Koj puas txhawj txog koj lub plawv dhia ceev? Cia peb kawm txog Short QT Syndrome (SQTS)!

Koj puas muaj tej lub sij hawm koj kiv taub hau los yog qaug zog? Los yog koj puas muaj ib tug neeg uas koj paub tam sim ntawd muaj mob plawv nres? Tej lub sij hawm qhov ua rau muaj tej yam no yog ib yam mob caj ces uas peb tsis tshua hnov ​​txog. Ib yam mob zoo li no yog Short QT Syndrome, los yog raws li cov kws kho mob hu ua Short QT Syndrome (SQTS) . Txawm hais tias lub npe yuav zoo li nyuaj me ntsis, cia peb tham txog nws yooj yim xwb.

Lub sijhawm QT yog dab tsi? Cov teeb liab hluav taws xob ntawm lub plawv!

Zoo, ua ntej cia peb saib seb lub sijhawm QT no yog dab tsi. Koj puas paub tias peb lub plawv dhia siv lub tshuab hluav taws xob? Nws zoo li lub tshuab hluav taws xob hauv tsev kom tig teeb. Vim yog cov tshuab hluav taws xob no ua rau cov chav ntawm lub plawv sib cog lus thiab nthuav dav, uas yog qhov uas ua rau cov ntshav ntws.

Tej zaum koj twb tau pom ib tug kws kho mob ua qhov kev kuaj ECG (electrocardiogram) thaum lawv kuaj koj lub plawv. Lawv ua qhov kev kuaj no los ntawm kev kom koj pw saum txaj thiab muab cov ntawv nplaum me me lo rau ntawm koj lub hauv siab thiab caj npab. Qhov ntawd yog qhov uas sau cov haujlwm hluav taws xob ntawm lub plawv. Thaum tus kws kho mob saib daim ntawv kaw no, nws pom ib qho qauv nthwv dej tshwj xeeb hu ua P, Q, R, S, T. Txhua tsab ntawv no qhia koj tias qhov sib txawv ntawm lub plawv ua haujlwm li cas.

Hais yooj yim xwb:

• nthwv dej P: Lub teeb liab hluav taws xob uas ua rau cov chav sab saud ntawm lub plawv, lub atria, kom sib zog.
• QRS complex: Lub teeb liab hluav taws xob uas ua rau cov chav hauv qab ntawm lub plawv, hu ua ventricles, kom sib zog. Qhov no yog qhov tseem ceeb tshaj plaws uas thawb cov ntshav mus rau lub cev.
• T wave: Cov hlab ntsha hauv lub plawv tau ua tiav qhov kev sib zog lawm, so dua, thiab tab tom npaj rau qhov kev dhia tom ntej. Nws zoo li khiav thiab tom qab ntawd so me ntsis.

Tam sim no ntawm no yog qhov tseem ceeb. Lub sijhawm QT yog lub sijhawm txij thaum pib ntawm QRS complex mus txog thaum kawg ntawm T nthwv dej. Qhov no yog li cas cov kws kho mob ntsuas seb nws siv sijhawm ntev npaum li cas rau koj lub plawv cov chav qis (cov 'ventricles') los npaj rau lub plawv dhia tom ntej tom qab ib lub plawv dhia. Feem ntau, lub sijhawm QT hauv lub plawv noj qab haus huv yog ntawm 0.35 thiab 0.45 vib nas this. Txawm li cas los xij, rau ib tus neeg uas muaj SQTS , lub sijhawm no tsawg dua 0.34 vib nas this. Qhov no txhais tau tias lub plawv pib dhia dua ua ntej nws tuaj yeem so.

Qhov txawv ntawm Short QT Syndrome (SQTS) thiab Long QT Syndrome yog dab tsi?

Qhov no tej zaum yuav tseem ceeb rau koj. Nrog rau SQTS, muaj lwm yam mob hu ua Long QT Syndrome (LQTS) . Nws zoo li sab tod ntawm lub npib, puas yog?

• Short QT Syndrome (SQTS): Lub sijhawm QT luv dua li qub (feem ntau tsawg dua 0.34 vib nas this).
• Kab mob QT ntev (LQTS): Lub sijhawm QT ntev dhau lawm (feem ntau ntau dua 0.45 vib nas this).

Ob qho mob no tuaj yeem ua rau muaj teeb meem uas cuam tshuam rau lub plawv dhia. Txawm li cas los xij, cov ua rau thiab kev kho mob yuav txawv. Hnub no peb tsuas yog yuav tham txog SQTS xwb.

Leej twg thiaj li tsim tau SQTS?

Qhov no yog ib qho mob tsis tshua muaj . Tsis paub meej tias muaj pes tsawg tus neeg hauv ntiaj teb no muaj nws, nws tsis tshua muaj. Qee qhov kev tshawb fawb tau pom tias cov tsos mob SQTS tuaj yeem tshwm sim rau qee tus neeg hauv thawj xyoo ntawm lub neej. Tom qab ntawd, nws tau hais tias cov tsos mob tuaj yeem rov tshwm sim hauv cov tub ntxhais hluas thiab txawm tias laus. Qhov no txhais tau tias nws tuaj yeem cuam tshuam rau cov neeg txhua lub hnub nyoog.

Dab tsi yog cov ua rau muaj SQTS?

SQTS yog ib yam kab mob caj ces . Ib yam li koj cov xim qhov muag thiab cov plaub hau raug txiav txim los ntawm koj cov noob caj ces, tus kab mob no kuj tuaj yeem tshwm sim los ntawm kev hloov pauv noob caj ces.

Muaj ob txoj kev uas qhov no yuav tshwm sim tau:

1. Kev tau txais qub txeeg qub teg los ntawm niam txiv: Yog tias koj niam lossis koj txiv muaj qhov kev hloov pauv caj ces no, koj kuj tuaj yeem tau txais qub txeeg qub teg.

2. Kev hloov pauv ntawm cov noob caj noob ces yam tsis muaj laj thawj: Qee zaum, qhov kev hloov pauv ntawm cov noob caj noob ces no tuaj yeem tshwm sim hauv koj lub cev yam tsis muaj laj thawj, txawm tias tsis muaj leej twg hauv koj tsev neeg muaj nws los xij.

Cov kev hloov pauv caj ces no hloov pauv qhov ua haujlwm ntawm cov khoom hu ua ion channels hauv cov hlwb plawv. Cov ion channels no pab cov teeb liab hluav taws xob ntawm lub plawv kom mus tau zoo. Thaum muaj teeb meem nrog lawv, lub sijhawm QT luv dua.

Cov tsos mob ntawm SQTS yog dab tsi?

Tsis yog txhua tus neeg uas muaj SQTS muaj cov tsos mob zoo ib yam. Tej zaum ib txhia neeg yuav tsis muaj cov tsos mob li. Txawm li cas los xij, feem ntau cov neeg muaj qee cov tsos mob.

Qhov tseem ceeb yog tias cov tsos mob no zoo ib yam li lwm yam mob plawv. Yog li ntawd, yog tias koj muaj tej yam zoo li no, nws yog qhov zoo tshaj plaws mus ntsib kws kho mob thiab mus kuaj mob.

Cov tsos mob tseem ceeb uas pom tau yog:

• Atrial Fibrillation (AFib): Qhov no yog cov tsos mob feem ntau. Nws tau tshaj tawm tias cuam tshuam rau kwv yees li 4 ntawm 5 tus neeg uas muaj SQTS. AFib yog thaum cov chav sab saud ntawm lub plawv (atria) tsis dhia zoo, tab sis hloov chaw "flutter." Qhov no ua rau lub plawv dhia tsis sib xws.
• Lub plawv dhia ceev: Kwv yees li 1 ntawm 3 tus neeg yuav muaj cov tsos mob no. Tej zaum yuav zoo li muaj ib tug neeg ntaus hauv lawv lub hauv siab, lossis tej zaum yuav zoo li lawv yeej hnov ​​​​​​qhov dhia ceev hauv lawv lub hauv siab.
• Kiv taub hau thiab tsaus muag lossis qaug zog: Qhov no tuaj yeem cuam tshuam txog li 1 ntawm 4 tus neeg. Nws tuaj yeem ua rau muaj kev xav tias qaug zog thiab qee zaum tsis nco qab.

Tu siab kawg li, muaj ib txhia neeg (kwv yees li 2 ntawm 5 tus) thawj zaug paub tias lawv muaj SQTS tom qab lawv lub plawv nres lossis lub plawv tuag tam sim ntawd. Qhov no yog tshwm sim los ntawm lub plawv dhia tsis xwm yeem (arrhythmia) hauv cov chav qis ntawm lub plawv, xws li ventricular fibrillation lossis ventricular tachycardia, uas ua rau lub plawv nres tam sim ntawd. Qhov no yog ib qho mob hnyav heev.

Xav txog seb, muaj ib tug tub hluas hnub nyoog 25 xyoo hu ua Asanka. Nws yog ib tug neeg ncaws pob zoo thiab noj qab nyob zoo. Muaj ib hnub, thaum nws ua si cricket nrog nws cov phooj ywg, nws cia li ntog rau hauv av thiab tuav nws lub hauv siab. Lawv maj nroos coj nws mus rau tsev kho mob, tiam sis nws tsis tau dim. Cov kev kuaj mob tom qab ntawd qhia tias Asanka muaj SQTS. Nws tu siab uas hnov ​​​​​​tej yam zoo li no, tiam sis nws yog ib qho tseem ceeb uas yuav tsum paub txog tej yam no.

Yuav kuaj mob SQTS li cas?

Yog koj xav tias koj muaj SQTS, tus kws kho mob yuav nug txog koj cov tsos mob ua ntej thiab seb puas muaj leej twg hauv koj tsev neeg muaj kab mob plawv. Tom qab ntawd lawv yuav ua cov kev kuaj mob hauv qab no:

• ECG (Electrocardiogram): Qhov no yog qhov kev kuaj tseem ceeb tshaj plaws. Nws ntsuas lub sijhawm QT. Feem ntau, yog tias lub sijhawm QT tsawg dua 0.34 vib nas this thiab muaj lwm yam tsos mob, qhov kev xav tias muaj SQTS. Qee zaum, txawm tias lub sijhawm QT yog nruab nrab ntawm 0.34 thiab 0.36 vib nas this, SQTS tuaj yeem suav nrog yog tias muaj lwm yam tsos mob (piv txwv li, keeb kwm tsev neeg ntawm SQTS, tsaus muag tsis paub meej).
• Kev kuaj noob caj noob ces: Qhov kev kuaj no yog ua los nrhiav seb puas muaj kev hloov pauv noob caj noob ces uas ua rau muaj SQTS. Qhov no tuaj yeem pab lees paub qhov kab mob thiab txiav txim siab seb lwm tus neeg hauv tsev neeg puas muaj kev pheej hmoo.

Qee zaum, koj yuav tsis muaj tsos mob thiab pom tias koj lub sijhawm QT luv dua thaum koj muaj ECG rau lwm qhov laj thawj.

Cov kev kho mob rau SQTS yog dab tsi?

Txawm hais tias SQTS yog ib qho mob hnyav heev los, nws kho tau. Nws yog kho los ntawm tus kws kho mob plawv. Nyob ntawm koj tus mob, koj tus kws kho mob yuav qhia cov kev kho mob hauv qab no:

• Lub Tshuab Ua Pa Hluav Taws Xob Rau Lub Plawv (ICD): Qhov no yog kev kho mob zoo tshaj plaws rau cov neeg laus uas muaj SQTS. Lub tshuab ICD yog ib lub tshuab me me uas raug phais muab tso rau hauv qab daim tawv nqaij ntawm lub hauv siab thiab txuas nrog lub plawv. Lub tshuab no saib xyuas lub plawv dhia tas li. Yog tias muaj lub plawv dhia tsis xwm yeem (arrhythmia), lub tshuab ICD yuav xa hluav taws xob mus rau lub plawv kom rov qab ua haujlwm. Nws zoo li tus neeg cawm siav thaum muaj xwm txheej ceev.
• Cov Tshuaj: Muaj cov tshuaj tiv thaiv kev mob plawv dhia tsis xwm yeem uas tswj lub plawv dhia. Piv txwv li, quinidine feem ntau siv rau SQTS. Koj tus kws kho mob kuj tseem yuav sau ntawv kom muab cov tshuaj xws li flecainide (Tambocor™) , ibutilide (Corvert® ), propafenone , amiodarone , sotalol , lossis beta-blockers (piv txwv li, metoprolol (Toprol XL®, Lopressor®) , carvedilol (Coreg®) ).

Tseem Ceeb: Cov tshuaj no tsuas yog yuav tsum noj yog tias koj tus kws kho mob tau sau ntawv kom noj xwb, thiab raws nraim li nws qhia rau koj. Kev siv cov tshuaj ntawm koj tus kheej tuaj yeem muaj cov teeb meem txaus ntshai.

Puas yuav txo tau qhov kev pheej hmoo ntawm SQTS?

Vim tias SQTS yog ib yam kab mob uas muaj los ntawm noob caj noob ces, tsis muaj ib txoj hauv kev los tiv thaiv nws kom tsis txhob loj hlob. Nws tsis yog ib yam dab tsi uas peb tuaj yeem tswj tau.

Txawm li cas los xij, yog tias koj raug kuaj pom tias muaj SQTS, nws yog ib qho tseem ceeb heev uas yuav tsum mus ntsib kws kho mob plawv tsis tu ncua thiab ua raws li lawv cov lus qhia. Lawv tuaj yeem saib xyuas koj lub plawv kom noj qab haus huv thiab pab txo qhov kev pheej hmoo ntawm cov teeb meem loj, tshwj xeeb tshaj yog kev tuag sai sai ntawm lub plawv, uas tuaj yeem tshwm sim vim yog SQTS.

Koj tuaj yeem nyob nrog SQTS tau ntev npaum li cas?

Qhov no yog ib lo lus nug uas ntau tus neeg nug. Lub sijhawm ntev npaum li cas koj tuaj yeem nyob nrog SQTS tuaj yeem sib txawv ntawm ib tus neeg mus rau ib tus neeg. Rau qee tus neeg, SQTS tuaj yeem ua rau tuag sai sai los ntawm lub plawv. Kev kwv yees hais tias cov neeg uas muaj SQTS muaj 40% kev pheej hmoo ntawm kev tuag sai sai los ntawm lub plawv thaum muaj hnub nyoog 40 xyoo. Qhov kev pheej hmoo no siab tshaj plaws rau cov menyuam mos hnub nyoog 0-1 thiab cov tub ntxhais hluas hnub nyoog 20-40. Yog tias qhov no tshwm sim rau tus menyuam mos hnub nyoog ntawm tus menyuam mos thiab 1 xyoos, cov kws kho mob kuj tseem yuav hu nws tias Sudden Infant Death Syndrome (SIDS) .

Tiam sis, tsis txhob ntshai qhov no. Qhov tseem ceeb uas yuav tsum nco ntsoov yog tias tsis yog txhua tus neeg uas muaj lub sijhawm luv luv ntawm QT (tsawg dua 360 milliseconds) ntawm ECG muaj SQTS, thiab tsis yog txhua tus neeg muaj kev pheej hmoo ntawm kev tuag sai sai ntawm lub plawv. Qee tus neeg uas muaj SQTS tuaj yeem ua neej nyob ib txwm yam tsis muaj tsos mob dab tsi. Vim tias SQTS yog ib qho mob tsis tshua muaj, cov kws tshawb fawb tseem tab tom tshawb nrhiav seb nws cuam tshuam li cas rau lub neej.

Koj tus kws kho mob tuaj yeem pab koj tswj koj tus mob thiab txo koj qhov kev pheej hmoo ntawm cov teeb meem los ntawm kev muab cov kev xaiv kho mob tsim nyog.

Koj xav nug koj tus kws kho mob dab tsi ntxiv?

Yog tias koj xav tias koj muaj SQTS, lossis yog tias koj tau kuaj pom tias muaj nws, nws yog ib lub tswv yim zoo los nug koj tus kws kho mob cov lus nug no:

• Cov tsos mob ntawm SQTS yog dab tsi? Kuv cov tsos mob puas haum rau qhov no?
• Kuv yuav tsum tau ua dab tsi los kuaj mob SQTS?
• Kuv muaj cov kev kho mob twg? Qhov twg zoo tshaj plaws rau kuv?
• Kuv yuav ua tau dab tsi hloov kuv lub neej kom kuv lub plawv noj qab nyob zoo? (piv txwv li, tsis txhob noj tshuaj, ua tej yam dej num me me)
• Muaj feem ntau npaum li cas uas kuv cov menyuam yuav tau txais SQTS? Puas muaj kev kuaj mob uas yuav tsum tau nrhiav?

Ntxiv rau cov lus nug no, tsis txhob ntshai tham nrog koj tus kws kho mob txog txhua yam uas koj xav lossis muaj kev tsis ntseeg txog.

Nov yog cov ntsiab lus luv luv ntawm yam peb tau tham txog (Cov Lus Coj Mus Tsev):

Zoo ces, cia peb nco ntsoov qhov peb tau tham txog:

• Short QT Syndrome (SQTS) yog ib yam kab mob uas tsis tshua muaj, uas yog los ntawm noob caj noob ces.
• Qhov tshwm sim hauv qhov no yog tias lub sijhawm QT, lub sijhawm hauv lub plawv lub zog hluav taws xob, luv luv tsis zoo. Hais yooj yim, nws txo lub sijhawm uas nws siv rau cov chav qis ntawm lub plawv los npaj rau lub plawv dhia tom ntej tom qab ib lub plawv dhia.
• Qhov no tuaj yeem ua rau muaj cov tsos mob xws li kiv taub hau, tsaus muag, thiab mob hauv siab.
• Qee zaum, tej zaum yuav tsis muaj tsos mob li.
• SQTS yog ib qho mob hnyav uas tuaj yeem ua rau lub plawv nres tam sim ntawd thiab txawm tias tuag tau.
• Txawm li cas los xij, qhov no tuaj yeem kuaj pom los ntawm ECG thiab kev kuaj noob caj noob ces.
• Qhov no tuaj yeem kho tau nrog cov khoom siv ICD thiab cov tshuaj.
• Yog koj muaj lus nug txog qhov no, lossis yog tias muaj leej twg hauv koj tsev neeg muaj hom kab mob plawv no, nco ntsoov mus ntsib kws kho mob kom tau lus qhia.

Nco ntsoov, nws yog ib qho tseem ceeb uas yuav tsum paub txog tej yam no thiab nrhiav kev pab kho mob raws sijhawm. Xav kom koj noj qab nyob zoo!

` Short QT syndrome, SQTS, kab mob plawv, ECG, QT interval, kab mob caj ces, lub plawv nres tam sim ntawd, ICD