Fabry natna hi thil awm lo, genetic condition a ni a, kan taksaa enzyme pawimawh tak a tlakchham vang a ni. Hei hian hun kal zelah taksa peng hrang hrang, thinlung, kal, leh nervous system te a nghawng thei a ni. Chuvangin, Fabry natna i vei bawk a nih chuan i doctor chuan Agalsidase Beta tih damdawi a pe che a ni mai thei. Vawiin hian he damdawi chungchang hi a awlsam leh chiang takin kan sawi dawn a ni.
Hei hi eng damdawi nge ni?
A awlsam zawngin sawi ila, Agalsidase Beta (brand name Fabrazyme) hi Fabry natna vei taksaa enzyme tlakchhamna thlaktu a ni. Damdawi lam hawi chuan hei hi ‘Enzyme Replacement Therapy’ (ERT) an ti a.
A pawimawh ber chu hei hi natna damdawi a ni lo tih hi a ni. Mahse, he enkawlna hian natnain taksa a tihchhiatna chu nasa takin a thunun thei a, natna lanchhuahna a tiziaawm thei bawk.
Doctor hnena hrilh tur pawimawh ber berte
He enkawlna hi i tan hmain doctor hian i hriselna dinhmun chungchangah thil engemaw a hriat a pawimawh hle. Chuvangin, a hnuaia mi te hi i neih chuan doctor hnenah hrilh ngei ngei tur a ni.
- Lung natna i neih chuan .
- Agalsidase Beta, mannitol, emaw damdawi dang emaw, ei tur emaw, dye dang emaw allergy i neih tawh chuan.
- If you are pregnant , emaw naupai thuai beisei i nih chuan.
- Nu i fa hnute pe mek i nih chuan .
He damdawi hi engtin nge i hman?
He damdawi hi thisen kalna kawng (vein) chhunga intravenous infusion (infusion) angin pek thin a ni. Hei hi in lama tih theih a ni lo. He enkawlna hi damdawi in emaw clinic emaw-a trained health care provider-in a pe chauh a, medical supervision hnuaiah a pe thin.
Naupang tê tê tan hman tur
He damdawi hi naupang tê tête hnena pek dawnin a bik takin fimkhur a ngai. A chang chuan naupang kum 2 mi lek hnenah pek a ni a, mahse naupang enfiahtu doctor chauhin thutlukna a siam thin.
Damdawi ka ei tam lutuk chuan engtin nge ni ang?
He damdawi hi damdawi inah pek a nih avangin professional enkawlna hnuaiah pek a nih avangin overdose chance hi a tlem hle tlangpui. Mahse, thil thleng nia i rinhlelh chuan Colombo National Hospital-a National Poisons Information Center-ah call nghal la, a nih loh leh Emergency Treatment Unit (ETU) hnai ber pan rawh.
Damdawi dose i ei loh chuan engtin nge i tih ang?
He enkawlna atan hian damdawi hi ni ruat leh hun ruatah ei a pawimawh hle. Eng emaw chhan vanga damdawi inah ni ruat saah i lo kal thei lo a nih chuan i doctor emaw clinic emaw hnenah hriattir lawk la, ni dang ruahman rawh.
Damdawi chu khawiah nge i dah?
He damdawi hi damdawi inah emaw, clinic-ah emaw pek a nih avangin in lama hruai emaw, dah emaw phal a ni lovang.
He damdawi nena inzawm thei damdawi dang
I damdawi ei thenkhat hi Agalsidase Beta nen an inzawm thei. Damdawi i ei zawng zawng (prescribed, over-the-counter, herbal products, vitamins) te hi doctor hnenah hrilh vek a pawimawh hle. A bik takin a hnuaia damdawi te hi i ei a nih chuan:
- amiodarone a ni
- chloroquine a ni
- gentamicin hmanga siam a ni
- Hydroxychloroquine hmanga siam a ni
- monobenzone a ni
He list-ah hian damdawi inzawmna awm thei zawng zawng a tel lo va, chuvangin i ei zawng zawng chu i doctor hnenah hriattir vek a him ber.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian side effect engemaw zat a nei thei. Ṭhenkhat chu a serious a, a then chu a common. Hengte hi hriat chian a pawimawh.
| Side effect a awm thei | Hrilhfiahna |
|---|---|
| Side effects awm thei chu doctor emaw nurse emaw hnenah hriattir nghal tur a ni | |
| Allergic Reaction na tak tak a awm thei | Vun vun rawng, hnim hring, hmai, hmui emaw lei emaw a hring. |
| Thâwk harsa | Thâwk a tawi, thawk rang. |
| Chest na emaw tightness emaw a awm | I thinlung chu a hrual ang maia inhriatna. |
| Lung na tak tak | I thinlung a thawk chak emaw, i heart rate a danglam emaw ang maia inhriatna. |
| Thildang | Luak na tak, kut emaw ke emaw a hring, lungngaihna. |
| Side effects a tlangpuiin a na lo (mahse a awm reng chuan doctor hnenah hriattir tur a ni) . | |
| Damdawi i inject laia i hriat dan | Khawsik emaw, khawsik emaw. |
| Natna tlangpui | Taksa na, lu na. |
| Digestive system lama harsatna awm thei | Nausea, luak chhuak, pum na emaw, nuam lo emaw. |
| Rilru dinhmun | Hrisel lohna, lungkhamna nei. |
He list-ah hian side effect awm thei zawng zawng a tel lo. Thil danglam tak i tawn chuan i doctor nen sawiho rawh.
Take-Home Thuchah a ni
- Agalsidase Beta (Fabrazyme) hi Fabry natna tan enzyme thlak danglamna damdawi a ni. Natna hi tidam kim lo mah se, a natna lan chhuah dan leh harsatna awmte control turin nasa takin a pui thei a ni.
- He damdawi hi damdawi inah thisenah pek a ni a, chuvangin a hun taka enkawl a pawimawh hle.
- Damdawi dang i ei lai te, allergy i neih te, naupai emaw, hnute i pek emaw i nih chuan i doctor hnenah i hrilh tur a ni.
- Damdawi i inject lai emaw, i inject hnu rei vak lovah emaw, thawk harsa, rilru na, vun rawng i neih chuan doctor emaw nurse emaw hnenah hrilh nghal rawh.
- He damdawi chungchanga zawhna i neih chuan i doctor zawh hreh lo la, hreh suh.
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