I naute te taksa chu a sen tawh em? Biliary Atresia a ni thei ang em?

I naute piang thar i en lai hian a taksa chu a sen deuh tih i hmu ngai em? A tlangpuiin nau piang thar tam zawk chuan kar khat emaw kar hnih emaw chhungin jaundice tlem an nei a, chu chu ni engemaw zat hnuah a reh tlangpui. Mahse, i naute bawlhhlawh rawng hi i ngaihtuah ngai em? A châng chuan a dum emaw, a dum emaw a lang ṭhin em? Heng thil pahnih hi i hmuh dun chuan thil pangngai anga ngaihin bum suh ang che. A chhan chu tunlaia kan sawi tur Biliary Atresia tih hming pu natna khirh tak chhinchhiahna a ni thei a ni.

A awlsam zawngin, Biliary Atresia chu eng nge ni?

Kan taksa chhunga thin (liver) hi factory tenau tak angin han ngaihtuah teh. He factory hian bawlhhlawh paihna atan "bile" an tih tui a siam chhuak thin. He bile hi liver atang hian tube (bile ducts) system tha tak tak hmangin a kal a, kan small intestine ah a tawp thin. Bile hian hna pawimawh pahnih a nei a. Pakhat chu taksa atanga bawlhhlawh duh loh paih chhuahna tura puih hi a ni. A dang chu kan ei tur, a bik takin thau te digest-a puih a, kan taksa mamawh nutrients te hip lut turin a pui a ni.

Biliary Atresia hi nau piang laiin bile phurtu tube nalh tak chu a block emaw, a siam tha lo emaw a ni. Chumi awmzia chu liver-a bile siam hian chhuahna tur a nei lo va, chu ai chuan liver chhungah a tang ta zawk tihna a ni. Hei hi khawpui pakhata bawlhhlawh paihna kawng zawng zawng khap ang mai a ni. Bawlhhlawh zawng zawng chu khawpui chhungah a pung khawm a, khawpui pum pui chu a chhe vek a ni. Bile chu liver chhunga a tlakbuak chuan liver nasa takin a tichhe tan thin.

Hei hi natna khirh tak a ni a, naute naupangte chu an thla hmasa berah a nghawng thin. Enkawl vat loh chuan thin (liver) nasa takin a tichhe thei a, thin (liver failure) pawh a thlen thei a ni.

Biliary Atresia natna lan chhuahna berte chu engte nge ni?

Heng symptoms te hi naute pian atanga kar tlemte chhungin a lang tan tlangpui. Nu leh pa in nih angin hei hi in ngaihven hle tur a ni.

Hun kal zelah symptom dang lang chhuak

I naute chu kar 6 atanga kar 10 vel a nih hunah chuan heng natna lanchhuahna te hi a lo lang thei bawk:

• Itchy skin: Taksa chhunga bile a pungkhawm hian vun a ti na nasa thei hle.
• Tap leh thinrim fo: Taksa lama harsatna avang hian naute chu a thinrim a, a tap fo thei bawk.
• Hlawhtling lo: Bile tel lo chuan chaw hi a hmin tha lo a, chuvangin taksain nutrients a hip lut lo. Chuvang chuan naute chu a thau tha lo hle a ni.
• Abdominal swelling: Liver a chhia a, pum chu tuiin a khat tan a, chu chuan pum chu a rawn chhuak a, a lo hring chhuak thin.

Engvangin nge Biliary Atresia hi a lo awm?

Nu leh pa tam tak chuan, "Engvangin nge kan naute chungah hetiang hian a lo awm?" "Thil dik lo kan ti em?" Researcher te chuan hei hi eng thil nge a thlen tih hi 100% in an la chiang lo.

Mahse, ngaihdan ber chu he natna hi nu pum chhunga naute a lo thanglian zel laiin bile ducts siam chhuah laia somatic genetic mutation avanga lo awm a ni. A pawimawh ber chu hei hi nu leh pa atanga fa hnena rochun thil a ni lo. Tin, he natna hi naupai laia i thil tih leh i sawi avanga lo awm a ni lo. Chuvangin ngaihtuah buai suh la, nangmah leh nangmah mawhpuh suh.

Enkawl loh chuan eng harsatna nge thleng thei?

Biliary atresia hi enkawl vat ngai a ni. Enkawlna tihkhawtlai hian harsatna lian tak a thlen thei a ni.

• Liver chhiatna awm reng (Cirrhosis): .Bile retention chhunzawm zel hian liver cells a thi a, liver a hliam a, lung ang mai a ni. Hei hian liver function a hloh vek thei a ni.
• Portal hypertension: Liver a hliam chuan a kal tlanga thisen kal a tikhawlo a, chu chuan thisen liver-a thisen phurtu vein-ah thisen sang a thlen thin.
• Ascites: Liver failure leh portal hypertension vangin pum chhungah tui a awm tan thin.
• Hepatomegaly: Liver chu a hring a, a lian a, chu chu bile a pungkhawm leh a hliam vang a ni.
• Esophageal Varices: Portal hypertension hian esophagus chhunga veins te chu a ti na a, a puak thei bawk. Hei hian chhungril lama thisen chhuak nasa tak a thlen thei a, chu chuan nunna a tichhe thei a ni.

Heng zawng zawng hian liver failure a thlen thei a ni. Mahse, a natna lan chhuah dan hi i hriat hmasak a, doctor i hmuh a, i enkawl tan chuan heng harsatna tam tak hi i ven theih a ni.

Engtin nge natna hi kan hriat theih ang? (Diagnosis) tih a ni.

I naute hian kar hnih aia rei jaundice a vei a nih chuan, emaw, an ek a hring nia i rinhlelh chuan naupang doctor pan nghal tur a ni. Doctor chuan i naute chu a enfiah hmasa ang.

• Vun leh mit a sen leh sen loh a enfiah thin.
• Pum a hring emaw, thin a lian em tih emaw chu kut hmangin an enfiah ang.

Chumi hnuah chuan natna hriat chian nan test eng emaw zat tih a ni.

Enkawl dan: Kasai Procedure

Biliary Atresia enkawlna main leh first line chu Kasai Procedure a ni . Hei hi damdawi hmanga tihdam theih natna a ni lo.

A awlsam zawngin, he surgery-ah hian surgeon chuan bile duct blocked chu a la chhuak a, naute ngei pawh a small intestine section tlemte a la a, liver-ah direct-in a thlunzawm a ni. Hei hi kawngpui chhe tawh tak paih chhuah a, a aiah ‘bypass’ thar siam ang mai a ni. He kawng thar hmang hian liver-a bile siam chhuah chu intestine-ah direct-in a luang tan ta a ni.

Surgery zawhah naute jaundice chu a reh zauh zauh a, a ek rawng chu a pangngaiin a lo let leh a, chaw ei a that chhoh zel chuan naute rihna pawh a sang chho tan ta a ni.

Mahse, Kasai surgery hi a chinfelna nghet tak a ni em?

A tam zawkah chuan Kasai surgery hi dam chhung zawnga solution a ni lo. A chhan chu operation hmain liver-ah chhiatna engemaw zat a awm tawh mai thei. Chu chhiatna chu hun kal zelah a pung zauh zauh thei a ni.

Naupang tam tak, Kasai surgery nei tawhte chuan naupan lai emaw, tleirawl lai emaw pawhin thin (liver transplant) an mamawh dawn a ni. Mahse hei hi hlauh tur a ni lo. Tunlai hian liver transplant hi a hlawhtling hle. Hei hmang hian naupang chuan hrisel tak, hun rei tak chhung nun theihna hun remchang a nei a ni.

Nu leh pa angin engtin nge in naute in enkawl?

I naute hian Biliary Atresia a vei tih i hriat chuan i khawvel pum pui chu a inthlak danglam vek ang maiin a lang thei. Hun harsa tak a ni. Mahse, nangmah chauh i ni lo. Medical team chuan engkim an hrilhfiah ang che a, an pui ang che.

• Special Nutrition: Naute hian ei tur dik tak a dawn theih nan doctor chuan special formula, vitamin leh additional nutritional supplement a pe ang.
• Hun rei tak chhunga damdawi lam enkawlna: Naute chu ni ruat saah clinic-ah hruai a ngai a ni. Doctor chuan naute than dan leh thin hnathawh dan a enfiah fo ang.
• Operation hnua fimkhur tur chhinchhiahna: Caesarean section operation hnua i naute i rawn hruai haw hunah heng chhinchhiahnate hi lo thlir reng ang che.
• Khawsik
• Taksa a sen leh chuan (jaundice) .
• Thluak a rawn sen leh emaw, zun a dum leh emaw chuan

Hetiang thil i hmuh chuan doctor ko nghal rawh.

• Nangmah pawh ngaihtuah teh: Heng zawng zawng nen hian rilru leh taksa lamah pawh i chau hle ang. Chhungte leh thiante hnenah tanpuina dil rawh. I chawlh hahdam leh mut hun siam rawh. Tin, nu leh pa dang fa nei tawhte nena inbiakna pawh i tan chakna nasa tak a ni ang.