Thutthleng a\anga tho chu harsa i ti thut mai a, a nih loh leh i sam hrual tura i kut i han phar chuan i kut chu a bengchheng ang maiin i hria ang tih han ngaihtuah teh. Chutih rual chuan i mit vel te, i kawr leh i rilruah te, purple rawng te te a lo lang bawk. Hetiang hi i chungah a thleng tawh em? Hei hi hahna pangngai mai mai niin i ngai mai thei. Mahse a châng chuan natna khirh zawk, hmuh tur awm lo Dermatomyositis tih chhinchhiahna a ni thei bawk. Ngaihtuah buai suh, thumal awlsam takin engkim kan sawi dawn a ni.
Dermatomyositis hi eng nge ni?
A awlsam zawngin sawi ila, Dermatomyositis hi natna awm lo tak a ni a, kan taksa ruhte a tichak lo va, vun a ti na bawk. Natna pawl (myopathy) zinga mi a ni a, taksa ruh tichhe thei a ni. He natna hian a chang chuan natna khirh tak tak a thlen thei a, chu chu thawk harsa leh ei harsa a ni.
Heng symptoms te hi mi thenkhat tan chuan thla tam tak chhungin zawi zawiin a lo awm thei a ni. Mahse mi dangte tan chuan an rawn lang nghal mai thei. Chuvangin heng symptoms te hi i neih chuan doctor pan vat a pawimawh. Enkawlna kan tan hma poh leh harsatna lian tham kan pumpelh theihna chance a sang zawk.
A tlem hle a, a bik takin a lan chhuah tirh atanga kum khatna chhungin natna hian thihna a thlen thei a ni. Cancer chi hrang hrang vei theihna a tipung bawk.
Dermatomyositis leh Lupus hi eng nge an danglamna?
Natna pakhat lupus tih hi i hre tawh mai thei. Dermatomyositis hi lupus leh autoimmune natna dangte nen a inang a ni. Mahse, an pahnih inkarah hian danglamna chiang tak tak a awm. Dermatomyositis thlen chhan dik tak hriat a la nih loh avangin autoimmune disease-ah dah a ni lo.
A danglamna chiang zawka hriat theih nan he table hi han en ila.
| Mihring ziarang | Lupus a ni | Dermatomyositis natna a ni |
|---|---|---|
| A lan chhuah dan ber | Joint na, vun sensitivity leh rashes, chhungril lam (thluak, lung, kal) a nghawng dan. Symptoms a lo thleng a, a kal zel bawk. | Muscle chak lohna leh vun natna bik (specific skin rashes) a awm. Muscle tihchhiat a ni. |
| Diagnosis tih a ni | Thisen test leh symptoms bik atanga chhut a ni. | Thisen test te, vun leh thau biopsies te, leh scan te. |
Heng natna pahnih hi a rang thei ang bera hriatchhuah leh enkawl a pawimawh hle. Symptom thar i neih chuan doctor pan nghal tur a ni.
He natna hi tuin nge vei tam ber?
Tu pawhin dermatomyositis an vei thei a, mahse group thenkhatah chuan an hlauhawm zawk.
- Naupang kum 5 leh 15 inkar tan.
- Kum 40 leh 60 inkar puitling tan.
- He natna hi mipa aiin hmeichhiain an hmu tam zawk.
Mahse, hei hi natna hmuh tur awm lo tak a ni tih hre reng ang che . A vaiin kum tin mi sang za zinga pakhat vel chauhvin he natna hi an vei thin.
He natna hian engtin nge taksa a nghawng a, cancer vei theihna a nghawng?
Dermatomyositis hi i dam chhung zawngin a nghawng thei che a ni. I taksa ruhte a chhiat nasat chuan i taksa peng thenkhat i hmang tha thei lo mai thei a, chu chuan chak lohna chi khat a thlen thei a ni. Hei hi kum tam tak chhung a thleng tlangpui a, mahse mi thenkhat tan chuan he taksa chak lohna hi a thleng rang zawk thin.
Chu bakah , a hlauhawm ber chu cancer hlauhawmna a ni.
Zirna hrang hrangah chuan dermatomyositis vei zinga 15% vel chuan an dam rei hnuah cancer chi khat emaw an vei theihna a awm tih a tarlang.
He natna nena cancer chi hrang hrang hmuh tam ber chu:
- Ovarian cancer a ni
- Lung cancer a ni
- Lymphoma natna (Lymphoma) a ni
- Hnute cancer a ni
- Colon cancer a ni
Chuvangin, he natna hi i vei tih hriatchhuah a nih chuan, i doctor nen zalen taka sawipui a pawimawh hle a, i cancer hlauhawmna leh a screening tih tur te pawh i sawipui a pawimawh hle.
Dermatomyositis natna lan chhuah dan chu engte nge ni?
He natna lanchhuahna lian ber pahnih chu taksa ruh chak lohna leh vun vun rawng a ni.Mi thenkhat tan chuan symptom pahnih hi a rualin a lang chhuak thin. Mi dangte tân chuan chhinchhiahna pakhat chu a hnu kar tam tak, thla tam tak, a nih loh leh kum tam tak hnuah pawh a lang chhuak a ni.
Heng features te hi chipchiar deuhin han thlir ila.
| Mihring ziarang chi khat | Sawifiahna leh entirnan |
|---|---|
| Muscle chak lohna | He chak lohna hian nitin hna thawh a ti harsa thei hle. Entir nan:
|
| Vun a hring chhuak | Heng hliam te hi a bik takin ni chhuahna hmunah a lang thin. An rawng chu purplish-pink a ni a, a hring deuh pawh a ni thei. A tamna hmunte chu:
|
| Thil dang pawh a awm |
|
Naupang thenkhat chuan he natna hi an nei a, an lo puitlin chuan a natna lan chhuah dan chu a bo vek thin. Mahse, damlo 80% ah chuan dam chhung (chronic) condition a ni. Chumi awmzia chu a hun hunah symptoms a lo lang leh thin tihna a ni.
Eng thilin nge hei hi a thlen?
Dik tak chuan mithiamte chuan dermatomyositis thlen chhan dik tak hi an la hre lo a, mahse thil engemaw zat a awm nia ngaih a ni.
- Genetic factors: Zirna thenkhatah chuan hei hi genetic condition a ni thei a, thlah khat atanga thlah dangah a kal zel a ni.
- Autoimmune issues: Kan sawi tawh ang khan hei hi autoimmune natna nen a inang hle. Chumi awmzia chu kan taksa venghimtu immune system hian kan taksa ruh leh vun cell hrisel tak takte hi a rawn bei sual thei tihna a ni.
- Viral infection: Evidence thenkhat chuan virus infection chu a reh tawh chuan Dermatomyositis a thlen thei tih a sawi.
- Environment factors: Zirchianna thenkhatah chuan boruak quality tha lo hmuna chengte pawhin he natna hi a lo awm theih nan a pui thei tih hmuhchhuah a ni.
Engtin nge natna hi kan hriat theih ang?
I doctor-in i natna lan chhuah dan a ngaihthlak hnuah, i natna hriat chian nan test eng emaw zat a ti ang.
| Test dan tur | Chutah chuan eng nge i hmuh? |
|---|---|
| Thisen test a ni | Anni hian taksa ruh a chhiat huna thisenah enzyme awm khawm tam zawk an zawng a, chubakah immune system hnathawh dan tilangtu autoantibodies an zawng bawk. |
| Biopsy tih a ni | Vun natna atanga tissue te tak te tak te leh taksa ruh atanga lak chhuah niin microscope hmangin an enfiah thin. Hei hian taksa peng chhungah inflammation a awm leh awm loh a nemnghet thei a ni. |
| Imaging test te pawh a awm | MRI (Magnetic Resonance Imaging) scan emaw chest X-ray emaw hmangin taksa ruh, nerve, lung leh taksa peng dangte dinhmun enfiah theih a ni. |
| EMG test a ni | Electromyography (EMG) hi taksa ruh leh nerve te electrical activity tehna a ni. Hei hian taksa chak lohna hi natna ngei vang nge, thil dang avanga lo awm tih hriat theih nan a pui thei a ni. |
Dermatomyositis hi eng enkawlna nge ni?
Dermatomyositis hi tihdam theih ni lo mah se, a natna lan chhuah dan control thei, taksa ruh tihchhiatna tihziaawm thei leh nun pangngaia nunpui thei tur enkawlna tha tak tak a awm nual. I doctor chuan i natna lan chhuah dan leh a nasat dan a zirin enkawlna tha ber a thlang ang.
- Corticosteroids: Heng damdawi te hian taksa peng hrang hranga inflammation a tihziaawm.
- Physical therapy: Muscle a chhiat chuan exercise leh physical therapy hi tihchak leh nan a pawimawh hle. Muscle te hi a chak poh leh natna avanga chhiatna lakah an do thei zawk thin.
- Immunosuppressant damdawi: Heng damdawi te hian immune system-in cell hrisel a beih loh nan a titawp a ni.
- Intravenous immunoglobulin (IVIg): Hei hi kan thisen atanga lo piang pakhat immunoglobulin chu taksa pawn lam atanga saline ang maia pekna a ni. Hei hian immune system a thawk tha lo chu a control thei a ni.
- Speech therapy: Thlarau ruhte chu a chak lo va, ei harsa a nih chuan speech therapy hian chu ruhte chu a tichak thei a ni.
Engtin nge symptoms te hi kan enkawl ang?
He natna nena nun hi hun rei tak chhunga zinkawng a nih avangin symptoms enkawl hi a pawimawh hle.
- Exercise hi skip suh: I doctor emaw, physical therapist emaw-in exercise a pek che chu an hrilh che ang chiah khan ti rawh. Hei hian i taksa ruhte a tichak thei ang.
- Damdawi hman dik: I doctor-in a pek hun chhung dik takin ei thin ang che.
- Ni laka inveng rawh: Hei hi a pawimawh hle. Ni chhuahnaah ultraviolet (UV) rays hian vun a tichhe thei a ni. Chuvangin, ni chhuahna hmuna i hun hman dan khap tlat ang che. I chhuak a nih chuan, .Sunscreen tha tak, SPF 50+ tal hmang rawh. Darkar hnih danah hnawih leh thin ang che.
- Doctor hmu fo rawh: I natna lan chhuah dan enfiah nan leh i dinhmun a danglam em tih enfiah turin doctor i hmu fo tur a ni.
He natna chungchanga hriat tur tam zawk
Dermatomyositis i vei tih hriat a nih chuan hlauhna i neih hi thil pangngai a ni. Nun chhung zawnga natna, thihna thlen thei natna a nih thu hriat chu thil mak tak a ni thei. Mahse, i natna hmuhchhuah hma leh enkawl i tan poh leh i dam theihna chance a sang zawk tih hre reng ang che.
He natna hi damdawi awm lo mah se, mi 80% chu natna lanchhuahna neiin natna khirh tak neiin an la awm reng a ni. Mahse, enkawl a nih chuan mi 20% vel chuan symptom awm lovin hun rei tak chhung remission an hmu thei a ni.
Thihna hlauhawmna hi 5% vel a ni. Mahse, thil ṭhenkhat chuan he hlauhawmna hi a tipung thei a ni:
- Enkawl tan tirh atanga thla 6 aia rei tihkhawtlai.
- Kum 60 chunglam a nih avangin.
- Symptom na tak tak nei.
- Natna, ril, lung emaw, thinlung emaw a nghawng thei.
- Cancer vei emaw, cancer thar nei emaw.
Engtikah nge Doctor ka hmuh ang?
Muscle chak lohna thar i neih chuan, a bik takin vun rawng a awm chuan doctor pan nghal vat rawh. Kan sawi tawh ang khan enkawlna i hmuh hma chuan harsatna lian tham i pumpelh thuai thei ang.
Doctor i hmuh hunah heng zawhnate hi zawh theihnghilh suh:
- Dermatomyositis emaw natna dang emaw ka nei em?
- Eng test nge ka tih ngai?
- Eng enkawlna nge ka mamawh a, eng chen nge ka mamawh ang?
- Cancer screening neih a ngai em?
I enkawl dan tur chu i doctor nen ruahmanna siam rawh. Hei hian a hnua i beisei tur leh i symptoms a zual zel a nih chuan eng nge i tih tur tih hriatthiamna tha zawk a pe ang che.
Take-Home Thuchah a ni
- Dermatomyositis hi natna hlauhawm tak a ni a, taksa ruh chak lohna leh vun natna bik a thlen thin.
- Symptom i hmuh chuan a rang thei ang bera doctor pan a pawimawh hle. Enkawl vat chuan harsatna lian tham a veng thei a ni.
- Hei hi damchhung natna a nih tlangpui avangin hun rei tak enkawl a ngai a ni.
- Doctor-in a tih angin damdawi ei a pawimawh a, physical therapy exercise tih a pawimawh a, a bik takin ni laka inven a pawimawh hle.
- He natna hian cancer vei theihna a tipung thei a, chuvangin doctor nen hemi chungchang leh test tul eng pawh sawipui rawh.











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