I chau a, i chau fo em? Tlemte i kal chak emaw, stairs i chhoh emaw hian thawk harsa i ti em? I vun chu a hma aia a sen deuh niin i hria bawk. Hengte hi taksaa thisen tlakchhamna chhinchhiahna a ni thei a, chu chu damdawi lama thisen tlakchhamna (anemia) kan tih chu a ni. Mahse a chang chuan he thisen tlakchhamna thlentu hi kan ngaihtuah aiin natna buaithlak zawk leh hmuh tur awm lo zawk a ni thei. Vawiin hian chutiang natna tlemte, mahse thisen kaihhnawih pawimawh tak pakhat chungchang kan sawi dawn a ni. Chu chu Pure Red Cell Aplasia a ni a, a tawi zawngin PRCA kan ti a ni.
A awlsam zawngin, he PRCA hi eng nge ni?
Kan taksaa ruhro (bone marrow) hi thisen siamna factory angin han ngaihtuah teh. He factory hian kan taksa mamawh cell chi thum a siam chhuak a, chungte chu thisen sen, thisen var, leh platelet te an ni. Thisen sen (red blood cells) hnathawh ber chu kan thaw chhunga oxygen lo lut chu kan taksa chhunga cell dang zawng zawng hnena phurh luh hi a ni. Truck service hmanga oxygen pe chhuak ang mai a ni.
Tunah chuan PRCA-ah chuan thisen siamna factory, chu chu ruhro (bone marrow) chuan thisen sen (red blood cells) chauh siam chhuah chu nasa takin a tihtlem emaw, a titawp vek emaw a ni . Cell chi dang (thisen var leh platelet) siam chhuah hi a pangngaiin a thleng thin. Chuvangin taksaa oxygen phurtu thisen sen (red blood cells) a tlem chuan kan taksa peng hrang hrangte hian an mamawh oxygen an dawng lo. Hei atanga lo chhuak thisen tlakchhamna na tak hi PRCA harsatna ber a ni.
PRCA vei mi pakhatin eng symptom nge a neih theih ang?
PRCA hian thisen tlakchhamna na tak nen a lan chhuah dan inang a nei a, mahse thisen tlakchhamna pangngai aiin a na zawk thei. Heng symptoms te hi i hriat chian a pawimawh hle.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Chau | Eng anga mut pawh nise nunna nei lo leh chau reng anga inhriatna. |
| Thâwk harsa (Dyspnea) . | Hna tlemte thawh hnu emaw, hla vak lo kal hnu emaw pawha thawk harsa tih hriat. |
| Luak chhuak thei | Lung hahna, a bik takin thut atanga tho chhuah. |
| Vun dum (pale skin) a ni | Vun, hmui leh nail hnuai lam chu a tlangpui aia var a lo ni ta a ni. |
| Lu na fo thin | Lu na fo hi thluaka oxygen mamawh tlem vang a ni. |
| Beng chhunga ri ri hriat (Pulsatile tinnitus) . | Thinlung thawk ri ang zelin beng chhungah hian whistling sound a ri a. |
| A rilru natna (Angina) . | Heart muscles-a oxygen tlakchham vangin rilru natna a awm. |
A pawimawh ber chu, heng symptoms pakhat emaw a aia tam emaw i neih chuan hlauthawng suh la, PRCA ah ngai suh. Chungte chu thisen tlakchhamna pangngaiah pawh hmuh theih a ni. Mahse heng symptoms te hi a la awm reng a nih chuan doctor pan a, thurawn lak hi a tha ber ngei ang .
Engvangin nge hetiang dinhmun hi PRCA an tih hi a lo awm?
PRCA hi natna pakhat chauh a ni lo. A chhan awm thei engemaw zat a awm. A châng chuan damdawi lam thil dang avanga side effect a ni thei bawk.
1. Immune system lama harsatna (Autoimmune Diseases) .
Hei hi PRCA thlentu ber a ni. A awlsam zawngin kan taksa invenna system, immune system hian kan ruhro chhunga stem cells, thisen sen siamtute chu a rawn bei sual tan ta a ni. Chutiang dinhmun entirnan:
- Lupus natna (Systemic Lupus Erythematosus) natna hi a awm lo.
- Rheumatoid Arthritis natna a ni
- Inflammatory Bowel Dise natna a awm thei
2. Cancer natna a ni
Cancer chi thenkhat chuan PRCA a thlen thei bawk.
- Thisen kaihhnawih cancer: Chronic Lymphocytic Leukemia (CLL) leh Large Granular Lymphocytic Leukemia (LGL) te hi thisen cancer chi hnih, hemi nena inzawm ber an ni.
- Tumors: Thymoma, thymus gland cancer hi PRCA nena inzawm cancer natna lian ber a ni.
3. Viral leh bacteria infection
Hri kai thenkhat pawh hian PRCA a thlen thei a, hun eng emaw chen emaw, a awm reng emaw pawh a ni thei.
- Virus: Heng zingah hian Parvovirus B19 hi hriat lar ber a ni. He virus hian ruhro chhunga cell, thisen sen (red blood cells) lo ni tur te chu direct-in a bei a. HIV, Epstein-Barr virus, leh hepatitis virus te pawhin a thlen thei bawk.
- Bacteria: Group C Streptococcus, Tuberculosis, leh Bacterial Sepsis ang chi natna te pawhin hetiang hi a thlen thei bawk.
4. Damdawi thenkhat
PRCA hi damdawi thenkhat side effect angin a awm thei bawk. Entirnan, Erythrocyte-Stimulating Agents (ESAs) hi thisen zam (red blood cells) siam chhuah tipung tura kal damlote hnena pek thin damdawi te hian a chang chuan he natna hi a thlen thei a ni.
5. Naupai lai
A tlem hle a, hmeichhe thenkhat chuan naupai laiin PRCA an nei thei. Vanneihthlak takin naute a pian hnuah a natna hi a reh mai thin.
6. Pian tirh atanga awm thin genetic conditions
Diamond-Blackfan Anemia hi pianpui thisen tlakchhamna awm lo tak a ni. Naupan lai atanga hmuhchhuah a ni tlangpui. Heng damlote hian PRCA an nei thei bawk.
Engtin nge doctor-te hian he natna hi dik taka an hriat theih?
A hmaa kan sawi tawh ang chi symptoms neia doctor i pan chuan a enfiah ang che a, he natna hi a rinhlelh chuan test eng emaw zat nei turin a refer ang che.
| Fiahna | Hetah hian eng nge i hmuh? |
|---|---|
| Thisen chhiar kim (CBC) 1.1. | Thisenah hian red blood cell count a tlem hle em tih an enfiah a, white blood cell leh platelet count pawh a normal em tih an enfiah bawk. |
| Reticulocyte chhiar zat | Hei hian thisen sen thar, puitling lo tak takte a kawk a ni. PRCA-ah chuan he zat hi a tlem hle. Chumi awmzia chu red cell thar siam a ni lo tihna a ni. |
| Peripheral Blood Smear hmanga tihfai a ni | Thisen tla khat lak a, microscope hmanga enfiah a, thisen sen (red blood cells) pianzia leh awm dan enfiah a ni. |
| Bone Marrow Aspiration/Biopsy hmanga tih a ni | Hei hi natna finfiahna atana test ber a ni . Anesthesia pek hnuah hip ang chi hmun atang hian bone marrow sample tlemte tak tak lak a ni. PRCA-ah chuan thisen sen siamtu stem cells chu a chhungah hmuh tur a awm lo. |
| Test dang pawh a awm | He natna thlentu hriat chian nan Parvovirus B19 virus test leh CT scan (Thymoma ang chi lumps awm leh awm loh enfiah nan) te pawh tih theih a ni. |
PRCA enkawlna tur hi engte nge ni?
PRCA enkawl dan hi natna thlentuah a innghat a ni. Chumi awmzia chu mi zawng zawng hi enkawl dan inang vek an ni lo tihna a ni. Doctor chuan i dinhmun chu uluk takin a zirchiang ang a, a enkawl dan tur dik ber a thlang ang.
- Immunosuppressants: Natna thlentu chu immune system lama harsatna a nih chuan heng damdawi te hian overactive immune system control turin hna an thawk a ni. Hemi atan hian Corticosteroids Prednisone leh Cyclosporine te hi hman a ni tlangpui.
- Thisen pek: Thisen tlakchhamna a nasat em avangin pawn lam atanga thisen pek a ni a, chu chuan thisen level a siam that leh thuai thin. Mahse, thisen pek chhunzawm zel chuan taksaa iron level chu a tul lovah a tipung thei a ni. Chutiang a nih chuan iron tam lutuk chu paih chhuah nan enkawlna hran (chelation therapy) a ngai dawn a ni.
- Surgery: Natna thlentu chu thymoma a nih chuan a enkawl dan tur chu surgery hmanga gland lakchhuah (Thymectomy) a ni.
- Immunoglobulin Therapy: PRCA hi parvovirus B19 infection avanga lo awm a nih chuan he enkawlna hian virus hi a do a, thisen sen (red blood cells) a tihchhiat loh nan a titawp a ni.
- Stem Cell thlak danglam dan:Diamond-Blackfan Anemia ang chi pianpui natna vei tan chuan enkawlnaah hian ruh natna nei thlak nan stem cell hrisel tak tak dah a ni.
Enkawlna hian side effect a nei em?
Ni e, enkawlna dang ang bawkin a side effect pawh a awm thei. Mahse, an ngaihtuah buai a ngai lo. I doctor chuan enkawl tan hmain heng zawng zawng hi a hriattir ang che. Side effects enkawl dan tur thurawn tul tak tak a pe bawk ang che.
Entirnan, immunosuppressant damdawi hian natna hrik i kai theihna a tipung thei a, i thisen sang a tisang thei a, i rihna a tisang thei bawk. Thisen pek hian khawsik leh allergy a thlen thei a ni. Chuvangin inenkawl lai hian i taksa a inthlak danglam dan hi ngun taka ngaihven a pawimawh hle.
PRCA nena i awm hian eng nge i hriat tur?
PRCA hi a chang chuan natna khirh tak a ni thei bawk. Chumi awmzia chu enkawl hnuah pawh a chang chuan natna hi a lo awm leh thei tihna a ni. Chuvangin damdawi lam enkawlna hnuaia awm reng a pawimawh hle.
- Maintenance Therapy: Mi thenkhat chuan natna lo kir leh tawh lo turin immunosuppressant damdawi hi a tlem berah an ei chhunzawm a ngai mai thei.
- Continuous Follow-up: Doctor hmuh hunbi neia i thisen test tir hi a pawimawh hle. Hei hian natna hi a lo lang leh dawn em tih emaw, harsatna dang a nei dawn em tih emaw hriat hmasak nan a pui thei che a ni.
- Nunphung hrisel: 1.1.
- Nutritious diet: Ei leh in inthlau tak ei a pawimawh a, chutah chuan iron tamna ei tur (spinach, sa, peas, lentils) te pawh a tel. I doctor hnenah i tana tha tur ei leh in chungchang zawt rawh.
- Tui in tam: Taksa tui tlakchhamna tur venna.
- Infection laka invenna: Kut sil fo thin ang che. Mipui tamna hmunah fimkhur rawh. Vaccine tul tak tak la rawh.
- Exercise: I taksain a tuar theih tur level-ah exercise la. Tin, hemi chungchangah hian doctor rawn hmasa phawt ang che.
PRCA chungchang i hriat chuan i hlauthawng mai thei. Chu chu thil pangngai a ni. Mahse, enkawl theih a ni tih hre reng ang che. A pawimawh ber chu damdawi lam thurawn la vat a, a enkawl dan dik taka zawm a, a natna lan chhuah dan ngaihthah lovin.
Take-Home Thuchah a ni
- PRCA hi thisen natna hmuh tur awm lo tak a ni a, ruhro hian thisen sen (red blood cells) a siam chhuak thei lo.
- A chhinchhiahna ber chu hah reng, vun rawng hring, leh thawk harsatna te hi a ni.
- Hei hi immune system lama harsatna, cancer, infection, leh damdawi thenkhat avanga lo awm thei a ni.
- Natna finfiah nan test ber chu bone marrow biopsy a ni.
- Enkawl dan hi natna thlentu azirin a inang lo va, enkawlna hian natna lan chhuah dan a thunun thei a ni.
- Hei hi a chang chuan a lo thleng leh thei a, chuvang chuan hun rei tak chhung damdawi lam enkawl leh checkup reng reng hi a pawimawh hle.
- Anemia ang chi symptom i neih chhunzawm zel chuan hlauthawng suh la, doctor pan nghal rawh.
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