Tui engzat pawh in la, tuihal ang maiin i inhria tih han ngaihtuah teh. Chutih rual chuan bathroom-a kal fo a ngai bawk. Zanah i mut tha thei lova, vawi eng emaw zat i tho a ngai bawk. Hei hi thil buaithlak deuh a ni lo maw? Mi tam takin hei hi thil pangngaiah ngai mah se, a chang chuan kan taksa chhunga harsatna dang eng emaw chhinchhiahna a ni thei. Vawiin hian hetiang natna hlauhawm tak, mahse enkawl theih tur chungchang kan sawi dawn a ni. Chu chu Arginine Vasopressin Disorders, a nih loh leh mi tam takin a hming hlui atanga an hriat angin Diabetes Insipidus a ni.
A awlsam zawngin, Arginine Vasopressin Disorders hi eng nge ni?
A hming hi a buaithlak deuh viau nachungin eng thil nge thleng tih hriatthiam a awl hle. A awlsam zawngin sawi ila, hei hi kan taksain tui mamawh zat a vawn theih lohna dinhmun a ni. Chuvang chuan tui mamawh zat pawh zun ah a chhuak thin.
A chhan ber chu kan taksaa hormone awm vang a ni. A hming chu Arginine Vasopressin (AVP) tih a ni. Doctor thenkhat chuan Antidiuretic Hormone (ADH) an ti bawk. He AVP hormone hi kan kal (kidney) te hnena thupek pe thin manager ang mai a ni. Kidney-te hnena, "Okay, tunah hian taksa hian tui a mamawh a, chuvangin tui tlem tal khawl khawm la, zun anga chhuak tui hi tihtlem rawh," titu kha a ni.
He natnaah hian he kalphung hi kawng lian pahnihin a tibuai thei a ni:
1. AVP Deficiency (AVP-D): Hei hi kan thluak hian AVP hormone mamawh zat a siam chhuah loh vang a ni. Chumi awmzia chu kal (kidney) zirtirtu tur an awm lo tihna a ni.
2. AVP Resistance (AVP-R): Hemiah hian thluak hian AVP hormone siam chhuah tling mahse, kal (kidney) hian thurawn hi a pawm lo. Manager chuan thurawn a pe a, mahse hnathawkte chuan an ngaihsak lo ang bawkin.
Engti kawng pawhin, a tawpah chuan a rah chhuah chu a inang vek a ni: kal (kidney) hian tui chu a mamawh angin a filter a, zun angin a paih chhuak thin. Chumi avang chuan taksain tui a mamawh chu a hloh ta a ni.
| Damdawi lam dinhmun chi hrang hrang | A awlsam zawngin, eng thil nge thleng? |
|---|---|
| AVP tlakchhamna (AVP-D) 1.1. | Thluak atanga kal (kidney) thlenga thuchah thawntu AVP hormone hi a tam tawk lo a ni. |
| AVP laka invenna (AVP-R) . | Thluak hian AVP hormone siam mahse, chu thuchah chu kal (kidney) hian a hrethiam (receive) tha thei lo. |
Hetiang natna lan chhuah dan hi engte nge ni?
Hetiang natna lan chhuah dan ber leh langsar berte chu:
- Tuihal lutuk (polydipsia): Tui i in tam lutuk pawhin tuihal lo ang maia inhriatna.
- Zun tam: Zun tur chuan vawi tam tak thawh a ngai a, nileng chauh ni lo, zan lamah pawh (nocturia).
- Zun tam lutuk: Zun chhuah zat hi a tam hle. Zun hi rawng nei lo leh tui tak a ni.
A tlangpuiin mi pakhatin ni khatah zun litre 1 leh 3 inkar a paih chhuak thin. Mahse he natna vei hian ni khatah zun litre 20 thleng a paih chhuak thei! Chu chu eng ang nge a nih tih han ngaihtuah teh!
Heng symptoms te hi i taksa chhungah thil pakhatin hna a thawk tha lo tih hriattirna chak tak a ni. Chuvangin heng symptoms te hi i neih chuan a rang thei ang bera Doctor pan a pawimawh hle.
Engtin nge heng symptoms te hi naupang tê têteah a lan?
Naupang tête chuan "Ka tuihal" tih dik takin an sawi thei lo mai thei. Chuvangin he natna hi an neih chuan a symptoms chu a danglam deuhin a lang thei.
- Tui tlakchhamna nasa tak
- Ek khal
- Luak chhuak
- Khawsik fo thin
- Hahdam lo leh tap reng reng
- Hlawhtling lo (thau tihpun loh) .
Engvangin nge hetiang dinhmun hi a lo awm?
Hei hi a chhan awm thei engemaw zat a awm a, chu chu a natna chi hrang hrang a zirin a ni.
Arginine Vasopressin tlakchhamna (AVP-D) awm chhan te .
Hei hi a tam ber chi a ni. AVP hormone (the hypothalamus or pituitary gland) siamtu thluak peng hrang hrang tihchhiat vang a ni.
- Lu hliam emaw, zai emaw: Heng hmunte hi zai emaw, thluaka accident emaw avanga tihchhiat theih a ni.
- Tumors: Thluak chhunga tumor thenkhat lo awm vang a ni.
- Inflammation: Natna hrang hrang sarcoidosis emaw tuberculosis emaw avanga inflammatory condition awm thin.
- Genetic causes: Genetic inthlak danglamna, rochun atanga lo chhuak.
- Idiopathic: A then phei chuan a chanve vel chu a chhan chiang tak hmuh tur a awm lo .
Arginine Vasopressin Resistance (AVP-R) awm chhan hrang hrang 1.1.
Thluak hian hormone a siam chhuah hi harsatna a awm lo, buaina chu kal (kidney)-ah a awm a ni.
- Genetic causes: Genetic problem, thlah kal zelah a lo thleng thin.
- Damdawi thenkhat: A bik takin rilru lam natna damdawi thenkhat, lithium ang chi te.
- Urinary tract tihkhawtlai a ni.
- Thisenah calcium level a sang (Hypercalcemia).
- Thisena potassium level hniam (Hypokalemia).
Naupai laia thil thleng bik (special conditions) te
A tlem hle a, hmeichhiate hian naupai laiin hun eng emaw chen he natna hi an nei thei a ni. Hei hi naupai laiin nausen (placenta) atanga enzyme siam hian nu AVP hormone a tihchhiat vang a ni. Hetiang hlauhawmna hi nu pahnih, fapa mal neite tan leh preeclampsia ang chi natna nei, liver hnathawh tichhe thei nute tan a sang zawk a ni. Mahse thu lawmawm tak chu he natna hi nau a pai hnu kar hnih atanga kar thum chhungin a bo vek tlangpui.
Hei hian eng harsatna nge a thlen theih?
He natna hlauhawm ber leh harsatna lian ber chu dehydration , chu chu taksa hnathawh theihna tura tui leh electrolyte tling lo hloh tihna a ni.
A tlangpuiin, i zun i siam chhuah zat nena inmil tur tui inin i hloh chu i khum thei a ni. Mahse eng emaw chhan vanga tui i in theih loh chuan tui tlakchhamna nasa tak i nei nghal vat thei a ni.
Hei hi nunna atana hlauhawm tak a ni thei . I luak chhuak, i luak chhuak, i chau lutuk, i muhil a, chu chu tui tlakchhamna chhinchhiahna a nih chuan damdawi in hnai ber emergency room (ETU)-ah kal nghal rawh.
Engtin nge doctor hian hei hi a hmuh theih?
Natna dang tlanglawn tak tak, tuihal leh zun tam tak thlen thei a awm bawk. Entirnan, zunthlum natna (diabetes mellitus) te. Chuvang chuan Doctor-in a tih hmasak ber chu a ang chi natna dang a awm leh awm loh enfiah hi a ni.
He natna hi dik taka hriat theih nan test eng emaw zat an ti thin.
- Tui tlakchhamna Test: Hei hi he natna hi hriat theihna rintlak ber a ni. He test-ah hian darkar engemaw zat chhung chu tui engmah in lovin i kal a ngai a ni. Hei hi damdawi inah doctor emaw nurse emaw enkawlna hnuaiah direct-a tih a ni. Hei hi a chhan chu hei hian tui tlakchhamna a thlen thei a ni. Hetiang dinhmun hi i neih chuan tui i in lo chung pawhin i taksa chuan zun tam tak a siam chhunzawm zel ang. Mi hrisel takah chuan i zun chhuah a tlahniam ang a, zun dum dum, concentrated tlemte chauh i siam chhuak ang.
- Test dangte chu:
- Thisen sugar level enfiah (zunthlum i vei loh nan).
- Urinalysis - Zun concentration (osmolality) enfiah thin ang che.
- Thisen test - Copeptin an tih thil pakhat tehna, chu chu hormone AVP nena inzawm a ni.
- MRI scan - thluaka pituitary gland emaw hypothalamus emaw tihchhiat a awm leh awm loh en nan.
Hei hi eng enkawlna nge ni?
Enkawl dan tur chu AVP-D emaw AVP-R emaw i neih danah a innghat a, mahse enkawlna eng pawh ni se, tui tlem in hi a ngai a ni.
AVP-D dinhmun enkawl dan
Hei atan hian damdawi hman ber chu Desmopressin a ni . Hei hi synthetic hormone a ni a, AVP hormone bo thlak nan hna a thawk a ni. Pill emaw, hnar spray emaw, injection emaw angin ei theih a ni. Naupai laia hun eng emaw chen atana thil awmte tan pawh pek a ni bawk.
AVP-R dinhmun enkawl dan
Hei hi enkawl hi a buaithlak deuh. A chhan chu hetah hian buaina chu hormone tlakchham vang ni lovin, kal (kidney)-in a chhan loh vang zawk a ni. Chuvangin inenkawlna chi hrang hrang hman ho a ngai a ni.
- Thiazide diuretics: Hengte hi zun chhuah tipungtu damdawi chi khat ni mahse, hetiang dinhmunah hian hna an thawk dan a inang lo va, zun chhuah a ti tlem bawk.
- Nonsteroidal anti-inflammatory drugs (NSAIDs): Painkiller category-a damdawi thenkhat.
- Hetiang dinhmun hi damdawi dang i ei avanga lo awm a nih chuan i doctor chuan chu damdawi chu a thlak ang a, damdawi dang a pe ang.
Engvangin nge a hming hi ‘Diabetes Insipidus’ tih atanga ‘Diabetes Insipidus’ tia thlak a nih?
Hei hi mi tam takin harsatna an neih a ni. Hun rei tak chhung chu he natna hi Diabetes Insipidus an ti a. Mahse kum 2022 khan damdawi lam pawl lian eng emaw zat an inzawm khawm a, he hming hi thlak an tum ta a ni.
A chhan ber chu "Diabetes" tih thumal avanga buaina chhuak vang a ni. "Diabetes" tih hi Diabetes Mellitus tihna atan kan hmang tlangpui. Kan ramah hian natna tlanglawn tak a ni. Thisen sugar level a san vang a ni. Natna pahnihte hian tuihal leh zun tam lutuk chhinchhiahna inang nei mah se, hengte hi natna hrang hrang pahnih an ni . Enkawl dan pawh a danglam vek.
"Diabetes Insipidus" tih hming avang hian damlo thenkhat chu zunthlum vei nia hriat dik loh an ni a, enkawlna pawh a dik lo hle. He buaina hi tihbo nan tunah chuan "Arginine Vasopressin Disorder" tih hming hi he natna sawina atan hman a ni ta.
Hetiang dinhmun nen hian hlawhtling taka nun theih a ni em?
Ni e, a theih ngei ang. Hetiang dinhmun hi enkawlna dik tak i hmuh a, i doctor-in a tih angin tui i in tam chuan harsatna lian tham i nei lo tlangpui.
Mahse, pawl thenkhat chu an hlauhawmna a sang deuh hlek a ni:
- Nausen te te te
- Kum 65 chunglamte
- Rilru lama harsatna nei emaw, hmasawnna lama harsatna nei emaw
Heng mite hian chutih laia tuihal emaw, tui dil emaw an nih chuan hriat harsa an ti thei a, chu chuan tui tlakchhamna a thlen nasa zawk a ni.
Bathroom-a awm reng ang maia i inhriat a, eng ang pawhin in la, i tuihalna i ti reh thei lo a nih chuan, hei hi manageable condition a ni tih hre reng ang che. I doctor chuan i tana tha tur treatment plan a siam ang. Tin, tui tlakchham loh nan ni khata tui i in tur zat a hrilh bawk ang che. Chuvangin damdawi lam thurawn zawng hi hlau suh.
Take-Home Thuchah a ni
- Tuihal reng reng leh zun tam hi thil pangngai a ni lo. Heng symptoms te hi i neih chuan Doctor pan tur a ni.
- He natna (Arginine Vasopressin Disorder) hi kan hriat angin Diabetes Mellitus nen a inang lo. Hengte hi natna chi hrang hrang pahnih a ni.
- Hei hi kan thluak atanga hormone siam chhuah AVP an tih buai vang a ni. A siam chhuah tlem emaw, kal (kidney) pawhin a chhang lo emaw a ni thei.
- He natna complication ber leh hlauhawm ber chu dehydration a ni a, chuvangin tui in tam hi a pawimawh hle.
- Ngaihtuah buai suh, he natna hi enkawltu tur damdawi tha tak tak a awm.











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