Mi pakhatin natna eng emaw avanga ei tur emaw, a ei theih lohna emaw dinhmun han ngaihtuah teh. Hetiang hunah hian engtin nge taksa mamawh chaw i pek? Taksa chu a chak lo thei lo. Vawiin hian hetiang thila enkawlna bik hman dan leh a tana damdawi pawimawh tak kan sawi dawn a ni.
He Cysteine hi eng nge ni?
A awlsam zawngin sawi ila, cysteine hi kan taksaa protein siamna atana pawimawh tak amino acid a ni. In sak nan brick a mamawh ang bawkin kan taksa chhunga cell leh tissue te siam leh enkawl turin protein a mamawh a ni. Heng amino acid te hi chutiang protein siamtu bulpui ber an ni.
He cystine injection hi Parenteral Nutrition tih enkawlnaah an hmang tlangpui a . Hei hi a tawi zawngin (PN) tih a ni. Hei hi damdawi lam thumal tlemte ni mah se, a awmzia chu a awlsam hle. Taksa chu vein kaltlangin direct-a ei tur mamawh pek a ni tihna a ni a, digestive system hmang lovin. Hetiang hian nutritional solution peknaah hian cysteine hi thil pawimawh tak angin dah a ni. Sri Lanka-ah chuan he damdawi hi `(ELCYS)` tih brand name hnuaiah hmuh theih a ni.
He damdawi hi i pek hmaa i doctor hnena i hrilh tur thilte
Hei hi specialized treatment a nih avangin i doctor hian i health history kimchang a hriat a pawimawh hle. A hnuaia thil awmte hi i neih chuan enkawlna i tan hmain doctor hnenah hrilh hmasa phawt ang che.
- Lung natna i neih chuan .
- Kidney nena inzawm natna i neih chuan .
- Liver natna i neih chuan .
- Nau piang laia awm leh taksain ei tur a tihchhiat dan tichhe thei genetic condition i neih chuan (`inborn error of metabolism`) .
- Tun hmaa cysteine, amino acid dang, damdawi dang, ei tur, dye emaw, preservatives emaw avanga allergy emaw, thil danglam tak emaw i neih chuan.
- Naupai emaw naupai tum emaw i nih chuan .
- Nu hnute pe lai i nih chuan .
Heng thu hriatte a\ang hian medical team chuan he enkawlna hi i tan a tha em tih leh engtin nge pek tur tih an rel ang.
Engtin nge he damdawi hi taksaah pek a nih?
He damdawi hi amah chauha pek a ni lo. Taksa ei tur pawimawh tak tak tam tak, sugar, vitamin leh minerals te awmna special nutritional solution-a tel anga siam a ni. Chumi hnuah chuan solution chu zawi zawiin taksaah vein hmangin an infuse a, chu chu saline ang chiah a ni.
He enkawlna hi damdawi in emaw clinic emaw ah doctor enkawlna hnuaiah pek thin a ni . Mahse, a \henah chuan damlo dinhmun a zirin doctor-te chuan he enkawlna hi in lama pek nise an ti mai thei.
He damdawi hi in lama i hman a ngai a nih chuan a buatsaih dan leh pek dan tur zirtirna mumal tak pek i ni ang. Chu thupekte chu dik taka zawm a pawimawh hle.
He damdawi hi in lama hman hunah hriat reng tur pawimawh tak dang a awm a, chu chu needle leh syringe hman tawhte dik taka paih hi a ni.
- Hengte hi bawlhhlawh bawlhhlawh pangngaiah dah ngai suh.
- Chungte chu paihna tur atana himna bawm bik (sharps container) -ah dah tur a ni.
- I neih loh chuan i doctor hnenah engtin nge i neih theih tih zawt la.
He damdawi hi naupang hnena pek dawnin fimkhur bik tur a ni a, chuvangin he damdawi hi naupang i pek dawn a nih chuan i doctor nen inbia ang che.
Damdawi dose tihpun a nih chuan eng nge tih tur?
Hei hi doctor enkawlna hnuaia pek a nih avangin overdose theihna a tlem hle. Mahse, he damdawi hi i ei tam lutuk nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah zawh nghal rawh . A nih loh leh damdawi in hnai ber Emergency Department (ETU)-ah kal rawh. Hetiang thil hi ngaihthah ngai suh.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a ni. Mahse, mi zawng zawngin an hmu vek lo. Chu side effects chu eng nge ni tih i en ang u. Hei hi a hnuaia table atang hian awlsam takin i hrethiam thei ang.
| Side effect awm dan (nature) a ni | Symptoms i neih theih te |
|---|---|
| Side effects awm thei chu i doctor emaw nursing staff emaw hnenah hriattir nghal tur a ni | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui, lei emaw kawr emaw a hring, thawk harsa. |
| Thisen chhuak | Ke na, a hring emaw, a lum emaw, thawk harsa, rilru na. |
| Gallbladder lama harsatna a awm | Pum natna nasa tak, luak chhuak, luak chhuak, khawsik. |
| Liver hliam a awm | Pum dinglam chunglam natna, chaw ei chak lohna, luak chhuak, bawlhhlawh rawng hring, zun dum emaw, sen emaw, mit emaw vun emaw sen (jaundice), leh chau danglam deuha inhriatna. |
| Thisenah acid level sang tak a awm | Thâwk harsa, chak lohna danglam tak, lu na, thinlung thawk chak emaw, mumal lo emaw, luak chhuak, luak chhuak. |
| Thisenah ammonia level sang tak a awm | Chak lohna danglam tak, buaina, ei duh lohna, luak chhuak, luak chhuak, seizures. |
| Thil pawi lo tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur a ni | |
| Flushing a ni | Vun chu a sen a, a lum tih a hriat. |
| Injection na hmuna harsatna awm | Injection pekna vein-ah natna, sen, emaw, a hring emaw. |
He list-ah hian side effect awm thei zawng zawng a tel lo. Thil danglam tak i hriat chuan doctor hnenah hrilh nghal rawh.
Engtin nge damdawi i dahkhawm leh i paih thin?
I medical team chuan he damdawi hi dah dan tur an pe ang che. Chu thupekte chu dik takin zawm rawh. Naupang tê leh ran vulhte hmuh theih lohna hmunah dah rawh . Damdawi expired hmang ngai suh.
I doctor emaw, i enkawlna hmuna damdawi in emaw hnenah damdawi hun kal tawh emaw, duh loh emaw paih dan tur dik tak zawt rawh.
Take-Home Thuchah a ni
- Cysteine hi amino acid pawimawh tak a ni a, chaw ei theih loh hunah vein kaltlangin special nutritional solution peknaah dah a ni.
- He enkawlna hi i tan hmain i damdawi lam dinhmun leh allergy zawng zawng doctor hnenah i hrilh hmasak phawt a pawimawh hle.
- Thâwk harsa, rilru na, pum na nasa tak, mit emaw vun sen emaw ang chi side effect na tak i neih chuan doctor pan nghal rawh.
- In lama enkawl i nih chuan needle leh syringe hman tawhte chu him takin paih mai tur a ni. Bawlhhlawhah paih ngai suh.
- Hei hi damdawi lam enkawlna bik a nih avangin doctor thurawn zawm fo ang che.











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