Sɔntɛnde yu kin fil lɛk se yu leg dɛn ebi smɔl, lɛk se dɛn mek am wit ston? Ɔ yu kin fil lɛk se yu nɔ de balans we yu de waka, ɔ yu an ɛn fut dɛn de lɔs dɛn trɛnk smɔl smɔl? If dɛn sik ya nɔ kam wantɛm wantɛm, bɔt smɔl smɔl ɛn smɔl smɔl, i kin impɔtant fɔ mek yu no bɔt dis sik we dɛn kɔl Primary Lateral Sclerosis (PLS). Nɔ wɔri, wi go tɔk bɔt ɔltin insay simpul wɔd dɛn.
Fɔ tɔk am simpul wan, wetin na praymari latɛral sklɛrosis (PLS)?
Primary Lateral Sclerosis, ɔ PLS fɔ shɔt, na wan sik we kin afɛkt wi nerv ɛn mɔsul dɛm. I kin mek wi mɔsul dɛn wik smɔl, ɔ smɔl smɔl, wik ɛn/ɔ stif.
Bɔku tɛm, dɛn sayn ya kin bigin fɔs na yu leg. As tɛm de go, dis wik ɛn stif kin go to ɔda mɔsul dɛn na yu bɔdi. Dis na sik we de go bifo , we min se di sik kin wɔs smɔl smɔl as tɛm de go.
Nɔr patikyula mɛrɛsin nɔr de fɔ dis sik (PLS), so di tritmɛnt de mɔr fɔ kɔntrol di sayn dɛm ɛn ɛp yu fɔ du di tin dɛm wae yu kin du ɛvride izi wan. Fɔ ɛgzampul, yuz sɔntin we de ɛp pɔsin lɛk ken ɔ tin fɔ waka .
Dis na wan sik wae nɔr kin bɔrku, wae min se dɛn nɔr kin si am na sosayti.
Wetin na di difrɛns bitwin PLS ɛn ALS?
Sɔntɛm yu dɔn yɛri bɔt wan sik we dɛn kɔl Amyotrophic Lateral Sclerosis (ALS) . Pan ɔl we dɛn tu sik ya kin gɛt fɔ du wit di nerv ɛn mɔsul dɛn, klia difrɛns de bitwin dɛn tu. Fɔ ɔndastand dis, lɛ wi fɔs luk aw wi bɔdi de kɔntrol di muvmɛnt.
Wan spɛshal kayn nɛv sɛl de we kin kɛr mɛsej frɔm wi bren to wi mɔsul dɛn, wi kin kɔl dɛn motoka nyuron . Tu kayn tin dɛn de:
1. di כp mכtal nyuron dεm (UMN): dis na di ‘men waya dεm’ we de kכri mεsej frכm di bren to di spεnal kכd.
2. di lכw mכtal nyuron dεm (LMN): dis na di ‘sכb-nyurכn dεm' we de kכri mεsej dεm dεn wan frכm di spεnal kכd to di mכsul dεm.
Naw i rili impɔtant fɔ ɔndastand dis difrɛns.
Fɔ tɔk am simpul wan, insay PLS , na di UMN nɔmɔ dɛn kin afɛkt. dat min se na di ‘men waya dεm’ nכmכ we de kכmכt na di bren to di spεnal kכd. Insay ALS , ɔl tu di UMN ɛn LMN kin afɛkt.
Di fɔs simptom dɛm fɔ ALS kin rili fiba di wan dɛm fɔ PLS. So sɔmtɛm, dɔktɔ kin fɔs no se yu gɛt PLS ɛn afta dat chenj am to ALS we sɔm sayn dɛn kin kam we kin afɛkt di LMN bak. Fɔ dis rizin, fɔ mek dɛn kɔnfɔm PLS gud gud wan, dɛn nid fɔ wach di sayn dɛn fɔ at le tri to 4 ia .
| Di kwaliti we pɔsin gɛt | Praymari Latɛral Sklɛrosis (PLS) . | Amyotrofik lateral sklεrosis (ALS) . |
|---|---|---|
| Di nerv dɛn we dɛn afɛkt | Ɔpa Mɔtal Nyurɔn dɛn (UMN) nɔmɔ . | כl tu di כpa mכtal nyuron dεm (UMN) εn di lכw mכtal nyuron dεm (LMN). |
| Di spid we di sik de skata | Rili slow (fɔ bɔku ia ɔ dikɛd ia). | Rili fast. |
| Impekt pan layfspan | Bɔku tɛm, i nɔ kin gɛt ɛni dairekt ifɛkt pan di layf we pɔsin de liv. | I kin afɛkt di we aw pɔsin de liv in layf. |
Wetin na di sayn dɛm fɔ PLS?
Di simptom dɛm fɔ PLS kin kam sloslo. Na sɔm pan di fɔs sayn dɛn we yu go notis:
- Di mɔsul dɛn na di leg dɛn kin stif.
- Di mɔsul dɛn we de na di leg dɛn wik.
- I nɔ izi fɔ waka ɔ gɛt prɔblɛm fɔ balans.
- Mɔsul dɛn de twitch ɔ spasm ɔ kramp we de mek yu fil pen.
As di sik de go bifo, ɔda sayn dɛn kin sho:
- di mכsul dεm stif εn wik na di finga dεm, an dεm, εn an dεm.
- I nɔ izi fɔ kɔntrol di urine(Urgent nid fɔ pis ɛn lik fɔ urine).
- Bak ɛn nɛk de pen.
Na sכm kayn we, di mכsul dεm na di tכng kin afekt bak. If na so i bi, yu kin si sayn dɛm lɛk:
- Fɔ tɔk smɔl smɔl (Dysarthria).
- I nɔ izi fɔ swɛla it (Dysphagia).
Wetin kin mek pɔsin gɛt PLS?
Infakt, wi stil nɔ no di rayt tin we kin mek pɔsin gɛt PLS pan big pipul dɛn. Bɔrku tɛm, i kin apin randomly, wae nɔr kin si ɛni rizin.
Bɔt wan kayn PLS de we nɔ kin apin so ɔltɛm we kin afɛkt pikin ɛn yɔŋ pipul dɛn. i de kכz fכ wan jεnεtik mכtεshכn (chenj in DNA).
Di impɔtant tin na dat PLS nɔto sik we pɔsin kin gɛt frɔm in mama ɛn papa. Dis min se yu kin gɛt am ilɛksɛf nɔbɔdi na yu famili nɔ bin dɔn gɛt am bifo.
Udat dɛn de pan denja pas ɔlman?
Ɛnibɔdi kin gɛt PLS. Bɔt dɛn kin no di sikman dɛn arawnd di ej we dɛn ol 50. Bɔt i kin kam bak pan pipul dɛn we yɔŋ ɔ pas dat. Dis sik kin bɔku smɔl pan man dɛn pas uman dɛn .
Aw dɛn kin no dis sik?
Afta yu dɔn lan bɔt yu sik, yu dɔktɔ go du yu bɔdi ɛn yu nyurolɔjik ɛgzam. Dɛn kin du tɛst bak fɔ no ɔda tin dɛn we gɛt di sem sayn lɛk PLS, lɛk ALS ɔ multiple sclerosis. Sɔm pan dɛn tɛst ya na:
- Blɔd tɛst: Chɛk fɔ ɔda tin dɛn we kin mek yu gɛt blɔd.
- Ilektrodiagnostik tɛst: Dis de sho aw yu nerv ɛn mɔsul dɛn de wok fayn fayn wan.
- MRI skan: Tek ditayli pikchɔ dɛn bɔt di bren ɛn di spɛnal kɔd fɔ si if ɛni ɔda prɔblɛm de.
- Lumbar pancture (spinal tap): Dis min se yu tek smɔl wata na yu spayna ɛn chɛk am fɔ si if i nɔ fayn.
Wetin na di tritmɛnt dɛn?
As wi bin dɔn tɔk bifo tɛm, no patikyula mɛrɛsin nɔ de fɔ PLS. Tritmɛnt na fɔ kɔntrol di sayn dɛm ɛn ɛp yu fɔ liv yusɛf as yu ebul.
- Mεdikeshכn dεm: Dɛn kin gi mεdikeshכn fכ ridyus di mכsul dεm we stif, lεm, εn i at fכ swεl (e.g. Baclofen, Tizanidine, Quinine, Diazepam).
- Fɔ trit yu bɔdi: Dɛn kin se yu fɔ du ɛksɛsayz fɔ mek yu nɔ gɛt bɔku bɔku mɔsul dɛn, fɔ mek yu ebul fɔ chenj, ɛn fɔ mek yu jɔyn dɛn ebul fɔ muv fayn fayn wan.
- Di tin dɛn we yu kin yuz fɔ ɛp yu: Dɛn kin yuz tin dɛn lɛk ken, waka , ɔ wilchia fɔ ɛp yu fɔ muv yusɛf.
- Spich therapy: If yu gɛt prɔblɛm fɔ tɔk, i kin ɛp.
Impɔtant: Bifo yu bigin fɔ tek ɛni mɛrɛsin, tɔk to yu dɔktɔ bɔt di bad tin dɛn we kin apin to yu.
Ustɛm yu fɔ go to dɔktɔ?
If yu fil se yu mɔsul dɛn de stif ɔ wikɛd smɔl smɔl, mek shɔ se yu go to yu dɔktɔ.
Dɔn bak, if dɛn dɔn ɔlrɛdi no se yu gɛt PLS ɛn wan mɛrɛsin we yu de tek de mek yu sik wɔs ɔ de mek yu gɛt sayd ɛfɛkt, tɛl yu dɔktɔ bɔt dat bak.
If yu wund bikɔs yu fɔdɔm ɔ aksidɛnt wantɛm wantɛm, go na di ɔspitul in Imejɛnsi Tritmɛnt Yunit (ETU) wantɛm wantɛm.
Na nɔmal tin fɔ fil pwɛl hat as yu mɔsul trɛnk de go dɔŋ smɔl smɔl ɛn yu nɔr kin ebul fɔ du di tin dɛm wae yu bin de du trade. If yu de fil strɛs bɔt dɛn chenj ya na yu bɔdi, fɔ tɔk to pɔsin we de advays yu bɔt yu maynd, dat go ɛp yu.
Mɛsej we dɛn kin kɛr go na os
- PLS na sik we de go bifo kwik kwik wan we gɛt fɔ du wit di nerv ɛn mɔsul dɛm.
- dis de כnli afekt di nεv dεm we de kכri mεsej frכm di bren to di spεnal kכd (UMN). Dis na aw i difrɛn frɔm ALS.
- Pan ɔl we no patikyula mɛrɛsin nɔ de fɔ dis, fayn tritmɛnt dɛn de fɔ kɔntrol di sik dɛn ɛn mek layf izi.
- Di impɔtant tin na dat, PLS nɔ kin mek pɔsin in layf shɔt .
- If yu mɔsul dɛn de wik ɔ stif smɔl smɔl, mek shɔ se yu go to dɔktɔ fɔ advays.











💬 Comments (0)
No kɔmɛnt nɔ de yet. Ad yu kɔmɛnt ya fɔ di fɔs tɛm.
Ad yu kɔmɛnt