Doctor-in i naute piang thar hian vagina, urethra leh anus awmna tur kawngkhar pakhat chauh a nei tih a hrilh che khan i hlauthawng hle a, i mangang hle bawk. A tam hle mai. Hetiang thu hre tur hian tumah an inpeih lo. Mahse, lungngai suh. Hei hi piansualna hmuh tur awm lo tak a ni a, surgery hmanga hlawhtling taka siamthat theih a ni. Engkim hi awlsam tak leh chiang takin sawi ila.
A awlsam zawngin Cloacal Malformation chu eng nge ni?
Cloacal Malformation hi piansualna a awm lo hle a, hmeichhe naupang chauh a nghawng a ni. A tlangpuiin hmeichhe naupang serh leh hnute (he hmun hi perineum kan ti) hian hawnna pathum a nei tur a ni . Anni chu,
1. Urethra ( zun chhuahna tube ) .
2. The vagina , thlasik leh mipat hmeichhiatna hmanna hmun.
3. Anus ( bawlhhlawh chhuahna kawng ) .
Mahse, Cloacal Malformation nei naupang chuan heng pathum ai hian hawnna pakhat chauh a nei a ni. Chumi awmzia chu zun, bawlhhlawh leh vaginal secretions te hi he opening pakhat hmang hian taksa atangin an chhuak vek tihna a ni. Hei hi natna bik a ni a, nau piangsual pawl `(Anorectal Malformation)` an tih zingah a tel a ni.
Ngaihtuah teh, naupai laiin naute lo seilian kar hmasa berah hian system pathum—intestinal system, urinary system, leh reproductive system—te chu common chamber pakhat "cloaca" an tih nen an inzawm vek a ni. Naute a lo seilian chhoh zel chuan he chamber hi zawi zawiin hmun thumah a inthen a, a hmaa kan sawi tawh angin hawnna pathumte chu a siam ta a ni. A chang chuan he inthenna kalphung hi a thleng dik lo. Chu chu system pathumte hi common tube-ah an inzawm vek a, taksa atanga chhuakin kawngkhar pakhat hmangin an inhawng chhuak vek a ni.
Hetiang dinhmun enkawlna chu he hawnna tlanglawn tak ai hian surgery hmanga hawnna hrang hrang pathum siam hi a ni. He surgery hi naupang dam kum khatna chhunga tih a ni tlangpui.
Hetiang dinhmun hi chi hrang hrang a awm em?
Awle. Cloacal Malformation condition nasat dan hi kan sawi tawh system pathum inzawmkhawmtu "common channel" sei zawng atanga teh a ni. He common channel hi khawi hmunah pawh centimetre 1 atanga centimetre 10 thleng a sei thei. He sei zawng hian naupangin surgery a mamawh tur chu a buaithlak zia a hril a ni.
- Having a Short Common Channel: Hei hi system pathumte hi taksa pawn lama hawnna hnaih takah an inzawm khawm hian a ni. Chumi awmzia chu common channel a tawi tihna a ni. Chutiang hunah chuan bawlhhlawh chu taksa atanga chhuak a awlsam zawk. Surgery pawh a awlsam hle. Tin, naupang hmalam hun hriselna a tha zawk hle bawk.
- Common Channel rei tak neih:Hei hi dinhmun buaithlak ber a ni. Hetah hian system pathumte hi taksa chhung thuk takah an inzawm khawm a ni. Chuvangin common duct hi a sei zawk a ni. Hei hian bawlhhlawh taksa chhuahsan a harsat phah a ni. Surgery pawh a buaithlak zual zel bawk.
Hetiang dinhmun hi a tlem hle a, nau piang thar 25,000 atanga 50,000 zinga pakhat vel ah a awm thin.
He natna lan chhuah dan leh a kaihhnawih harsatna dangte chu engte nge ni?
A langsar ber leh langsar ber chu hmeichhe naupang chu a awm tur pathum ai chuan hawnna pakhat chauh neia piang a ni. Tin, he natna hian hriselna lama harsatna dang a thlen thei bawk. He table-ah hian han en ila.
| Symptom/a kaihhnawih harsatna | Hrilhfiahna awlsam tak |
|---|---|
| A bulpui ber a ni | Anus, vagina leh urethra aiah hawnna pakhat. |
| Clitoris a lian chho zel | Naupang thenkhat vagina hi mipa zang ang maiin a lang thei. |
| Rectum pangngai lo | Anus awmna hmun danglam emaw, a lan dan danglam emaw. |
| Reproductive system lama harsatna awm thei | A châng chuan vagina, uterus, cervix pakhat aia tam a awm thei bawk. |
| Urinary system lama harsatna awm thei | Kidney, ureter, bladder-ah harsatna hrang hrang a awm thei. |
| System dang a harsatna awm thei | Thinlung, ruhro, chaw ei leh in lama harsatna dang a awm theihna a awm bawk. |
Engvangin nge ka fa chungah hetiang hian a lo awm? Eng nge a chhan?
He zawhna hi i rilruah a lo lang hi thil awmdan pangngai a ni. Mahse doctor-te chuan eng thil nge a thlen tih erawh an hre chiang lo. Researcher-te chuan random occurrence niin an ngai a, a chhan chiang tak a awm lo.
Hei hi i sualna a ni lo tak zet a ni. Hetiang dinhmun hi i naupai laia i thil tih leh i tih loh avanga lo awm a ni tih ngaihtuahin lungchhiat suh. Chu chu a dik lo tak zet a ni.
Engtin nge he dinhmun hi kan hriat theih ang?
Hetiang dinhmun hi pian hma leh pian hnuah pawh hriat theih a ni.
Pian hma (naupai lai) .
A châng chuan, he natna hi ultrasound scan hmangin hriat theih a ni a, chu chu naupai kar 20 vêlah tih a ni. Doctor-te chuan scan-ah naute serh chhungah tuiin a khat, a hring (swelled sac) a awm a nih chuan an ringhlel a ni. He rinhlelhna hi nemnghet turin naupai laiin Magnetic Resonance Imaging (MRI) test pawh tih theih a ni.
Pian hnuah
Hetiang dinhmun hi naute pian hnuah hriat chhuah a ni fo thin. Naute enfiahtu naupang enkawltu chuan kawngkhar pathum ni lovin pakhat chauh a awm tih a hmu ang. Naute hian a pum a hring thei bawk. Tichuan, taksa chhunga thil thleng dik tak hriat chian nan test eng emaw zat tih a ni ang.
- Ultrasound scan: Naute kal (kidney, bladder), leh ruhro (spine) te dinhmun enfiah thin ang che.
- X-ray: X-ray technique bik, fluoroscopy ang chi hmangin zun kawng hnathawh dan a hriat theih.
- Echocardiogram: He test hi thinlungah harsatna a awm leh awm loh hriat nan tih a ni.
Engtin nge enkawl a nih? Surgery chungchang i zir dawn teh ang
Cloacal Malformation enkawlna chu operation a ni . A tum ber chu hawnna pakhat ni lovin hawnna hrang hrang pathum (anus, vagina, leh urethra) siam a ni. A tum ber chu naupang chu a pangngaia ek chhuah leh zun theihna pek leh a thunun theihna tur a ni.
Hei hi surgery vawi khata tih theih a ni lo. A tlangpuiin operation hrang hrang tih a ngai thin. Chumi atan chuan naupang surgeon leh naupang urologist tanpuina lak a pawimawh hle.
Enkawl dan hi step lian pathum ah then theih a ni.
Step 1: Operation hmasa ber (na pian atanga darkar 48 chhungin) .
Hei hian a tum ber chu bawlhhlawh (feces leh zun) te naupang taksa atanga a chhuah dan tur dik tak siam a ni.
- Colostomy: Naupangin ek chhuahna tur kawng a neih loh avangin surgery hmangin a pum chhungah kawngkhar siam a ni a, chu chu a chhungril thenkhat chu vun chung lamah hruaiin a ni. He hawnna hmunah hian bag an dah a, chu chuan bawlhhlawh a khawlkhawm thei a ni.
- Urinary incontinence: Urinary incontinence: Urinary incontinence hi zun a hring emaw a block emaw avangin catheter hmangin zun hi a chhuak thin.
- Vagina: Vagina chhungah tui a awm khawm chuan surgeon chuan a tui chu a la chhuak ang.
Step 2: Major reconstructive surgery (thla 6 leh thla 12 inkar) .
He surgery lian tak hi naupang chu a upa deuh a, a hriselna a nghet tawh hnuah tih a ni. Heta thil thleng chu common channel chu section hrang hrangah then a ni a, chu chuan anus, vagina leh urethra hran a siam a ni. Common channel a tawi a nih chuan he surgery hi a awlsam hle. Common channel a sei chuan surgery chu a buaithlak zual hle.
Step 3: Colostomy tihdanglam
Main surgery zawhah chuan anus siam thar chu a dam tawh chuan original colostomy chu lakchhuah a ni. Chumi awmzia chu pum chhunga hawnna siam chu khar a ni a, intestines chu a awmna pangngaiah a inzawm leh tihna a ni. Chumi hnuah chuan naupang chuan a hnute siam thar hmangin a ek chhuak thei a ni.
Naupang thenkhat chu nakin lawkah operation dang an mamawh mai thei a, chu chu i doctor chuan a hrilhfiah ang che.
Naupang hmalam hun chu eng ang nge ni ang?
Hei hi nu leh pa zawng zawng rilrua zawhna lian ber a ni. Thu lawmawm tak chu result a tha hle tlangpui .
- Bowel leh bladder control: Naupang common duct tawi, a buaithlak lo zawkte chuan an bowels leh bladder control kim theihna chance 90% an nei a. Hei hian normal takin toilet train an ti thei tihna a ni. Naupang common duct sei tak, a buaithlak zawk nei pawhin control tha tak an neih theihna chance 70% an nei a ni. Naupang thenkhat chuan zun control harsa an ti thei (urinary incontinence). Chutiang hunah chuan ni khatah vawi tam tak tube hman a ngai mai thei a, chu chuan an bladder chu a hlip thei a ni.
- Sex nun leh naupai: Hetiang natna vei naupang tam tak hian puitling an nih chuan sex nun pangngai, lungawithlak tak an nei thei a ni. Tin, nau an pai thei bawk. Mahse, hmeichhe pangngai aiin a harsa zawk mai thei. Nau an pai tak tak a nih chuan naute hrin nan cesarean section (C-section) neih a tha fo thin.
Nu leh pa angin eng nge i tih theih?
He zinkawngah hian in thawhhlawkzia a pawimawh hle.
- Medical team nen hna thawk ho rawh: I fa surgeon, urologist, leh pediatrician te nen inbiak reng rawh.
- Follow-ups atan kal ngei ngei tur a ni:Operation hnuah i fa chu an taksa system a thawk tha em tih enfiah nan clinic-ah a kal fo a ngai dawn a ni. An zinga pakhat mah lo hmu lo la.
- I fa tana thurawn pe rawh: I fa a lo seilian chhoh zel chuan zun emaw, ril emaw control chungchangah harsatna a awm a nih chuan zak suh la, doctor hnenah hrilh rawh.
- Zawhna zawt rawh: Zawhna emaw rinhlelhna emaw i neih chuan doctor hnenah zawt rawh. I dikna a ni.
Doctor hnena zawhna i zawh theih ṭhenkhat chu:
- Engtin nge he surgery hi tih a nih? Kum engzat nge a nih?
- Ka fa hian hrehawm a ti em?
- Ka fa chu operation hnua a dam leh hunah eng nge ka beisei ang?
- Naupang chu a lo puitlin chuan operation tam zawk a mamawh dawn em?
- Nakin lawkah chuan hnute, zunthlum, emaw, hnute kawng emaw-ah harsatna a awm dawn em?
- Ka fa hian nakin lawkah him takin fa a nei thei dawn em ni?
Hetiang thil zir avanga mangang, hlauhna leh lungkhamna lo awm hi tawngkam hmanga sawi theih a ni lo. Mahse, tunlai hian medical science hi a hmasawn hle tih hre reng ang che. Surgery hian he dinhmun hi hlawhtling takin a siam tha thei a, i fa chu naupang dangte ang bawka nun pangngai leh hlim taka awm theihna hun remchang a pe thei a ni.
Take-Home Thuchah a ni
- Cloacal Malformation hi piansualna a awm lo hle a, naute hmeichhiaah chauh a awm thin.
- Hei hi i sualna leh i kawppui sualna a ni lo. Ngaihtuah buai suh.
- Enkawlnaah hian operation hrang hrang a awm a, chu chuan naupang chhungah kawngkhar hrang hrang pathum a siam a ni.
- Enkawlna result hi a hlawhtling hle fo thin a, a bik takin a buaithlak lo zawkah chuan.
- Doctor-te nena inzawmna nei reng leh follow-up clinic-a kal hi naupang hmalam hun hriselna atan a pawimawh hle.
- Hetiang natna vei naupang tam tak hi nun pangngai, hrisel leh hlim takin an hmang thin.











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