ploj mus tom qab yug menyuam. Tab sis rau lwm tus, LVNC tuaj yeem muaj cov teebmeem mus sij hawm ntev.

Cov kws kho mob kuaj mob LVNC no li cas?

Tus kws kho mob yuav ua ntau yam kev kuaj mob kom paub tseeb tias koj puas muaj tus mob "(LVNC)" no. Cia peb saib seb lawv yog dab tsi:

• Echocardiogram: Qhov no saib seb koj lub plawv nqus ntshav tau zoo npaum li cas, cov hlab ntsha ua haujlwm tau zoo npaum li cas, thiab seb puas muaj teeb meem dab tsi nrog cov hlab ntsha. Nws zoo li kev ntsuas ultrasound ntawm lub plawv. Qhov no yog qhov uas koj thawj zaug pom qhov xwm txheej ntawm lub plawv sab laug.
• Electrocardiogram (ECG): Qhov no ntsuas qhov hluav taws xob ntawm koj lub plawv. Nws tuaj yeem nrhiav tau txhua yam teeb meem nrog koj lub plawv dhia.
• Kev kuaj duab tshwj xeeb: Cov no suav nrog kev ntsuas CT ntawm lub plawv thiab kev ntsuas magnetic resonance imaging (MRI). Cov no tuaj yeem qhia cov qauv ntawm lub plawv, xws li lub plawv ua li cas thiab qhov tuab ntawm nws cov phab ntsa. Hauv LVNC, qhov zoo li daim txhuam cev pom tseeb ntawm cov kev ntsuas no.
• Kev kuaj mob plawv (Coronary angiogram): Qhov no kuaj seb cov ntshav ntws li cas los ntawm cov hlab ntsha plawv uas muab ntshav mus rau lub plawv, thiab seb puas muaj kev thaiv. Qee zaum qhov kev kuaj no kuj yuav tsum tau ua kom paub tseeb tias tsis muaj lwm yam mob plawv.

Cov kev kho mob rau tus mob LVNC no yog dab tsi?

Kev kho mob rau LVNC sib txawv nyob ntawm koj cov tsos mob. Tsis yog txhua tus neeg tau txais kev kho mob tib yam. Piv txwv li, yog tias koj muaj mob plawv tsis ua haujlwm, koj tus kws kho mob yuav sau ntawv rau cov tshuaj xws li:

• Cov tshuaj angiotensin-converting enzyme inhibitors (ACE inhibitors): Piv txwv li, benazepril (Lotensin®) lossis lisinopril (Prinivil®, Zestril®) lossis sacubitril-valsartan (Entresto®) (angiotensin-neprilysin inhibitors). Cov no ua haujlwm los ntawm kev so thiab qhib koj cov hlab ntsha (cov hlab ntsha thiab cov hlab ntsha) kom yooj yim rau cov ntshav ntws los ntawm lawv. Qhov no txo ​​qhov kev ua haujlwm ntawm lub plawv.
• Cov tshuaj Beta-blockers: Piv txwv li, metoprolol (Lopressor®, Toprol XL®) lossis atenolol (Tenormin®). Cov tshuaj no thaiv qee cov tshuaj hormones (piv txwv li adrenaline), txo cov ntshav siab thiab tswj lub plawv dhia.
• Digoxin (Digoxin®, Lanoxin®): Qhov no tswj koj lub plawv dhia, ua rau lub plawv muaj zog me ntsis, thiab ua kom cov ntshav ncig zoo dua.
• Cov tshuaj diuretics lossis "tshuaj ntsiav dej": Cov no ua haujlwm los ntawm kev ua rau lub cev tso cov ntsev thiab dej ntau dhau los ntawm cov zis. Qhov no txo ​​qhov o thiab txo qhov hnyav ntawm lub plawv.

Qee zaum, yog tias muaj kev pheej hmoo ntawm kev nres plawv tam sim ntawd, tus kws kho mob yuav pom zoo kom muab ib lub cuab yeej hu ua Implantable Cardioverter Defibrillator (ICD) cog rau hauv qab daim tawv nqaij ntawm lub plawv. Qhov no yog ib lub cuab yeej me me uas siv roj teeb. Nws ntes tau lub plawv dhia ceev ceev, uas ua rau tuag taus thiab xa hluav taws xob mus rau lub plawv kom rov qab ua haujlwm li qub. Hauv cov xwm txheej hnyav heev, yog tias lwm yam kev kho mob tsis ua tiav, yuav tsum tau hloov plawv .

Tus mob LVNC no puas kho tau tag nrho? Puas kho tau rov qab?

Auj, tsis yog. Tam sim no tsis muaj kev kho rau LVNC . Yog li ntawd, nws tsis tuaj yeem rov qab tau. Tab sis tsis txhob txhawj. Kev kho mob tuaj yeem txhim kho koj lub neej zoo dua thiab txo cov teeb meem uas tuaj yeem tshwm sim vim yog kab mob plawv . Thiab, zoo li kuv tau hais ua ntej, hauv cov xwm txheej hnyav tshaj plaws, kev hloov plawv yuav tsum tau ua.

Peb yuav ua li cas kom tsis txhob muaj qhov teeb meem LVNC no?

Tsis muaj ib txoj kev twg los tiv thaiv tau LVNC. Qhov no yog vim nws feem ntau yog los ntawm cov yam ntxwv ntawm caj ces. Txawm li cas los xij, yog tias koj muaj qhov kev hloov pauv ntawm caj ces uas ua rau muaj tus mob no, lossis yog tias koj xav tias koj yuav muaj nws (piv txwv li, yog tias ib tug neeg hauv koj tsev neeg muaj tus mob no), kev kuaj caj ces yuav pab tau heev.Ib tug kws pab tswv yim txog caj ces yuav piav qhia koj cov txiaj ntsig ntawm kev kuaj mob rau koj thiab koj tsev neeg. Lawv yuav pab koj nkag siab txog lub ntsiab lus ntawm kev muaj LVNC thiab koj qhov kev pheej hmoo ntawm kev kis tus kab mob mus rau koj cov menyuam yog dab tsi.

Puas muaj lwm yam mob uas cuam tshuam nrog tus mob LVNC no?

Yog. Qee zaum qhov mob no hu ua '(LVNC)' kuj pom tau tias yog ib feem ntawm lwm yam mob caj ces (syndrome). Cov no nyuaj me ntsis, tab sis cov kws kho mob kuj xav txog cov mob no thaum kuaj mob '(LVNC)'. Nov yog ob peb yam piv txwv:

• Barth syndrome
• Noonan syndrome
• Roifman syndrome
• Toriello Carey syndrome

Yav tom ntej ntawm ib tug neeg uas muaj LVNC yuav zoo li cas? Lub neej cia siab yog dab tsi?

Tus neeg uas muaj tus kab mob LVNC yuav muaj tus cwj pwm txawv. Nws txawv ntawm ib tus neeg mus rau ib tus neeg. Yog tias kho tau zoo, cov tsos mob yuav raug tswj tau , thiab qee tus neeg muaj lub neej ntev li qub.

LVNC yog ib qho mob uas yuav ua rau tuag taus, tab sis nws tsis yog li ntawd tas li . Feem ntau cov neeg uas muaj LVNC tsis tuag los ntawm tus kab mob no. Qhov tseem ceeb tshaj plaws yog mus ntsib kws kho mob plawv tsis tu ncua thiab mus kuaj mob . Nws tuaj yeem pab koj tswj koj txoj kev noj qab haus huv ntawm lub plawv thiab txo koj txoj kev pheej hmoo ntawm cov teeb meem.

Yog tias kuv lossis kuv tus menyuam muaj LVNC, kuv yuav tsum nug tus kws kho mob li cas?

Yog tias koj lossis koj tus menyuam muaj (LVNC), lossis yog tias koj muaj kev txhawj xeeb, nws yog ib lub tswv yim zoo los nug koj tus kws kho mob cov lus nug zoo li no:

• Dab tsi yog qhov ua rau kuv/kuv tus menyuam muaj mob LVNC tshaj plaws? (piv txwv li, nws puas yog caj ces lossis lwm yam)
• Koj puas pom zoo kom kuaj noob caj noob ces rau LVNC? Yog tias yog, puas yog qhov tseem ceeb rau lwm tus neeg hauv tsev neeg?
• Kuv/kuv tus menyuam yuav tsum tau kuaj dab tsi thiaj li paub tias muaj tus kab mob LVNC? Kuv yuav tsum tau tos txais dab tsi ntawm lawv?
• Cov kev kho mob rau LVNC yog dab tsi? Kev kho mob twg zoo tshaj plaws rau kuv/kuv tus menyuam? Puas muaj tej yam tshwm sim tsis zoo rau cov kev kho mob no?
• Yog tias kuv tus menyuam lossis kuv lub plawv nres tam sim ntawd, cov tsos mob yog dab tsi? Kuv yuav tsum ua li cas tam sim ntawd?

Cov lus nug no yuav pab koj tham nrog koj tus kws kho mob thiab nkag siab zoo dua txog koj tus mob.

Yog li ntawd, tej yam tseem ceeb tshaj plaws uas peb yuav tsum nco ntsoov los ntawm zaj dab neeg no yog dab tsi?

Lub plawv sab laug tsis ua haujlwm (LVNC) yog ib yam kab mob plawv uas tsis tshua muaj, feem ntau yog los ntawm niam txiv los. Qhov no yog thaum lub plawv sab laug tsis loj hlob zoo. Hloov chaw ua ib daim leeg nqaij du thiab muaj zog, nws ua tuab thiab zoo li daim ntaub. Qhov no ua rau lub plawv tsis tso ntshav tau zoo.

Yog koj muaj `(LVNC)`,Qhov tseem ceeb tshaj plaws yog mus ntsib kws kho mob plawv tsis tu ncua thiab ua raws li lawv cov lus qhia. Txawm hais tias tsis muaj kev kho rau qhov no, kev kho mob uas koj tus kws kho mob muab rau koj tuaj yeem txo koj qhov kev pheej hmoo ntawm cov teeb meem thiab txhim kho koj lub neej zoo. Nws yog ib qho tseem ceeb kom tsis txhob ntshai thiab tau txais kev kho mob zoo . Nco ntsoov, koj tsis nyob ib leeg, thiab cov kws kho mob nyob ntawd los pab koj.

Kab mob plawv, sab laug ventricle, LVNC, cov tsos mob ntawm kab mob plawv, lub plawv tsis ua haujlwm, cov kab mob caj ces, kev kho mob plawv