I hriat mi pakhat chu a rilru a buai nghal tih i hmu ngai em? A nih loh leh mi hrisel tak chu an muthilh laiin a thi tih i hre tawh em? Chutiang thil thlen chhan chu mi tam takin an hriat ngai loh thinlung natna thup a ni thei. Vawiin hian chutiang natna khirh tak leh pawimawh tak hriat tur pakhat, Brugada Syndrome chungchang kan sawi dawn a ni.
Brugada Syndrome hi eng nge ni?
A awlsam zawngin sawi ila, hei hi kan thinlung electrical system-a harsatna a ni. Kan thinlung hi electrical signal system ang maiin a na a. He natnaah hian thinlung hnuai lam (ventricles)-a electrical signal kal danah thil dik lo a awm a.
Hei hian thinlung chu hlauhawm takin a ti na a, a khur ang maiin a ti na hle. Hei hi damdawi lamah chuan `Ventricular fibrillation (v-fib)` an ti a. Chutiang a lo thlen chuan thinlung hian taksaah thisen a pump tha thei lo. A bik takin thluaka thisen kal a tihbuai chuan muhil a awm thei.
Hetiang dinhmun hlauhawm ber chu cardiac death rang tak a thlen thei tih hi a ni. Hei hi damlo chu a chawlh laiin a thleng fo thin a, a bik takin mut laiin a thleng fo thin. Research atanga a lan dan chuan khawvel pumah Brugada syndrome hi sudden cardiac death 4% vel a ni.
Mahse hei hi chu a awm lo hle. A vaiin mi 10,000 zinga 3 leh 5 inkarin he natna hi an vei a ni.
He natna lan chhuah dan engte nge ni?
Brugada syndrome hi kum eng pawhah a lang thei a, mahse kum 40 vel ah a langsar ber a, mak tak maiin he natna vei zinga 70% aia tam hian chhinchhiahna an nei lo Mi tu emaw chuan natna lan chhuahna a nei a nih chuan a hnuaia mi hi a tawng thei a ni:
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Fainting/Syncope tih hi a ni | Heart rhythm mumal lo hian thluaka thisen kalna a tibuai a, chu chuan hriatna a hloh nghal a, a tlu nghal thei bawk. |
| Luak chhuak thei | Lung a na hle tih a hriat. |
| Lung na tak tak | Thinlung na tak ang maia hriatna, thinlung chu rilru chhunga inher ang maia hriatna. |
| Thâwk harsa | Thâwk harsa, a bik takin zan lamah. |
| Cardiac Arrest a ni | Hei hi a symptom hmasa ber a ni mai thei . Hei vang hian mi thenkhat chu an muthilh laiin an thi thin. |
Eng thilin nge he dinhmun hi a tizual?
Brugada syndrome vei mi pakhatah chuan natna lan chhuahna tichhuak thei emaw, tizual thei emaw thil thenkhat hriat a pawimawh.
- Khawsik: Khawsik hi he natna dotu ber pakhat a ni. Brugada syndrome i neih chuan doctor-in a tih angin, khawsik i neih veleh paracetamol ang damdawi ei a pawimawh hle.
- Dehydration: Taksaah tui a awm loh chuan.
- Binge drinking: Vawi khata zu tam tak in.
- Damdawi thenkhat: Lung lam natna thenkhat atana hman thin `Sodium channel blockers` te, leh rilru lam natna damdawi `Lithium` leh `Tricyclic antidepressants` te.
- Ruihhlo: Ruihhlo, cocaine leh marijuana ang chi.
Doctor in he natna hi i nei tih a nemnghet a nih chuan i doctor hnenah i ei loh tur damdawi list zawt ngei ang che. Condition dang damdawi i ei dawnin Brugada syndrome i vei tih doctor hnenah hrilh tur a ni.
Engvangin nge he natna hi a lo awm?
A tam zawkah chuan 70% velin he natna hi a chhan bik hmuh tur a awm lo. Mahse, mi thenkhat tan chuan genetic a ni. A awlsam zawngin sawi ila, rochun a ni.
- Genetic causes: Kan taksaa gene 18 aia tam inthlak danglamna hian hetiang hi a thlen thei a ni. Chung zingah chuan a tam ber chu `SCN5A` gene-a mutation a ni. Heng genes inthlak danglamna hian thinlunga electrical signals inthlunzawmna a tibuai a ni.
- Heredity: Nu leh pa pakhatin he natna nena inzawm gene mutation a neih chuan naupangin a rochun theihna chance 50% a awm.
Tu nge hlauhawm ber?
- Mipa tan: He natna hi hmeichhia aiin mipaah a let 8-10 velin a tam zawk.
- Chhungkaw chanchin: I chhungkuaa mi tu emaw Brugada syndrome nei a nih chuan, emaw, kum naupang tak a nih laiin mi pakhatin a thih thut a nih chuan, nang pawh i hlauhawm thei bawk.
- Asian atanga lo chhuak: He natna hi khawthlang ram aiin Asia ram a mite zingah a tam zawk tih hmuhchhuah a ni.
Engtin nge natna hi dik taka kan hriat theih ang?
I natna lan chhuah dan leh chhungkaw chanchin a ngaihthlak hnuah i doctor chuan he natna hi i vei em tih finfiah nan test eng emaw zat a ti ang.
| Fiahna | Engtin nge i tih? |
|---|---|
| Electrocardiogram (EKG) hmanga tih a ni. | Line graph-a thinlung electrical activity tarlanna test. Doctor-te chuan he natna nena inzawm, he pattern-ah hian pattern bik an zawng thin. A châng chuan he pattern hi a lang reng lo va, chuvangin EKG hi vawi tam tak tih a ngai mai thei. |
| Damdawi hmanga EKG test (Drug Challenge Test) . | EKG pangngaiin rinhlelh awm tak a lantir chuan Brugada pattern thup chu pholan tumin vein-ah damdawi bik an inject a ni. Hei hi hmun him, damdawi in intensive care unit ang chiahah tih a ni. |
| Genetic Testing neih a ni | I hmui emaw thisen emaw sample hmangin he natna nena inzawm genetic mutation i nei em tih hriat theih a ni. I chhungkuaa mi tu emaw chuan he natna hi an nei a nih chuan midang pawhin he test hi an nei thei bawk. |
| Electrophysiology (EP Test) hmanga thil tih a ni. | He test hi test dang hnuah pawh diagnosis a la chiang lo a nih chuan tih thin a ni. Hei hian ke chhunga vein kaltlangin cannula (catheter) nalh tak tak chu thinlung chhungah dahin thinlung chhunga electrical activity tehna a huam a ni. |
Engtin nge enkawl a nih?
Brugada syndrome hi a dam kim thei lo. Mahse, cardiac thih thut loh nan enkawlna pek theih a ni. Enkawlna tum ber chu heart rhythm irregularities hlauhawm tak tak (ventricular arrhythmias) lo awm tur tihtawp a, a lo awm chuan control a ni.
Enkawlna ber leh tangkai ber chu ICD device dah hi a ni .
- ICD (Implantable Cardioverter Defibrillator): Hei hi hmanraw te tak te a ni. Pacemaker ang mai a ni. Vun hnuaiah, thinlung bulah, rilruah surgery tenau tak hmangin dah a ni. Thinlung rhythm a enkawl chhunzawm zel a ni. Thinlung rhythm hlauhawm taka a inthlak chuan he device hian a hrechhuak a, electric shock te tak te a pe a, chu chuan rhythm chu a siam tha leh thin. Hei hi nunna chhanhimna hmanrua a ni.
- Damdawi: Damdawi thenkhat, `Quinidine` te hian thinlung thawk mumal lo a control thei a. Mahse, hengte hi mi zawng zawng tan a inhmeh lo.
- Ablation: Thil bik thenkhatah chuan enkawlna hmanrua, thinlung chhunga electrical signal mumal lo awmna hmun zawng chhuakin radio wave hmanga tihchhiat a ni.
Doctor-te chuan EKG record, chhungkaw chanchin leh test result dangte aṭangin asymptomatic patient-te enkawl leh enkawl loh tur an rel ṭhin. Because sometimes the first symptom is sudden death , a hlauhawmna tehfung leh a tul anga enkawl a pawimawh.
Engtikah nge Emergency Treatment Unit (ETU) ah i kal ang?
Sudden cardiac arrest (cardiac arrest) i neih chuan damdawi lam pan vat a ngai dawn a ni. Chutih hunah chuan tanpuina i ko thei dawn lo a nih avangin hemi chungchang hi i chhungte leh i hmangaih te hriattir a pawimawh hle.
Cardiac arrest hlauhawm i nih chuan i chhungte leh i thiante hnai tak takte hnenah CPR (cardiopulmonary resuscitation) tih dan zir turin hrilh rawh. Emergency a awm chuan 1990 call la, ambulance call rawh. He hriatna hian i nunna a chhanhim thei a ni.
Take-Home Thuchah a ni
- Brugada syndrome hi natna khirh tak a ni a, thinlung electrical system-ah a awm a, thihna thut hial a thlen thei a ni.
- Khawsik hi he natna tizualtu lian tak a ni. Khawsik i neih chuan tihhniam vat rawh.
- I chhungte zinga mi tu emaw kum naupan laia thi thut emaw, i hriatna hloh fo emaw a nih chuan doctor pan nghal la, EKG test nei rawh.
- ICD hmanrua dah hi he natna laka nunna chhanhimna atana enkawlna tha ber a ni.
- He natna hi i vei a nih chuan i doctor-in damdawi a pek che, i hman tur atana tha lo list kha hre reng ang che.
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