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Yu pikin gɛt dis kayn at prɔblɛm? Lɛ wi lan bɔt (Atrioventricular Canal Defect)!

Yu pikin gɛt dis kayn at prɔblɛm? Lɛ wi lan bɔt (Atrioventricular Canal Defect)!

Sɔntɛnde, yu go dɔn notis se yu pikin we dɛn jɔs bɔn kin gɛt prɔblɛm fɔ blo, i kin tray tranga wan fɔ gi am tin fɔ it, ɔ i kin ivin tɔn blu. Sɔmtɛm dɛn tin ya kin bi sayn fɔ smɔl prɔblɛm wit yu pikin in at. Dat na tru, wan hat kכndyushכn we de we dεn bכn dεn kכl am Atrioventricular Canal Defect , we wi de tכk bכt tide.

Wetin na dis (Atrioventricular Canal Defect)?

Fɔ tɔk am simpul wan, Atrioventricular Canal Defect na at prɔblɛm we kin de we dɛn bɔn am. Sɔntɛnde dɔktɔ dɛn kin kɔl am AVSD - Atrioventricular Septal Defect . Fɔ tɔk di kɔrɛkt tin, na bɔku at prɔblɛm dɛn we kin kam togɛda. di men wan na dat wan ol כ ol de na di wכl na di midul pan di at (wi kכl dis di septum) . I kin min bak se di valv dɛn na di at nɔ de wok fayn.

Tink bɔt am lɛk ol we de na wata paip. Insay at we gɛt wɛlbɔdi, di blɔd we gɛt bɔku ɔksijɛn we dɛn kin pɔmp frɔm di lɛft say na wi at nɔ kin miks wit di blɔd we nɔ gɛt ɔksijɛn we kɔmɔt na di rayt say. Bɔt bikɔs ɔf dis ol, da blɔd de we gɛt bɔku ɔksijɛn kin miks wit di blɔd we nɔ gɛt ɔksijɛn. Bɔku tɛm, dis ol kin mek tumɔs blɔd go na di lɔng dɛn. Dɔn di blɔd we de go na di ɔda pat dɛn na di bɔdi kin go dɔŋ. If dis kin go fɔ lɔng tɛm, sɔntɛnde i kin go di ɔda we. Dat min se, mɔ blɔd we nɔ gɛt ɔksijɛn de go na di bɔdi, ɛn smɔl smɔl de go na di lɔng dɛn. We dat apin, di ɔksijɛn we de na di bɔdi kin go dɔŋ ɛn di skin kin tɔn blu. Wi kin kɔl am saynosis .

Dis kin mek di at wok tranga wan, we kin mek yu gɛt ɔda wɛlbɔdi prɔblɛm dɛn lɛk we at kin pwɛl .

If dɛn nɔ trit dis (Atrioventricular Canal Defect) fayn, sɔntɛnde i kin afɛkt di pikin in layf. If dɛn nɔ du ɔpreshɔn, pikin dɛn we gɛt dis sik kin jɔs liv fɔ shɔt tɛm, lɛk tu to tri ia. Bɔt nɔ wɔri! Di bɛst tin na dat ɔpreshɔn fɔ kɔrɛkt dis kin rili wok fayn. Dɔktɔ dɛn kin no dis sik bifo i siriɔs, ivin bifo dɛn bɔn di pikin.

Na avrej, na kɔntri dɛn lɛk Amɛrika, na lɛk wan pan ɛvri 1,700 pikin dɛn kin bɔn wit dis prɔblɛm ɛvri ia. dis de mek bitwin 3% εn 5% pan כl di hat dεm we dεn bכn wit.

Dɛn kin kɔl dis kɔndishɔn sɔm ɔda nem dɛn. Yu dɔktɔ kin yuz wan pan dɛn nem ya:

  • Atrioventrikular septal difεkt (AVSD) .
  • Difεkt na di εndokardial kushכn

Difrɛn kayn Atrioventricular Canal Defect de?

Yɛs, dis at prɔblɛm kin kam difrɛn we dɛn. dat min se i dipכnt pan tin dεm lεk di sayz fכ di ol na di at εn di nכmba fכ di valv dεm.

Komplit (Atrioventrikulεr Kanal Dεfεkt) .

wetin kin apin pan dis na di tu כp chεmba dεm na di at (wi kכl dεm atria) εn di tu lכw chεmba dεm (wi kכl dεm vεntrikl) .(dεn kכl am) wan big ol de fכm bitwin di tu chεmba dεm na di at. Dat min se ɔl di 4 chɛmba dɛn na di at gɛt kɔnekshɔn togɛda. nכmal wan, tu valv dεm fכ de bitwin di כp εn lכw chεmba dεm. Bɔt insay dis kes, na wan big valv nɔmɔ de. I kin bi se in flap nɔ opin ɔ lɔk fayn.

Patεl (Partial Atrioventrikulεr Kanal Dεfεkt) .

insay dis kayn we, di ol de bitwin di tu כp chεmba dεm na di at (dis na di wan we kכmכn pas כl) כ bitwin di tu lכw chεmba dεm. Ɔl di 4 chɛmba dɛn nɔ gɛt kɔnekshɔn. Tu valv dɛn de bitwin di ɔpa ɛn di ɔda chɛmba dɛn. bכt wan valv (bכku tεm di mitral valv, we de bitwin di כp chεmba (lεft atrium) εn di lכw chεmba (lεft vεntrikl) na di lεft sayd) nכ de wok fayn.

Transishɔnal Atrioventrikular Kanal Difɛkt

Insay dis, wan ol de bitwin di tu chɛmba dɛn we de ɔp ɛn wan smɔl ol de bitwin di tu chɛmba dɛn we de dɔŋ. di tu valv dεm bitwin di כp εn lכw chεmba dεm (AV valv dεm) de separet.

Unbalanced Komplit Atrioventrikular Kanal Difekt

Yu mɛmba aw insay wan kɔmplit at prɔblɛm, wan big valv de? da valv de de nia wan lכw chεmba (vεntrikul) pas di כda wan. Dɔn di chɛmba we gɛt mɔ blɔd kin big pas di ɔda wan. Dɔktɔ dɛn kin kɔl da smɔl chɛmba de ‘haypoplastik’ .

Wetin na di sayn dɛm fɔ dis?

Di sayn dɛm fɔ dis at prɔblɛm kin apin ivin bifo dɛn bɔn yu pikin. Chek fɔ si if yu pikin gɛt ɛni wan pan dɛn tin ya:

  • Blu skin kɔlɔ (Cyanosis): Ɛspɛshali na say dɛn lɛk di lip, di tɔŋ, ɛn di finga dɛn.
  • I nɔ izi fɔ drink milk: I kin fil taya ɛn taya afta yu dɔn drink smɔl milk.
  • Swet afta yu dɔn drink milk.
  • Fɔ taya kwik kwik wan: Taya ivin afta yu dɔn du smɔl tin.
  • Di at we de blo.
  • I nɔ izi fɔ yu fɔ blo (Dyspnea) ɔ fɔ blo kwik kwik wan.
  • We yu gɛt bɔku bɔku wet kin apin smɔl smɔl.
  • Swel (edema) na di bɛlɛ ɔ di leg dɛn.
  • Wik puls.

Bɔt pikin dɛn we gɛt sɔm kayn prɔblɛm ɔ we kin chenj, nɔ kin sho dɛn sik ya fɔs. Dɛn sayn ya kin apin leta we i smɔl, ɔ we i yɔŋ, ɔ ivin we i big.

Wetin mek dis (Atrioventricular Canal Defect) kin apin?

Risach pipul dɛn stil nɔ no bɛtɛ bɛtɛ wan wetin kin mek pɔsin gɛt Atrioventricular Septal Defect (AVSD) . Dɛn tink se na tin dɛn we de mek pɔsin gɛt jɛnɛtiks ɛn di tin dɛn we de apin na di say we i de . Bɔt wan tin klia: strɔng link de bitwin dis at sik ɛn Daun sindrom . Na lɛk 40% pan di pikin dɛn we gɛt Daun sindrom gɛt AVSD .

Wetin na de risk factor wae kin afekt dis?

Di masta sabi pipul dɛm nɔr dɔn no yet di rayt risk factor dɛm wae kin mek dis sik. I kin bi se sɔntin de we kin mek pɔsin gɛt sɔntin fɔ du wit in jɛnɛtiks. Sɔntɛm wan abnɔmal jin we dɛn pas frɔm di mama ɔ di papa kin mek di pikin gɛt mɔ chans fɔ gɛt at sik we i stil de na di bɛlɛ.

Apat frɔm dat, dɛn tin ya we yu gɛt bɛlɛ kin mek yu pikin gɛt at sik we dɛn bɔn wit:

  • Sɔm mɛrɛsin dɛn.
  • Ilɛgal drɔgs (Rɛkrɛshɔn drɔgs).
  • Drink dɛn we gɛt rɔm.
  • Fɔ gɛt pɔyzin ɔ kemikal dɛn we de na di envayrɔmɛnt.
  • Di tin dɛn we yu nɔ gɛt bɛtɛ tin fɔ it ɔ vaytamɛn.
  • Fat.
  • Di tin dɛn we dɛn kin mek wit tabak.
  • Nɔr fɔ kɔntrol sik dɛm wae nɔr de mɛn lɛk Dayabitis ɔr Haypatɛnshɔn.
  • Vayral sik dɛm lɛk influenza (flu) ɔ flu.

Wetin na di poshubul kɔmplikeshɔn dɛm fɔ Atrioventricular Canal Defect?

If dis sik bad bad wan, we min se dɛn nɔ trit am fayn, prɔblɛm dɛn lɛk dis kin apin:

  • Abnɔmal hat rit patɛn (Aritmia).
  • Kɔnjɛstiv at we nɔ de wok fayn.
  • Infεkshכn dεm na di at (Endocarditis).
  • di bכdi prεshכn na di bכdi we de go na di lכng (Pulmonary hypertension).

Aw dɛn kin no dis sik?

di gud nyus na dat bכku tεm, dכkta dεm kin no dis (Atrioventricular Septal Defect) bifo dεn bכn di pikin wit fכ tεst dεm:

  • di ultrasound bifo di pikin bכn: dis kin si pikchכ dεm fכ di pikin in muvmεnt dεm na di bεlε, inklud di at. I kin no bak wan big septal difεkt .
  • Fetal echocardiogram: dis de sho imej dεm fכ di at klia wan pas כltra saund. Di dɔktɔ kin gɛt bɛtɛ aidia bɔt aw di at de ɛn aw i de pɔmp blɔd.

Afta dɛn dɔn bɔn di pikin, dɔktɔ kin lisin to di pikin in at bit wit stetɔskɔp . If yu yɛri wan ɔnusual "lawd" sawnd (wi kɔl am at murmur ), i kin bi di sawnd we blɔd de flɔ tru di ol.

Ɔda tɛst dɛn we dɛn kin du afta dɛn bɔn pikin na:

  • Chεst X-ray: Chεk di saiz εn shep fכ di pikin in at.
  • Ilektrokardiogram (EKG/ECG): Luk di ilɛktrik aktiviti we di pikin in at de du.
  • Echocardiogram: Na wan rili ditayli luk pan di strכkchכ fכ di pikin in at.
  • Cardiac catheterization: Lan mɔ bɔt aw di pikin in sik tranga.
  • Cardiac Magnetic Resonance Imaging (Hat MRI): Si di pat dεm na di pikin in at εn aw dεn de wok.

Sɔntɛnde, if pikin gɛt smɔl septal dɛfekt , i nɔ kin sho ɛni sayn fɔs. If na so i bi, i kin tek sɔm ia bifo dɔktɔ no bɔt di sik.

Wetin na di tritmɛnt dɛm fɔ dis?

Di tritmɛnt we dɛn kin yuz mɔ fɔ Atrioventricular Canal Defect na ɔpreshɔn we dɛn kin du wit opin at . Insay dis ɔpreshɔn, di dɔktɔ kin pat di ol na di pikin in at ɛn lɔk am. if di defεkt kכmplit , dεn de sheb di wan at valv to tu, we de mek tu difrεnt valv dεm, wan na di rayt say εn wan na di lεft say.

Bebi we gɛt AV kanal we nɔ balans kin nid fɔ du bɔku ɔpreshɔn, ɛn dis kin dɔn wit ɔpreshɔn we dɛn kɔl Fontan prosidur .

I bɛtɛ fɔ mek dɛn du dis ɔpreshɔn kwik kwik wan, bifo di sik pwɛl di at fɔ ɔltɛm. Bɔku pikin dɛn kin gɛt dis ɔpreshɔn insay di fɔs siks mɔnt we dɛn de liv. Sɔm pikin dɛn we gɛt sɔm pat pan di sik bɔt we nɔ gɛt ɛni sayn kin gɛt dis ɔpreshɔn insay di fɔs tri ia we dɛn de liv.

Sɔntɛnde, if di pikin nɔ gɛt wɛlbɔdi fɔ mek dɛn du am ɔpreshɔn, ɔ i nɔ gɛt bɛtɛ wet, dɛn kin gi am mɛrɛsin fɔ kɔntrol di sik dɛn te i gɛt wet ɛn trɛnk.

  • Diuretics na mɛrɛsin we de pul di wata we pasmak na di bɔdi.
  • Digoxin de ɛp di pikin in at fɔ bit tranga wan.
  • ACE inhibitors de mek di blɔd vesel dɛn big ɛn mek i izi fɔ mek di blɔd flɔ.

Wan ɔda we fɔ sɔlv di prɔblɛm fɔ shɔt tɛm na wan tin we dɛn kɔl pulmonary artery banding . dis de ridyus di bכdi we de fכlכ tru di pulmonari atεri to di pikin in lכng. Bebi dεm we dεn bin dכn bכnd pulmonary artery banding kin gεt fכ rεpair fכ pεrmanεnt leta.

Kɔmplikɛshɔn kin apin afta dɛn dɔn trit am?

Yɛs, sɔntɛnde tin dɛn lɛk dis kin apin afta dɛn dɔn du di ɔpreshɔn:

  • di at blכk: dis min se di at in puls signal nכ de rich di lכw pat na di at fayn fayn wan.
  • Wan lek lef ɔ rayt AV valv.
  • wan ol na di wכl na di lכw chεmba (Ventricular septal defect).
  • Narrowing (Stenosis) fכ di lεft כ rayt AV valv.
  • wan tin we de ambɔg di bכdi fכ fכlכ dεn dכn di aorta valv (Subaortic stenosis).

Dɛn nɔ kin ebul fɔ stɔp dis (Atrioventricular Canal Defect)?

Rili no we nɔ de fɔ mek dis (Atrioventricular Septal Defect) nɔ apin, bikɔs bɔku tɛm i kin gɛt fɔ du wit di jɛnɛtik kɔz dɛm.

Bɔt if yu gɛt bɛlɛ, yu kin du dɛn tin ya fɔ mek yu pikin nɔ gɛt at sik we dɛn bɔn wit:

  • Nɔ tek drɔgs we nɔ rayt, rɔm, ɛn tin dɛn we dɛn kin yuz fɔ smok, kpatakpata.
  • Gɛt ɔl di vaysin dɛn we yu nid fɔ protɛkt yusɛf frɔm sik.
  • Mek yu gɛt wɛlbɔdi wet.
  • If yu gɛt wɛlbɔdi prɔblɛm dɛn we nɔ de mɛn, manej dɛn fayn fayn wan.
  • Tek vaytamɛn dɛn bifo yu bɔn, mɔ di fɔlik asid, lɛk aw yu dɔktɔ tɛl yu.

If mi pikin gɛt dis sik, aw tumara bambay go tan lɛk?

If dɛn nɔ du ɔpreshɔn, pikin dɛn we gɛt AV kanal difrɛns kin jɔs liv fɔ tu to tri ia. Sɔm kin liv te dɛn yɔŋ.

Bɔt di gud nyus na dat lɛk 90% pan di pikin dɛn we dɛn dɔn du da ripɛnt ɔpreshɔn de kin liv 10 ia afta da tritmɛnt de. Dat min se dɛn kin liv at le 10 ia mɔ afta di ɔpreshɔn. Na lɛk 65% de liv 20 ia afta di ɔpreshɔn.

Bɔt mɛmba dis: Ivin afta dɛn dɔn du di ɔpreshɔn, pɔsin we gɛt Atrioventricular Canal Defect (AVCD) nɔ go gɛt at we nɔmal ɔl. Dɛn go nid fɔ kɔntinyu fɔ gɛt ɛkokadiogram ɔltɛm fɔ wach aw dɛn at de wok. Dis go ɛp fɔ kech ɛni kɔmplikeshɔn kwik kwik wan.

Di pat we dɛn kin put oba di ol kin las fɔ ɔl in layf. Bɔt as tɛm de go, wan pan di at valv dɛn we dɛn dɔn ripɛnt kin bigin fɔ lik. If dat apin, bitwin 10% ɛn 20% pan pipul dɛn go nid fɔ gɛt ɔpreshɔn fɔ di sɛkɔn tɛm .

Bɔku pipul dɛn nɔ nid mɛrɛsin ɔ ɔda ɔpreshɔn afta dɛn dɔn du dɛn ɔpreshɔn. Bɔt, di at kin apin leta. If dis apin, dɔktɔ kin tɛl yu fɔ du tin dɛn we go ambɔg yu lɛk fɔ pul yu bɔdi .

Aw a go kia fɔ mi pikin?

Yu go nid fɔ stɔp yu pikin fɔ du bɔku tin dɛn . Aks yu pikin in pikin dɛn kadyolɔjis - dɔktɔ we spɛshal pan at sik na pikin dɛn - bɔt dis.

Dɛn kin advays pikin dɛn we gɛt atrioventricular septal defect (AVSD) fɔ tek antibayɔtik bifo dɛn go to di dɛntist. Dis kin ɛp fɔ mek yu nɔ gɛt wan kayn at infɛkshɔn we dɛn kɔl ɛndokadaytis . Tɔk to yu pikin in dɔktɔ we de mɛn in at bɔt dis bak.

Ustɛm mi pikin fɔ go to dɔktɔ?

Yu fɔ rili kɛr yu pikin go to dɛn pikin dɛn we de mɛn dɛn at ɔltɛm. Dɛn kin wach yu pikin in at fɔ ɛni prɔblɛm. Sɔm pikin dɛn we gɛt AV kanal difrɛns kin nid fɔ gɛt mɔ tritmɛnt afta dɛn dɔn du dɛn ɔpreshɔn. Di pat kin lik, ɔ wan valv we dɛn dɔn ripɛnt kin lik ɔ i kin smɔl.

Pikin we gɛt AV kanal difrɛns kin gɛt nyurolɔjik ɔ divɛlɔpmɛnt prɔblɛm bak . Dɛn kin nid ɛp bak fɔ du dat.

We yu pikin dɔn big, i fɔ muf to big pɔsin we sabi bɔt at we dɛn bɔn wit ɛn go chɛk-ap wan tɛm insay di ia.

Us kwɛstyɔn dɛn a fɔ aks mi pikin in dɔktɔ?

Yu kin aks yu pikin in dɔktɔ kwɛstyɔn dɛn lɛk:

  • Us kayn AV kanal dɛfekt mi pikin gɛt?
  • Wetin na de sayn dɛm wae de sho se de sik de wɔs?
  • Ustɛm i go nid fɔ du ɔpreshɔn?
  • Mi pikin go nid mɛrɛsin afta di ɔpreshɔn?
  • A go gɛt fɔ stɔp mi pikin fɔ du tin?

I nɔmal fɔ gɛt difrɛn kayn filin dɛn we yu yɛri se yu nyu bɔbɔ gɛt at sik lɛk Atrioventricular Canal Defect . Bɔt yu pikin in dɔktɔ dɛn de fɔ ɛp yu, ɛn dɛn want fɔ du wetin bɛtɛ fɔ yu pikin. Fɛn ɔut ɛksaktɔli wetin spɛshal fɔ yu pikin in kɔndishɔn. If ɛnitin de we yu nɔ shɔ bɔt, aks yu dɔktɔ bɔt am. Naw na di tɛm fɔ advatayz fɔ yu pikin in wɛlbɔdi.

So, wetin na di tin dɛn we wi nid fɔ mɛmba frɔm ɔl dɛn tin ya?

  • Atrioventricular Canal Defect na at kכndyushכn we de de we dεn bכn am. I kin mɔs bi bikɔs ɔf wan ol na di at ɛn prɔblɛm wit di valv dɛn.
  • Fɔ no di pɔsin kwik kwik wan ɛn fɔ du ɔpreshɔn di rayt tɛm rili impɔtant. Dɛn ɔpreshɔn dɛn ya kin rili wok fayn.
  • Bebi dεm we gεt Daun sεndr כm kin gεt dis kכndyushכn.
  • Dɛn nid fɔ de kia fɔ di dɔktɔ fɔ lɔng tɛm ivin afta dɛn dɔn du di ɔpreshɔn. Yu nid fɔ de tɔk to dɔktɔ we de mɛn yu at fɔ di res ɔf yu layf.
  • If yu gɛt bɛlɛ, fɔ fala wɛlbɔdi layf ɛn fala dɔktɔ advays kin ɛp fɔ mek yu pikin nɔ gɛt at sik we dɛn bɔn wit.
  • Nɔ fred, di dɔktɔ dɛn de fɔ ɛp yu ɛn yu pikin. Aks kwɛstyɔn, mek dɛn no bɔt am.

` At sik, hat difεkt we dεn bכn wit, pikin in at, ol na di at, Atrioventricular Canal Defect, AVSD, pikin at sik

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Yu pikin gɛt dis kayn at prɔblɛm? Lɛ wi lan bɔt (Atrioventricular Canal Defect)!

Yu pikin gɛt dis kayn at prɔblɛm? Lɛ wi lan bɔt (Atrioventricular Canal Defect)!

Sɔntɛnde, yu go dɔn notis se yu pikin we dɛn jɔs bɔn kin gɛt prɔblɛm fɔ blo, i kin tray tranga wan fɔ gi am tin fɔ it, ɔ i kin ivin tɔn blu. Sɔmtɛm dɛn tin ya kin bi sayn fɔ smɔl prɔblɛm wit yu pikin in at. Dat na tru, wan hat kכndyushכn we de we dεn bכn dεn kכl am Atrioventricular Canal Defect , we wi de tכk bכt tide.

Wetin na dis (Atrioventricular Canal Defect)?

Fɔ tɔk am simpul wan, Atrioventricular Canal Defect na at prɔblɛm we kin de we dɛn bɔn am. Sɔntɛnde dɔktɔ dɛn kin kɔl am AVSD - Atrioventricular Septal Defect . Fɔ tɔk di kɔrɛkt tin, na bɔku at prɔblɛm dɛn we kin kam togɛda. di men wan na dat wan ol כ ol de na di wכl na di midul pan di at (wi kכl dis di septum) . I kin min bak se di valv dɛn na di at nɔ de wok fayn.

Tink bɔt am lɛk ol we de na wata paip. Insay at we gɛt wɛlbɔdi, di blɔd we gɛt bɔku ɔksijɛn we dɛn kin pɔmp frɔm di lɛft say na wi at nɔ kin miks wit di blɔd we nɔ gɛt ɔksijɛn we kɔmɔt na di rayt say. Bɔt bikɔs ɔf dis ol, da blɔd de we gɛt bɔku ɔksijɛn kin miks wit di blɔd we nɔ gɛt ɔksijɛn. Bɔku tɛm, dis ol kin mek tumɔs blɔd go na di lɔng dɛn. Dɔn di blɔd we de go na di ɔda pat dɛn na di bɔdi kin go dɔŋ. If dis kin go fɔ lɔng tɛm, sɔntɛnde i kin go di ɔda we. Dat min se, mɔ blɔd we nɔ gɛt ɔksijɛn de go na di bɔdi, ɛn smɔl smɔl de go na di lɔng dɛn. We dat apin, di ɔksijɛn we de na di bɔdi kin go dɔŋ ɛn di skin kin tɔn blu. Wi kin kɔl am saynosis .

Dis kin mek di at wok tranga wan, we kin mek yu gɛt ɔda wɛlbɔdi prɔblɛm dɛn lɛk we at kin pwɛl .

If dɛn nɔ trit dis (Atrioventricular Canal Defect) fayn, sɔntɛnde i kin afɛkt di pikin in layf. If dɛn nɔ du ɔpreshɔn, pikin dɛn we gɛt dis sik kin jɔs liv fɔ shɔt tɛm, lɛk tu to tri ia. Bɔt nɔ wɔri! Di bɛst tin na dat ɔpreshɔn fɔ kɔrɛkt dis kin rili wok fayn. Dɔktɔ dɛn kin no dis sik bifo i siriɔs, ivin bifo dɛn bɔn di pikin.

Na avrej, na kɔntri dɛn lɛk Amɛrika, na lɛk wan pan ɛvri 1,700 pikin dɛn kin bɔn wit dis prɔblɛm ɛvri ia. dis de mek bitwin 3% εn 5% pan כl di hat dεm we dεn bכn wit.

Dɛn kin kɔl dis kɔndishɔn sɔm ɔda nem dɛn. Yu dɔktɔ kin yuz wan pan dɛn nem ya:

  • Atrioventrikular septal difεkt (AVSD) .
  • Difεkt na di εndokardial kushכn

Difrɛn kayn Atrioventricular Canal Defect de?

Yɛs, dis at prɔblɛm kin kam difrɛn we dɛn. dat min se i dipכnt pan tin dεm lεk di sayz fכ di ol na di at εn di nכmba fכ di valv dεm.

Komplit (Atrioventrikulεr Kanal Dεfεkt) .

wetin kin apin pan dis na di tu כp chεmba dεm na di at (wi kכl dεm atria) εn di tu lכw chεmba dεm (wi kכl dεm vεntrikl) .(dεn kכl am) wan big ol de fכm bitwin di tu chεmba dεm na di at. Dat min se ɔl di 4 chɛmba dɛn na di at gɛt kɔnekshɔn togɛda. nכmal wan, tu valv dεm fכ de bitwin di כp εn lכw chεmba dεm. Bɔt insay dis kes, na wan big valv nɔmɔ de. I kin bi se in flap nɔ opin ɔ lɔk fayn.

Patεl (Partial Atrioventrikulεr Kanal Dεfεkt) .

insay dis kayn we, di ol de bitwin di tu כp chεmba dεm na di at (dis na di wan we kכmכn pas כl) כ bitwin di tu lכw chεmba dεm. Ɔl di 4 chɛmba dɛn nɔ gɛt kɔnekshɔn. Tu valv dɛn de bitwin di ɔpa ɛn di ɔda chɛmba dɛn. bכt wan valv (bכku tεm di mitral valv, we de bitwin di כp chεmba (lεft atrium) εn di lכw chεmba (lεft vεntrikl) na di lεft sayd) nכ de wok fayn.

Transishɔnal Atrioventrikular Kanal Difɛkt

Insay dis, wan ol de bitwin di tu chɛmba dɛn we de ɔp ɛn wan smɔl ol de bitwin di tu chɛmba dɛn we de dɔŋ. di tu valv dεm bitwin di כp εn lכw chεmba dεm (AV valv dεm) de separet.

Unbalanced Komplit Atrioventrikular Kanal Difekt

Yu mɛmba aw insay wan kɔmplit at prɔblɛm, wan big valv de? da valv de de nia wan lכw chεmba (vεntrikul) pas di כda wan. Dɔn di chɛmba we gɛt mɔ blɔd kin big pas di ɔda wan. Dɔktɔ dɛn kin kɔl da smɔl chɛmba de ‘haypoplastik’ .

Wetin na di sayn dɛm fɔ dis?

Di sayn dɛm fɔ dis at prɔblɛm kin apin ivin bifo dɛn bɔn yu pikin. Chek fɔ si if yu pikin gɛt ɛni wan pan dɛn tin ya:

  • Blu skin kɔlɔ (Cyanosis): Ɛspɛshali na say dɛn lɛk di lip, di tɔŋ, ɛn di finga dɛn.
  • I nɔ izi fɔ drink milk: I kin fil taya ɛn taya afta yu dɔn drink smɔl milk.
  • Swet afta yu dɔn drink milk.
  • Fɔ taya kwik kwik wan: Taya ivin afta yu dɔn du smɔl tin.
  • Di at we de blo.
  • I nɔ izi fɔ yu fɔ blo (Dyspnea) ɔ fɔ blo kwik kwik wan.
  • We yu gɛt bɔku bɔku wet kin apin smɔl smɔl.
  • Swel (edema) na di bɛlɛ ɔ di leg dɛn.
  • Wik puls.

Bɔt pikin dɛn we gɛt sɔm kayn prɔblɛm ɔ we kin chenj, nɔ kin sho dɛn sik ya fɔs. Dɛn sayn ya kin apin leta we i smɔl, ɔ we i yɔŋ, ɔ ivin we i big.

Wetin mek dis (Atrioventricular Canal Defect) kin apin?

Risach pipul dɛn stil nɔ no bɛtɛ bɛtɛ wan wetin kin mek pɔsin gɛt Atrioventricular Septal Defect (AVSD) . Dɛn tink se na tin dɛn we de mek pɔsin gɛt jɛnɛtiks ɛn di tin dɛn we de apin na di say we i de . Bɔt wan tin klia: strɔng link de bitwin dis at sik ɛn Daun sindrom . Na lɛk 40% pan di pikin dɛn we gɛt Daun sindrom gɛt AVSD .

Wetin na de risk factor wae kin afekt dis?

Di masta sabi pipul dɛm nɔr dɔn no yet di rayt risk factor dɛm wae kin mek dis sik. I kin bi se sɔntin de we kin mek pɔsin gɛt sɔntin fɔ du wit in jɛnɛtiks. Sɔntɛm wan abnɔmal jin we dɛn pas frɔm di mama ɔ di papa kin mek di pikin gɛt mɔ chans fɔ gɛt at sik we i stil de na di bɛlɛ.

Apat frɔm dat, dɛn tin ya we yu gɛt bɛlɛ kin mek yu pikin gɛt at sik we dɛn bɔn wit:

  • Sɔm mɛrɛsin dɛn.
  • Ilɛgal drɔgs (Rɛkrɛshɔn drɔgs).
  • Drink dɛn we gɛt rɔm.
  • Fɔ gɛt pɔyzin ɔ kemikal dɛn we de na di envayrɔmɛnt.
  • Di tin dɛn we yu nɔ gɛt bɛtɛ tin fɔ it ɔ vaytamɛn.
  • Fat.
  • Di tin dɛn we dɛn kin mek wit tabak.
  • Nɔr fɔ kɔntrol sik dɛm wae nɔr de mɛn lɛk Dayabitis ɔr Haypatɛnshɔn.
  • Vayral sik dɛm lɛk influenza (flu) ɔ flu.

Wetin na di poshubul kɔmplikeshɔn dɛm fɔ Atrioventricular Canal Defect?

If dis sik bad bad wan, we min se dɛn nɔ trit am fayn, prɔblɛm dɛn lɛk dis kin apin:

  • Abnɔmal hat rit patɛn (Aritmia).
  • Kɔnjɛstiv at we nɔ de wok fayn.
  • Infεkshכn dεm na di at (Endocarditis).
  • di bכdi prεshכn na di bכdi we de go na di lכng (Pulmonary hypertension).

Aw dɛn kin no dis sik?

di gud nyus na dat bכku tεm, dכkta dεm kin no dis (Atrioventricular Septal Defect) bifo dεn bכn di pikin wit fכ tεst dεm:

  • di ultrasound bifo di pikin bכn: dis kin si pikchכ dεm fכ di pikin in muvmεnt dεm na di bεlε, inklud di at. I kin no bak wan big septal difεkt .
  • Fetal echocardiogram: dis de sho imej dεm fכ di at klia wan pas כltra saund. Di dɔktɔ kin gɛt bɛtɛ aidia bɔt aw di at de ɛn aw i de pɔmp blɔd.

Afta dɛn dɔn bɔn di pikin, dɔktɔ kin lisin to di pikin in at bit wit stetɔskɔp . If yu yɛri wan ɔnusual "lawd" sawnd (wi kɔl am at murmur ), i kin bi di sawnd we blɔd de flɔ tru di ol.

Ɔda tɛst dɛn we dɛn kin du afta dɛn bɔn pikin na:

  • Chεst X-ray: Chεk di saiz εn shep fכ di pikin in at.
  • Ilektrokardiogram (EKG/ECG): Luk di ilɛktrik aktiviti we di pikin in at de du.
  • Echocardiogram: Na wan rili ditayli luk pan di strכkchכ fכ di pikin in at.
  • Cardiac catheterization: Lan mɔ bɔt aw di pikin in sik tranga.
  • Cardiac Magnetic Resonance Imaging (Hat MRI): Si di pat dεm na di pikin in at εn aw dεn de wok.

Sɔntɛnde, if pikin gɛt smɔl septal dɛfekt , i nɔ kin sho ɛni sayn fɔs. If na so i bi, i kin tek sɔm ia bifo dɔktɔ no bɔt di sik.

Wetin na di tritmɛnt dɛm fɔ dis?

Di tritmɛnt we dɛn kin yuz mɔ fɔ Atrioventricular Canal Defect na ɔpreshɔn we dɛn kin du wit opin at . Insay dis ɔpreshɔn, di dɔktɔ kin pat di ol na di pikin in at ɛn lɔk am. if di defεkt kכmplit , dεn de sheb di wan at valv to tu, we de mek tu difrεnt valv dεm, wan na di rayt say εn wan na di lεft say.

Bebi we gɛt AV kanal we nɔ balans kin nid fɔ du bɔku ɔpreshɔn, ɛn dis kin dɔn wit ɔpreshɔn we dɛn kɔl Fontan prosidur .

I bɛtɛ fɔ mek dɛn du dis ɔpreshɔn kwik kwik wan, bifo di sik pwɛl di at fɔ ɔltɛm. Bɔku pikin dɛn kin gɛt dis ɔpreshɔn insay di fɔs siks mɔnt we dɛn de liv. Sɔm pikin dɛn we gɛt sɔm pat pan di sik bɔt we nɔ gɛt ɛni sayn kin gɛt dis ɔpreshɔn insay di fɔs tri ia we dɛn de liv.

Sɔntɛnde, if di pikin nɔ gɛt wɛlbɔdi fɔ mek dɛn du am ɔpreshɔn, ɔ i nɔ gɛt bɛtɛ wet, dɛn kin gi am mɛrɛsin fɔ kɔntrol di sik dɛn te i gɛt wet ɛn trɛnk.

  • Diuretics na mɛrɛsin we de pul di wata we pasmak na di bɔdi.
  • Digoxin de ɛp di pikin in at fɔ bit tranga wan.
  • ACE inhibitors de mek di blɔd vesel dɛn big ɛn mek i izi fɔ mek di blɔd flɔ.

Wan ɔda we fɔ sɔlv di prɔblɛm fɔ shɔt tɛm na wan tin we dɛn kɔl pulmonary artery banding . dis de ridyus di bכdi we de fכlכ tru di pulmonari atεri to di pikin in lכng. Bebi dεm we dεn bin dכn bכnd pulmonary artery banding kin gεt fכ rεpair fכ pεrmanεnt leta.

Kɔmplikɛshɔn kin apin afta dɛn dɔn trit am?

Yɛs, sɔntɛnde tin dɛn lɛk dis kin apin afta dɛn dɔn du di ɔpreshɔn:

  • di at blכk: dis min se di at in puls signal nכ de rich di lכw pat na di at fayn fayn wan.
  • Wan lek lef ɔ rayt AV valv.
  • wan ol na di wכl na di lכw chεmba (Ventricular septal defect).
  • Narrowing (Stenosis) fכ di lεft כ rayt AV valv.
  • wan tin we de ambɔg di bכdi fכ fכlכ dεn dכn di aorta valv (Subaortic stenosis).

Dɛn nɔ kin ebul fɔ stɔp dis (Atrioventricular Canal Defect)?

Rili no we nɔ de fɔ mek dis (Atrioventricular Septal Defect) nɔ apin, bikɔs bɔku tɛm i kin gɛt fɔ du wit di jɛnɛtik kɔz dɛm.

Bɔt if yu gɛt bɛlɛ, yu kin du dɛn tin ya fɔ mek yu pikin nɔ gɛt at sik we dɛn bɔn wit:

  • Nɔ tek drɔgs we nɔ rayt, rɔm, ɛn tin dɛn we dɛn kin yuz fɔ smok, kpatakpata.
  • Gɛt ɔl di vaysin dɛn we yu nid fɔ protɛkt yusɛf frɔm sik.
  • Mek yu gɛt wɛlbɔdi wet.
  • If yu gɛt wɛlbɔdi prɔblɛm dɛn we nɔ de mɛn, manej dɛn fayn fayn wan.
  • Tek vaytamɛn dɛn bifo yu bɔn, mɔ di fɔlik asid, lɛk aw yu dɔktɔ tɛl yu.

If mi pikin gɛt dis sik, aw tumara bambay go tan lɛk?

If dɛn nɔ du ɔpreshɔn, pikin dɛn we gɛt AV kanal difrɛns kin jɔs liv fɔ tu to tri ia. Sɔm kin liv te dɛn yɔŋ.

Bɔt di gud nyus na dat lɛk 90% pan di pikin dɛn we dɛn dɔn du da ripɛnt ɔpreshɔn de kin liv 10 ia afta da tritmɛnt de. Dat min se dɛn kin liv at le 10 ia mɔ afta di ɔpreshɔn. Na lɛk 65% de liv 20 ia afta di ɔpreshɔn.

Bɔt mɛmba dis: Ivin afta dɛn dɔn du di ɔpreshɔn, pɔsin we gɛt Atrioventricular Canal Defect (AVCD) nɔ go gɛt at we nɔmal ɔl. Dɛn go nid fɔ kɔntinyu fɔ gɛt ɛkokadiogram ɔltɛm fɔ wach aw dɛn at de wok. Dis go ɛp fɔ kech ɛni kɔmplikeshɔn kwik kwik wan.

Di pat we dɛn kin put oba di ol kin las fɔ ɔl in layf. Bɔt as tɛm de go, wan pan di at valv dɛn we dɛn dɔn ripɛnt kin bigin fɔ lik. If dat apin, bitwin 10% ɛn 20% pan pipul dɛn go nid fɔ gɛt ɔpreshɔn fɔ di sɛkɔn tɛm .

Bɔku pipul dɛn nɔ nid mɛrɛsin ɔ ɔda ɔpreshɔn afta dɛn dɔn du dɛn ɔpreshɔn. Bɔt, di at kin apin leta. If dis apin, dɔktɔ kin tɛl yu fɔ du tin dɛn we go ambɔg yu lɛk fɔ pul yu bɔdi .

Aw a go kia fɔ mi pikin?

Yu go nid fɔ stɔp yu pikin fɔ du bɔku tin dɛn . Aks yu pikin in pikin dɛn kadyolɔjis - dɔktɔ we spɛshal pan at sik na pikin dɛn - bɔt dis.

Dɛn kin advays pikin dɛn we gɛt atrioventricular septal defect (AVSD) fɔ tek antibayɔtik bifo dɛn go to di dɛntist. Dis kin ɛp fɔ mek yu nɔ gɛt wan kayn at infɛkshɔn we dɛn kɔl ɛndokadaytis . Tɔk to yu pikin in dɔktɔ we de mɛn in at bɔt dis bak.

Ustɛm mi pikin fɔ go to dɔktɔ?

Yu fɔ rili kɛr yu pikin go to dɛn pikin dɛn we de mɛn dɛn at ɔltɛm. Dɛn kin wach yu pikin in at fɔ ɛni prɔblɛm. Sɔm pikin dɛn we gɛt AV kanal difrɛns kin nid fɔ gɛt mɔ tritmɛnt afta dɛn dɔn du dɛn ɔpreshɔn. Di pat kin lik, ɔ wan valv we dɛn dɔn ripɛnt kin lik ɔ i kin smɔl.

Pikin we gɛt AV kanal difrɛns kin gɛt nyurolɔjik ɔ divɛlɔpmɛnt prɔblɛm bak . Dɛn kin nid ɛp bak fɔ du dat.

We yu pikin dɔn big, i fɔ muf to big pɔsin we sabi bɔt at we dɛn bɔn wit ɛn go chɛk-ap wan tɛm insay di ia.

Us kwɛstyɔn dɛn a fɔ aks mi pikin in dɔktɔ?

Yu kin aks yu pikin in dɔktɔ kwɛstyɔn dɛn lɛk:

  • Us kayn AV kanal dɛfekt mi pikin gɛt?
  • Wetin na de sayn dɛm wae de sho se de sik de wɔs?
  • Ustɛm i go nid fɔ du ɔpreshɔn?
  • Mi pikin go nid mɛrɛsin afta di ɔpreshɔn?
  • A go gɛt fɔ stɔp mi pikin fɔ du tin?

I nɔmal fɔ gɛt difrɛn kayn filin dɛn we yu yɛri se yu nyu bɔbɔ gɛt at sik lɛk Atrioventricular Canal Defect . Bɔt yu pikin in dɔktɔ dɛn de fɔ ɛp yu, ɛn dɛn want fɔ du wetin bɛtɛ fɔ yu pikin. Fɛn ɔut ɛksaktɔli wetin spɛshal fɔ yu pikin in kɔndishɔn. If ɛnitin de we yu nɔ shɔ bɔt, aks yu dɔktɔ bɔt am. Naw na di tɛm fɔ advatayz fɔ yu pikin in wɛlbɔdi.

So, wetin na di tin dɛn we wi nid fɔ mɛmba frɔm ɔl dɛn tin ya?

  • Atrioventricular Canal Defect na at kכndyushכn we de de we dεn bכn am. I kin mɔs bi bikɔs ɔf wan ol na di at ɛn prɔblɛm wit di valv dɛn.
  • Fɔ no di pɔsin kwik kwik wan ɛn fɔ du ɔpreshɔn di rayt tɛm rili impɔtant. Dɛn ɔpreshɔn dɛn ya kin rili wok fayn.
  • Bebi dεm we gεt Daun sεndr כm kin gεt dis kכndyushכn.
  • Dɛn nid fɔ de kia fɔ di dɔktɔ fɔ lɔng tɛm ivin afta dɛn dɔn du di ɔpreshɔn. Yu nid fɔ de tɔk to dɔktɔ we de mɛn yu at fɔ di res ɔf yu layf.
  • If yu gɛt bɛlɛ, fɔ fala wɛlbɔdi layf ɛn fala dɔktɔ advays kin ɛp fɔ mek yu pikin nɔ gɛt at sik we dɛn bɔn wit.
  • Nɔ fred, di dɔktɔ dɛn de fɔ ɛp yu ɛn yu pikin. Aks kwɛstyɔn, mek dɛn no bɔt am.

` At sik, hat difεkt we dεn bכn wit, pikin in at, ol na di at, Atrioventricular Canal Defect, AVSD, pikin at sik

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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