Kan taksa peng thenkhat, ke leh peng leh taksa peng hrang hrangte chu a thang tha lo emaw, a lo thanglian kim lo emaw tih hi i hre ngai em? Hei hi doctor ten aplasia an tih chu a ni . He hming i hriat hian i hlauthawng deuh mai thei. Mahse, lungngai suh, he thu hi awlsam tak leh chiang takin kan sawi dawn a ni. Tichuan hei hi hriatthiamna tha zawk i nei thei ang.
(Aplasia) hi eng nge ni tak tak?
A awlsam zawngin aplasia hi i taksa peng pakhat, tissue emaw, organ emaw, i taksa peng dang emaw pawh nise, a lo thanglian loh emaw, a thawk tha lo emaw a ni. A tam zawkah chuan heng dinhmunte hi pian tirh emaw, pian hma emaw hian a awm a, naute chu a pum chhungah a la awm laiin a awm thin. A châng chuan, doctor-in nausen emaw, nausen piang thar emaw a enfiah hian, kut emaw, ke emaw ang chi ṭhenkhat chu a bo emaw, a siam ṭhat loh emaw an hmu thei a ni. Mahse, aplasia natna thenkhat, a bik takin ruhro ang chi chhungril tissue te hi naupan lai emaw, puitling emaw pawh nise hriat theih a ni.
A pawimawh ber chu aplasia hi natna pakhat chauh a ni lo. Taksa peng pakhat a insiam kim loh laia thil awm dan eng pawh sawina atana doctor ten an hman thin thumal a ni.
Engtin nge (Aplasia) hi (Agenesis), (Hypoplasia), leh (Dysplasia) te nen a danglam?
Heng thute hi ngaihthlak a buaithlak deuh thei a, a chhan chu awmzia inang an neih vang a ni. Mahse, danglamna tlemte a awm. Eng nge an nih i en ang u.
- (Agenesis): Hei hi taksa peng pakhat a lo thanglian loh tak tak hun a ni . Damdawi lam thumal thenkhatah chuan (Aplasia) tih hian taksa peng hrang hrang (organ structure) bulpui, hmasawn lo tak tak a awm tihna a ni. Mahse (Agenesis)-ah chuan chu taksa peng pakhat mah a lo thang lian lo. Entirnan, kal (kidney) a lo thang lian lo a nih chuan (Renal Agenesis) an ti a.
- Hypoplasia: Hei hi taksa peng pakhat a lo thanglian loh vang a ni . Chu chu awm mahse a tlem emaw, a kim lo emaw tihna a ni. A châng chuan aplasia hi agenesis (a awm lohna) leh hypoplasia (underdevelopment) inkara awm anga ngaih a ni.
- Dysplasia: Hei hi taksa peng emaw taksa peng emaw , a pianphung dik lo, a pianzia dik lo taka lo thanglian hi a ni. Aplasia ang lo takin dysplasia hi a hmaa hmasawnna lama harsatna (i.e., a then a lo thang lian tan a, chutah a tawp ta) avanga lo awm a ni ngai lo. Dysplasia hi cell emaw tissue emaw a lo thanglian dan pangngai lo a ni tlangpui. Entirnan, cancer natna bul tan tirh lamah chuan cell-ah inthlak danglamna pangngai lo (`dysplasia`) a awm a, chu chu a hnuah cancer-ah a lo chang ta a ni.
Heng thumalte hi i chiang lo a nih chuan i doctor hnenah hrilhfiah turin hrilh ngei ang che . Chu chuan nangmah emaw, i fa emaw dinhmun hriat chian zâwk tûrin a ṭanpui ang che.
Aplasia chi hrang hrangte chu engte nge ni?
Aplasia chi hrang hrang hi a awm vek lo. Mahse, aplasia chi tlemte kan hriat tam ber, emaw, hriat lar zawk emaw a awm. Chung zingah chuan thisen sen, vun, ruh, leh germ cell (i.e. sperm leh egg) te a tel a ni. Aplasia hian taksa peng dang, lung leh mit nerve te pawh a nghawng thei bawk.
Pure Red Cell Aplasia (PRCA) chungchang hi han sawi ila
Hetiang dinhmunah hian i thisen sen (`Red Blood Cells`) te chu a lo thang tha lo. A tlangpuiin kan ruhro (`Bone Marrow`) hian ni 120 danah thisen sen thar a siam thin. Hetih lai hian thisen sen (red blood cells) te chu an dinhmun hmasa ber ``Erythroblast`` atang khan thisen sen (red blood cells) puitling takah an lo thang lian a ni.
PRCA i neih chuan i ruhro hian erythroblasts a siam tlem hle thei a, a siam chhuak lo thei bawk. Hei hian taksain a mamawh thisen sen (red blood cells) a hloh phah a, thisen tlakchhamna (anemia) a thlen thin. Hei hi thisen sen (red blood cells) chauh a nghawng avangin "pure" an ti. Thisen cell dang – thisen var leh platelet te hi a pangngaiin an siam chhuak thin. Mahse, thisen cell chi thumte hi a siam ṭhat loh chuan aplastic anemia an ti a ni.
PRCA hi pian tirh lamah a awm thei (congenital PRCA), a nih loh leh dam chhungin a lo awm thei bawk. PRCA hi pianpui chi khat chu Diamond-Blackfan Anemia an ti a.
Aplasia Cutis Congenita chu eng nge ni?
Hei hi i naute piang thar vun, a bik takin lu vun a lo thanglian loh emaw, hmun thenkhatah a bo vek emaw a nih chuan a ni. A châng chuan, chu vun hnuaia tissue leh ruhte chu a ṭhang kim lo. Naute taksa, kut leh ke hmun thenkhatah vun a tlachham thei bawk.
(Aplasia Cutis Congenita) hi lu vunah hliam angin a lang thei a, a hnuaiah sam a awm lo. A nih loh leh, vun lo thanglian lo chu membrane te tak te, sam nei lo angin a lang thei bawk.
A hming ang bawkin (`Congenita`), hei hi pianpui natna a ni a, pian tirh atanga awm tihna a ni.
Radial Aplasia chungchang hi i zir dawn teh ang
Hei hi i kut hmawr ruh pahnih zinga pakhat, radius chu a lo thanglian loh vang a ni. I kut hmawr ah hian ruh sei tak pahnih a awm a, chungte chu radius leh ulna te an ni. Ulna chu i elbow atanga i kutphah thlengin a tlan a, i kut zungtang te tak te awmna lam a ni. Radius hi i elbow atanga i wrist thlengin a kal a, i kutpui awmna lam a ni. Radial aplasia vei chuan kut chu a deformed, bent a nei thei. Thumb chu a bo emaw, a tlangpui aia tawi emaw pawh a ni thei.
(Radial Aplasia) tih a ni.Radial Ray Deficiency hi natna chi khat a ni. Radius ruh thanna lama harsatna a ni. Radial Ray Deficiencies hi a nasat loh atanga a nasat thlengin a awm thei. A chang chuan Radius ruh hi a lo piang a, mahse a pangngai aia tawi zawk a ni. Hun dangah chuan Radius ruh hi a lo thang lian ngai lo.
Germ Cell Aplasia emaw Sertoli-Cell-Only Syndrome emaw hi eng nge ni?
Hei hi mi pakhatin a testicles (`Testes`) a germ cells (`Germ Cells`) a hloh hian a ni. Germ cells hi reproductive cells an ni. Mipaah chuan a hnua sperm (`Sperm`) lo ni ta chu germ cells te hi an ni. Germ cells a bo chuan sperm a siam chhuak thei lo. Chumi awmzia chu germ cell aplasia vei te hian fa an nei thei lo (`Infertility`).
Germ cell aplasia hi Sertoli-Cell-Only Syndrome an ti bawk. Hei hi a chhan chu, germ cells awm lo mahse, Sertoli cells chu reproductive system-ah a la awm reng a ni. A tlangpuiin Sertoli cell hian germ cell te chu sperm ah a lo thanglian thei a ni. Mahse, germ cells a awm loh chuan Sertoli cells hian sperm siamnaah chanvo a nei lo.
Pulmonary Aplasia pawh han en ila.
Pulmonary Aplasia hi mi pakhat chu a piang a, a lung a lo thang chak lo hle a ni. Hei hi dinhmun pakhat chauh a ni lo va, chi hrang hrang a awm thei bawk. Lung hmasawnna tlakchhamna (Pulmonary Agenesis) atanga hmasawnna tlem (Pulmonary Hypoplasia) thlengin a awm thei.
Pulmonary Aplasia hi Pulmonary Agenesis leh Pulmonary Hypoplasia inkar hmun khatah a awm a. Aplasia-ah chuan lung structure rudimentary tak a lo piang a, mahse lung hnathawh kim tak hna chu a thawk thei lo.
Vawi tam tak chu lung pakhat chu a bo emaw, a lo thanglian lo emaw a ni a, pakhat zawk chu a pangngai a ni.
Thymic Aplasia hi eng nge ni?
I thymus gland hi thisen var chi khat T-cells an tih siamtu gland a ni. T-cells hian i taksain natna hrik a do theih nan a pui thin. Thymic Aplasia -ah chuan i thymus gland a lo thang lian lo. Thymus gland nei lo i pian chuan natna hrik i kai tam zawk.
Thymus gland awm lohna hi DiGeorge Syndrome an tih natna lan chhuahna pakhat a ni. DiGeorge Syndrome hian taksa system hrang hrang a nghawng thei a ni. I immune system leh heart function a nghawng thei a, naupan lai pawhin hmasawnna a tikhawtlai thei bawk.
Optic Nerve Aplasia pawh hi i hrechiang ang u.
(Optic Nerve Aplasia) tih a ni.Mit pakhat emaw, mit pahnih emawa thil pawimawh tak tak, mit nerve pawh tiamin, pian tirh atanga hloh a ni. I mit nerve hian i mit hmuhnaah hmun pawimawh tak a chang a ni. I mit chu i thluak nena inbiakpawhna leh hmuh theih information process tir theitu a ni. Optic nerve vang hian i mit hian thil chi hrang hrang, a lem leh rawng ang chi a hmuh hian i thluak chuan chu thu chu a hriatthiam theih tur hmuh theih lem (visual image)-ah a chantir thei a ni.
Optic Nerve Aplasia hian mit lama harsatna hrang hrang a thlen thei a, chu chu i dinhmun nasat dan azirin a ni. Mit pahnih tichhe thei, Aplasia natna hian thluak thanna kawngah harsatna a thlen thei bawk.
Engtiang chiahin nge aplasia hi a hluar?
Aplasia hi a awm lo hle . A chi hrang hrang awm tam ber chu `(Radial Aplasia)` leh acquired form ``Pure Red Cell Aplasia`` (PRCA) te hi a ni. `(Radial Aplasia)` hian nau piang thar 30,000 zinga 1 vel a vei a ni. `(Radial Ray Deficiencies)` (chutah chuan `(Radial Aplasia)` pawh a tel) hi pianpui natnain kut a nghawng tam ber a ni. Congenital form of (PRCA) pawh hi a tlem hle a, nau piang maktaduai khatah 5 atanga 7 vel an awm nia chhut a ni. Acquired form hi a tam zawk deuh a, mahse case engzat nge awm tih erawh kan hre chiang lo.
Aplasia hi engte nge ni?
Aplasia chi tam tak hi genetic mutations avanga lo awm a ni a, chu chu nu leh pate hnen atanga rochun a ni. I gene-ah hian eng taksa mizia nge i neih dawn tih tichiangtu thupek a awm a. Entîr nân, heng thupêkte hian taksa peng pakhat chu khawiah nge a lo pian chhuah ang a, engtin nge a lo pian chhuah ang tih a hril a ni. I nu leh i pa hnen atangin gene i hmu a. Gene pakhatin mutation, emaw defect a neih chuan aplasia ang chi harsatna i nei thei a ni.
A tlem berah chuan aplasia hi hun kal zelah a lo awm thei. Entirnan, acquired PRCA hi thil dang leh dinhmun dang avanga lo awm a ni a, chung zingah chuan infection, autoimmune diseases, leh cancer chi hrang hrang te pawh a tel.
A then phei chuan doctor leh scientist te chuan aplasia awm chhan hi an hmu thei lo. Chutiang aplasia chi chu idiopathic an ti a .
Engtin nge (Aplasia) hi kan hriat theih ang?
Naupai lai hian aplasia chi thenkhat chu test hmangin hriat theih a ni a, chu chu ultrasound scan hmangin a ni. Aplasia chi dang chu pawn lamah hmuh tur a awm lo va, pian tirh chauhvin a lang.
He natna hi a na lo a nih chuan, emaw, thisen leh ruhro a inrawlh a nih chuan, naupan lai thlengin a lan chhuah loh theih a ni. Aplasia chi hrang hrang a zirin i dinhmun hriat theih nan imaging procedure hrang hrang, thisen test leh genetic testing te i neih a ngai mai thei.
(Aplasia) hi eng enkawlna nge ni?
I dinhmun a zirin enkawlna kawng hrang hrang a inang lo. Surgery hi kut leh ke emaw, kut leh ke emaw, a lo thanglian lo hnathawh tihchangtlun nan tih theih a ni. PRCA natna khirh takah chuan thisen pek a ngai mai thei. I dinhmun azirin damdawi hi symptoms control nan emaw, aplasia avanga harsatna lo thleng tur ven nan emaw pek theih a ni.
Aplasia chi thenkhat, germ cell aplasia te hi enkawl theih a ni lo.
Aplasia hi tihdam theih a ni em?
I dinhmun a ṭhat leh ṭhat loh chu aplasia i neih chi leh a thlentu thilte a zirin a ni. Entirnan, acquired pure red cell aplasia (PRCA) hi tihdam theih a ni a, chu chu i taksain thisen sen a siam theih lohna tur thilin a tidam thei a ni. Thisen sen siam chhuahna tikhawlotu dinhmun hnuaia awm enkawl hian a chang chuan aplasia hi a ti \ha thei a ni.
Aplasia hi pianpui natna, tihdanglam theih loh, tihdam kim theih loh tihna a ni. Chutiang hunah chuan doctor chuan zai emaw, damdawi ei emaw, a nih loh leh enkawlna bik emaw a rawt thei a ni. Chûngte chuan kut, ke, a nih loh leh ke ruh hnathawh a tichak thei a, a nih loh leh natna lan chhuah dân a thunun thei bawk.
"(Aplasia)" tih thumal hian awmzia hrang hrang a nei thei. Thil tam takah a innghat a, chu chu taksa peng eng nge a nghawng tih te, i natna lan chhuah dan te, leh i natna a nasat loh leh a nasat dan te a ni. Heng thumalte hi i buaipui suh. Nangmah emaw i fate dinhmun chu "(Aplasia)," "(Agenesis)," emaw chutiang chi thumal dang hmanga sawifiah a nih chuan, chu thumalte awmzia leh hun kal zelah eng nge i beisei tur tih chu i doctor hnenah zawt rawh. Enkawlna tur a awm em tih leh a tul em tih zawt rawh. Chutiang a nih chuan, eng enkawlna chi nge ṭanpui thei tih sawiho rawh. Heng hmasawnna lama harsatnate hian i nitin nunah engtin nge a nghawng (a nih loh leh a nghawng loh) zawt rawh.
Kan hriat reng tur pawimawh ber berte
Okay, chuvangin, kan sawi tawh (Aplasia) atang hian ngaihdan i neih ka beisei. A tawi zawngin:
- Aplasia tih awmzia chu taksa peng pakhat a lo thang tha lo tihna a ni.
- Hei hi natna inang a ni lo va, chi hrang hrang leh level hrang hrangah a awm thei .
- Aplasia chi thenkhat chu pianpui a ni a, thenkhat erawh chu dam chhungin a lo awm thung.
- A chhan hrang hrang a awm a; genetic cause, infection, natna dang, leh a chang chuan a chhan hmuh tur a awm lo.
- Enkawlna chu aplasia chi leh a nasat danah a innghat a ni. Ṭhenkhat chuan natna lan chhuah dân thunun tûr leh nunphung tihchangtlun nân operation, damdawi, a nih loh leh enkawlna bik dang an mamawh thei a ni.
- Congenital aplasia hi tihdam kim theih ni lo mah se, uluk taka enkawl leh puihna a awm chuan a tam zawk chu nun pangngaia nun theih a ni.
- A pawimawh ber chu doctor pan a, nangmah emaw, i fain emaw he natna chungchangah hian rinhlelhna i neih chuan thurawn leh thu dik tak i dawng a ni.Hlauthawng suh la, zawhna zawt la, thil awmdan chu uluk takin hrethiam rawh.
He thu hi i tangkaipui ngei kan beisei!
` Aplasia, Taksa peng lian lo, Pianpui chhiatna, Pure Red Cell Aplasia, Aplasia Cutis Congenita, Radial Aplasia, Germ Cell Aplasia











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