Kidni ston na sɔntin we de mek wi ɔl fred smɔl, nɔto so? Yu go mɔs dɔn yɛri bɔt da pen de. Bɔt yu no se difrɛn kayn ston dɛn de na di kidni? Tide wi go tɔk bɔt wan kayn ston we nɔ bɔku bɔt we rili impɔtant. Dat na sistin ston dɛn. Lɛ wi si wetin mek dɛn kin fɔm, wetin na di sayn dɛm, ɛn wetin dɛn kin du bɔt dɛn.
Fɔ tɔk am simpul wan, wetin na sistin ston?
Cystine Stones na wan kayn kidni ston bak. Kidni ston na tin dɛn we at ɛn we tan lɛk ston we dɛn kin mek bay we difrɛn kayn kemikal dɛn kin gɛda na wi urine. Sistin ston na wan kemikal we dɛn kɔl sistin . Sistin na impɔtant amino asid fɔ wi bɔdi. Fɔ tɔk di kɔrɛkt tin, na smɔl pat pan di prɔtin dɛn we de ɛp fɔ bil mɔsul ɛn fɔ mek di tisu dɛn na wi bɔdi fayn.
Nɔmal wan, wi kidni dɛn kin tek dis sistin bak insay di bɔdi. Bɔt pan sɔm pipul dɛm, dis prɔses nɔr kin woke fayn fayn wan. afta dat, di sistin we nכ kin ebul fכ abzכp de kכmכt na di urine εn, as tεm de go, i de fכm ston. Dɛn sistin ston ya kin gro smɔl pas ɔda kidni ston dɛn. So sɔntɛnde dɛn kin nid fɔ pul dɛn tru ɔpreshɔn fɔ stɔp di damej we de na di kidni ɔ di urinary tract.
So wetin na Sistinuria?
di men tin we kin mek dεn sistin ston ya de na wan jεnεtik kכndyushכn we dεn kכl sistinuria . Dis na wan sik we nɔ kin apin so ɔltɛm, we pɔsin kin gɛt frɔm in mama ɛn papa. Fɔ tɔk am simpul wan, if yu gɛt dis sik, yu bɔdi nɔ go ebul fɔ sɔlv wan kemikal we dɛn kɔl sistin fayn fayn wan. So i kin gɛda na yu urine ɛn mek ston.
Di impɔtant tin na dat, sistinuria na sik we pɔsin kin gɛt fɔ ɔl in layf. No mɛrɛsin nɔ de fɔ am. Bɔt if yu gɛt di rayt tritmɛnt, yu kin ebul fɔ kɔntrol di sik fayn fayn wan ɛn liv nɔmal layf .
Bikɔs dis na tin we pɔsin kin gɛt frɔm in jɛnɛtiks, pikin fɔ gɛt di jin frɔm in mama ɛn papa fɔ mek i gɛt am . Pɔsin we gɛt dis sik kin gɛt sistin ston bɔku tɛm insay in layf.
Aw dis sik kin kɔmɔn? Wetin na di sayn dɛm we de sho se yu gɛt dis sik?
Dis nɔto sɔntin we kin apin to ɔlman, i nɔ kin apin smɔl. Bɔku tɛm, if yu tek 1 ɔ 2 pan 100 pipul dɛn we gɛt kidni ston, na wan ɔ tu pan dɛn nɔmɔ go gɛt sistin ston. Bɔt i sɔprayz fɔ no se dɛn kin si dis sik mɔ pan pikin dɛn ɛn yɔŋ pipul dɛn . Na lɛk 80% pan di pipul dɛm we gɛt sistin ston kin gɛt dɛn fɔs ston bifo dɛn rich 20. Bɔt dɛn ston ya kin fɔm ɛni ej.
As fɔ di sayn dɛm, dɛn kin rili fiba di wan dɛm fɔ ɔda kidni ston dɛm. Bɔku tɛm, dɛn nɔ kin fil di sayn dɛn te ston dɔn fɔm.
| Di sayn we de sho se di sik de | Tɔk bɔt |
|---|---|
| Bɔku pen na di bak ɔ di bɔdi we de na di bɔdi | I kin fil lɛk shap pen we pɔsin de chuk am. Bɔku tɛm, dɛn kin fil dis na wan say. |
| Pen na di bɛlɛ we de dɔŋ ɔ di groin | As di ston de muv dɔŋ di urinary tract, yu kin fil pen na di ɔnda bɛlɛ. |
| Blɔd we de na di urine | Yurin kin tan lɛk pink, rɛd, ɔ brawn. |
| Vɔmit ɛn nɔs | Nɔs ɛn vɔmit kin apin wit bad bad pen. |
| Pen we yu de pis | We di ston de nia di blad, yu kin fil bɔn ɔ pen we yu de pis. |
Sɔntɛnde, dɛn sistin ston ya kin big fɔ blok di urinary tract ɛn mek yu gɛt urinary tract infection (UTI) .
Us prɔblɛm dɛn kin apin?
Sistinuria na wan sik wae de kam wae yu de liv yu layf, ɛn if yu nɔr de mɛn am fayn, e kin mek yu gɛt prɔblɛm. E fayn fɔ woke wit yu dɔktɔ fɔ mɛn dis sik.
Prɔblɛm dɛn we kin apin na:
- Kidni infεkshכn: Ston kin mek di urine fכ fכlכ εn alaw di jεm dεm fכ go insay di kidni dεm.
- di uriteral obstruction: di tכb we de kכri urine frכm di kidni to di blad (ureter) kin blok wit ston.
- Urinary tract infection (UTI) we kin kam bɔku tɛm.
- Di kidni we kin pwɛl ɔltɛm:If dɛn nɔ trit am fɔ lɔng tɛm, di kidni wok kin go dɔŋ.
Aw di dɔktɔ kin no bɔt dis? Wetin na di tritmɛnt dɛn?
If yu gɛt sayn dɛn we fiba di kidni ston, yu dɔktɔ go du bɔku tɛst fɔ no if dɛn tin ya na sistin ston.
Di we aw dɛn kin no di sik
- Aks yu fɔ di ditel dɛm: De dɔktɔ go aks yu bɔt yu sik ɛn if ɛnibɔdi na yu famili dɔn gɛt dis kayn prɔblɛm.
- Test: Dɛn kin ɔda fɔ du urine test ɛn imej tɛst lɛk ɔltra saund skan ɔ CT skan .
- Test di ston: If yu gɛt ston we dɔn pas na yu urine, yu kin sɛn am to lab fɔ tɛst fɔ no uskayn ston i bi. dis na di onli we fכ 100% kכnfכm se na sistin stכn.
Di we aw dɛn kin trit am
Di men gol fɔ trit sistin ston na fɔ mek nyu ston nɔ fɔm ɛn fɔ pul di ston dɛn we dɔn de. Yu dɔktɔ go mek wan tritmɛnt plan we go fayn fɔ yu.
- Chenj na di we aw pipul dɛn de liv dɛn layf ɛn di tin dɛn we dɛn de it
- Drink plɛnti wata: Dis na di tin we impɔtant pas ɔl. Yu dɔktɔ kin tɛl yu fɔ drink at le 3-4 lita wata fɔ wan de. Dat min se yu fɔ mek am abit fɔ drink wan glas wata ɛvri awa. Nɔ sɔprayz if yu grap na nɛt fɔ drink wata. Wata de mek yu urine diluyt ɛn i de ridyus di sistin we de gɛda.
- Sɔl (sɔdiɔm) kɔntrol: Ridyus di sɔl we yu de ad to yu it. Nɔ it tin dɛn lɛk tin dɛn we dɛn kin put insay tin fɔ it ɛn tin dɛn we dɛn dɔn frɔz ɔ we dɛn pak, we gɛt bɔku sɔl.
- Ridyus animal protin: Yu kin ridyus di animal protin we yu de it lɛk mit, fish, ɛn eg ɛn pe atɛnshɔn pan plant-based protein insted.
- Mɛrɛsin dɛn we dɛn kin yuz
If yu de fil pen bikɔs ɔf ston, yu dɔktɔ go gi yu mɛrɛsin fɔ mɛn yu pen. Apat frɔm dat, spɛshal mɛrɛsin dɛn de we kin ɛp fɔ mek nyu sistin ston nɔ kam. Tiopronin ɛn d-penicillamine na dɛn kayn mɛrɛsin ya. Dɛn tin ya kin ɛp fɔ sɔlv di sistin. Dɛn mɛrɛsin ya fɔ jɔs tek ɔnda dɔktɔ in sɔpɔtishɔn .
- Ɔpreshɔn
If di ston dɛn rili big, we de blok di urinary tract, ɔ mek pɔsin fil pen bad bad wan, dɛn kin nid fɔ du ɔpreshɔn fɔ pul dɛn.
- Yureteroskopi: Dɛn kin pas wan smɔl kamɛra we kin chenj chenj na di yuret fɔ no usay di ston de ɛn dɛn kin brok am ɔ pul am kpatakpata.
- Pɛrkyutan Nɛfrolitɔtɔmi: .Na we dɛn kin kɔt smɔl pat na di bak in skin ɛn pas wan tiub insay di kidni fɔ pul di ston. Dɛn kin du dis fɔ ston dɛn we rili big.
Aw yu de liv wit dis sityueshɔn? Na sɔntin we wi fɔ fred?
Sistinuria na wan sik we pɔsin kin gɛt we i de liv in layf. Bɔt if dɛn de manej am fayn, natin nɔ de fɔ wɔri bɔt. Dis sik nɔ kin rili mek pɔsin in layf de pan denja. If dɛn trit am fayn, i nɔ kin go bifo to siriɔs tin lɛk we di kidni nɔ de wok fayn.
Di tin we impɔtant pas ɔl na fɔ mek yu ɛn yu dɔktɔ kɔntinyu fɔ gɛt gud padi biznɛs. If yu fala di instrɔkshɔn dɛn gud gud wan ɛn go na di klinik dɛn di rayt tɛm, yu go ebul fɔ kɔntrol dis sik bɛtɛ bɛtɛ wan.
Fɔ wach aw di tritmɛnt go wok fayn, di dɔktɔ go de du urine tɛst ɔltɛm fɔ chɛk di lɛvɛl we di sistin de na di urine. If nid de, dɛn go ajɔst di tritmɛnt plan fɔ du dat. Bikɔs dis na tin we pɔsin kin gɛt we i kam pan yu jɛnɛtiks, i go fayn bak fɔ mek yu go to yu jenɛtik advays if yu de plan fɔ mek yu gɛt famili.
Mɛsej we dɛn kin kɛr go na os
- Sistin ston na wan kayn kidni ston we kin kam bikɔs ɔf wan sik we nɔ kin apin so ɔltɛm, we dɛn kɔl sistinuria.
- Pan ɔl we dis sik kin de fɔ ɔl yu layf, dɛn kin ebul fɔ mɛn am fayn fayn wan wit di rayt tritmɛnt ɛn chenj dɛn layf.
- Fɔ drink bɔku wata ɔl di de na di impɔtant ɛn simpul we fɔ mek ston nɔ kam.
- I rili impɔtant fɔ fala di it we nɔ gɛt bɔku sɔl ɛn animal prɔtin.
- If yu gɛt sɔm sayn dɛn lɛk bad bad pen na yu bak, yu bɛlɛ, ɔ yu bɛlɛ we de dɔŋ, ɔ blɔd de na yu urine, nɔ west tɛm ɛn go to dɔktɔ wantɛm wantɛm .
- Fɔ fala yu dɔktɔ in instrɔkshɔn ɛn mɛrɛsin dɛn ɛksaktɔli. Nɔr wɔri, yu kin liv wɛl bɔdi layf wit dis sik.











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