I mit (cornea) ah hian harsatna a awm em? Corneal dystrophy chungchang hi i zir dawn teh ang!

I mit chu a hlim hmel em? Eng changin eng en harsa i ti em? A nih loh leh i mitah thil dik lo awm ang maiin i inhria reng em? Hengte hi mitmeng (cornea) nena inzawm natna (symptoms) a ni thei bawk. Vawiin hian chutiang dinhmun pakhat, "Corneal Dystrophy" chungchang kan sawi dawn a ni. Lungngai suh, he thu hi awlsam takin, i hriatthiam theih dan tur angin kan sawi dawn a ni.

Corneal Dystrophy hi eng nge ni?

A awlsam zawngin, corneal dystrophy hi i mit , i mit atanga a lan dan (transparent part) cornea , tichhe thei natna pawl pakhat sawina tlangpui a ni. Hemi hnuaiah hian natna chi hrang hrang 20 chuang a awm a. Heng dystrophy chi hrang hrangte hian mit (cornea) tissue te hi a tidanglam thei a, a tichhia thei bawk. Glass thianghlim takah chuan hmun te te emaw, streak emaw awm ang mai a ni a, chu chu i en chuan chiang takin i hmu thei lo. He chhiatna hi a nasat chuan i mit hmuhnaah inthlak danglamna i nei thei a, mit hmuhna pawh a hloh thei bawk.

A pawimawh ber chu heng corneal dystrophies te hi genetic condition a ni. Chu chu kan DNA inthlak danglamna avanga lo awm an ni tihna a ni . Inthlâk danglamna ṭhenkhat chu i nu leh pate hnên aṭanga i rochun theih a ni. Mi dangte chu beisei loh takin, a takin a thleng thei bawk. Natna chi thenkhat chu mithiamte’n an la hriat chian loh vang a ni.

Corneal dystrophy chi hrang hrang a awm em?

Ni e, mitmeng (cornea) layer hrang hrangte an nghawng dan azirin an thliar hrang a ni. A bik takin a hnuaia mi ang hian:

• Cornea pawn lam layer (epithelial leh subepithelial) tichhe thei te.
• Cornea pawn lam leh layer layer (Epithelial-stromal) tichhe thei te.
• Cornea (Stromal) layer lai tak (middle layer ) tichhe thei te.
• Cornea chhungril ber (endothelial) tichhe thei te.

Tunah chuan heng chi hrang hrangte hi chipchiar deuhin han thlir ila.

Epithelial leh subepithelial mit lam natna (corneal dystrophy) a awm thin

Hengte hi mit (cornea) chunglam layer-te nghawng thei natna a ni. Entirna thenkhat chu:

• Epithelial basement membrane-a natna hrik awm
• Epithelial recurrent erosion dystrophies (subtype pathum a awm bawk) .
• Gelatinous drop ang chi natna (dystrophy) a awm
• Lisch epithelial natna (epithelial dystrophy) a ni
• Meesmann natna (dystrophy) a ni
• Subepithelial mucinous dystrophy a awm a, a natna hi a hring vek a ni

Heng dystrophies tam zawk hi naupan laiah a lang thin . Mahse, epithelial basement membrane dystrophy hi puitlingah a lang tlangpui (a lang fo lo nain). A dang chu gelatinous drop ang chi corneal dystrophy a ni.Hei hi kum 20 hma kum eng pawhah a thleng thei.

Epithelial-stromal natna (epithelial-stromal dystrophy) a awm thin

Chungte chuan mit (cornea) pawn lam layer leh a hnuaia middle layer te chu a nghawng vek a ni.

• Granular corneal dystrophy (a chi 1 leh 2) a awm a.
• Lattice corneal dystrophy (hei pawh hian subtype leh chi hrang hrang a nei bawk) .
• Reis-Bückler-a natna (dystrophy) a ni
• Thiel-Behnke natna (dystrophy) a ni

Heng zawng zawng hi naupan laiah a awm tam zawk . Lattice corneal dystrophy type 1 hi kum 20 hnuah pawh a awm thei.

Stromal dystrophies te hi a awm a

Chungte chuan mit (cornea) lai tak, a thuk tak chu a nghawng ber a ni.

• Macular dystrophy natna a ni
• Schneider-a crystalline dystrophy natna a ni
• Pianpui atanga lo piang chhuak stromal dystrophy
• Fleck dystrophy natna a ni
• A hnunglam atanga amorphous dystrophy a awm
• Descemet hmaa natna (dystrophy) a awm
• François-a chu central cloudy dystrophy a ni

Stromal dystrophies hian naupang a vei tlangpui . Mahse, heng zinga pahnih hi i upat deuh deuh chuan a lo awm thei a ni. Schneider corneal dystrophy hi kum 30 hnuah a lo awm thei a, pre-Descemet corneal dystrophy hi kum 30 hnuah a lo awm tlangpui.

Endothelial mit lam natna (corneal dystrophies) a awm thin

Hengte hi mit (cornea) chhunga layer nalh tak takte nghawng thei natna an ni.

• Fuchs endothelial dystrophy natna a ni
• A hnunglam atanga polymorphous dystrophy a awm
• Pianpui atanga lo piang chhuak endothelial dystrophy
• X-a inzawm endothelial dystrophy a awm

Corneal dystrophy zawng zawng zingah Fuchs endothelial corneal dystrophy hi a tam ber , United States-a corneal transplant tih zawng zawng zinga 39% a ni.

Corneal dystrophy natna lan chhuah dan chu engte nge ni?

Corneal dystrophy symptoms hi i neih chi bik a zirin a inang lo. Mi thenkhat chuan symptom engmah an nei lo mai thei . Symptoms a lan tak tak chuan mit pahnih a nghawng tlangpui a, hun kal zelah a na zual zauh zauh thin.

I mit chu glass pianzia ṭha famkim, chiang tak, flawless ang mai a ni ang tih han ngaihtuah teh. Mahse corneal dystrophy hian chu chu a thlak danglam thei a ni. Heng dinhmun tam takah hian mit (cornea)-ah hian tissue thar a lo thang lian a, a nih loh leh a lo awm tur lohna hmunah a lo piang chhuak thin. Tichuan, glass chiang tak atanga thlir ai chuan glass hlui, flawed, blown atanga thlir ang mai a ni. Chu chu hmuh a harsa khawp mai, a ni lawm ni?

Chutiang bawkin tissue thar siam emaw, a pungkhawm emaw chuan mitmeng (cornea) a nghawng layer kaltlangin hmuh a harsa hle. Hei vang hian mitmeng (corneal dystrophy) nei zingah chuan mit hmuhna (blurred or foggy vision) hi a awm fo thin.

A lan chhuah dan tlangpui chu:

• Visual acuity loss: Hei hi mit (cornea) chunglam a lo inthlak emaw, a dam tha lo emaw a nih chuan a thleng thin. Chumi awmzia chu glasses emaw contact lens emaw i vuah pawhin i mit a fiah lo tihna a ni.
• Corneal haze: Hei hian i mit chu a thim angin a lang thei. Hei hi mitmeng (cornea) tihchhiat emaw, inthlak danglamna emaw avanga residual effect a ni fo thin.
• Foreign body sensation: Mit chhunga thil awm ang maiin a lang , mahse i en chuan engmah i hmu lo.
• Mit na emaw mit na emaw: Heng symptoms te hi rei tak inkhar hnua i harh hian a langsar zawk thei a, entirnan zing i thawh hian a langsar zawk thei.
• Light sensitivity (Photophobia): Chumi awmzia chu êng eng tak chu tuar theih loh a lo ni a, hrehawmna emaw, natna emaw a thlen thei tihna a ni.
• Mit tui (Epiphora): I mit a vawt nia i hriat chuan i mittui tlakna system hian a compensate turin mittui tam zawk siam a tum vang pawh a ni thei.
• Nystagmus: Mit chu a sir lehlamah emaw, a sir lehlamah emaw, a chet chak loh thunun loh .

Eng thilin nge mitmeng (corneal dystrophy) a thlen?

Heng corneal dystrophy chi hrang hrang hi genetic factors nen a inzawm vek a ni . Hengte hi "de novo" inthlak danglamna (i taksaah random taka thleng tihna) emaw, i nu leh pa pakhat emaw, pahnih emaw atanga rochun a ni thei bawk.

Inherited variation thenkhatah chuan nu leh pa pakhat atanga gene copy pakhat chauh a ngai a ni. Variation dangte chuan mutated gene copy pahnih, nu leh pa pakhat atanga pakhat lak a ngai a ni. Tin, corneal dystrophy chi hrang hrang a la awm a, eng genetic variation bik nge a thlen tih chiang taka hriat tumin zirchianna neih belh a ngai bawk.

Hetiang dinhmun hi tute nge hlauhawm ber?

Corneal dystrophies tam zawk hian hnam leh sex a zirin mi a nghawng dan a inang lo. A danglamna awm chhun chu Fuchs endothelial corneal dystrophy a ni.A risk factor bik engemaw zat a awm a:

• Hnam: Mihring varte hian an nei tam zawk.
• Kum: Kum 30 chunglam te hian an vei tam zawk.
• Gender: Hmeichhiain an nei tam zawk.

Corneal dystrophy avanga harsatna awm thei te chu engte nge ni?

Heng dinhmunte hi corneal dystrophy umbrella hnuaia awmte hian i mitmeng kal tlanga êng kal dan a nghawng a ni. Chumi avang chuan i mitmeng (cornea) chiang tak chu a tlahniam a, a chhunga êng kal tlang chu a tichhe ta a ni. Hei hian a awmzia chu corneal dystrophy hian mitdelna nasa tak a thlen thei a , mahse total blindness a thlen lo tihna a ni .

Mahse, mitdelna nasa tak chu harsatna lian tak a ni thei. I lirthei khalh theihna, lehkha chhiar leh nitin hna tam tak thawh theihna a nghawng thei a ni.

Engtin nge corneal dystrophy hi hriat theih?

Mit lam thiam, mit lam doctor emaw, mit lam doctor emaw chuan mit lam natna (corneal dystrophy) a nei tih a hmuchhuak thei a ni. Chutiang ti tur chuan hmanraw leh hmanraw hrang hrang an hmang a ni. A pawimawh ber chu mit enfiah a ni a , a bik takin slit lamp exam hi a ni . Slit lamp exam-ah hian i mit chhung lam chu microscope bik hmanga en a ni. Hei hian doctor-te chu corneal dystrophy nena inzawm thil danglam emaw, chhiatna emaw awm thei chu a hmu thei a ni.

I mit specialist-in a hman theih test dangte chu:

• Corneal topography: Hei hian i mit (cornea) chunglam "map" a siam a. Corneal surface-ah hian a chhehvel hmun aiin a sang emaw a hniam emaw a awm leh awm loh a entir a ni.
• Pachymetry: Hei hian i mit (cornea) thickness a teh thin. Hei hian mit (cornea) layer thuk zawka harsatna awm (endothelial dystrophy ang chi) hriatchhuahna kawngah a pui thei a ni.
• Genetic testing: Hei hi a tlangpuiin i hmui emaw thisen emaw sample lak a, DNA inthlak danglamna chiang tak zawn a ni. Hei hian corneal dystrophy chi bik i neih chu a nemnghet thei a ni.
• Optical Coherence Tomography (OCT): Hei hi i mit (retina) en nan hman thin ni mahse, he test hian i mit (cornea) scan hlu tak tak a pe thei bawk. Hei hi mit lam enkawlna thenkhat ruahman hunah a tangkai hle.
• Corneal biopsy: Mit specialist chuan i mit atanga tissue sample te tak te a la thei a, lab-ah test turin a thawn thei bawk. Pathologist chuan sample chu a zirchiang ang a, corneal dystrophy i nei em tih leh, a neih chuan eng chi nge i neih tih a hre ang. He test hi corneal dystrophy tan chuan a awm vak lo a, mahse a natna hriatchhuahna kawngah a pui thei hle.

I natna lan chhuah dan leh thil dang a zirin test dang pawh tih theih a ni. I mit specialist chuan test dang an rawt theih dan tur a hrilh belh thei che a ni.

Corneal dystrophy hi engtin nge enkawl a nih?

Corneal dystrophy enkawl dan hrang hrang a awm a. Enkawlna chu mit (cornea) layer a nghawng dan leh a natna nasat danah a innghat a ni.

Enkawl dan a inang lo thei a, chuvangin i mit doctor hi i enkawl dan tur hriat theihna tha ber a ni. Enkawl dan tur chipchiar takin, harsatna awm thei te, side effects te, leh thil dangte chipchiar takin an hrilhfiah thei che a ni.

Enkawl dan tlangpui thenkhat chu hetiang hi a ni:

Topical treatment te pawh a awm bawk

Hengte hian i mit (cornea) chunglam a natna lan chhuah dan leh a nghawng dan enkawlna lam an ngaihtuah ber a ni. Entirnan:

• Damdawi hmanga mittui tlak emaw hriak emaw: Hengte hian natna lan chhuah dan te, mit natna, mit chhunga thil awm hriatna, leh vawt te a tidam thei a ni.
• Antibiotics: Hengte hian i mit (cornea) a chhiat a, natna hrik a kai awlsam chuan natna kai loh nan a pui thei a ni.
• Contact lens bik: Contact lens pangngai ang bawkin hengte hi mit (cornea) chung lamah an bun thin. A danglamna ber chu i mit (cornea) a dam theih nan an pui a, chhiatna dang a veng bawk.

Thlalak hmanga enkawlna hmanga keratectomy (PTK) tih a ni.

Phototherapeutic keratectomy (PTK) hi laser beam tha tak tak hmanga mitmeng thenkhat lakchhuah a ni. I mit specialist chuan a chhiatna hmunte chu chiang takin a target thei a, a paih chhuak thei bawk.

Cornea transplant a ni

I mit (cornea) inthlak danglamna emaw, chhiatna emaw a nasat lutuk chuan mit hmuhna (cornea transplant) hi duhthlan tur a ni thei. Heng surgery-ah hian i mit (corneal tissue) chu donor thi tawh atanga tissue thar hmanga thlak a ni. Chungte chu full emaw partial transplant emaw pawh a ni thei.

Corneal dystrophy i neih chuan eng nge i beisei theih ang?

Corneal dystrophy i neih chuan i beisei theih chu a danglam deuh thei. Mi tam zawk chu heng zinga pakhat hi an vei tih hmuhchhuah a ni a, a tlangpuiin kum 20 an tlin hmain an vei tih hmuhchhuah a ni.

Corneal dystrophy hi a tlangpuiin a zual zel a ni. Hei hian a nghawng chu hun kal zelah a pung zauh zauh tihna a ni - a tlangpuiin kum tam tak chhung, a chang chuan kum sawm tam tak chhung pawhin a pung chho zel tihna a ni. Mi thenkhat chuan a tir lamah chuan symptom an nei lo va, chuvangin kum tam tak chhung chu heng natna zinga pakhat hi an nei tih pawh an hre lo mai thei. Mi thenkhat chuan symptom leh harsatna an nei ngai lo.

Thil chi hrang hrang i tawn theih a tam em avangin, i mit doctor hnenah i beisei tur zawt la, i mit doctor zawt la, i beisei tur chu i zawt thei ang. I tâna inzawm tlat thei chu an hrilh thei che a ni.

Corneal dystrophy hi eng chen nge a awm?

Corneal dystrophies hi dam chhung zawnga natna a ni. Anmahni nen hian i piang a ni. Corneal transplant hian heng natna te hi a "tidam" thei a, mahse chu chu guarantee a ni lo. Mi tam takin mit (corneal transplant) an neih chuan a tawpah chuan mit (cornea) thlak (transplanted cornea)-ah hian natna hi an vei ang. Chutiang a nih chuan enkawlna dang – mitmeng thlak vawi hnihna pawh ni se – a ngai mai thei.

Hetiang dinhmun hi eng nge a thlir ang?

Corneal dystrophy hian eng emaw chen chu mitdelna a thlen fo thin , mahse chu mitdelna chu mitdelna tluantling (eng pawh i hriat theih lohna dinhmun) thlenga a kal hi a tlem hle.

Cornea transplant i neih chuan transplant dawngtu dangte ang bawkin risk i tawk ang. I immune system-in transplanted tissue a beih loh nan i dam chhung zawng immunosuppressant damdawi i ei a ngai dawn a ni. Tin, immunosuppressant treatment hmang pawhin rejection a awm thei bawk.

I outlook tichhe thei variable tam tak a awm avangin i condition atana outlook zawt tur tha ber chu i mit doctor hi a ni. I dinhmun bik chungchangah thu chiang tak an pe thei a ni.

Corneal dystrophy hi a veng thei ang em?

Corneal dystrophies hi genetic condition a ni a, chu chu ven dan tur emaw, vei theihna tihziaawmna tur emaw a awm lo tihna a ni.

Corneal dystrophy ka neih chuan engtin nge ka in enkawl ang?

Corneal dystrophy i neih chuan mit doctor pan fo tur a ni a, a rawt angin. I dinhmun an enfiah thei a, i mit tissue inthlak danglamna an zawng thei a, i symptoms i neih apiang an zawng thei bawk. I treatment plan chu a rei thei ang bera a hlawhtlin theih nan an siamrem thei a, an update thei bawk.

I mit specialist chuan i mit damdawi a pe a nih chuan a pek ang chiah khan i hmang tur a ni . Damdawi hian heng natna lan chhuah dan tihtlem emaw, tissue inthlak danglamna emaw, chhiatna emaw a tikhawtlai thei a ni.

A bik takin corneal transplant chi hrang hrang i neih tawh chuan i damdawi ei tur chu a tih ang chiah chiah i ei a pawimawh hle. Chutianga i tih chuan i taksain tissue transplanted chu a hnawl loh nan a pui ang. Hei hian harsatna lian tham tak tak leh mitdelna awm reng tur pawh a veng thei a ni.

Engtikah nge ka mit lam doctor ka hmuh ang?

Hun ruat sa angin follow-up visit i nei fo ang.Hei atan hian i mit specialist i hmu tur a ni. Tin, i mit hmuhnaah symptom emaw, inthlak danglamna emaw i hmuh chuan emaw, enkawlna pakhatin side effect a neih emaw, a hlawk lo zawka a lan emaw chuan, chu chu i sawipui tur a ni. I harsatna tawhte chinfel dan tur zawng turin an puih che an tum ang.

Ka mit lam doctor hnenah eng zawhna nge ka zawh ang?

I mit lam doctor hnenah heng zawhnate hi i zawt thei ang:

• Eng chi corneal dystrophy nge ka neih?
• Eng treatment(s) nge i rawt?
• Emergency medical attention mamawhna symptoms a awm em?
• Ka dinhmun hi hun rei tak chhunga ka thlir dan tur chu eng nge ni?
• Ka thlirna tihchangtlun nan ka tih theih tur a awm em?

A tawp berah chuan eng nge hriat reng tur

Corneal dystrophies hi mit natna a ni a , i naupan lai atanga a lang fo thin . Heng natnate hriatthiam tum hian i rilru a buai a nih chuan nangmah chauh i ni lo. Corneal dystrophies hi chi hrang hrang sawmhnih chuang a awm a. Heng natnate hian nghawng a neih dan pawh a inang lo thei hle.

Mahse, nangmah chauhin corneal dystrophy hi hriatthiam emaw, enkawl emaw tum a ngai lo. I mit doctor chuan i dinhmun chiang tak, a nghawng dan leh enkawl dan tur a hriatthiam theih nan a pui thei che a ni. Tin, enkawlna kawng tam tak a awm avangin i dinhmun enkawl dan tur leh i nunah nghawng a neih tlem theihna tur chance tha zawk i nei bawk. Hlau suh, chak takin awm la, i doctor thurawn zawm rawh.

` Corneal Dystrophy, mit mit (cornea), mit natna (genetic eye diseases), mit hmuh lohna, mit enkawlna, mit (corneal transplant), mit hriselna