Yu dɔn ɛva gɛt smɔl kɔt we yu nɔ bin ebul fɔ stɔp fɔ blɔd fɔ lɔng tɛm? Ɔ yu kin gɛt big blu brus ivin afta yu dɔn bɔmp smɔl? Sɔntɛnde wi kin tink se dɛn tin ya na nɔmal tin, bɔt dɛn kin bi sayn fɔ se wi gɛt smɔl prɔblɛm wit wi blɔd. Tide, wi go tɔk bɔt wan sik we pipul dɛn nɔ kin tɔk bɔt bɔt we kin rili kɔmɔn we kin afɛkt di we aw blɔd kin klɔt. Dat na von Willebrand sik.
Fɔ tɔk am simpul wan, wetin na di sik we dɛn kɔl von Willebrand (VWD)?
von Willebrand disease (VWD) na wan sik wae kin apun wae wi blɔd kin klɔt nɔr de wok fayn fayn wan. Na mɔ wikɛd tin we wi kin gɛt frɔm wi bɔdi pas sik.
Imajin, we wi kɔt wan pan wi blɔd vesel, wan smɔl kayn sɛl (pletlɛt) na wi bɔdi kin kam fɔ stɔp di blɔd ɛn sial di wund. I tan lɛk se yu ful-ɔp wan ol na di wɔl wit brik. dis pletlet dεm de stik togeda εn gεt spεshal "gכm" lεk protin na wi bכdi we de εp dεm fכ mek wan strכng klot. Na dat wi kin kɔl von Willebrand factor (VWF) .
Pɔsin we gɛt VWD nɔ kin gɛt dis VWF protin na in bɔdi, ɔ di prɔtin we i gɛt nɔ kin wok fayn. Dɔn, bikɔs di blɔd we de klɔt nɔ de fɔm fayn, i kin tek lɔng tɛm fɔ lɛ i stɔp fɔ blɔd ivin if i wund smɔl.
Dis na de sik wae kin kam wae pɔrsin kin gɛt blɔd we dɛn kin gɛt frɔm ɔda pipul dɛn na di wɔl. Dɛn se na lɛk wan pan ɛvri 100 pipul dɛn kin gɛt dis sik.
Wetin na di men kayn VWD?
Dɛn kin sheb dis sik mɔ to tri kayn. Wan kayn de bak we nɔr kin bɔn bɔt i kin kam leta.
| Kayn | Tɔk bɔt |
|---|---|
| Tayp 1 | dis na di kayn we we kכmכn pas כl (bitwin 60% - 80%). i kin bi we di bכdi gεt tu sכm VWF protin. Bɔrku tɛm, di sayn dɛm nɔr kin so. |
| Tayp 2 we de na di wɔl | di sεkכn mכst kכmכn tכp (bitwin 15% - 30%). pan ɔl we di VWF protin de ya, in wok wik. I tan lɛk ol gɔm, i nɔ gɛt yus ilɛksɛf i de de. Di sayn dɛm kin bi smɔl to smɔl. |
| Tayp 3 we yu de du | Dis na di kayn we we kin rili bad ɛn we nɔ kin apin so ɔltɛm. na ya, di VWF protin de kכlכsכl nכ de na di bכdi. So, de sayn dɛm kin rili bad. |
| VWD we dɛn dɔn gɛt | Dis nɔto sɔntin we dɛn bɔn yu wit. I kin kam wit sɔm ɔtoimyun sik dɛm (e.g. lupus), at sik, sɔm kayn kansa, ɔr mɛrɛsin wae yu de tek. |
Wetin na di sayn dɛm fɔ dis sik?
Di simptom dɛn kin difrɛn difrɛn wan bay di kayn VWD we yu gɛt.
Mild ɛn mɔdaret simptom dɛm fɔ tayp 1 ɛn 2
- Ivin smɔl injuri kin mek yu gɛt big blu brus: Yu notis se yu bɔdi de tɔn blu na say dɛn?
- Nɔs blɔd ɔltɛm: Sɔm pipul dɛn kin gɛt blɔd na dɛn nos ɔltɛm, ɛn i nɔ kin izi fɔ lɛ dɛn stɔp am.
- Blɔd we de kɔmɔt pasmak afta dɛn dɔn du di ɔpreshɔn ɔ pul di tut: Yu nɔ tink se di blɔd kin stɔp fɔ sɔm awa afta dɛn dɔn pul di tut?
- Uman dɛn kin gɛt bɔku blɔd we dɛn de gɛt prɛgnɛshɔn: Di blɔd kin bɔku dat yu fɔ chenj yu pad wan tɛm insay di awa? I kin kam wit klot? As tɛm de go, dis kin mek pɔsin gɛt anemia we nɔ gɛt ayɔn .
- Blɔd we de na di stɔl ɔ di urine.
Sivεr simptom dεm fכ tayp 3
Na dis kayn, ɔl di sayn dɛm wae wi dɔn tɔk bɔt kin tranga. Pantap dat,
- Blɔd we de kɔmɔt wantɛm wantɛm ɛn we nɔ gɛt wan rizin.
- Blɔd kin lik insay di jɔyn dɛn ɛn di sɔft tisu dɛn, ɛn dis kin mek i swel ɛn i kin fil bad bad wan.
Di impɔtant tin na dat nɔto ɔlman we gɛt dɛn sik ya gɛt VWD. Bɔt if yu gɛt wan ɔ mɔ pan dɛn sik ya ɔltɛm, i go fayn fɔ mek yu go to dɔktɔ fɔ advays.
Aw yu no dis?
Yu dɔktɔ go aks yu fɔs bɔt yu sik ɛn yu famili mɛdikal histri. Bikɔs dis na tin we pɔsin kin gɛt frɔm in mama ɛn papa, i impɔtant fɔ no if ɛni ɔda pɔsin na yu famili dɔn gɛt dis kayn prɔblɛm we i kin gɛt we i de blɔd.
Dɔn, dɛn go du sɔm spɛshal tɛst dɛn fɔ si aw lɔng i kin tek fɔ mek yu blɔd klɔt ɛn aw i kin klɔt fayn. Di men tin, .
- fכ mכsu di amoun fכ VWF protin na di bכdi (Antigen test).
- Fɔ tɛst aw da prɔtin de de wok.
Sɔntɛnde, tin lɛk strɛs ɛn ɛksesaiz kin chenj di VWF lɛvɛl, so yu kin nid fɔ mek dɛn du dɛn tɛst ya pas wan tɛm fɔ gɛt di kɔrɛkt rizɔlt.
Wetin na di tritmɛnt dɛn? Aw fɔ manej?
Pan ɔl we dɛn nɔ go ebul fɔ mɛn VWD, dɛn kin kɔntrol am ɛn manej am fɔ liv nɔmal layf. Di tin we impɔtant pas ɔl na fɔ ridyus di risk fɔ blɔd.
1. Fɔ avɔyd sɔm mɛrɛsin dɛn
Yu nɔ fɔ tek sɔm mɛrɛsin dɛn we de mek di blɔd tan. Bɔku tɛm yu dɔktɔ go tɛl yu fɔ nɔ tek aspirin ɛn NSAID (lɛk ibuprofen ɛn naproxen). Acetaminophen na wan we we nɔ bad fɔ pen ɔ fiva. Bɔt mek shɔ se yu aks yu dɔktɔ bifo yu tek ɛni mɛrɛsin.
2. Spɛshal tritmɛnt dɛn
Di tritmɛnt de dipen pan aw yu sik ɛn di kayn sik wae yu gɛt.
- Desmopressin Acetate (DDAVP): Dis na di tritmɛnt we dɛn kin yuz mɔ. Dɛn kin gi am as sprɛy na yu nos ɔ as injɛkshɔn. i de wok bay we i de mek di VWF protin we de na wi sεl dεm kכmכt na di bכdi. Dis mɛrɛsin kin mek wata nɔ de na di bɔdi, so yu dɔktɔ kin tɛl yu fɔ lɛ yu nɔ it bɔku wata.
- Klɔtin Faktɔ Kɔnsɛntret: Na kɔnsɛntret we gɛt di VWF protin we dɛn gi insay di bɛlɛ (IV). Dɛn kin yuz dis pan sik dɛn we rili bad ɛn bifo dɛn du di ɔpreshɔn.
- Ɔda mɛrɛsin dɛn: Insay kes dɛm lɛk fɔ pul di tut, dɛn kin gi pil ɔ likwid mɛrɛsin lɛk aminocaproic acid ɔ tranexamic acid fɔ stɔp di blɔd we de klɔt fɔ mek i nɔ sɔlv.
- Speshal tritmɛnt fɔ uman dɛn: Fɔ uman dɛn we gɛt ebi ebi prɛgnɛshɔn, bɔn kɔntrol pils kin mek di VWF lɛvɛl go ɔp. mכt dεm de bak lεk fכ wɛr כmon we gεt lכp (levonorgestrel intrauterine device) כ fכ pul di layn na di uterus (endometrial ablation).
Fɔ dɔn, if yu gɛt siriɔs sik lɛk Tayp 3, if yu gɛt blɔd, na imejensi. Yu fɔ go na ɔspitul in Imejɛnsi Dipatmɛnt (ETU) wantɛm wantɛm. Di delay kin mek pɔsin in layf de pan denja.
Mɛsej we dɛn kin kɛr go na os
- von Willebrand disease (VWD) na wan kכmכn, inhεrit kכndyushכn we de afekt di blכd kכlכt prכsεs.
- If yu gɛt sɔm sayn dɛn lɛk fɔ de brus ɔltɛm, fɔ blɔd na yu nos, ɔ fɔ blɔd bɔku we yu de gɛt mɔnt, wɔri.
- If yu gɛt dɛn kayn sik ya, nɔr frayd fɔ go to dɔktɔ we sabi du in wok ɛn go to advays.
- If dɛn dɔn no se yu gɛt VWD, nɔ tek aspirin ɔ NSAID pen kil ɔltogɛda if yu nɔ gɛt dɔktɔ advays.
- If yu de trit yu fayn fayn wan, yu kin liv wɛl bɔdi, nɔrmal layf wit dis sik.
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