Nu ni tur i nih emaw, member thar i chhungte zawm tura beisei emaw i nih chuan he thawnthu hi i tan a pawimawh hle ang. A châng chuan kan naupang tête hi kan hriat ngai loh piansualna neiin he khawvelah hian an lo kal thei a ni. Chu chu vawiin a kan sawi tur dinhmun zinga mi a ni a, a buaithlak deuh a, mahse hriat hlawh tak a ni.
CDH chu eng nge ni? A awlsam zawngin i hrethiam ang u.
Okay, tunah chuan he `(Congenital Diaphragmatic Hernia)` emaw `(CDH)` hi a tawi zawngin eng nge a nih i en ang u. A awlsam zawngin sawi ila, hei hi pian tirh atanga lo awm thin dinhmun a ni. Hei hi naute pum chhunga a la awm laiin a thleng thin. Kan rilru leh kan pum inthenna ruh pakhat a awm a, chu chu `Diaphragm` kan ti a ni. Pindan pahnih inthenna kulh ang a ni. He diaphragm hi a chak tawk lo a nih chuan, a chhungah khur a awm chuan pum chhunga taksa peng hrang hrang – chu chu pum, intestines, liver, etc. – te chu chest cavity ah an lut thei a ni. Chu chu `(Hernia)`, a nih loh leh hernia kan tih chu a ni.
Tûnah chuan nausen pum chhûnga a lo seilian lai hian hetiang thil hi lo thleng ta se eng nge thleng ang tih han ngaihtuah teh. Pum chhunga taksa peng hrang hrangte chu rilru chhunga an kal chuan chutah chuan hmun a awm tawk lo a ni lawm ni? Buaina ber chu lungin a thang tha thei tur khawpa hmun a neih loh vang a ni. Lung a te deuh chuan, chu chu `(Pulmonary Hypoplasia)` an tih natna a lo awm chuan naute chu a pian hnuah thawk a harsat a, thisen hian oxygen a hmu tlem hle. Chu mai ni lovin, lung chhunga thisen sang pawh a sang thei hle. Hei hian thinlungah pressure nasa tak a siam bawk. Chuvangin, naute `(CDH)` vei chuan a pian hnu lawkah specialized medical treatment a mamawh a ni.
Naute CDH vei hian eng symptoms nge a neih?
I naute hian a pian hnu lawka thawk harsatna nasa tak a neih chuan a natna (CDH) chhinchhiahna lian tak a ni thei. Chu bâkah, hetiang thilte pawh i hmu thei bawk:
- Lung na tak tak (Tachycardia) a ni.
- Cyanosis chu oxygen tlakchham vanga vun rawng dum (bluish discoloration) a ni.
- Thâwk ri hniam tak tak (a bik takin a sir khatah).
- I beng chu i rilruah i dah chuan intestine thawm hriat.
- A rilru chu a bulge chhuak a, barrel ang maiin a lang a, chutih laiin pum chu a pil lut ang maiin a lang.
I naute hian heng symptoms pakhat emaw a aia tam emaw a neih chuan doctor pan nghal a tha ber.
Engvangin nge he CDH hi a lo awm? A chhante chu engte nge ni?
A nihna takah chuan doctor-te tan chuan he ``(CDH)`` natna thlen chhan dik tak hi eng nge ni tih chiang taka sawi a harsa hle. Mahse, zirchianna chuan a hnuaia thilte hi a inrawlh thei tih hmuhchhuah a ni:
- Genetic factors: Chu chu thil thenkhat, thlah kal zelah an lo inthleng thin tihna a ni.
- Naupai laiin thil tha lo tak tak nena inzawmna: Chemical thenkhat leh cigarette ang chi thil.
- Nausen tana ei tur tha tawk lo: Naute hian a nu ei tur a\angin a ei tur a hmu \hin.
Hengte hi tuna a chhan awmte chu a ni a, mahse hemi chungchangah hian zirchianna dang neih belh zel a ni.
CDH vang hian eng harsatna nge thleng thei?
Kan sawi tawh ang khan CDH vei naute tam tak chu an lung (Pulmonary Hypoplasia) an nei tha lo hle. Hei hian harsatna chi hrang hrang a thlen thei a ni:
- Thisena oxygen level hniam (Hypoxemia): Hei hian naute taksa peng zawng zawng, a bik takin thluak leh thinlung a nghawng a ni. Hetiang dinhmun hi a nasat emaw, a awm reng emaw chuan hun rei tak chhung chhiatna a thlen thei a ni.
- Lung kawng (arteries)-a thisen sang (Pulmonary Hypertension): Hei hian thinlung dinglam lamah harsatna nasa tak a siam a, thinlung a tichhe thei hial a ni.
- Lung Infection: Lung tha lo taka lo thanglian chuan awlsam takin Pneumonia ang chi infection a nei thei a. Hernia chu operation hmanga siamthat a nih hnuah pawh heng natna hrik kai theihna hi dam chhung zawngin a awm thei a ni.
Hei bakah hian naute `(CDH)` vei te hian harsatna dang an nei thei a ni:
- Chaw pek harsatna: Hei hi pum chhunga taksa peng hrang hrangte pressure vang emaw, nau neih laiin damdawi lam hmalakna tam tak vang emaw pawh a ni thei. Naute thenkhat chu hun rei tak chhung tube-a pek an ngai thei a, an thanlenna pawh a tlahniam thei bawk.
- Developmental Delays: Naute thenkhat chu oxygen tlakchham vangin hun engemaw chen chu taksa, tawng emaw hnathawhna lama therapy an mamawh thei.
- Sensorineural Hearing Loss: CDH vei naute thenkhat chuan an hriatna an hloh zauh zauh thin. Scientist-te chuan hei hi a natna avanga lo awm nge a nih tih an la chiang lo.
Nu emaw, pa emaw chuan hetiang thil a hriat hian eng ang phurrit nge a neih ang tih han ngaihtuah teh. Mahse, tunah chuan medical science hi a hmasawn hle tih hre reng ang che.
Doctor-te hian engtin nge CDH hi an hriat theih?
A tam zawkah chuan doctor-te chuan i naupai laiin nau neih hmaa ultrasound scan pangngai (routine prenatal ultrasound scan) an tih hian he natna hi an hmu thei a ni. An hmuhchhuah veleh test dang an nei leh dawn a ni. Entirnan, nausen MRI an ti ang a, hernia chu chiang zawkin an en ang. Nausen thinlungah nghawng a nei em tih enfiah turin nausen echocardiogram an ti bawk ang.
A châng chuan, naute pian hnuah chauh doctor-te chuan CDH hi an hre lo mai thei. Naute a pian hnuah, medical team-te chuan thawk harsa, septum deviated, emaw, rilru bulging emaw ang chi thil an hmuh chuan an ringhlel mai thei. Chumi hnuah chuan chest X-ray leh echocardiogram an ti ang . Naute thisen oxygen level enfiah nan leh genetic abnormalities dang enfiah nan thisen sample an la thei bawk .
A tlem hle a, naute CDH vei te hian an pian tirh hian symptom lian tham an nei lo thei. Hernia hi a te lutuk a nih chuan naupan lai, puitling thleng pawhin hriat theih a ni lo.
CDH enkawl dan tur chu engte nge ni?
He natna, ``Congenital Diaphragmatic Hernia'' hi enkawl a nih veleh enkawl tan a ni. He enkawlna chungchang i hriat hian i hlauthawng mai thei a, mahse doctor-te hian i naute venhim nan engkim an ti tih hre reng ang che.
Nau neih hmaa enkawlna
I naupai laiin CDH i vei tih hmuhchhuah a nih chuan i doctor chuan uluk takin a lo en reng ang che. Organ system dangte harsatna a awm leh awm loh an enfiah ang a, a châng chuan dinhmun khirh zawka tel ve thei a nih avangin. I naute chu a pian hma (premature labor) a nih leh nih loh an enfiah bawk ang a, chutiang a nih chuan naute hriselna atana pui turin nau neih tir (induce labor) nge tih pawh an rel ang.
Thil bik thenkhatah chuan nausen pian hmain medical team hian nausen chu an enkawl thei a ni. ``Fetoscopic Tracheal Occlusion (FETO)`` hi chutiang nausen surgery pakhat a ni. Nausen pum chhunga nausen chu a lo seilian chhoh zel chuan nausen lung lian leh te hnathawh thatna atan a pui a ni. Hei hi camera te tak te ``Fetoscopy`` tih hmanga tih a ni a, i vun kaltlangin i nausen pum chhunga incision te te siam hmangin tih a ni.
He `(FETO)` tih danah hian doctor chuan nausen `(Trachea)` chhungah balloon te tak te a thun a. Tichuan, nautein a ei `(Amniotic Fluid)` chu balloon hnung lamah leh lung chhungah a khawlkhawm a, chu chuan lung chu a ti hring chhuak ta a ni. He inflating hian lungte than leh hnathawh a tichak a, `(CDH)` avanga chhiatna thenkhat siamthatna atan a pui bawk.
Nausen piang thar enkawlna
CDH vei naute piangte hian an pian hnu lawkah specialist team atanga intensive care an mamawh tlangpui. Naute lung a lo thang kim lo (Pulmonary Hypoplasia) chuan oxygen support pek hmasak tur a ni. Naute ṭhenkhat tan chuan hei hi mechanical ventilator nena inzawm thawkna tube a ni thei .
Naute ṭhenkhat chuan nunna atana ṭanpuina nasa zawk an mamawh mai thei. Hei hi Extracorporeal Membrane Oxygenation (ECMO) tih a ni. Hei hian naute lung puitling lo leh a chang chuan thinlung chu bypass a, machine hmanga thisenah oxygen dah belh a, naute taksaa thawn kir leh a huam a ni.
A dawtah chuan naute chu operation a ngai dawn a ni. Naute hi Neonatal Intensive Care Unit (NICU)-ah dah a ni ang a, naute chu zai theihna tur khawpa a dinhmun a ṭhat hma chu dah a ni ang. Hei hian a tlangpuiin lung chhunga thisen sang (pulmonary hypertension) a reh a, extracorporeal membrane oxygenation (ECMO) a mamawh tawh loh hma loh chuan a kawk a ni.
Surgery atan hian Pediatric Anesthesiologist chuan naute chu anesthesia hnuaiah a muthilh tir ang . Tichuan Pediatric Surgeon pakhatin a surgery chu a ti ang.Surgery-ah hian rilru atanga taksa peng sawn chhuah tawhte chu pum chhungah sawn lehin, diaphragm-a chhiatna awm chu siamthat a ni. A tam zawkah chuan, chu chu operation zawng zawng zinga a chanve vel a ni a, doctor-te chuan minimally invasive surgery (MIS) an ti thei a, chutah chuan incision lian tak ni lovin millimeter 3 vel zeta sei te te an siam thei a ni
Recovery time hi eng ang nge ni?
I naute chu operation aṭanga a dam leh chuan zawi zawiin oxygen i la chhuak ang. Thâwk chhuahna tube chu lak chhuah a nih hma loh chuan tube hmangin i chawm chhunzawm ang. Chumi hnuah chuan speech therapist leh lactation specialist te chuan nang leh i naute chu ka atanga chaw pek tan tir turin an pui ang che. Naute thenkhat chuan oxygen leh tube feeding te chu midang aiin an hnute pek chhuah loh nan hun an hmang rei zawk. I medical team chuan a tul chhung chu an thlawp ang che.
CDH vei naute hmalam hun chu eng nge ni?
Thu lawmawm tak chu CDH vei nausen piangte damchhuahna rate chu nasa takin a lo tha chho ta a ni. Naute 10 zinga 7 leh 9 inkar an dam. Heng naute hi natna khirh tak tak neia piang ni mahse, ni hmasa ber an paltlang chuan an dam theihna chance a sang zawk hle. Naupang thenkhat chuan hun rei tak chhung harsatna an nei thei a, mahse dam rei tak, famkim an dam thei bawk. Medical science lama hmasawnna avang hian hun rei lote chhunga damchhuah zat leh hun rei tak chhunga hriselna lama hlawhtlinna pawh nitin a tha chho zel a ni.
Hun rei tak chhunga hmalam hun tur chu thil engemaw zatah a innghat a:
- Naute chu a hun hmaa piang a ni em?
- Naute pian tirh khan a dinhmun a va chhe em em.
- Hernia lian tham tak a ni.
- Eng organ nge rilru chhungah lut tawh?
- Hriselna lama harsatna dang a awm em?
Nausen hun rei tak thawk emaw, ei leh in lama tanpuina mamawh te chu harsatna kal zel, lung natna rei tak, an than chak lohna, hriatna hloh, leh an thanlenna tlai te ang chi te an vei theihna a sang zawk a ni. I fa doctor chuan an kum hmasa zawng zawngah uluk takin a enkawl ang.
I naute hian congenital diaphragmatic hernia a nei tih hriat chu a hlauhawm hle thei a, a buaithlak hle bawk. I naute chu a pian hnu lawkah intensive care unit (ICU)-ah hruai a ni ang a, damdawi ina rei tak a awm a ngai pawh a ni thei. Mahse medical science lama hmasawnna a awm avangin he natna thlirna hi a hma aia tha zawkin a awm ta a ni. Hei hi hun harsa tak ni mahse, hetah hian nang leh i nau piang thar tanpui turin doctor leh nurse team an awm a ni. Diagnosis a nih atang khan, i naute naupan lai zawng zawngah an thlawp ang che.
Kan hriat reng tur thilte
He natna ``Congenital Diaphragmatic Hernia - CDH'' an tih hi a na deuh viau nachungin, i hriat lawk chuan hlauthawng lovin i hmachhawn thei a ni.
- CDH hi pian tirh atanga lo awm a ni a, diaphragm-a chhiatna a awm avangin pum chhunga taksa peng hrang hrangte chu rilru chhungah a kal lut thin.
- Hei hian lung hmasawnna a nghawng ber a ni.
- Hei hi naupai laiin scan hmangin hriat theih a ni.
- An pian hnu lawkah specialized treatment leh surgery an mamawh nghal a ni.
- Damdawi lam thiamna lama hmasawnna a awm avangin heng nausen tam zawkte hian nun tha tak an hmang thei a ni.
Hemi chungchangah hian zawhna leh ngaihtuahna dang i neih chuan i doctor emaw nurse emaw nen inbia ngei ang che. Thu belhchian dawl zawk an pe thei che a, i rilru atanga lungkhamna awm chu paih bo turin an pui thei bawk che a ni. Nangmah chauh i ni lo tih hre reng ang che.
` CDH, Congenital Diaphragmatic Hernia, Diaphragmatic hernia, Nau piangsual, Lung than chhoh dan, Naute hriselna, Surgery











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